Skip to content

Migrate ncit

NCIT

Interactive FlatGithub table

Migratable terms

mondo_id mondo_label xref xref_source original_label definition parents
ID LABEL A oboInOwl:hasDbXref >A oboInOwl:source SPLIT= A IAO:0000115
MONDO:0853241 primary central nervous system neoplasm NCIT:C102871 MONDO:equivalentTo Primary Central Nervous System Neoplasm A benign or malignant neoplasm that arises from the brain or the spinal cord. MONDO:0006130
MONDO:0853254 adrenal cortical carcinoma by ensat stage NCIT:C104030 MONDO:equivalentTo Adrenal Cortical Carcinoma by ENSAT Stage A term that refers to the staging of adrenal cortical carcinoma according to the European Network for the Study of Adrenal Tumors (ENSAT). MONDO:0006639
MONDO:0853255 ovarian high grade serous adenocarcinoma NCIT:C105555 MONDO:equivalentTo Ovarian High Grade Serous Adenocarcinoma A rapidly growing serous adenocarcinoma that arises from the ovary. It is characterized by the presence of high grade cytologic features and frequent mitotic figures. MONDO:0005211
MONDO:0853256 ovarian low grade serous adenocarcinoma NCIT:C105556 MONDO:equivalentTo Ovarian Low Grade Serous Adenocarcinoma A slow-growing serous adenocarcinoma that arises from the ovary. It usually originates from borderline neoplastic processes or adenofibromas. It is characterized by the presence of low grade cytologic features and infrequent mitotic figures. MONDO:0005211
MONDO:0853260 uveal melanoma by gene expression profile NCIT:C111030 MONDO:equivalentTo Uveal Melanoma by Gene Expression Profile MONDO:0006486
MONDO:0853262 glioblastoma by gene expression profile NCIT:C111691 MONDO:equivalentTo Glioblastoma by Gene Expression Profile Classification of glioblastoma into molecular subtypes as defined by gene expression profiling. MONDO:0018177
MONDO:0853267 thymoma by masaoka-koga stage NCIT:C112006 MONDO:equivalentTo Thymoma by Masaoka-Koga Stage A staging system for thymoma based on the anatomic extent of disease at the time of surgery. MONDO:0006456
MONDO:0853279 uterine carcinosarcoma, homologous type NCIT:C113238 MONDO:equivalentTo Uterine Carcinosarcoma, Homologous Type A carcinosarcoma of the uterus characterized by the presence of sarcomatous elements that arise from the tissues of the uterus. MONDO:0006485
MONDO:0853280 uterine carcinosarcoma, heterologous type NCIT:C113239 MONDO:equivalentTo Uterine Carcinosarcoma, Heterologous Type A carcinosarcoma of the uterus characterized by the presence of sarcomatous elements composed of tissues that are not found in the uterus (e.g., bone, cartilage, skeletal muscle). MONDO:0006485
MONDO:0853284 main duct pancreatic intraductal papillary-mucinous neoplasm NCIT:C113664 MONDO:equivalentTo Main Duct Pancreatic Intraductal Papillary-Mucinous Neoplasm An intraductal papillary-mucinous neoplasm of the pancreas that arises from the main pancreatic duct. MONDO:0004286
MONDO:0853285 branch duct pancreatic intraductal papillary-mucinous neoplasm NCIT:C113665 MONDO:equivalentTo Branch Duct Pancreatic Intraductal Papillary-Mucinous Neoplasm An intraductal papillary-mucinous neoplasm of the pancreas that arises in one of the branches of the main pancreatic duct. It usually has an indolent behavior. MONDO:0004286
MONDO:0853286 mixed type pancreatic intraductal papillary-mucinous neoplasm NCIT:C113667 MONDO:equivalentTo Mixed Type Pancreatic Intraductal Papillary-Mucinous Neoplasm An intraductal papillary-mucinous neoplasm of the pancreas that arises primarily from the main pancreatic duct and extends to the branch ducts. MONDO:0004286
MONDO:0853303 adult undifferentiated high grade pleomorphic sarcoma of bone NCIT:C114782 MONDO:equivalentTo Adult Undifferentiated High Grade Pleomorphic Sarcoma of Bone An undifferentiated high grade pleomorphic sarcoma that arises from the bone and occurs during adulthood. MONDO:0002618
MONDO:0853306 metastatic malignant neoplasm in the soft tissues NCIT:C114831 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Soft Tissues A malignant neoplasm that has spread to the soft tissues from another anatomic site. MONDO:0024880
MONDO:0853313 adult epithelioid hemangioendothelioma NCIT:C114923 MONDO:equivalentTo Adult Epithelioid Hemangioendothelioma An epithelioid hemangioendothelioma that occurs during adulthood. MONDO:0015523
MONDO:0853316 central nervous system hodgkin lymphoma NCIT:C114951 MONDO:equivalentTo Central Nervous System Hodgkin Lymphoma A Hodgkin lymphoma that arises from the central nervous system. MONDO:0004952
MONDO:0853326 adult fibrolamellar carcinoma NCIT:C114992 MONDO:equivalentTo Adult Fibrolamellar Carcinoma Fibrolamellar variant of hepatocellular carcinoma that occurs during adulthood. MONDO:0016216
MONDO:0853331 hepatocellular carcinoma by bclc stage NCIT:C115132 MONDO:equivalentTo Hepatocellular Carcinoma by BCLC Stage A staging classification system for hepatocellular carcinoma that uses variables related to tumor stage, liver functional status, physical status, and cancer-related symptoms, and links the stages with a treatment algorithm. (HPB (Oxford) 2005; 7(1):35-41) MONDO:0007256
MONDO:0853337 adult myelodysplastic syndrome NCIT:C115153 MONDO:equivalentTo Adult Myelodysplastic Syndrome Myelodysplastic syndrome that occurs in adulthood. MONDO:0018881
MONDO:0853343 distal urethral carcinoma NCIT:C115210 MONDO:equivalentTo Distal Urethral Carcinoma A carcinoma that arises from the distal part of the urethra. MONDO:0021327
MONDO:0853344 familial testicular germ cell tumor NCIT:C115211 MONDO:equivalentTo Familial Testicular Germ Cell Tumor Germ cell tumor that arises from the testis and is diagnosed in at least two relatives. MONDO:0010108
MONDO:0853348 proximal urethral carcinoma NCIT:C115334 MONDO:equivalentTo Proximal Urethral Carcinoma A carcinoma that arises from the proximal part of the urethra. MONDO:0021327
MONDO:0853359 invasive bladder urothelial carcinoma associated with urethral carcinoma NCIT:C115966 MONDO:equivalentTo Invasive Bladder Urothelial Carcinoma Associated with Urethral Carcinoma Invasive urothelial carcinoma of the bladder which is associated with the presence of in situ or infiltrating urethral carcinoma. MONDO:0040678
MONDO:0853386 congenital cystic hygroma NCIT:C116899 MONDO:equivalentTo Congenital Cystic Hygroma A congenital lymphatic malformation usually arising from the neck and characterized by cystic dilation of the lymphatic vessels. MONDO:0009761
MONDO:0853405 anaplastic plasmacytoma NCIT:C118421 MONDO:equivalentTo Anaplastic Plasmacytoma A plasmacytoma characterized by the presence of malignant plasma cells with anaplastic features. MONDO:0005615
MONDO:0853427 adult penile carcinoma NCIT:C118820 MONDO:equivalentTo Adult Penile Carcinoma A carcinoma of the penis that occurs during adulthood. MONDO:0006360
MONDO:0853431 adult salivary gland carcinoma NCIT:C118825 MONDO:equivalentTo Adult Salivary Gland Carcinoma A carcinoma of the salivary gland that occurs during adulthood. MONDO:0000521
MONDO:0853434 orbital melanoma NCIT:C118828 MONDO:equivalentTo Orbital Melanoma A melanoma that arises from the structures of the orbit. MONDO:0002889
MONDO:0853464 malignant kidney neoplasm except pelvis NCIT:C120456 MONDO:equivalentTo Malignant Kidney Neoplasm Except Pelvis A malignant neoplasm that affects the renal parenchyma but not the pelvis. MONDO:0002367
MONDO:0853467 mammary-type myofibroblastoma NCIT:C121181 MONDO:equivalentTo Mammary-Type Myofibroblastoma A benign mesenchymal neoplasm characterized by the presence of spindle shaped myofibroblasts and mast cells in a collagenous stroma. It is histologically identical to the myofibroblastoma of breast. It usually arises from the subcutaneous tissue and the most common sites of involvement are the inguinal/groin, paratesticular, and vulvovaginal areas. MONDO:0040675
MONDO:0853473 leiomyosarcoma of deep soft tissue NCIT:C121571 MONDO:equivalentTo Leiomyosarcoma of Deep Soft Tissue A rare leiomyosarcoma that arises from the deep soft tissue in the retroperitoneum or abdominal cavity. MONDO:0018078
MONDO:0853476 spindle cell/sclerosing rhabdomyosarcoma NCIT:C121654 MONDO:equivalentTo Spindle Cell/Sclerosing Rhabdomyosarcoma An uncommon variant of rhabdomyosarcoma with spindle cell or sclerosing morphology. It affects both children and adults and it is more common in males. MONDO:0005212
MONDO:0853478 soft tissue angiosarcoma NCIT:C121671 MONDO:equivalentTo Soft Tissue Angiosarcoma An angiosarcoma that arises from the soft tissues, usually in the deep muscles of the lower extremities, retroperitoneum, mediastinum, and mesentery. MONDO:0018078
MONDO:0853479 conventional schwannoma NCIT:C121677 MONDO:equivalentTo Conventional Schwannoma A common, usually encapsulated benign nerve sheath tumor composed of well-differentiated Schwann cells. MONDO:0002546
MONDO:0853481 solitary circumscribed neuroma NCIT:C121681 MONDO:equivalentTo Solitary Circumscribed Neuroma A benign peripheral nerve sheath tumor characterized by the presence of Schwann cells, axons, and perineurial fibroblasts. It usually arises from the skin of the head and neck or the oral mucosa. It presents as a solitary and painless nodular mass. MONDO:0002547
MONDO:0853483 hybrid nerve sheath tumor NCIT:C121686 MONDO:equivalentTo Hybrid Nerve Sheath Tumor A benign nerve sheath tumor characterized by the combination of histologic features seen in schwannomas, neurofibromas, and perineuriomas. MONDO:0002547
MONDO:0853491 malignant mixed tumor, not otherwise specified NCIT:C121787 MONDO:equivalentTo Malignant Mixed Tumor, Not Otherwise Specified A malignant myoepithelioma characterized by the presence of a minor ductal component. MONDO:0003158
MONDO:0853492 benign phosphaturic mesenchymal tumor NCIT:C121788 MONDO:equivalentTo Benign Phosphaturic Mesenchymal Tumor A phosphaturic mesenchymal tumor with benign histologic features. It may recur locally but does not metastasize. Complete excision is curative. MONDO:0006368
MONDO:0853493 malignant phosphaturic mesenchymal tumor NCIT:C121789 MONDO:equivalentTo Malignant Phosphaturic Mesenchymal Tumor A phosphaturic mesenchymal tumor characterized by the presence of nuclear atypia, high mitotic activity, increased cellularity, marked pleomorphism, and necrosis. It usually develops in lesions that have recurred locally and metastasizes to other sites. MONDO:0006368
MONDO:0853494 sclerosing pecoma NCIT:C121790 MONDO:equivalentTo Sclerosing PEComa A tumor with perivascular epithelioid cell differentiation characterized by the presence of cords of neoplastic cells in a densely collagenous stroma. MONDO:0006359
MONDO:0853495 undifferentiated soft tissue sarcoma NCIT:C121793 MONDO:equivalentTo Undifferentiated Soft Tissue Sarcoma A term that refers to a heterogeneous group of uncommon soft tissue sarcomas that do not show an identifiable line of differentiation using currently available technologies. This is a diagnosis of exclusion and includes undifferentiated pleomorphic sarcoma (also known as malignant fibrous histiocytoma), undifferentiated spindle cell sarcoma, undifferentiated round cell sarcoma, and undifferentiated epithelioid sarcoma. MONDO:0018078
MONDO:0853498 osteochondromyxoma NCIT:C121842 MONDO:equivalentTo Osteochondromyxoma A rare benign chondroid and osteoid matrix-producing neoplasm of bone characterized by extensive myxoid changes. It may be a locally destructive neoplasm and has been reported in patients with Carney complex. MONDO:0000631
MONDO:0853499 subungual exostosis NCIT:C121844 MONDO:equivalentTo Subungual Exostosis A benign tumor that affects the distal phalanx, most often the great toe. Grossly it consists of a cartilage cap and a bony stalk. Microscopically it is characterized by an osteochondromatous proliferation with a gradual transition of a peripheral spindle-cell proliferation to hyaline cartilage to trabecular bone. Pain and swelling are present. Simple resection is usually curative. MONDO:0024470
MONDO:0853500 bizarre parosteal osteochondromatous proliferation NCIT:C121845 MONDO:equivalentTo Bizarre Parosteal Osteochondromatous Proliferation A benign lesion that usually affects the proximal small bones of the hands or feet. Grossly it consists of a cartilage cap and a bony stalk. Microscopically it is characterized by the presence of spindle cells, cartilage, and bone, usually in a disorganized pattern compared to subungual exostosis. Enlarged (bizarre) chondrocytes are present in the cartilage. Swelling with or without pain is present. Recurrences following resection have been reported in approximately half of cases. MONDO:0024470
MONDO:0853501 intermediate chondrogenic neoplasm NCIT:C121846 MONDO:equivalentTo Intermediate Chondrogenic Neoplasm A locally aggressive or rarely metastasizing cartilaginous matrix-producing neoplasm characterized by the presence of neoplastic chondrocytes. MONDO:0024469
MONDO:0853502 chondrosarcoma, grade 2 NCIT:C121870 MONDO:equivalentTo Chondrosarcoma, Grade 2 An intermediate-grade chondrosarcoma arising in the medulla of bone or within the cartilaginous cap of a pre-existing osteochondroma. It is characterized by the presence of increased cellularity and a greater degree of nuclear atypia and hyperchromasia as compared to grade 1 chondrosarcoma. Mitotic activity is present. MONDO:0008977
MONDO:0853503 chondrosarcoma, grade 3 NCIT:C121871 MONDO:equivalentTo Chondrosarcoma, Grade 3 A high-grade chondrosarcoma arising in the medulla of bone or within the cartilaginous cap of a pre-existing osteochondroma. It is characterized by the presence of increased cellularity and a greater degree of nuclear atypia, hyperchromasia, and mitotic activity as compared to grade 2 chondrosarcoma. MONDO:0008977
MONDO:0853504 benign notochordal cell tumor NCIT:C121901 MONDO:equivalentTo Benign Notochordal Cell Tumor An intraosseous benign tumor of notochord origin that arises in the bones of the base of the skull, vertebral bodies, sacrum or coccyx. It contains vacuolated tumor cells without atypia, but lacks myxoid matrix, necrosis, and lobular architecture, which are features that characterize its malignant counterpart, chordoma. Most lesions are incidental findings. MONDO:0002597
MONDO:0853507 intermediate osteogenic neoplasm NCIT:C121925 MONDO:equivalentTo Intermediate Osteogenic Neoplasm A non-metastasizing, locally aggressive, bone-forming neoplasm. MONDO:0045053
MONDO:0853508 intermediate bone neoplasm NCIT:C121926 MONDO:equivalentTo Intermediate Bone Neoplasm A locally aggressive or rarely metastasizing neoplasm that arises from the bone. MONDO:0019060
MONDO:0853510 primary bone non-hodgkin lymphoma NCIT:C121930 MONDO:equivalentTo Primary Bone Non-Hodgkin Lymphoma A non-Hodgkin lymphoma that arises from the bone, without lymph node or other extranodal involvement. The femur, spine, and pelvic bones are the most frequently affected areas. The majority of cases are diffuse large B-cell lymphomas. Most patients present with pain in the affected area. Systemic symptoms are rare. MONDO:0017814
MONDO:0853512 bone epithelioid hemangioendothelioma NCIT:C121941 MONDO:equivalentTo Bone Epithelioid Hemangioendothelioma A low-grade malignant blood vessel neoplasm arising from the bone. It is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma. MONDO:0024499
MONDO:0853515 acute lymphoblastic leukemia by gene expression profile NCIT:C121973 MONDO:equivalentTo Acute Lymphoblastic Leukemia by Gene Expression Profile Gene expression-based patient cluster groups in acute lymphoblastic leukemia. MONDO:0004967
MONDO:0853523 borderline ovarian serous tumor/atypical proliferative ovarian serous tumor NCIT:C122584 MONDO:equivalentTo Borderline Ovarian Serous Tumor/Atypical Proliferative Ovarian Serous Tumor A non-invasive serous neoplasm that arises from the ovary and shows greater cellular proliferation and cytologic atypia as compared to benign ovarian serous tumors, but less as compared to low-grade ovarian serous carcinoma. MONDO:0020662
MONDO:0853524 borderline ovarian serous tumor-micropapillary variant/non-invasive low grade ovarian serous carcinoma NCIT:C122585 MONDO:equivalentTo Borderline Ovarian Serous Tumor-Micropapillary Variant/Non-Invasive Low Grade Ovarian Serous Carcinoma A non-invasive serous neoplasm that arises from the ovary and shows micropapillary and/or cribriform architectural patterns. It is composed of round epithelial cells with scant cytoplasm and moderate nuclear atypia. MONDO:0020662
MONDO:0853525 infant leukemia NCIT:C122603 MONDO:equivalentTo Infant Leukemia An acute lymphoblastic or acute myeloid leukemia that occurs in infancy. MONDO:0004355
MONDO:0853528 childhood acute myeloid leukemia not otherwise specified NCIT:C122625 MONDO:equivalentTo Childhood Acute Myeloid Leukemia Not Otherwise Specified Acute myeloid leukemias that occur in childhood and do not fulfill the criteria for inclusion in the group of acute myeloid leukemias which have recurrent genetic abnormalities or myelodysplastic changes, or are therapy-related. This category includes entities classified according to the French-American-British classification scheme. MONDO:0015667
MONDO:0853529 hypoplastic myelodysplastic syndrome NCIT:C122686 MONDO:equivalentTo Hypoplastic Myelodysplastic Syndrome Myelodysplastic syndrome characterized by decreased cellularity in the bone marrow. MONDO:0018881
MONDO:0853530 cytogenetically normal acute myeloid leukemia NCIT:C122687 MONDO:equivalentTo Cytogenetically Normal Acute Myeloid Leukemia Acute myeloid leukemia not associated with cytogenetic abnormalities. MONDO:0018874
MONDO:0853532 childhood acute myeloid leukemia with abnormalities of chromosome 5q NCIT:C122725 MONDO:equivalentTo Childhood Acute Myeloid Leukemia with Abnormalities of Chromosome 5q A rare acute myeloid leukemia that occurs in childhood and is characterized primarily by deletions of 5q. MONDO:0004996
MONDO:0853533 childhood acute myeloid leukemia with abnormalities of chromosome 7 NCIT:C122726 MONDO:equivalentTo Childhood Acute Myeloid Leukemia with Abnormalities of Chromosome 7 A rare acute myeloid leukemia that occurs in childhood and is characterized by deletion of chromosome 7. MONDO:0004996
MONDO:0853659 childhood lymphomatoid granulomatosis NCIT:C123392 MONDO:equivalentTo Childhood Lymphomatoid Granulomatosis Lymphomatoid granulomatosis that occurs during childhood. MONDO:0019466
MONDO:0853660 childhood langerhans cell histiocytosis with risk organ involvement NCIT:C123395 MONDO:equivalentTo Childhood Langerhans Cell Histiocytosis with Risk Organ Involvement Langerhans cell histiocytosis that occurs during childhood and involves the bone marrow, spleen, liver, or lung. MONDO:0017025
MONDO:0853661 childhood langerhans cell histiocytosis without risk organ involvement NCIT:C123396 MONDO:equivalentTo Childhood Langerhans Cell Histiocytosis without Risk Organ Involvement Langerhans cell histiocytosis that occurs during childhood and does not involve the bone marrow, spleen, liver, or lung. MONDO:0017025
MONDO:0853668 fusion-positive rhabdomyosarcoma NCIT:C123735 MONDO:equivalentTo Fusion-Positive Rhabdomyosarcoma A rhabdomyosarcoma characterized by the presence of chromosomal translocation t(1;13)(p36;q14) that results in PAX7-FOXO1 gene fusion; or translocation t(2;13)(q35;q14) that results in PAX3-FOXO1 gene fusion. MONDO:0005212
MONDO:0853669 fusion-negative rhabdomyosarcoma NCIT:C123736 MONDO:equivalentTo Fusion-Negative Rhabdomyosarcoma A rhabdomyosarcoma characterized by the absence of chromosomal translocation t(1;13)(p36;q14) or t(2;13)(q35;q14) and therefore the absence of PAX7-FOXO1 or PAX3-FOXO1 gene fusion. MONDO:0005212
MONDO:0853671 refractory malignant germ cell tumor NCIT:C123739 MONDO:equivalentTo Refractory Malignant Germ Cell Tumor Malignant germ cell tumor resistant to treatment. MONDO:0006290
MONDO:0853673 childhood germinomatous germ cell tumor NCIT:C123838 MONDO:equivalentTo Childhood Germinomatous Germ Cell Tumor A germinomatous germ cell tumor occurring in children. MONDO:0020580
MONDO:0853675 childhood nongerminomatous germ cell tumor NCIT:C123841 MONDO:equivalentTo Childhood Nongerminomatous Germ Cell Tumor A nongerminomatous germ cell tumor occurring in children. MONDO:0021656
MONDO:0853680 childhood mixed germ cell tumor NCIT:C123848 MONDO:equivalentTo Childhood Mixed Germ Cell Tumor A mixed germ cell tumor occurring in children. MONDO:0015864
MONDO:0853693 childhood astrocytoma NCIT:C124275 MONDO:equivalentTo Childhood Astrocytoma An astrocytoma that occurs during childhood. MONDO:0019781
MONDO:0853694 childhood atypical choroid plexus papilloma NCIT:C124291 MONDO:equivalentTo Childhood Atypical Choroid Plexus Papilloma An atypical choroid plexus papilloma that occurs during childhood. MONDO:0002684
MONDO:0853721 ovarian adenomatoid tumor NCIT:C126331 MONDO:equivalentTo Ovarian Adenomatoid Tumor A rare benign mesothelial tumor that arises from the ovary. It is characterized by the presence of gland-like structures. MONDO:0004230
MONDO:0853728 chronic eosinophilic leukemia with fip1l1-pdgfra NCIT:C126351 MONDO:equivalentTo Chronic Eosinophilic Leukemia with FIP1L1-PDGFRA Chronic eosinophilic leukemia characterized by the rearrangement of the PDGFRA gene, most often resulting in the formation of FIP1L1-PDGFRA fusion transcripts. MONDO:0015689
MONDO:0853729 primary peritoneal high grade serous adenocarcinoma NCIT:C126353 MONDO:equivalentTo Primary Peritoneal High Grade Serous Adenocarcinoma A serous adenocarcinoma that arises from the lining of the peritoneum. It is characterized by high grade histopathologic features. MONDO:0006386
MONDO:0853730 primary peritoneal low grade serous adenocarcinoma NCIT:C126354 MONDO:equivalentTo Primary Peritoneal Low Grade Serous Adenocarcinoma A serous adenocarcinoma that arises from the lining of the peritoneum. It is characterized by low grade histopathologic features. MONDO:0006386
MONDO:0853731 peritoneal desmoplastic small round cell tumor NCIT:C126356 MONDO:equivalentTo Peritoneal Desmoplastic Small Round Cell Tumor A desmoplastic small round cell tumor that occurs in the abdominal and/or pelvic peritoneum. MONDO:0019373
MONDO:0853732 pelvic fibromatosis NCIT:C126358 MONDO:equivalentTo Pelvic Fibromatosis Fibromatosis that occurs in the pelvis. It affects almost always females. It is characterized by the presence of elongated spindle-shaped fibroblasts, collagenous stroma formation, and an infiltrative growth pattern. It recurs if incompletely resected but lacks metastatic potential. MONDO:0007608
MONDO:0853733 abdominal inflammatory myofibroblastic tumor NCIT:C126359 MONDO:equivalentTo Abdominal Inflammatory Myofibroblastic Tumor Inflammatory myofibroblastic tumor that arises from the abdominal cavity. MONDO:0015798
MONDO:0853734 thyroid gland cribriform morular carcinoma NCIT:C126408 MONDO:equivalentTo Thyroid Gland Cribriform Morular Carcinoma A thyroid gland carcinoma characterized by the presence of cribriform, trabecular, follicular, papillary, and solid growth patterns and squamoid morulae formation. It may occur with familial adenomatous polyposis or sporadically. MONDO:0015075
MONDO:0853735 thyroid gland papillary carcinoma with fibromatosis/fasciitis-like/desmoid-type stroma NCIT:C126410 MONDO:equivalentTo Thyroid Gland Papillary Carcinoma with Fibromatosis/Fasciitis-Like/Desmoid-Type Stroma A rare morphologic variant of papillary thyroid gland carcinoma characterized by the presence of abundant and cellular stroma resembling nodular fasciitis, fibromatosis, or other proliferative myofibroblastic processes. (WHO) MONDO:0005075
MONDO:0853736 fallopian tube high grade serous adenocarcinoma NCIT:C126456 MONDO:equivalentTo Fallopian Tube High Grade Serous Adenocarcinoma A rapidly growing serous adenocarcinoma that arises from the fallopian tube. It is characterized by the presence of high grade cytologic features and frequent mitotic figures. MONDO:0006208
MONDO:0853738 fallopian tube lymphoma NCIT:C126464 MONDO:equivalentTo Fallopian Tube Lymphoma An exceedingly rare lymphoma that arises from the fallopian tube. MONDO:0002158
MONDO:0853742 broad ligament serous adenocarcinoma NCIT:C126479 MONDO:equivalentTo Broad Ligament Serous Adenocarcinoma A rare serous adenocarcinoma that arises from the broad ligament. MONDO:0002741
MONDO:0853743 oropharyngeal poorly differentiated carcinoma NCIT:C126750 MONDO:equivalentTo Oropharyngeal Poorly Differentiated Carcinoma A high-grade carcinoma that arises from the oropharynx. It is characterized by the presence of malignant cells which bear minimal resemblance to the cells from which they arose. MONDO:0044704
MONDO:0853745 endometrial dedifferentiated carcinoma NCIT:C126769 MONDO:equivalentTo Endometrial Dedifferentiated Carcinoma A carcinoma that arises from the endometrium and is characterized by the presence of an undifferentiated carcinomatous component and a second component of either FIGO grade 1 or 2 endometrioid carcinoma. MONDO:0002447
MONDO:0853748 uterine corpus hydropic leiomyoma NCIT:C126975 MONDO:equivalentTo Uterine Corpus Hydropic Leiomyoma A variant of leiomyoma arising from the uterine corpus. It is characterized by conspicuous zonal edema. Hyalinization may also be present. MONDO:0007886
MONDO:0853749 uterine corpus high grade endometrial stromal sarcoma NCIT:C126998 MONDO:equivalentTo Uterine Corpus High Grade Endometrial Stromal Sarcoma A rare, high grade sarcoma that arises from the endometrial stroma. It is characterized by round cell morphology. It was previously also known as undifferentiated uterine sarcoma. In 2014, high grade endometrial stromal sarcoma was reclassified and is currently considered a distinct and rare neoplasm. It appears to have a prognosis that falls between low grade endometrial stromal sarcoma and undifferentiated sarcoma. MONDO:0002923
MONDO:0853751 benign uterine corpus pecoma NCIT:C127071 MONDO:equivalentTo Benign Uterine Corpus PEComa A benign neoplasm with perivascular epithelioid cell differentiation arising from the uterine corpus. It is characterized by the absence of pleomorphism and scarcity or absence of mitotic figures. It usually affects perimenopausal women. Patients present with a pelvic mass or abnormal bleeding. MONDO:0004221
MONDO:0853753 uterine corpus germ cell tumor NCIT:C127077 MONDO:equivalentTo Uterine Corpus Germ Cell Tumor A benign or malignant germ cell tumor that arises from the uterine corpus. Representative examples include teratoma and yolk sac tumor. MONDO:0021254
MONDO:0853764 cervical neuroendocrine neoplasm NCIT:C128041 MONDO:equivalentTo Cervical Neuroendocrine Neoplasm A neuroendocrine neoplasm that arises from the cervix. This category includes neuroendocrine tumor grade 1, neuroendocrine tumor grade 2, and neuroendocrine carcinoma (small cell and large cell neuroendocrine carcinoma). MONDO:0019496
MONDO:0853771 vaginal papillary carcinoma NCIT:C128060 MONDO:equivalentTo Vaginal Papillary Carcinoma A rare squamous cell carcinoma that arises from the vagina resembling transitional cell carcinoma of the urinary tract. MONDO:0002979
MONDO:0853775 ovarian cancer by figo stage NCIT:C128081 MONDO:equivalentTo Ovarian Cancer by FIGO Stage A category of staging terms for ovarian cancer according to the International Federation of Gynecology and Obstetrics (FIGO), 2014. AJCC ovarian cancer stage terms from the 6th and 7th editions that are synonymous to the FIGO ovarian cancer staging classification of 2014 are included as preferred terms. MONDO:0005140
MONDO:0853776 ovarian cancer by ajcc v6 and v7 stage NCIT:C128106 MONDO:equivalentTo Ovarian Cancer by AJCC v6 and v7 Stage A category of staging terms for ovarian cancer according to the American Joint Committee on cancer (AJCC) 6th and 7th editions. International Federation of Gynecology and Obstetrics (FIGO) ovarian cancer staging terms prior to 2014 are included in this category if synonymous with the AJCC terms. MONDO:0005140
MONDO:0853779 vaginal germ cell tumor NCIT:C128112 MONDO:equivalentTo Vaginal Germ Cell Tumor A germ tumor that arises from the vagina. MONDO:0005040
MONDO:0853781 vulvar squamous intraepithelial lesion, hpv-associated NCIT:C128142 MONDO:equivalentTo Vulvar Squamous Intraepithelial Lesion, HPV-Associated An intraepithelial lesion of the vulvar squamous epithelium associated with HPV infection. It is characterized by maturation abnormalities and nuclear hyperchromasia that are confined to the basement membrane. MONDO:0005198
MONDO:0853784 vulvar adenocarcinoma of mammary gland type NCIT:C128162 MONDO:equivalentTo Vulvar Adenocarcinoma of Mammary Gland Type A primary invasive malignant epithelial neoplasm of the vulva showing morphological features of recognized breast adenocarcinomas. (WHO, 2014) MONDO:0024336
MONDO:0853787 vulvar mucinous adenocarcinoma, intestinal-type NCIT:C128166 MONDO:equivalentTo Vulvar Mucinous Adenocarcinoma, Intestinal-Type A rare vulvar mucinous adenocarcinoma that resembles a large intestinal adenocarcinoma. MONDO:0004957
MONDO:0853788 vulvar keratoacanthoma NCIT:C128167 MONDO:equivalentTo Vulvar Keratoacanthoma A keratoacanthoma that arises from the vulva. It grows rapidly and may regress spontaneously. It is considered a variant of well-differentiated squamous cell carcinoma with distinct clinical behavior. MONDO:0024609
MONDO:0853797 vulvar germ cell tumor NCIT:C128294 MONDO:equivalentTo Vulvar Germ Cell Tumor A rare germ cell tumor that arises from the vulva. MONDO:0005040
MONDO:0853835 b acute lymphoblastic leukemia, philadelphia chromosome negative NCIT:C128629 MONDO:equivalentTo B Acute Lymphoblastic Leukemia, Philadelphia Chromosome Negative A B-acute lymphoblastic leukemia (B-ALL) that does not have the cytogenetic abnormality t(9;22)(q34;q11.2). Most cases of B-ALL do not have this translocation. MONDO:0020511
MONDO:0853837 nk-cell lymphoma, unclassifiable NCIT:C128697 MONDO:equivalentTo NK-Cell Lymphoma, Unclassifiable A very rare NK-cell lymphoma with pathologic and clinical features posing difficulty in its exact diagnosis and classification. MONDO:0000430
MONDO:0853840 cutaneous malignant melanoma 2 NCIT:C128801 MONDO:equivalentTo Cutaneous Malignant Melanoma 2 An autosomal dominant genetic disorder caused by mutations in the CDKN2A gene, encoding cyclin-dependent kinase inhibitor 2A. The condition is characterized by cutaneous malignant melanoma associated with this genetic alteration. MONDO:0018961
MONDO:0853846 glioblastoma, not otherwise specified NCIT:C129295 MONDO:equivalentTo Glioblastoma, Not Otherwise Specified A central nervous system tumor with morphological features of glioblastoma in which there is insufficient information on the IDH genes status. MONDO:0018177
MONDO:0853849 oligodendroglioma, idh-mutant and 1p/19q-codeleted NCIT:C129318 MONDO:equivalentTo Oligodendroglioma, IDH-Mutant and 1p/19q-Codeleted An oligodendroglioma carrying IDH gene family mutation and combined whole-arm losses of 1p and 19q (1p/19q codeletion). MONDO:0016695
MONDO:0853850 oligodendroglioma, not otherwise specified NCIT:C129319 MONDO:equivalentTo Oligodendroglioma, Not Otherwise Specified A central nervous system tumor with morphological features of oligodendroglioma in which there is insufficient information on the IDH genes and 1p/19q codeletion status. MONDO:0016695
MONDO:0853851 anaplastic oligodendroglioma, idh-mutant and 1p/19q-codeleted NCIT:C129321 MONDO:equivalentTo Anaplastic Oligodendroglioma, IDH-Mutant and 1p/19q-Codeleted An anaplastic oligodendroglioma carrying IDH gene family mutation and combined whole-arm losses of 1p and 19q (1p/19q codeletion). MONDO:0016696
MONDO:0853852 anaplastic oligodendroglioma, not otherwise specified NCIT:C129322 MONDO:equivalentTo Anaplastic Oligodendroglioma, Not Otherwise Specified A central nervous system tumor with morphological features of anaplastic oligodendroglioma in which there is insufficient information on the IDH genes and 1p/19q codeletion status. MONDO:0016696
MONDO:0853853 oligoastrocytoma, not otherwise specified NCIT:C129323 MONDO:equivalentTo Oligoastrocytoma, Not Otherwise Specified A central nervous system tumor with morphological features of oligoastrocytoma in which there is insufficient information on the IDH genes status. MONDO:0016702
MONDO:0853854 anaplastic oligoastrocytoma, not otherwise specified NCIT:C129324 MONDO:equivalentTo Anaplastic Oligoastrocytoma, Not Otherwise Specified A central nervous system tumor with morphological features of anaplastic oligoastrocytoma in which there is insufficient information on the IDH genes status. MONDO:0016703
MONDO:0853855 diffuse glioma NCIT:C129325 MONDO:equivalentTo Diffuse Glioma A glioma that has diffusely infiltrated the surrounding central nervous system tissues. MONDO:0021042
MONDO:0853856 anaplastic pleomorphic xanthoastrocytoma NCIT:C129327 MONDO:equivalentTo Anaplastic Pleomorphic Xanthoastrocytoma A WHO grade 3 pleomorphic xanthoastrocytoma characterized by the presence of five or more mitoses per 10 high-power fields. Necrosis may be present. Patients have shorter survival rates when compared to those with WHO grade 2 pleomorphic xanthoastrocytoma. MONDO:0019781
MONDO:0853857 diffuse leptomeningeal glioneuronal tumor NCIT:C129424 MONDO:equivalentTo Diffuse Leptomeningeal Glioneuronal Tumor A relatively slow growing diffuse leptomeningeal neoplasm usually affecting children and adolescents. It is characterized by the presence of clear glial neoplastic cells reminiscent of oligodendroglioma. A neuronal component may be present. The prognosis is variable. MONDO:0016729
MONDO:0853858 multinodular and vacuolated neuronal tumor NCIT:C129427 MONDO:equivalentTo Multinodular and Vacuolated Neuronal Tumor A low-grade tumor affecting the cerebral hemispheres. It is composed of cells with glial and/or neuronal differentiation forming multiple nodules with prominent vacuolation. MONDO:0016729
MONDO:0853859 medulloblastoma molecular subtypes NCIT:C129439 MONDO:equivalentTo Medulloblastoma Molecular Subtypes A term that refers to the classification of medulloblastomas according to their molecular characteristics. MONDO:0007959
MONDO:0853860 medulloblastoma, not otherwise specified NCIT:C129447 MONDO:equivalentTo Medulloblastoma, Not Otherwise Specified A medulloblastoma which has not been further characterized. MONDO:0007959
MONDO:0853861 small cell adenocarcinoma NCIT:C129449 MONDO:equivalentTo Small Cell Adenocarcinoma An adenocarcinoma composed of small malignant cells. MONDO:0004970
MONDO:0853862 central nervous system solitary fibrous tumor NCIT:C129526 MONDO:equivalentTo Central Nervous System Solitary Fibrous Tumor A mesenchymal, non-meningothelial neoplasm arising from the central nervous system. It is characterized by a collagenous and low cellularity spindle cell and/or hemangiopericytomatous histopathological pattern, recurrent intrachromosomal rearrangement on chromosome 12q that results in the fusion of the NAB2 and STAT6 genes, high recurrence rates, and long-term risk of systemic metastasis. MONDO:0003244
MONDO:0853863 central nervous system mesenchymal chondrosarcoma NCIT:C129534 MONDO:equivalentTo Central Nervous System Mesenchymal Chondrosarcoma A mesenchymal chondrosarcoma that arises from the central nervous system. MONDO:0002217
MONDO:0853864 central nervous system epithelioid hemangioendothelioma NCIT:C129536 MONDO:equivalentTo Central Nervous System Epithelioid Hemangioendothelioma A low-grade malignant blood vessel neoplasm that arises from the central nervous system. It is characterized by the presence of epithelioid endothelial cells. MONDO:0037740
MONDO:0853865 central nervous system angiolipoma NCIT:C129538 MONDO:equivalentTo Central Nervous System Angiolipoma An angiolipoma that arises from the central nervous system. MONDO:0003844
MONDO:0853866 central nervous system undifferentiated pleomorphic sarcoma NCIT:C129566 MONDO:equivalentTo Central Nervous System Undifferentiated Pleomorphic Sarcoma A rare undifferentiated pleomorphic sarcoma (formerly known as malignant fibrous histiocytoma) involving the central nervous system. MONDO:0002217
MONDO:0853868 central nervous system anaplastic large cell lymphoma, alk-positive NCIT:C129598 MONDO:equivalentTo Central Nervous System Anaplastic Large Cell Lymphoma, ALK-Positive An anaplastic large cell lymphoma, ALK-positive, arising from the central nervous system. MONDO:0006128
MONDO:0853869 central nervous system anaplastic large cell lymphoma, alk-negative NCIT:C129599 MONDO:equivalentTo Central Nervous System Anaplastic Large Cell Lymphoma, ALK-Negative An anaplastic large cell lymphoma, ALK-negative, arising from the central nervous system. MONDO:0006128
MONDO:0853870 central nervous system intravascular large b-cell lymphoma NCIT:C129602 MONDO:equivalentTo Central Nervous System Intravascular Large B-Cell Lymphoma A rare extranodal B-cell non-Hodgkin lymphoma that affects the central nervous system. It is characterized by the presence of lymphoma cells exclusively in the lumina of small vessels, particularly capillaries. MONDO:0017596
MONDO:0853881 acute myeloid leukemia with biallelic cebpa mutation NCIT:C129782 MONDO:equivalentTo Acute Myeloid Leukemia with Biallelic CEBPA Mutation An acute myeloid leukemia with double mutations of the CEBPA gene. MONDO:0017894
MONDO:0853882 acute myeloid leukemia with monoallelic cebpa mutation NCIT:C129783 MONDO:equivalentTo Acute Myeloid Leukemia with Monoallelic CEBPA Mutation An acute myeloid leukemia with single mutations of the CEBPA gene. MONDO:0017894
MONDO:0853884 b lymphoblastic leukemia/lymphoma, bcr-abl1-like NCIT:C129787 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma, BCR-ABL1-Like B lymphoblastic leukemia/lymphoma characterized by a gene-expression profile similar to that of BCR-ABL1-positive B lymphoblastic leukemia/lymphoma, absence of the pathognomonic BCR-ABL1 rearrangement, alterations of lymphoid transcription factor genes, and a poor outcome. MONDO:0035605
MONDO:0853887 metastatic transitional cell carcinoma NCIT:C129828 MONDO:equivalentTo Metastatic Transitional Cell Carcinoma A carcinoma that arises from transitional cells and has spread from its original site of growth to another anatomic site. MONDO:0024879
MONDO:0853888 chronic myelomonocytic leukemia with eosinophilia associated with t(5;12)(q31;p12) NCIT:C129852 MONDO:equivalentTo Chronic Myelomonocytic Leukemia with Eosinophilia Associated with t(5;12)(q31;p12) Chronic myelomonocytic leukemia characterized by the presence of eosinophilia, PDGFRB gene rearrangement, and t(5;12)(q31;p12). MONDO:0015690
MONDO:0853892 chronic myelomonocytic leukemia-0 NCIT:C130035 MONDO:equivalentTo Chronic Myelomonocytic Leukemia-0 A chronic myelomonocytic leukemia characterized by the presence of less than 5 percent blasts in the bone marrow and less than 2 percent blasts in the peripheral blood. MONDO:0020311
MONDO:0853893 myelodysplastic syndrome with ring sideroblasts and single lineage dysplasia NCIT:C130037 MONDO:equivalentTo Myelodysplastic Syndrome with Ring Sideroblasts and Single Lineage Dysplasia A myelodysplastic syndrome with ring sideroblasts and dysplastic changes involving only one myeloid cell lineage in the bone marrow. MONDO:0019157
MONDO:0853894 b lymphoblastic leukemia/lymphoma with intrachromosomal amplification of chromosome 21 NCIT:C130039 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma with Intrachromosomal Amplification of Chromosome 21 B lymphoblastic leukemia/lymphoma characterized by amplification of a portion of chromosome 21. It usually occurs in children and is associated with an adverse prognosis. MONDO:0035605
MONDO:0853943 anastomosing hemangioma NCIT:C131760 MONDO:equivalentTo Anastomosing Hemangioma An unusual variant of capillary hemangioma. It is characterized by a unique anastomosing sinusoidal-like architecture which may mimic angiosarcoma. It was originally described in the kidney but rare cases have been reported in other sites. MONDO:0002407
MONDO:0853956 acute megakaryoblastic leukemia with cbfa2t3-glis2 NCIT:C132109 MONDO:equivalentTo Acute Megakaryoblastic Leukemia with CBFA2T3-GLIS2 A non-Down syndrome acute megakaryoblastic leukemia that occurs in childhood. It is associated with CBFA2T3-GLIS2 chimeric oncogene and has an unfavorable prognosis. MONDO:0004996
MONDO:0853959 small intestinal myeloid sarcoma NCIT:C132260 MONDO:equivalentTo Small Intestinal Myeloid Sarcoma An extramedullary myeloid tumor that arises from the small intestine. It often presents with abdominal pain and obstruction. MONDO:0000956
MONDO:0853961 atypical pituitary neuroendocrine tumor NCIT:C132296 MONDO:equivalentTo Atypical Pituitary Neuroendocrine Tumor A usually aggressive and invasive pituitary neuroendocrine tumor characterized by excessive p53 immunoreactivity, increased mitotic activity, and MIB-1 proliferative index greater than 3%. MONDO:0006373
MONDO:0853963 lip and oral cavity cancer by ajcc v8 stage NCIT:C132728 MONDO:equivalentTo Lip and Oral Cavity Cancer by AJCC v8 Stage A term that refers to the staging of lip and oral cavity carcinoma according to the American Joint Committee on Cancer, 8th edition. MONDO:0023644
MONDO:0853964 lip and oral cavity cancer by ajcc v6 and v7 stage NCIT:C132736 MONDO:equivalentTo Lip and Oral Cavity Cancer by AJCC v6 and v7 Stage A term that refers to the staging of lip and oral cavity carcinoma according to the American Joint Committee on Cancer, 6th and 7th editions. MONDO:0023644
MONDO:0853965 major salivary gland cancer by ajcc v7 stage NCIT:C132778 MONDO:equivalentTo Major Salivary Gland Cancer by AJCC v7 Stage A term that refers to the staging of major salivary gland cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0006284
MONDO:0853966 major salivary gland cancer by ajcc v8 stage NCIT:C132779 MONDO:equivalentTo Major Salivary Gland Cancer by AJCC v8 Stage A term that refers to the staging of major salivary gland cancer according to the American Joint Committee on Cancer, 8th edition. MONDO:0006284
MONDO:0853968 pharyngeal carcinoma by ajcc v8 stage NCIT:C132814 MONDO:equivalentTo Pharyngeal Carcinoma by AJCC v8 Stage A term that refers to the staging of pharyngeal carcinoma according to the American Joint Committee on Cancer, 8th edition. MONDO:0021345
MONDO:0853973 metastatic malignant germ cell tumor NCIT:C132854 MONDO:equivalentTo Metastatic Malignant Germ Cell Tumor A malignant germ cell tumor that has spread from its original site of growth to another anatomic site. MONDO:0024880
MONDO:0853979 sinonasal cancer by ajcc v8 stage NCIT:C133074 MONDO:equivalentTo Sinonasal Cancer by AJCC v8 Stage A term that refers to the staging of nasal cavity and paranasal sinus carcinoma according to the American Joint Committee on Cancer, 8th edition. MONDO:0056819
MONDO:0853980 lung adenofibroma NCIT:C133091 MONDO:equivalentTo Lung Adenofibroma A very rare benign neoplasm that arises from the lung. It is characterized by the presence of a stromal and an epithelial component. It resembles the adenofibromas that arise from the organs of the female reproductive system. MONDO:0021043
MONDO:0853981 laryngeal cancer by ajcc v8 stage NCIT:C133156 MONDO:equivalentTo Laryngeal Cancer by AJCC v8 Stage A term that refers to the staging of laryngeal carcinoma according to the American Joint Committee on Cancer, 8th edition. MONDO:0002358
MONDO:0853984 cutaneous squamous cell carcinoma of the head and neck NCIT:C133252 MONDO:equivalentTo Cutaneous Squamous Cell Carcinoma of the Head and Neck A squamous cell carcinoma that arises from the skin of the head and neck. MONDO:0010150
MONDO:0853986 esophageal cancer by ajcc v8 stage NCIT:C133399 MONDO:equivalentTo Esophageal Cancer by AJCC v8 Stage A term that refers to the staging of esophageal carcinoma according to the American Joint Committee on Cancer, 8th edition. MONDO:0019086
MONDO:0853991 gastroesophageal junction adenocarcinoma by ajcc v8 stage NCIT:C133548 MONDO:equivalentTo Gastroesophageal Junction Adenocarcinoma by AJCC v8 Stage A term that refers to the staging of gastroesophageal junction adenocarcinoma according to the American Joint Committee on Cancer, 8th edition. MONDO:0003219
MONDO:0853993 gastric cancer by ajcc v8 stage NCIT:C133638 MONDO:equivalentTo Gastric Cancer by AJCC v8 Stage A term that refers to the staging of gastric cancer according to the American Joint Committee on Cancer, 8th edition. MONDO:0004950
MONDO:0853994 small intestinal cancer by ajcc v7 stage NCIT:C133716 MONDO:equivalentTo Small Intestinal Cancer by AJCC v7 Stage A term that refers to the staging of small intestinal cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0005522
MONDO:0853996 appendix carcinoma by ajcc v7 stage NCIT:C133733 MONDO:equivalentTo Appendix Carcinoma by AJCC v7 Stage A term that refers to the staging of appendiceal carcinoma according to the American Joint Committee on Cancer, 7th edition. Carcinoid tumors are staged separately. (from AJCC 7th Ed.) MONDO:0003196
MONDO:0853997 anal canal cancer by ajcc v6 and v7 stage NCIT:C133787 MONDO:equivalentTo Anal Canal Cancer by AJCC v6 and v7 Stage A term that refers to the staging of anal canal cancer according to the American Joint Committee on Cancer, 6th and 7th editions. This staging system applies to carcinomas arising in the anal canal only; melanomas, carcinoid tumors, sarcomas, and perianal tumors are not included. (from AJCC 6th and 7th Eds.) MONDO:0007108
MONDO:0853998 anal cancer by ajcc v8 stage NCIT:C133794 MONDO:equivalentTo Anal Cancer by AJCC v8 Stage A term that refers to the staging of anal cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to all carcinomas arising in the anal canal, including carcinomas that arise within anorectal fistulas and those arising in the perianal area (anal margin). High-grade neuroendocrine carcinomas (small cell neuroendocrine carcinoma and large cell neuroendocrine carcinoma) are staged using this system. There is no AJCC staging system for anal mucosal melanomas and anal well-differentiated neuroendocrine tumors. (from AJCC 8th Ed.) MONDO:0003199
MONDO:0854000 small intestinal adenocarcinoma by ajcc v8 stage NCIT:C133893 MONDO:equivalentTo Small Intestinal Adenocarcinoma by AJCC v8 Stage A term that refers to the staging of small intestinal adenocarcinoma according to the American Joint Committee on Cancer, 8th edition. Nonadenocarcinomas arising in the small intestine should have a TNM assigned but are not assigned a stage classification. (from AJCC 8th Ed.) MONDO:0003198
MONDO:0854002 appendix carcinoma by ajcc v8 stage NCIT:C134117 MONDO:equivalentTo Appendix Carcinoma by AJCC v8 Stage A term that refers to the staging of appendiceal carcinoma according to the American Joint Committee on Cancer, 8th edition. This staging system applies to carcinomas of the appendix, including high-grade neuroendocrine carcinomas, mixed adenoneuroendocrine carcinomas, and goblet cell carcinoids. Well-differentiated neuroendocrine tumors (carcinoids) are staged according to the classification for neuroendocrine tumors of the appendix. (from AJCC 8th Ed.) MONDO:0003196
MONDO:0854009 colorectal cancer by ajcc v8 stage NCIT:C134180 MONDO:equivalentTo Colorectal Cancer by AJCC v8 Stage A term that refers to the staging of colorectal cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to adenocarcinomas, high-grade neuroendocrine carcinomas, and squamous cell carcinomas of the colon and rectum. Appendiceal carcinomas, anal carcinomas, and well-differentiated neuroendocrine tumors (carcinoids) are not covered by this staging system. (from AJCC 8th Ed.) MONDO:0024331
MONDO:0854013 intrahepatic cholangiocarcinoma by ajcc v7 stage NCIT:C134514 MONDO:equivalentTo Intrahepatic Cholangiocarcinoma by AJCC v7 Stage A term that refers to the staging of intrahepatic cholangiocarcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0003210
MONDO:0854014 hepatocellular carcinoma by ajcc v8 stage NCIT:C134515 MONDO:equivalentTo Hepatocellular Carcinoma by AJCC v8 Stage A term that refers to the staging of hepatocellular carcinoma according to the American Joint Committee on Cancer, 8th edition. This staging system applies to hepatocellular carcinomas and fibrolamellar carcinomas (fibrolamellar variant of hepatocellular carcinoma). Intrahepatic cholangiocarcinomas, combined hepatocellular-cholangiocarcinomas, and sarcomas of the liver are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0007256
MONDO:0854017 intrahepatic bile duct cancer by ajcc v8 stage NCIT:C134604 MONDO:equivalentTo Intrahepatic Bile Duct Cancer by AJCC v8 Stage A term that refers to the staging of intrahepatic bile duct cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to intrahepatic cholangiocarcinomas, combined hepatocellular-cholangiocarcinomas (mixed hepatocholangiocarcinomas), and primary neuroendocrine tumors of the liver. Primary sarcomas of the liver, pure hepatocellular carcinomas, hilar cholangiocarcinomas, and gallbladder carcinomas are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0018531
MONDO:0854018 gallbladder cancer by ajcc v8 stage NCIT:C134660 MONDO:equivalentTo Gallbladder Cancer by AJCC v8 Stage A term that refers to the staging of gallbladder cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to gallbladder carcinomas. Well-differentiated neuroendocrine tumors and sarcomas are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0003220
MONDO:0854019 hilar cholangiocarcinoma by ajcc v7 stage NCIT:C134742 MONDO:equivalentTo Hilar Cholangiocarcinoma by AJCC v7 Stage A term that refers to the staging of hilar cholangiocarcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0003345
MONDO:0854020 hilar cholangiocarcinoma by ajcc v8 stage NCIT:C134743 MONDO:equivalentTo Hilar Cholangiocarcinoma by AJCC v8 Stage A term that refers to the staging of hilar cholangiocarcinoma according to the American Joint Committee on Cancer, 8th edition. Hilar well-differentiated neuroendocrine tumors and sarcomas are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0003345
MONDO:0854022 distal bile duct cancer by ajcc v7 stage NCIT:C134810 MONDO:equivalentTo Distal Bile Duct Cancer by AJCC v7 Stage A term that refers to the staging of distal bile duct cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0003707
MONDO:0854023 distal bile duct cancer by ajcc v8 stage NCIT:C134811 MONDO:equivalentTo Distal Bile Duct Cancer by AJCC v8 Stage A term that refers to the staging of distal bile duct cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to bile duct adenocarcinomas, biliary intraepithelial neoplasia, high-grade neuroendocrine carcinomas, and papillary carcinomas that arise from the distal bile duct. Tumors arising in the ampulla of Vater, sarcomas, and well-differentiated neuroendocrine tumors (carcinoids) are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0003707
MONDO:0854024 ampulla of vater cancer by ajcc v7 stage NCIT:C134863 MONDO:equivalentTo Ampulla of Vater Cancer by AJCC v7 Stage A term that refers to the staging of ampulla of Vater cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0017590
MONDO:0854025 ampulla of vater cancer by ajcc v8 stage NCIT:C134864 MONDO:equivalentTo Ampulla of Vater Cancer by AJCC v8 Stage A term that refers to the staging of ampulla of Vater cancer according to the American Joint Committee on Cancer, 8th edition. This staging system does not apply to well-differentiated neuroendocrine (carcinoid) tumors but does apply to high-grade neuroendocrine carcinomas, such as small cell carcinoma and large cell neuroendocrine carcinoma. (from AJCC 8th Ed.) MONDO:0017590
MONDO:0854026 pancreatic cancer by ajcc v6 and v7 stage NCIT:C134902 MONDO:equivalentTo Pancreatic Cancer by AJCC v6 and v7 Stage A term that refers to the staging of exocrine and endocrine pancreatic cancer including well-differentiated neuroendocrine tumors according to the American Joint Committee on Cancer, 6th and 7th editions. MONDO:0005192
MONDO:0854027 pancreatic cancer by ajcc v8 stage NCIT:C134909 MONDO:equivalentTo Pancreatic Cancer by AJCC v8 Stage A term that refers to the staging of exocrine pancreatic cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to pancreatic ductal adenocarcinoma, acinar cell carcinoma, intraductal papillary mucinous neoplasm with associated invasive carcinoma, intraductal tubulopapillary neoplasm with associated invasive carcinoma, colloid carcinoma, mucinous cystic neoplasm with associated invasive carcinoma, solid pseudopapillary neoplasm, large cell neuroendocrine carcinoma, small cell neuroendocrine carcinoma, and pancreatoblastoma. Well-differentiated neuroendocrine tumors are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0005192
MONDO:0854029 lung non-squamous non-small cell carcinoma NCIT:C135017 MONDO:equivalentTo Lung Non-Squamous Non-Small Cell Carcinoma A non-small cell lung carcinoma without evidence of squamous differentiation. MONDO:0005233
MONDO:0854030 gastric neuroendocrine tumor by ajcc v8 stage NCIT:C135045 MONDO:equivalentTo Gastric Neuroendocrine Tumor by AJCC v8 Stage A term that refers to the staging of a gastric neuroendocrine tumor according to the American Joint Committee on Cancer, 8th edition. This staging system applies to gastric "carcinoid" tumors (NET G1 and G2, and rare well-differentiated G3). Gastric high-grade neuroendocrine carcinoma and gastric mixed adenoneuroendocrine carcinoma are not included in this staging system. (from AJCC 8th Ed.) MONDO:0015062
MONDO:0854031 duodenal neuroendocrine tumor by ajcc v8 stage NCIT:C135075 MONDO:equivalentTo Duodenal Neuroendocrine Tumor by AJCC v8 Stage A term that refers to the staging of a duodenal neuroendocrine tumor according to the American Joint Committee on Cancer, 8th edition. This staging system applies to well-differentiated neuroendocrine tumors of the duodenum. Carcinomas of the duodenum, including high-grade (grade 3), poorly differentiated neuroendocrine carcinomas are not included in this staging system. (from AJCC 8th Ed.) MONDO:0015063
MONDO:0854032 jejunal neuroendocrine tumor by ajcc v8 stage NCIT:C135119 MONDO:equivalentTo Jejunal Neuroendocrine Tumor by AJCC v8 Stage A term that refers to the staging of a jejunal neuroendocrine tumor, following the rules of the TNM AJCC v8 classification system. This classification system applies to small bowel "carcinoid" tumors (NET G1 and G2, and rare well-differentiated G3) arising in the jejunum. This classification system does not apply to high-grade neuroendocrine carcinomas, mixed adenoneuroendocrine carcinomas, and neuroendocrine tumors of the duodenum. (from AJCC 8th Ed.) MONDO:0015064
MONDO:0854033 ileal neuroendocrine tumor by ajcc v8 stage NCIT:C135124 MONDO:equivalentTo Ileal Neuroendocrine Tumor by AJCC v8 Stage A term that refers to the staging of an ileal neuroendocrine tumor, following the rules of the TNM AJCC v8 classification system. This classification system applies to small bowel "carcinoid" tumors (NET G1 and G2, and rare well-differentiated G3) arising in the ileum. This classification system does not apply to high-grade neuroendocrine carcinomas, mixed adenoneuroendocrine carcinomas, and neuroendocrine tumors of the duodenum. (from AJCC 8th Ed.) MONDO:0015065
MONDO:0854034 digestive system neuroendocrine tumor by ajcc v7 stage NCIT:C135129 MONDO:equivalentTo Digestive System Neuroendocrine Tumor by AJCC v7 Stage A term that refers to the staging of a digestive system neuroendocrine tumor, following the rules of the TNM AJCC v7 classification system. MONDO:0000386
MONDO:0854036 appendix neuroendocrine tumor by ajcc v8 stage NCIT:C135156 MONDO:equivalentTo Appendix Neuroendocrine Tumor by AJCC v8 Stage A term that refers to the staging of an appendiceal neuroendocrine tumor, following the rules of the TNM AJCC v8 classification system. This staging system applies to appendiceal NETs (carcinoid tumors) (NET G1 and G2, and rare well-differentiated G3). High-grade neuroendocrine carcinomas (NEC), goblet cell carcinoids, mixed adenocarcinomas, and adenocarcinomas of the appendix are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0015066
MONDO:0854042 pancreatic neuroendocrine tumor by ajcc v8 stage NCIT:C135560 MONDO:equivalentTo Pancreatic Neuroendocrine Tumor by AJCC v8 Stage A term that refers to the staging of a pancreatic neuroendocrine tumor, following the rules of the TNM AJCC v8 classification system. This staging system applies to well-differentiated neuroendocrine tumors arising in the pancreas. Carcinomas of the pancreas, including high-grade (grade 3), poorly differentiated neuroendocrine carcinomas are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0019954
MONDO:0854043 thymic epithelial neoplasm by ajcc v8 stage NCIT:C136320 MONDO:equivalentTo Thymic Epithelial Neoplasm by AJCC v8 Stage A term that refers to the staging of a thymic epithelial neoplasm, following the rules of the TNM AJCC v8 classification system. This staging system applies to thymomas, thymic carcinomas, thymic neuroendocrine tumors, and combined thymic carcinomas. (from AJCC 8th Ed.) MONDO:0018079
MONDO:0854045 pleural malignant mesothelioma by ajcc v7 stage NCIT:C136374 MONDO:equivalentTo Pleural Malignant Mesothelioma by AJCC v7 Stage A term that refers to the staging of pleural malignant mesothelioma, following the rules of the TNM AJCC v7 classification system. MONDO:0005112
MONDO:0854046 pleural malignant mesothelioma by ajcc v8 stage NCIT:C136399 MONDO:equivalentTo Pleural Malignant Mesothelioma by AJCC v8 Stage A term that refers to the staging of pleural malignant mesothelioma, following the rules of the TNM AJCC v8 classification system. This staging system applies to pleural diffuse malignant mesothelioma only. Localized pleural malignant mesotheliomas and other primary tumors of the pleura are not staged using this staging system. (from AJCC 8th Ed.) MONDO:0005112
MONDO:0854048 lung cancer by ajcc v8 stage NCIT:C136467 MONDO:equivalentTo Lung Cancer by AJCC v8 Stage A term that refers to the staging of lung cancer, following the rules of the TNM AJCC v8 classification system. This staging system derives from analyses of the new retrospective and prospective databases of the International Association for the Study of Lung Cancer (IASLC). These databases contain information on patients diagnosed with lung cancer from 1999 to 2010 originating from 35 different databases in 16 countries around the world. This staging system applies to carcinomas of the lung, including non-small cell and small cell carcinomas, and bronchopulmonary carcinoid tumors. It does not apply to sarcomas or other rare tumors of the lung. (from AJCC 8th Ed.) MONDO:0005138
MONDO:0854057 bone cancer by ajcc v7 stage NCIT:C136610 MONDO:equivalentTo Bone Cancer by AJCC v7 Stage A term that refers to the staging of bone cancer, following the rules of the TNM AJCC v7 classification system. MONDO:0002129
MONDO:0854058 bone cancer by ajcc v8 stage NCIT:C136612 MONDO:equivalentTo Bone Cancer by AJCC v8 Stage A term that refers to the staging of appendicular skeleton, trunk, skull, and facial bones cancer, following the rules of the TNM AJCC v8 classification system. This staging system applies to osteosarcoma, chondrosarcoma, Ewing sarcoma, spindle cell sarcoma, hemangioendothelioma, angiosarcoma, fibrosarcoma/myofibroid sarcoma, chordoma, adamantinoma, and other cancers arising in the bone. It does not apply to primary malignant lymphoma of the bone and multiple myeloma. There are no AJCC prognostic stage groupings for spine and pelvis. (from AJCC 8th Ed.) MONDO:0002129
MONDO:0854060 soft tissue sarcoma by ajcc v8 stage NCIT:C136693 MONDO:equivalentTo Soft Tissue Sarcoma by AJCC v8 Stage A term that refers to the staging of soft tissue sarcoma, following the rules of the TNM AJCC v8 classification system. MONDO:0018078
MONDO:0854061 soft tissue sarcoma by ajcc v7 stage NCIT:C136707 MONDO:equivalentTo Soft Tissue Sarcoma by AJCC v7 Stage A term that refers to the staging of soft tissue sarcoma, following the rules of the TNM AJCC v7 classification system. MONDO:0018078
MONDO:0854062 uterine corpus sarcoma by ajcc v7 stage NCIT:C136708 MONDO:equivalentTo Uterine Corpus Sarcoma by AJCC v7 Stage A term that refers to the staging of uterine corpus sarcoma, following the rules of the TNM AJCC v7 classification system. MONDO:0005210
MONDO:0854063 invasive lung mucinous adenocarcinoma NCIT:C136709 MONDO:equivalentTo Invasive Lung Mucinous Adenocarcinoma An invasive adenocarcinoma that arises from the lung. It is characterized by the presence of tall columnar cells and mucin production. This category refers to cases formerly classified as mucinous bronchioloalveolar carcinoma, excluding cases that meet the criteria for adenocarcinoma in situ or mucinous minimally invasive adenocarcinoma. MONDO:0040677
MONDO:0854064 lung enteric adenocarcinoma NCIT:C136710 MONDO:equivalentTo Lung Enteric Adenocarcinoma A well-differentiated adenocarcinoma located in the lung periphery. It resembles colorectal adenocarcinoma with acinar and/or cribriform architecture and papillotubular structures. MONDO:0006254
MONDO:0854065 lung keratinizing squamous cell carcinoma NCIT:C136713 MONDO:equivalentTo Lung Keratinizing Squamous Cell Carcinoma A squamous cell lung carcinoma characterized by the presence of keratinization, pearl formation, and/or intercellular bridges. MONDO:0005097
MONDO:0854066 lung non-keratinizing squamous cell carcinoma NCIT:C136714 MONDO:equivalentTo Lung Non-Keratinizing Squamous Cell Carcinoma A squamous cell lung carcinoma characterized by the absence of keratinization, pearl formation, and intercellular bridges. MONDO:0005097
MONDO:0854067 lung non-mucinous adenocarcinoma in situ NCIT:C136716 MONDO:equivalentTo Lung Non-Mucinous Adenocarcinoma In Situ Lung adenocarcinoma in situ characterized by the presence of type II pneumocyte and/or Clara cell differentiation. Almost all cases of lung adenocarcinoma in situ are non-mucinous. MONDO:0000503
MONDO:0854068 lung mucinous adenocarcinoma in situ NCIT:C136717 MONDO:equivalentTo Lung Mucinous Adenocarcinoma In Situ A very rare lung adenocarcinoma in situ variant characterized by the presence of tall columnar cells with basal nuclei and abundant cytoplasmic mucin. MONDO:0000503
MONDO:0854069 lung squamous cell carcinoma in situ NCIT:C136719 MONDO:equivalentTo Lung Squamous Cell Carcinoma In Situ A preinvasive bronchial neoplastic lesion affecting the squamous epithelium. It is characterized by the absence of progression of maturation from base to luminal surface, basilar zone expansion with cellular crowding throughout the epithelium, absence of the intermediate zone, and surface flattening confined to the most superficial cells. The nuclear-to-cytoplasmic ratio is often high and variable, the chromatin is coarse and uneven, and mitotic figures are present through full thickness. The cell size may be markedly increased. Anisocytosis and pleomorphism may be present. (Adapted from WHO, 2015) MONDO:0005097
MONDO:0854075 cutaneous melanoma by ajcc v8 stage NCIT:C137645 MONDO:equivalentTo Cutaneous Melanoma by AJCC v8 Stage A term that refers to the staging of cutaneous melanoma, following the rules of the TNM AJCC v8 classification system. This staging system does not apply to melanoma of the conjunctiva, melanoma of the uvea, mucosal melanoma arising in the head and neck, and mucosal melanoma of the urethra, vagina, rectum, and anus. (from AJCC 8th Ed.) MONDO:0005012
MONDO:0854076 occult breast carcinoma NCIT:C137674 MONDO:equivalentTo Occult Breast Carcinoma Breast carcinoma presenting with isolated axillary lymphadenopathy, without clinical or mammographic evidence of breast tumor. MONDO:0004989
MONDO:0854077 breast pleomorphic lobular carcinoma in situ NCIT:C137839 MONDO:equivalentTo Breast Pleomorphic Lobular Carcinoma In Situ Breast lobular carcinoma in situ characterized by the presence of neoplastic large cells with marked nuclear pleomorphism. MONDO:0006270
MONDO:0854089 prostate carcinoma by gene expression profile NCIT:C138167 MONDO:equivalentTo Prostate Carcinoma by Gene Expression Profile A header term that includes the following prostate carcinoma subtypes determined by gene expression profiling: luminal A prostate carcinoma, luminal B prostate carcinoma, and basal-like prostate carcinoma. MONDO:0005159
MONDO:0854090 duodenal-type follicular lymphoma NCIT:C138185 MONDO:equivalentTo Duodenal-Type Follicular Lymphoma A localized low-grade follicular lymphoma within the gastrointestinal tract, which is distinct from other gastrointestinal tract follicular lymphomas. It has features that overlap with in situ follicular neoplasia as well as some features resembling an extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue. The prognosis is excellent. MONDO:0018906
MONDO:0854092 high grade b-cell lymphoma with myc and bcl2 and/or bcl6 rearrangements NCIT:C138195 MONDO:equivalentTo High Grade B-Cell Lymphoma with MYC and BCL2 and/or BCL6 Rearrangements High-grade B-cell lymphoma characterized by the abnormal rearrangement of MYC gene, BCL2 gene, and/or BCL6 gene. Patients with this type of lymphoma usually respond poorly to standard treatments and have a poor prognosis. MONDO:0044889
MONDO:0854094 double-expressor lymphoma NCIT:C138899 MONDO:equivalentTo Double-Expressor Lymphoma A diffuse large B-cell lymphoma characterized by double expression of MYC and BCL2 proteins without MYC and BCL2 gene aberrations. These lymphomas may have a worse prognosis than other diffuse large B-cell lymphomas, not otherwise specified, but they are not as aggressive as the high-grade B-cell lymphomas, with rearrangements of MYC and BCL2 and/or BCL6 genes. MONDO:0018905
MONDO:0854097 follicular helper t-cell lymphoma NCIT:C139005 MONDO:equivalentTo Follicular Helper T-Cell Lymphoma A group of node-based peripheral T-cell lymphomas with phenotypic features of T follicular helper (TFH) cells. This category includes the following: follicular helper T-cell lymphoma, angioimmunoblastic-type; follicular helper T-cell lymphoma, follicular-type; and follicular helper T-cell lymphoma, not otherwise specified. MONDO:0000430
MONDO:0854098 multiple myeloma myeloma by ds stage NCIT:C139008 MONDO:equivalentTo Multiple Myeloma Myeloma by DS Stage A header term that refers to the staging of multiple myeloma according to the Durie/Salmon staging system. MONDO:0009693
MONDO:0854099 multiple myeloma by iss stage NCIT:C139009 MONDO:equivalentTo Multiple Myeloma by ISS Stage A header term that refers to the staging of multiple myeloma according to the International Staging System. MONDO:0009693
MONDO:0854100 type d lymphomatoid papulosis NCIT:C139014 MONDO:equivalentTo Type D Lymphomatoid Papulosis A variant of lymphomatoid papulosis which mimics primary cutaneous aggressive epidermotropic CD8-positive cytotoxic T-cell lymphoma. MONDO:0020326
MONDO:0854101 type e lymphomatoid papulosis NCIT:C139015 MONDO:equivalentTo Type E Lymphomatoid Papulosis A variant of lymphomatoid papulosis characterized by the presence of atypical lymphocytes which exhibited distinct angioinvasion. MONDO:0020326
MONDO:0854102 lymphomatoid papulosis with dusp22-irf4 gene rearrangement NCIT:C139017 MONDO:equivalentTo Lymphomatoid Papulosis with DUSP22-IRF4 Gene Rearrangement A variant of lymphomatoid papulosis associated with chromosomal rearrangements involving the DUSP22-IRF4 locus at 6p25.3. MONDO:0020326
MONDO:0854105 breast cancer by ajcc v8 stage NCIT:C139532 MONDO:equivalentTo Breast Cancer by AJCC v8 Stage A term that refers to the staging of breast cancer, following the rules of the TNM AJCC v8 classification system. It applies to invasive (infiltrating) carcinoma of the breast and ductal carcinoma in situ of the breast. It does not apply to breast sarcoma, phyllodes tumor, and breast lymphoma. (from AJCC 8th Ed.) MONDO:0004989
MONDO:0854108 fibroadenoma of anogenital mammary-type glands NCIT:C139547 MONDO:equivalentTo Fibroadenoma of Anogenital Mammary-Type Glands A benign epithelial-stromal neoplasm that arises from the perineum and resembles the breast fibroadenoma. MONDO:0000383
MONDO:0854109 vulvar composite hidradenoma papilliferum and fibroadenoma NCIT:C139548 MONDO:equivalentTo Vulvar Composite Hidradenoma Papilliferum and Fibroadenoma A benign composite neoplasm that arises from the vulva and is characterized by mixed histopathologic features of hidradenoma papilliferum and fibroadenoma. MONDO:0021043
MONDO:0854111 vulvar cancer by ajcc v8 stage NCIT:C139618 MONDO:equivalentTo Vulvar Cancer by AJCC v8 Stage A term that refers to the staging of vulvar cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to all carcinomas of the vulva. Melanoma of the vulva is staged according to the classification for melanoma of the skin. (AJCC 8th Ed.) MONDO:0005215
MONDO:0854112 vaginal cancer by ajcc v8 stage NCIT:C139657 MONDO:equivalentTo Vaginal Cancer by AJCC v8 Stage A term that refers to the staging of vaginal cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to all carcinomas of the vagina. There is no AJCC staging system for mucosal melanoma of the vagina. (from AJCC 8th Ed.) MONDO:0015867
MONDO:0854113 cervical cancer by ajcc v8 stage NCIT:C139733 MONDO:equivalentTo Cervical Cancer by AJCC v8 Stage A term that refers to the staging of cervical cancer according to the American Joint Committee on Cancer, 8th edition. MONDO:0005131
MONDO:0854114 uterine corpus cancer by ajcc v8 stage NCIT:C139801 MONDO:equivalentTo Uterine Corpus Cancer by AJCC v8 Stage A term that refers to the staging of uterine corpus cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to carcinomas and carcinosarcomas. It does not apply to uterine corpus sarcomas: leiomyosarcomas, endometrial stromal sarcomas, and adenosarcomas. These sarcomas are staged according to the classification for uterine corpus sarcomas. (from AJCC 8th Ed.) MONDO:0006003
MONDO:0854115 uterine corpus sarcoma by ajcc v8 stage NCIT:C139869 MONDO:equivalentTo Uterine Corpus Sarcoma by AJCC v8 Stage A term that refers to the staging of uterine corpus sarcoma according to the American Joint Committee on Cancer, 8th edition. This staging system applies to leiomyosarcomas, endometrial stromal sarcomas, and adenosarcomas of the uterine corpus. It does not apply to carcinosarcomas which are staged according to the carcinomas and carcinosarcomas of the uterine corpus. (from AJCC 8th Ed.) MONDO:0005210
MONDO:0854119 ovarian cancer by ajcc v8 stage NCIT:C139963 MONDO:equivalentTo Ovarian Cancer by AJCC v8 Stage A term that refers to the staging of ovarian cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to ovarian carcinomas. Nonepithelial primary ovarian cancers may be staged using this classification but should be reported separately. (from AJCC 8th Ed.) MONDO:0005140
MONDO:0854120 fallopian tube cancer by ajcc v8 stage NCIT:C139983 MONDO:equivalentTo Fallopian Tube Cancer by AJCC v8 Stage A term that refers to the staging of fallopian tube cancer according to the American Joint Committee on Cancer, 8th edition. MONDO:0006206
MONDO:0854121 primary peritoneal cancer by ajcc v7 stage NCIT:C140003 MONDO:equivalentTo Primary Peritoneal Cancer by AJCC v7 Stage A term that refers to the staging of primary peritoneal cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0015686
MONDO:0854122 primary peritoneal cancer by ajcc v8 stage NCIT:C140004 MONDO:equivalentTo Primary Peritoneal Cancer by AJCC v8 Stage A term that refers to the staging of primary peritoneal cancer according to the American Joint Committee on Cancer, 8th edition. MONDO:0015686
MONDO:0854123 gestational trophoblastic tumor by ajcc v7 stage NCIT:C140032 MONDO:equivalentTo Gestational Trophoblastic Tumor by AJCC v7 Stage A term that refers to the staging of gestational trophoblastic tumor according to the American Joint Committee on Cancer, 7th edition. MONDO:0018944
MONDO:0854124 penile cancer by ajcc v8 stage NCIT:C140075 MONDO:equivalentTo Penile Cancer by AJCC v8 Stage A term that refers to the staging of penile cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to penile squamous cell carcinoma and associated histologic subtypes. It does not apply to urethral carcinomas, sarcomas, and melanomas. (from AJCC 8th Ed.) MONDO:0006360
MONDO:0854125 prostate cancer by ajcc v8 stage NCIT:C140163 MONDO:equivalentTo Prostate Cancer by AJCC v8 Stage A term that refers to the staging of prostate cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to adenocarcinomas and squamous cell carcinomas of the prostate gland. It does not apply to sarcomas, urothelial cell carcinomas, and urothelial carcinoma of bladder involving prostate. (from AJCC 8th Ed.) MONDO:0005159
MONDO:0854126 testicular cancer by ajcc v8 stage NCIT:C140225 MONDO:equivalentTo Testicular Cancer by AJCC v8 Stage A term that refers to the staging of testicular cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to postpubertal germ cell tumors of the testis and malignant sex cord-stromal tumors of the testis. It does not apply to spermatocytic tumors (no AJCC staging system), nonmalignant sex cord-/gonadal -stromal tumors (no AJCC staging system), prepubertal germ cell tumors (no AJCC staging system), hematolymphoid tumors (hematologic malignancies staging system), and paratesticular neoplasms (no AJCC staging system). (from AJCC 8th Ed.) MONDO:0005447
MONDO:0854127 testicular cancer by ajcc v6 and v7 stage NCIT:C140241 MONDO:equivalentTo Testicular Cancer by AJCC v6 and v7 Stage A term that refers to the staging of testicular cancer according to the American Joint Committee on Cancer, 6th and 7th editions. MONDO:0005447
MONDO:0854128 renal cell cancer by ajcc v8 stage NCIT:C140322 MONDO:equivalentTo Renal Cell Cancer by AJCC v8 Stage A term that refers to the staging of kidney cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to carcinomas arising in the kidney. It does not apply to urothelial carcinomas (are staged according to the classification for renal pelvis and ureter), lymphomas (are staged according to the classification for Hodgkin and non-Hodgkin lymphoma), sarcomas (are staged according to the classification for soft tissue sarcoma of the abdomen and thoracic visceral organs), and Wilms tumor (no AJCC staging system). (from AJCC 8th Ed.) MONDO:0005549
MONDO:0854130 renal pelvis and ureter cancer by ajcc v8 stage NCIT:C140355 MONDO:equivalentTo Renal Pelvis and Ureter Cancer by AJCC v8 Stage A term that refers to the staging of renal pelvis and ureter cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to renal pelvis and ureter urothelial (transitional cell) carcinoma, including histologic variants micropapillary and nested subtypes. It does not apply to renal cell carcinomas (are staged according to the classification for kidney), renal medullary carcinomas (are staged according to the classification for kidney), collecting duct carcinomas (are staged according to the classification for kidney), lymphomas (are staged according to the classification for Hodgkin and non-Hodgkin lymphoma), and mesenchymal tumors (are staged according to the classification for soft tissue sarcoma of the abdomen and thoracic visceral organs). (from AJCC 8th Ed.) MONDO:0020654
MONDO:0854134 renal pelvis and ureter cancer by ajcc v7 stage NCIT:C140376 MONDO:equivalentTo Renal Pelvis and Ureter Cancer by AJCC v7 Stage A term that refers to the staging of renal pelvis and ureter cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0020654
MONDO:0854137 bladder cancer by ajcc v8 stage NCIT:C140416 MONDO:equivalentTo Bladder Cancer by AJCC v8 Stage A term that refers to the staging of bladder cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to carcinomas arising in the bladder. The typical carcinoma of the bladder is urothelial carcinoma. These carcinomas may include other histologic elements, including adenocarcinoma, squamous cell carcinoma, and small cell neuroendocrine carcinoma, but should be classified as urothelial unless the cancer is composed entirely of the alternative histology. All histologic cell types that are derived primarily from the urinary bladder epithelium should follow this staging system. It does not apply to prostatic urothelial carcinomas (are staged according to the classification for urethra), lymphomas (are staged according to the classification for Hodgkin and non-Hodgkin lymphoma), and sarcomas (are staged according to the classification for soft tissue sarcoma of the abdomen and thoracic visceral organs). (from AJCC 8th Ed.) MONDO:0004986
MONDO:0854139 urethral cancer by ajcc v8 stage NCIT:C140457 MONDO:equivalentTo Urethral Cancer by AJCC v8 Stage A term that refers to the staging of urethral cancer according to the American Joint Committee on Cancer, 8th edition. This staging system applies to urothelial (transitional cell), squamous, and glandular carcinomas of the urethra and to urothelial (transitional cell) carcinomas of the prostate and prostatic urethra. It does not apply to squamous cell carcinomas of the penile foreskin (are staged according to the classification for penis), primary urothelial carcinomas of the bladder with transmural involvement of the prostate (are staged according to the classification for urinary bladder), prostatic adenocarcinomas (are staged according to the classification for prostate), mucosal melanomas of the urethra (no AJCC staging system), lymphomas (are staged according to the classification for Hodgkin and non-Hodgkin lymphoma), and sarcomas (are staged according to the classification for soft tissue sarcoma of the abdomen and thoracic visceral organs). (from AJCC 8th Ed.) MONDO:0021327
MONDO:0854141 urethral cancer by ajcc v7 stage NCIT:C140464 MONDO:equivalentTo Urethral Cancer by AJCC v7 Stage A term that refers to the staging of urethral cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0021327
MONDO:0854142 eyelid carcinoma by ajcc v7 stage NCIT:C140511 MONDO:equivalentTo Eyelid Carcinoma by AJCC v7 Stage A term that refers to the staging of eyelid carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0003876
MONDO:0854143 eyelid carcinoma by ajcc v8 stage NCIT:C140513 MONDO:equivalentTo Eyelid Carcinoma by AJCC v8 Stage A term that refers to the staging of eyelid carcinoma according to the American Joint Committee on Cancer, 8th edition. This staging system applies to all primary carcinomas of the eyelid, including basal cell carcinoma (BCC), squamous cell carcinoma (SCC), sebaceous carcinoma, and other rare carcinomas, such as all varieties of sweat gland carcinoma (e.g., eccrine carcinoma). It does not apply to carcinomas of the head and neck with direct extension to eyelid (are staged according to the cutaneous squamous cell carcinomas of the head and neck), Merkel cell carcinomas of the eyelid (are staged according to the classification for Merkel cell carcinomas), and melanomas of the eyelid (are staged according to the classification for melanomas of the skin). (from AJCC 8th Ed.) MONDO:0003876
MONDO:0854144 choroidal and ciliary body melanoma by ajcc v8 stage NCIT:C140659 MONDO:equivalentTo Choroidal and Ciliary Body Melanoma by AJCC v8 Stage A term that refers to the staging of choroidal and ciliary body melanoma, following the rules of the TNM AJCC v8 classification system. MONDO:0006486
MONDO:0854145 uveal melanoma by ajcc v7 stage NCIT:C140672 MONDO:equivalentTo Uveal Melanoma by AJCC v7 Stage A term that refers to the staging of uveal melanoma, following the rules of the TNM AJCC v7 classification system. MONDO:0006486
MONDO:0854146 retinoblastoma by ajcc v8 stage NCIT:C140750 MONDO:equivalentTo Retinoblastoma by AJCC v8 Stage A term that refers to the staging of retinoblastoma according to the American Joint Committee on Cancer, 8th edition. This staging system does not apply to central nervous system component of "trilateral retinoblastoma" (is staged according to the classification for brain and spinal cord), retinoma (or retinocytoma) (no AJCC staging system), and medulloepithelioma (no AJCC staging system). (from AJCC 8th Ed.) MONDO:0008380
MONDO:0854148 differentiated thyroid gland carcinoma by ajcc v7 stage NCIT:C140959 MONDO:equivalentTo Differentiated Thyroid Gland Carcinoma by AJCC v7 Stage A term that refers to the staging of differentiated thyroid gland carcinoma, following the rules of the TNM AJCC v7 classification system. MONDO:0015447
MONDO:0854150 differentiated thyroid gland carcinoma by ajcc v8 stage NCIT:C140965 MONDO:equivalentTo Differentiated Thyroid Gland Carcinoma by AJCC v8 Stage A term that refers to the staging of differentiated thyroid gland carcinoma, following the rules of the TNM AJCC v8 classification system. MONDO:0015447
MONDO:0854153 thyroid gland anaplastic carcinoma by ajcc v7 stage NCIT:C140999 MONDO:equivalentTo Thyroid Gland Anaplastic Carcinoma by AJCC v7 Stage A term that refers to the staging of thyroid gland anaplastic carcinoma, following the rules of the TNM AJCC v7 classification system. MONDO:0006468
MONDO:0854154 thyroid gland anaplastic carcinoma by ajcc v8 stage NCIT:C141000 MONDO:equivalentTo Thyroid Gland Anaplastic Carcinoma by AJCC v8 Stage A term that refers to the staging of thyroid gland anaplastic carcinoma, following the rules of the TNM AJCC v8 classification system. MONDO:0006468
MONDO:0854155 thyroid gland medullary carcinoma by ajcc v7 stage NCIT:C141041 MONDO:equivalentTo Thyroid Gland Medullary Carcinoma by AJCC v7 Stage A term that refers to the staging of thyroid gland medullary carcinoma, following the rules of the TNM AJCC v7 classification system. MONDO:0015277
MONDO:0854156 thyroid gland medullary carcinoma by ajcc v8 stage NCIT:C141042 MONDO:equivalentTo Thyroid Gland Medullary Carcinoma by AJCC v8 Stage A term that refers to the staging of thyroid gland medullary carcinoma, following the rules of the TNM AJCC v8 classification system. Differentiated and anaplastic thyroid gland carcinomas are staged according to the classification for thyroid-differentiated and anaplastic carcinoma. (from AJCC 8th Ed.) MONDO:0015277
MONDO:0854157 adrenal cortical carcinoma by ajcc v7 stage NCIT:C141098 MONDO:equivalentTo Adrenal Cortical Carcinoma by AJCC v7 Stage A term that refers to the staging of adrenal cortical carcinoma, following the rules of the TNM AJCC v7 classification system. MONDO:0006639
MONDO:0854158 adrenal cortical carcinoma by ajcc v8 stage NCIT:C141100 MONDO:equivalentTo Adrenal Cortical Carcinoma by AJCC v8 Stage A term that refers to the staging of adrenal cortical carcinoma, following the rules of the TNM AJCC v8 classification system. Adrenal medullary pheochromocytoma is staged according to the classification for adrenal neuroendocrine tumors. There is no AJCC staging system for neuroblastic tumors of the adrenal gland. (from AJCC 8th Ed.) MONDO:0006639
MONDO:0854159 adrenal gland pheochromocytoma and sympathetic paraganglioma by ajcc v8 stage NCIT:C141128 MONDO:equivalentTo Adrenal Gland Pheochromocytoma and Sympathetic Paraganglioma by AJCC v8 Stage A term that refers to the staging of adrenal gland pheochromocytoma and sympathetic paraganglioma, following the rules of the TNM AJCC v8 classification system. Parasympathetic paragangliomas are not staged because they are largely benign. This staging system does not apply to neuroendocrine tumors of the pancreas (are staged according to the classification for neuroendocrine tumors of the pancreas) and carotid body tumors (not staged). (from AJCC 8th Ed.) MONDO:0021072
MONDO:0854166 chronic lymphocytic leukemia- modified rai staging system NCIT:C141206 MONDO:equivalentTo Chronic Lymphocytic Leukemia- Modified Rai Staging System A term that refers to the staging of chronic lymphocytic leukemia according to modified Rai staging system. This system is mainly used in North America. MONDO:0004948
MONDO:0854167 chronic lymphocytic leukemia- binet staging system NCIT:C141208 MONDO:equivalentTo Chronic Lymphocytic Leukemia- Binet Staging System A term that refers to the staging of chronic lymphocytic leukemia according to Binet staging system. This system is in wide use outside the United States. MONDO:0004948
MONDO:0854189 multiple myeloma by riss stage NCIT:C141393 MONDO:equivalentTo Multiple Myeloma by RISS Stage A staging system for multiple myeloma based on the Revised International Staging System (RISS) criteria. This staging system does not apply to smoldering multiple myeloma (no AJCC staging system), monoclonal gammopathy of undetermined significance (no AJCC staging system), and Waldenstrom macroglobulinemia (no AJCC staging system). (from AJCC 8th Ed.) MONDO:0009693
MONDO:0854192 thoracic nut carcinoma NCIT:C142781 MONDO:equivalentTo Thoracic NUT Carcinoma A highly aggressive, poorly differentiated carcinoma that arises from the thoracic structures. It is characterized by mutations and rearrangement of the NUT gene. It usually presents at an advanced stage with pleuritic chest pain and pleural effusion, non-productive cough, shortness of breath, and weigh loss. MONDO:0005563
MONDO:0854193 benign lung pecoma NCIT:C142784 MONDO:equivalentTo Benign Lung PEComa A benign lung tumor that arises from perivascular epithelioid cells (PECs). MONDO:0002732
MONDO:0854200 pulmonary artery intimal sarcoma NCIT:C142825 MONDO:equivalentTo Pulmonary Artery Intimal Sarcoma A sarcoma arising from the arterial intima of pulmonary arteries. MONDO:0006255
MONDO:0854201 primary pulmonary myxoid sarcoma with ewsr1-creb1 fusion NCIT:C142827 MONDO:equivalentTo Primary Pulmonary Myxoid Sarcoma with EWSR1-CREB1 Fusion A sarcoma that arises from the lung. It is related to a bronchus and is often predominantly endobronchial. It is characterized by the proliferation of round and spindle cells within a myxoid stroma. It is associated with the presence of an EWSR1::CREB1 fusion gene. MONDO:0002426
MONDO:0854212 refractory rhabdoid tumor NCIT:C142858 MONDO:equivalentTo Refractory Rhabdoid Tumor Rhabdoid tumor that does not respond to treatment. MONDO:0002728
MONDO:0854225 atypical type a thymoma NCIT:C146640 MONDO:equivalentTo Atypical Type A Thymoma A rare type A thymoma displaying atypical features (hypercellularity, increased mitotic activity, and focal necrosis). MONDO:0002588
MONDO:0854227 thymic hepatoid adenocarcinoma NCIT:C146717 MONDO:equivalentTo Thymic Hepatoid Adenocarcinoma A very rare adenocarcinoma arising from the thymus. It is characterized by the presence of malignant polygonal cells resembling hepatocytes. MONDO:0006243
MONDO:0854229 malignant mediastinal germ cell tumor stage grouping of the pediatric study group NCIT:C146848 MONDO:equivalentTo Malignant Mediastinal Germ Cell Tumor Stage Grouping of the Pediatric Study Group A term that refers to the staging of mediastinal malignant germ cell tumors according to the Pediatric Study Group staging criteria. This staging system is not an official UICC TNM classification. (WHO Classification of Tumors of the Lung, Pleura, Thymus and Heart, 2015) MONDO:0006298
MONDO:0854230 metastatic epithelioid hemangioendothelioma NCIT:C146858 MONDO:equivalentTo Metastatic Epithelioid Hemangioendothelioma An epithelioid hemangioendothelioma that has spread from its original site of growth to another anatomic site. MONDO:0015523
MONDO:0854231 mediastinal mixed germ cell tumor NCIT:C146861 MONDO:equivalentTo Mediastinal Mixed Germ Cell Tumor A malignant germ cell tumor that arises from the mediastinum. It is characterized by the presence of at least two different germ cell tumor components. The different germ cell tumor components include choriocarcinoma, embryonal carcinoma, yolk sac tumor, teratoma, and seminoma. MONDO:0006298
MONDO:0854234 mediastinal epithelioid hemangioendothelioma NCIT:C146988 MONDO:equivalentTo Mediastinal Epithelioid Hemangioendothelioma An epithelioid hemangioendothelioma that arises from the mediastinum. MONDO:0037743
MONDO:0854235 cardiac extraskeletal osteosarcoma NCIT:C147003 MONDO:equivalentTo Cardiac Extraskeletal Osteosarcoma An extraskeletal osteosarcoma that arises from the heart. It produces osteoid and bone, and occasionally shows chondroblastic differentiation. MONDO:0002621
MONDO:0854236 cardiac myxofibrosarcoma NCIT:C147004 MONDO:equivalentTo Cardiac Myxofibrosarcoma A low-grade sarcoma that arises from the heart. It is composed of spindle or rounded cells in a myxoid stroma. The most common location is the left atrium. MONDO:0019202
MONDO:0854237 cardiac yolk sac tumor NCIT:C147006 MONDO:equivalentTo Cardiac Yolk Sac Tumor A yolk sac tumor that arises within the myocardium or cardiac chambers. MONDO:0001991
MONDO:0854242 pericardial sarcoma NCIT:C147098 MONDO:equivalentTo Pericardial Sarcoma A rare sarcoma that arises from the pericardium. The two most common types are angiosarcoma and synovial sarcoma. Patients present with symptoms related to pericardial effusion. MONDO:0018078
MONDO:0854249 recurrent lymphoproliferative disorder NCIT:C147861 MONDO:equivalentTo Recurrent Lymphoproliferative Disorder The reemergence of a lymphoproliferative disorder after a period of remission.
MONDO:0854250 oropharyngeal p16ink4a-negative squamous cell carcinoma NCIT:C147906 MONDO:equivalentTo Oropharyngeal p16INK4a-Negative Squamous Cell Carcinoma An oropharyngeal squamous cell carcinoma which is negative for p16INK4a by immunohistochemistry. This negative immunohistochemistry result does not exclude human papillomavirus infection. MONDO:0044704
MONDO:0854251 central nervous system b-cell non-hodgkin lymphoma NCIT:C147948 MONDO:equivalentTo Central Nervous System B-Cell Non-Hodgkin Lymphoma A B-cell non-Hodgkin lymphoma that arises from the brain, meninges, or spinal cord. MONDO:0015759
MONDO:0854253 refractory melanoma NCIT:C147983 MONDO:equivalentTo Refractory Melanoma Melanoma that does not respond to treatment. MONDO:0036501
MONDO:0854268 refractory round cell liposarcoma NCIT:C148299 MONDO:equivalentTo Refractory Round Cell Liposarcoma Round cell liposarcoma that does not respond to treatment. MONDO:0005238
MONDO:0854269 metastatic round cell liposarcoma NCIT:C148300 MONDO:equivalentTo Metastatic Round Cell Liposarcoma Round cell liposarcoma that has spread to other anatomic sites. MONDO:0005238
MONDO:0854270 refractory sarcoma NCIT:C148301 MONDO:equivalentTo Refractory Sarcoma A sarcoma that does not respond to treatment. MONDO:0036501
MONDO:0854284 refractory leukemia NCIT:C148426 MONDO:equivalentTo Refractory Leukemia Leukemia that is resistant to treatment. MONDO:0005059
MONDO:0854293 castration-naive prostate carcinoma NCIT:C148536 MONDO:equivalentTo Castration-Naive Prostate Carcinoma Advanced prostatic carcinoma which was not previously treated with androgen-deprivation therapy. MONDO:0004956
MONDO:0854294 thoracic esophagus adenocarcinoma NCIT:C150027 MONDO:equivalentTo Thoracic Esophagus Adenocarcinoma An adenocarcinoma that arises from the thoracic esophagus. MONDO:0005028
MONDO:0854295 thoracic esophagus squamous cell carcinoma NCIT:C150029 MONDO:equivalentTo Thoracic Esophagus Squamous Cell Carcinoma A squamous cell carcinoma that arises from the thoracic esophagus. MONDO:0005580
MONDO:0854296 cervical esophagus adenocarcinoma NCIT:C150031 MONDO:equivalentTo Cervical Esophagus Adenocarcinoma An adenocarcinoma that arises from the cervical esophagus. MONDO:0021326
MONDO:0854297 cervical esophagus squamous cell carcinoma NCIT:C150032 MONDO:equivalentTo Cervical Esophagus Squamous Cell Carcinoma A squamous cell carcinoma that arises from the cervical esophagus. MONDO:0021326
MONDO:0854298 gastric cardia squamous cell carcinoma NCIT:C150034 MONDO:equivalentTo Gastric Cardia Squamous Cell Carcinoma A squamous cell carcinoma that arises from the gastric cardia. MONDO:0003834
MONDO:0854317 high risk neuroblastoma NCIT:C150281 MONDO:equivalentTo High Risk Neuroblastoma Neuroblastoma usually presenting with metastatic disease and MYCN gene amplifications. MONDO:0005072
MONDO:0854322 hhv8-related lymphoproliferative disorder NCIT:C150399 MONDO:equivalentTo HHV8-Related Lymphoproliferative Disorder A lymphoproliferative disorder caused by the human herpesvirus 8 (HHV8). This category includes the following: HHV8-positive multicentric Castleman disease; HHV8-positive diffuse large B-cell lymphoma, not otherwise specified; primary effusion lymphoma; and germinotropic lymphoproliferative disorders.
MONDO:0854323 hhv8-positive multicentric castleman disease NCIT:C150404 MONDO:equivalentTo HHV8-Positive Multicentric Castleman Disease Multicentric Castleman disease associated with HHV8 infection.
MONDO:0854324 extracavitary primary effusion lymphoma NCIT:C150406 MONDO:equivalentTo Extracavitary Primary Effusion Lymphoma A rare HHV8-positive B-cell lymphoma indistinguishable from primary effusion lymphoma presenting as solid tumor mass. (WHO 2017) MONDO:0018842
MONDO:0854325 body cavity primary effusion lymphoma NCIT:C150407 MONDO:equivalentTo Body Cavity Primary Effusion Lymphoma A large B-cell lymphoma presenting as a serous effusion without detectable tumor masses. It is universally associated with human herpes virus 8 (HHV8), also called Kaposi sarcoma-associated herpesvirus. It mostly occurs in the setting of immunodeficiency. The most common sites of involvement are the pleural, pericardial, and peritoneal cavities. (WHO 2017) MONDO:0018842
MONDO:0854332 refractory malignant bone neoplasm NCIT:C150525 MONDO:equivalentTo Refractory Malignant Bone Neoplasm Malignant bone neoplasm that is resistant to treatment. MONDO:0002129
MONDO:0854334 refractory malignant female reproductive system neoplasm NCIT:C150527 MONDO:equivalentTo Refractory Malignant Female Reproductive System Neoplasm Malignant female reproductive system neoplasm that is resistant to treatment. MONDO:0001416
MONDO:0854335 refractory malignant neoplasm of multiple primary sites NCIT:C150529 MONDO:equivalentTo Refractory Malignant Neoplasm of Multiple Primary Sites Malignant neoplasm of multiple primary sites that is resistant to treatment. MONDO:0036501
MONDO:0854339 refractory malignant male reproductive system neoplasm NCIT:C150534 MONDO:equivalentTo Refractory Malignant Male Reproductive System Neoplasm Malignant male reproductive system neoplasm that is resistant to treatment. MONDO:0005836
MONDO:0854340 refractory malignant mesothelioma NCIT:C150535 MONDO:equivalentTo Refractory Malignant Mesothelioma Malignant mesothelioma that is resistant to treatment. MONDO:0006292
MONDO:0854342 refractory malignant soft tissue neoplasm NCIT:C150537 MONDO:equivalentTo Refractory Malignant Soft Tissue Neoplasm Malignant soft tissue neoplasm that is resistant to treatment. MONDO:0024637
MONDO:0854345 refractory malignant endocrine neoplasm NCIT:C150541 MONDO:equivalentTo Refractory Malignant Endocrine Neoplasm Malignant endocrine neoplasm that is resistant to treatment. MONDO:0021069
MONDO:0854347 refractory malignant urinary system neoplasm NCIT:C150543 MONDO:equivalentTo Refractory Malignant Urinary System Neoplasm Malignant urinary system neoplasm that is resistant to treatment. MONDO:0006295
MONDO:0854349 refractory malignant skin neoplasm NCIT:C150546 MONDO:equivalentTo Refractory Malignant Skin Neoplasm Malignant skin neoplasm that is resistant to treatment. MONDO:0002898
MONDO:0854350 prostate adenocarcinoma without neuroendocrine differentiation NCIT:C150557 MONDO:equivalentTo Prostate Adenocarcinoma without Neuroendocrine Differentiation A prostate adenocarcinoma characterized by the absence of focal or diffuse neuroendocrine differentiation. MONDO:0005082
MONDO:0854351 igm monoclonal gammopathy of undetermined significance NCIT:C150566 MONDO:equivalentTo IgM Monoclonal Gammopathy of Undetermined Significance Monoclonal gammopathy of undetermined significance defined by a serum IgM paraprotein concentration less than 30g/L; bone marrow lymphoplasmacytic infiltration of less than 10%; and no evidence of anemia, constitutional symptoms, hyperviscocity, lymphadenopathy, hepatosplenomegaly, or other end-organ damage that can be attributed to the underlying lymphoproliferative disorder. It is a precursor condition that may progress to lymphoplasmacytic lymphoma/ Waldenstrom macroglobulinemia, other B-cell neoplasms, or primary amyloidosis. Progression to plasma cell myeloma occurs rarely, if at all. (WHO 2017) MONDO:0004225
MONDO:0854352 invasive bladder carcinoma NCIT:C150570 MONDO:equivalentTo Invasive Bladder Carcinoma A carcinoma that arises from the bladder mucosa and invades the bladder wall. MONDO:0004986
MONDO:0854353 localized cerebral neoplasm NCIT:C150573 MONDO:equivalentTo Localized Cerebral Neoplasm A cerebral neoplasm that is confined to a specific site without evidence of spread to other anatomic sites. MONDO:0021632
MONDO:0854358 non-igm monoclonal gammopathy of undetermined significance NCIT:C150588 MONDO:equivalentTo Non-IgM Monoclonal Gammopathy of Undetermined Significance Monoclonal gammopathy of undetermined significance defined by the presence in the serum of an IgG, IgA, or (rarely) IgD paraprotein at a concentration of less than 30g/L; clonal bone marrow plasma cells less than 10%; and absence of end-organ damage such as hypercalcemia, renal insufficiency, anemia, bone marrow lesions, and amyloidosis attributable to the plasma cell proliferative disorder. The risk of progression to plasma cell myeloma, light-chain amyloidosis, or a related disorder is 1% per year. (WHO 2017) MONDO:0004225
MONDO:0854359 testicular follicular lymphoma NCIT:C150589 MONDO:equivalentTo Testicular Follicular Lymphoma A distinctive variant of follicular lymphoma arising from the testis. It has been reported with higher frequency in children, but is also seen rarely in adults. It differs biologically from nodal follicular lymphoma because it lacks evidence of the BCL2 translocation. It is usually of high cytological grade, usually grade 3A, but has a good prognosis, even without additional therapy beyond surgical excision. (WHO 2017) MONDO:0001472
MONDO:0854363 metastatic malignant neoplasm in the viscera NCIT:C150597 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Viscera A malignant neoplasm which has spread from its original site of growth to any visceral site. MONDO:0024880
MONDO:0854365 resectable malignant neoplasm NCIT:C150602 MONDO:equivalentTo Resectable Malignant Neoplasm Malignant neoplasm that is amenable to surgical resection. MONDO:0004992
MONDO:0854374 immunodeficiency-related lymphoproliferative disorder NCIT:C150672 MONDO:equivalentTo Immunodeficiency-Related Lymphoproliferative Disorder A lymphoproliferative disorder that occurs in a patient with immunodeficiency.
MONDO:0854376 tumors derived from langerhans cells NCIT:C150692 MONDO:equivalentTo Tumors Derived from Langerhans Cells This category includes two main sub-groups, according to the degree of cytological atypia and clinical aggressiveness: Langerhans cell histiocytosis and Langerhans cell sarcoma. (WHO 2017) MONDO:0006247
MONDO:0854377 langerhans cell histiocytosis, monostotic NCIT:C150701 MONDO:equivalentTo Langerhans Cell Histiocytosis, Monostotic Langerhans cell histiocytosis presenting as a solitary lesion. MONDO:0018310
MONDO:0854378 langerhans cell histiocytosis, polyostotic NCIT:C150702 MONDO:equivalentTo Langerhans Cell Histiocytosis, Polyostotic Langerhans cell histiocytosis presenting with multiple sites of involvement. MONDO:0018310
MONDO:0854379 langerhans cell histiocytosis, disseminated NCIT:C150703 MONDO:equivalentTo Langerhans Cell Histiocytosis, Disseminated Langerhans cell histiocytosis presenting with disseminated disease. MONDO:0018310
MONDO:0854381 transformed non-hodgkin lymphoma NCIT:C151957 MONDO:equivalentTo Transformed Non-Hodgkin Lymphoma Histologic transformation of a usually indolent non-Hodgkin lymphoma to an aggressive non-Hodgkin lymphoma. MONDO:0018908
MONDO:0854382 acute leukemia of ambiguous lineage, not otherwise specified NCIT:C151975 MONDO:equivalentTo Acute Leukemia of Ambiguous Lineage, Not Otherwise Specified Acute leukemia of ambiguous lineage, expressing combinations of markers that do not allow for its classification as either acute undifferentiated leukemia or mixed phenotype acute leukemia, and definitive classification along a single lineage is difficult. (WHO 2017) MONDO:0019460
MONDO:0854385 abdominal rhabdomyosarcoma NCIT:C151982 MONDO:equivalentTo Abdominal Rhabdomyosarcoma Rhabdomyosarcoma involving the organs and structures in the abdomen. MONDO:0005212
MONDO:0854388 abdominal undifferentiated pleomorphic sarcoma NCIT:C151985 MONDO:equivalentTo Abdominal Undifferentiated Pleomorphic Sarcoma Undifferentiated pleomorphic sarcoma involving the organs and structures in the abdomen. MONDO:0002142
MONDO:0854389 mixed phenotype acute leukemia, rare types NCIT:C151990 MONDO:equivalentTo Mixed Phenotype Acute Leukemia, Rare Types A very rare mixed phenotype acute leukemia in which the blasts express combinations of B, T, myeloid, and megakaryocytic lineage markers but are negative for KMT2A rearrangement and t(9;22)(q34;q11.2) translocation. The prognosis is usually unfavorable. MONDO:0020743
MONDO:0854394 metastatic sarcoma NCIT:C152076 MONDO:equivalentTo Metastatic Sarcoma A sarcoma that has spread from its original site of growth to another anatomic site. MONDO:0005089
MONDO:0854395 refractory malignant head and neck neoplasm NCIT:C152078 MONDO:equivalentTo Refractory Malignant Head and Neck Neoplasm A malignant head and neck neoplasm that is resistant to treatment. MONDO:0005627
MONDO:0854414 refractory ewing sarcoma/peripheral primitive neuroectodermal tumor NCIT:C153286 MONDO:equivalentTo Refractory Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor A malignant small round cell tumor with or without neural differentiation that is resistant to treatment. MONDO:0021038
MONDO:0854420 metastatic chordoma NCIT:C153323 MONDO:equivalentTo Metastatic Chordoma A chordoma that has spread from its original site of growth to other anatomic sites. MONDO:0024880
MONDO:0854422 castration-sensitive prostate carcinoma NCIT:C153336 MONDO:equivalentTo Castration-Sensitive Prostate Carcinoma Metastatic prostatic carcinoma which is sensitive to androgen-deprivation therapy. MONDO:0004956
MONDO:0854468 sinonasal poorly differentiated carcinoma NCIT:C154324 MONDO:equivalentTo Sinonasal Poorly Differentiated Carcinoma A poorly differentiated carcinoma that arises from the nasal cavity and/or paranasal sinuses. MONDO:0056819
MONDO:0854469 densely granulated corticotroph pituitary neuroendocrine tumor NCIT:C154339 MONDO:equivalentTo Densely Granulated Corticotroph Pituitary Neuroendocrine Tumor A corticotroph pituitary neuroendocrine tumor composed of basophilic PAS-positive cells that are diffusely and strongly positive for ACTH, consistent with the abundance of secretory granules seen at the ultrastructural level. (WHO) MONDO:0006068
MONDO:0854470 sparsely granulated corticotroph pituitary neuroendocrine tumor NCIT:C154340 MONDO:equivalentTo Sparsely Granulated Corticotroph Pituitary Neuroendocrine Tumor A corticotroph pituitary neuroendocrine tumor composed of faintly basophilic or chromophobic PAS-positive cells with weak or patchy positivity for ACTH, consistent with the scant, small secretory granules seen ultrastructurally. (WHO) MONDO:0006068
MONDO:0854471 crooke cell tumor NCIT:C154342 MONDO:equivalentTo Crooke Cell Tumor A corticotroph pituitary tumor composed of cells with Crooke hyaline change. Ring-like cytokeratin expression is typical of these neoplasms. ACTH expression is dislocated to the cell periphery and juxtanuclear region. Ultrastructurally, intermediate filaments are arranged in a ring-like pattern. (WHO) MONDO:0006068
MONDO:0854472 non-functioning corticotroph pituitary neuroendocrine tumor NCIT:C154429 MONDO:equivalentTo Non-Functioning Corticotroph Pituitary Neuroendocrine Tumor Corticotroph pituitary neuroendocrine tumor not associated with a hormonal syndrome. MONDO:0019613
MONDO:0854479 anaplastic sarcoma of the kidney NCIT:C154496 MONDO:equivalentTo Anaplastic Sarcoma of the Kidney A rare tumor, usually occurring in young adults (mean age 12 years) with slight female predominance. It is characterized by a proliferation of anaplastic spindle cells with bizarre, pleomorphic nuclei and atypical mitotic figures. Most cases show chondroid differentiation. MONDO:0002930
MONDO:0854480 multiple synchronous pituitary neuroendocrine tumors of distinct lineages NCIT:C154520 MONDO:equivalentTo Multiple Synchronous Pituitary Neuroendocrine Tumors of Distinct Lineages Multiple pituitary neuroendocrine tumors composed of adenohypopheseal cells of two or more lineages or a null cell tumor in combination with a lineage-specific pituitary neuroendocrine tumor in the same gland. MONDO:0006373
MONDO:0854485 cutaneous melanoma of the extremity NCIT:C155305 MONDO:equivalentTo Cutaneous Melanoma of the Extremity A cutaneous melanoma that arises from the upper or lower extremity. MONDO:0005012
MONDO:0854489 sarcoma of the extremity NCIT:C155647 MONDO:equivalentTo Sarcoma of the Extremity A sarcoma that arises from the soft tissues or bones of the upper or lower extremity. MONDO:0005089
MONDO:0854492 mixed gangliocytoma-pituitary neuroendocrine tumor NCIT:C155767 MONDO:equivalentTo Mixed Gangliocytoma-Pituitary Neuroendocrine Tumor A pituitary neoplasm composed of mature ganglionic cells admixed with pituitary neoplastic neuroendocrine cells. MONDO:0021043
MONDO:0854495 ependymal pituicytoma NCIT:C155774 MONDO:equivalentTo Ependymal Pituicytoma A very rare, low-grade neoplasm that arises from the posterior pituitary. It is composed of epithelioid and oncocytic cells forming sheets and fascicles. It shows histopathological features reminiscent of ependymomas, including perivascular pseudorosettes and true rosettes. There is no evidence of necrosis or increased mitotic activity. Despite the presence of ependymal histopathological features, these neoplasms probably are not related to ependymomas. Their prognosis is unknown. MONDO:0003257
MONDO:0854496 sellar meningioma NCIT:C155776 MONDO:equivalentTo Sellar Meningioma A rare meningioma that arises from the sellar region. MONDO:0002998
MONDO:0854500 sellar solitary fibrous tumor NCIT:C155784 MONDO:equivalentTo Sellar Solitary Fibrous Tumor An extremely rare meningeal solitary fibrous tumor that arises from the sellar region. MONDO:0002720
MONDO:0854518 metastatic malignant pancreatic neoplasm NCIT:C155852 MONDO:equivalentTo Metastatic Malignant Pancreatic Neoplasm A malignant neoplasm that arises from the pancreas and has metastasized to another anatomic site. MONDO:0009831
MONDO:0854521 chest wall sarcoma NCIT:C155873 MONDO:equivalentTo Chest Wall Sarcoma A sarcoma that arises from the anatomic structures that surround the lungs and the pleura. MONDO:0005089
MONDO:0854523 unresectable desmoid fibromatosis NCIT:C155877 MONDO:equivalentTo Unresectable Desmoid Fibromatosis Desmoid fibromatosis that is not amenable to surgical resection. MONDO:0007608
MONDO:0854527 smoldering waldenstrom macroglobulinemia NCIT:C155910 MONDO:equivalentTo Smoldering Waldenstrom Macroglobulinemia Waldenstrom macroglobulinemia with serum IgM monoclonal protein equal or more than 3 g/dL and/or at least 10% bone marrow lymphoplasmacytic infiltration but no evidence of constitutional symptoms, symptomatic anemia, or hyperviscosity. (Blood 2008, 112:2709) MONDO:0100280
MONDO:0854528 metastatic malignant neoplasm in the thoracic cavity NCIT:C155919 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Thoracic Cavity A malignant neoplasm that has spread to the thoracic cavity from another anatomic site. MONDO:0024880
MONDO:0854529 medullary hemangioblastoma NCIT:C155949 MONDO:equivalentTo Medullary Hemangioblastoma A hemangioblastoma that arises from the medulla oblongata. MONDO:0003902
MONDO:0854530 chromophobe renal cell carcinoma associated with birt-hogg-dube syndrome NCIT:C155951 MONDO:equivalentTo Chromophobe Renal Cell Carcinoma Associated with Birt-Hogg-Dube Syndrome Chromophobe renal cell carcinoma that develops in a patient with Birt-Hogg-Dube syndrome. MONDO:0017885
MONDO:0854531 uterine ligament papillary cystadenoma NCIT:C155952 MONDO:equivalentTo Uterine Ligament Papillary Cystadenoma A cystadenoma that arises from the broad or other uterine ligaments. It is characterized by the presence of small papillary projections in the inner surface of the cysts. It may be sporadic or associated with von Hippel-Lindau disease. MONDO:0021091
MONDO:0854533 thyroid gland spindle cell follicular adenoma NCIT:C155957 MONDO:equivalentTo Thyroid Gland Spindle Cell Follicular Adenoma A rare thyroid gland follicular adenoma composed predominantly of spindle cells. MONDO:0005032
MONDO:0854534 thyroid gland black follicular adenoma NCIT:C155958 MONDO:equivalentTo Thyroid Gland Black Follicular Adenoma A thyroid gland follicular adenoma seen in patients treated with minocycline. The tumors have black discoloration visible on macroscopic examination and cytoplasmic accumulation of black pigment. (WHO 2017) MONDO:0005032
MONDO:0854545 hypothalamic-chiasmatic pilomyxoid astrocytoma NCIT:C156038 MONDO:equivalentTo Hypothalamic-Chiasmatic Pilomyxoid Astrocytoma A pilomyxoid astrocytoma occurring in the hypothalamic-chiasmatic region. MONDO:0016692
MONDO:0854546 fourth ventricle medulloblastoma NCIT:C156039 MONDO:equivalentTo Fourth Ventricle Medulloblastoma A medulloblastoma occurring in the fourth ventricle. MONDO:0007959
MONDO:0854547 third ventricle germinoma NCIT:C156040 MONDO:equivalentTo Third Ventricle Germinoma A germinoma that arises from the third ventricle. MONDO:0002214
MONDO:0854549 temporal lobe pleomorphic xanthoastrocytoma NCIT:C156042 MONDO:equivalentTo Temporal Lobe Pleomorphic Xanthoastrocytoma A pleomorphic xanthoastrocytoma that arises from the temporal lobe of the brain. MONDO:0016690
MONDO:0854550 spindle cell variant thyroid gland papillary carcinoma NCIT:C156045 MONDO:equivalentTo Spindle Cell Variant Thyroid Gland Papillary Carcinoma Papillary carcinoma of the thyroid gland with focal areas of spindle cell metaplasia. MONDO:0005075
MONDO:0854551 hobnail variant thyroid gland papillary carcinoma NCIT:C156050 MONDO:equivalentTo Hobnail Variant Thyroid Gland Papillary Carcinoma A rare variant of papillary thyroid gland carcinoma in which more than 30% of cells have hobnail features. (WHO) MONDO:0005075
MONDO:0854584 metastatic neuroblastoma NCIT:C156101 MONDO:equivalentTo Metastatic Neuroblastoma A neuroblastoma that has metastasized from its original site of growth to another anatomic site. MONDO:0024880
MONDO:0854588 thyroid gland follicular carcinoma, encapsulated angioinvasive NCIT:C156122 MONDO:equivalentTo Thyroid Gland Follicular Carcinoma, Encapsulated Angioinvasive An encapsulated follicular carcinoma of the thyroid gland which shows angioinvasion. MONDO:0005034
MONDO:0854589 thyroid gland follicular carcinoma, widely invasive NCIT:C156123 MONDO:equivalentTo Thyroid Gland Follicular Carcinoma, Widely Invasive A follicular carcinoma of the thyroid gland with extension into surrounding thyroid or extrathyroid tissues. MONDO:0040677
MONDO:0854594 thyroid gland mucinous carcinoma NCIT:C156267 MONDO:equivalentTo Thyroid Gland Mucinous Carcinoma A rare primary carcinoma of the thyroid gland characterized by the presence of clusters of malignant epithelial cells associated with abundant extracellular mucin deposition. MONDO:0015075
MONDO:0854595 intrathyroidal thymoma NCIT:C156268 MONDO:equivalentTo Intrathyroidal Thymoma A rare thymoma arising within or is attached to the thyroid gland. MONDO:0015074
MONDO:0854598 orbital alveolar soft part sarcoma NCIT:C156276 MONDO:equivalentTo Orbital Alveolar Soft Part Sarcoma An alveolar soft part sarcoma involving the orbit. It usually occurs in children. MONDO:0004943
MONDO:0854599 bladder alveolar soft part sarcoma NCIT:C156277 MONDO:equivalentTo Bladder Alveolar Soft Part Sarcoma An alveolar soft part sarcoma involving the bladder. MONDO:0001374
MONDO:0854600 cellular nerve sheath myxoma NCIT:C156278 MONDO:equivalentTo Cellular Nerve Sheath Myxoma A nerve sheath myxoma with increased cellularity. MONDO:0006317
MONDO:0854601 colon liposarcoma NCIT:C156279 MONDO:equivalentTo Colon Liposarcoma A liposarcoma that arises from the colon. MONDO:0003352
MONDO:0854608 thyroid gland schwannoma NCIT:C156340 MONDO:equivalentTo Thyroid Gland Schwannoma A rare schwannoma that arises from the thyroid gland. MONDO:0004820
MONDO:0854616 thyroid gland solitary fibrous tumor NCIT:C156349 MONDO:equivalentTo Thyroid Gland Solitary Fibrous Tumor A rare solitary fibrous tumor that arises from the thyroid gland. MONDO:0016238
MONDO:0854631 metastatic neuroendocrine neoplasm NCIT:C156485 MONDO:equivalentTo Metastatic Neuroendocrine Neoplasm A neuroendocrine neoplasm that has spread from its original site of growth to another anatomic site. MONDO:0019496
MONDO:0854639 malignant abdominal neoplasm NCIT:C156714 MONDO:equivalentTo Malignant Abdominal Neoplasm A primary or metastatic malignant neoplasm that affects the organs and structures of the abdomen. MONDO:0004992
MONDO:0854640 malignant pelvic neoplasm NCIT:C156715 MONDO:equivalentTo Malignant Pelvic Neoplasm A primary or metastatic malignant neoplasm that affects the organs and structures of the pelvis. MONDO:0004992
MONDO:0854647 metastatic basal cell carcinoma NCIT:C156769 MONDO:equivalentTo Metastatic Basal Cell Carcinoma A carcinoma that arises from the basal cells and has metastasized to another anatomic site. MONDO:0024879
MONDO:0854656 adrenal cortical sex cord-stromal tumor NCIT:C156943 MONDO:equivalentTo Adrenal Cortical Sex Cord-Stromal Tumor An extremely rare sex cord-stromal tumor that arises from the adrenal cortex. The reported cases were solitary and unilateral. MONDO:0006055
MONDO:0854657 adrenal gland schwannoma NCIT:C156944 MONDO:equivalentTo Adrenal Gland Schwannoma A rare schwannoma that arises from the adrenal medulla. MONDO:0021468
MONDO:0854658 adrenal gland lymphoma NCIT:C156945 MONDO:equivalentTo Adrenal Gland Lymphoma A rare lymphoma that arises from the adrenal gland. MONDO:0002817
MONDO:0854659 adrenal gland sarcoma NCIT:C156956 MONDO:equivalentTo Adrenal Gland Sarcoma A rare sarcoma that arises from the adrenal gland. MONDO:0002817
MONDO:0854660 primary vitreoretinal non-hodgkin lymphoma NCIT:C157065 MONDO:equivalentTo Primary Vitreoretinal Non-Hodgkin Lymphoma An uncommon and potentially fatal intraocular non-Hodgkin lymphoma that involves the uvea, retina, vitreous body, and optic nerve. It is a subset of primary central nervous system non-Hodgkin lymphoma. The majority of cases are diffuse large B-cell lymphomas. MONDO:0004351
MONDO:0854663 unresectable paraganglioma NCIT:C157126 MONDO:equivalentTo Unresectable Paraganglioma Paraganglioma that is not amenable to surgical resection. MONDO:0000448
MONDO:0854669 breast histiocytoid carcinoma NCIT:C157235 MONDO:equivalentTo Breast Histiocytoid Carcinoma A rare variant of invasive lobular breast carcinoma characterized by the presence of histiocyte-like malignant cells with pale cytoplasm forming sheets or linear patterns. Apocrine differentiation may be present. It usually has an aggressive clinical course. MONDO:0005051
MONDO:0854670 adrenal gland ganglioneuroblastoma, intermixed NCIT:C157243 MONDO:equivalentTo Adrenal Gland Ganglioneuroblastoma, Intermixed An intermixed ganglioneuroblastoma arising from the adrenal gland. MONDO:0004477
MONDO:0854671 adrenal gland ganglioneuroblastoma, nodular NCIT:C157244 MONDO:equivalentTo Adrenal Gland Ganglioneuroblastoma, Nodular A nodular ganglioneuroblastoma arising from the adrenal gland. MONDO:0004477
MONDO:0854672 composite paraganglioma NCIT:C157246 MONDO:equivalentTo Composite Paraganglioma A neoplasm that combines morphologic characteristics of paraganglioma and neuroectodermal tumors such as neuroblastoma, ganglioneuroma, ganglioneuroblastoma, or peripheral nerve sheath tumor. MONDO:0000448
MONDO:0854679 peripheral hemangioblastoma NCIT:C157450 MONDO:equivalentTo Peripheral Hemangioblastoma A hemangioblastoma that arises from peripheral nerves or extraneural tissues. MONDO:0016748
MONDO:0854680 metastatic squamous cell carcinoma in the cervical lymph nodes NCIT:C157452 MONDO:equivalentTo Metastatic Squamous Cell Carcinoma in the Cervical Lymph Nodes A squamous cell carcinoma that has spread from its original site of growth to the cervical lymph nodes. MONDO:0044907
MONDO:0854688 bap1-mutant clear cell renal cell carcinoma NCIT:C157614 MONDO:equivalentTo BAP1-Mutant Clear Cell Renal Cell Carcinoma A clear cell renal cell carcinoma that is associated with a mutation in BAP1 gene. These tumors are typically high grade and associated with poor outcome. MONDO:0005005
MONDO:0854691 transformed chronic lymphocytic leukemia to diffuse large b-cell lymphoma NCIT:C157624 MONDO:equivalentTo Transformed Chronic Lymphocytic Leukemia to Diffuse Large B-Cell Lymphoma Histologic transformation of an indolent chronic lymphocytic leukemia to an aggressive diffuse large B-cell lymphoma. MONDO:0004948
MONDO:0854692 metastatic adenoid cystic carcinoma NCIT:C157638 MONDO:equivalentTo Metastatic Adenoid Cystic Carcinoma An adenoid cystic carcinoma that has spread from the original site of growth to other anatomic sites. MONDO:0004971
MONDO:0854698 refractory lymphoproliferative disorder NCIT:C157686 MONDO:equivalentTo Refractory Lymphoproliferative Disorder Lymphoproliferative disorder that is resistant to treatment.
MONDO:0854705 kidney synovial sarcoma NCIT:C157737 MONDO:equivalentTo Kidney Synovial Sarcoma A synovial sarcoma arising from the kidney. MONDO:0002930
MONDO:0854706 kidney neuroendocrine neoplasm NCIT:C157743 MONDO:equivalentTo Kidney Neuroendocrine Neoplasm An epithelial neoplasm with neuroendocrine differentiation that arises from the kidney. It includes neuroendocrine tumor, small cell neuroendocrine carcinoma, large cell neuroendocrine carcinoma, and paraganglioma. MONDO:0019496
MONDO:0854708 metanephric tumor NCIT:C157748 MONDO:equivalentTo Metanephric Tumor A neoplasm arising from the distal convoluted tubule and collecting duct areas of the kidney. MONDO:0002513
MONDO:0854714 bladder neuroendocrine neoplasm NCIT:C157758 MONDO:equivalentTo Bladder Neuroendocrine Neoplasm A neuroendocrine neoplasm that arises from the bladder. MONDO:0019496
MONDO:0854748 subcutaneous disorder NCIT:C157995 MONDO:equivalentTo Subcutaneous Disorder A disorder of the subcutaneous tissue.
MONDO:0854749 kidney epithelioid angiomyolipoma NCIT:C158032 MONDO:equivalentTo Kidney Epithelioid Angiomyolipoma An angiomyolipoma that arises from the kidney and is composed exclusively or predominantly of epithelioid cells. It is often associated with cytologic atypia and may recur or metastasize. MONDO:0004555
MONDO:0854750 kidney mixed epithelial and stromal tumor family NCIT:C158046 MONDO:equivalentTo Kidney Mixed Epithelial and Stromal Tumor Family A family of tumors ranging from predominantly cystic tumors (adult cystic nephromas) to tumors that are variably solid (mixed epithelial and stromal tumors) and contain biphasic epithelial and stromal components with spindle stroma, glands, and cysts. Most of these tumors are benign. (WHO 2016). MONDO:0021163
MONDO:0854756 bladder non-invasive urothelial neoplasm NCIT:C158374 MONDO:equivalentTo Bladder Non-Invasive Urothelial Neoplasm A non-invasive neoplasm that arises from the urothelial lining of the bladder. MONDO:0003755
MONDO:0854773 platinum-sensitive lung small cell carcinoma NCIT:C158495 MONDO:equivalentTo Platinum-Sensitive Lung Small Cell Carcinoma Lung small cell carcinoma that is sensitive to platinum therapy. MONDO:0008433
MONDO:0854780 borderline ovarian mixed epithelial tumor/atypical proliferative ovarian mixed epithelial tumor NCIT:C158616 MONDO:equivalentTo Borderline Ovarian Mixed Epithelial Tumor/Atypical Proliferative Ovarian Mixed Epithelial Tumor A low grade, non-invasive mixed epithelial proliferative neoplasm that arises from the ovary. In most cases is composed of serous and endocervical-type mucinous cells. MONDO:0021043
MONDO:0854781 endometrioid tumor, variant with squamous differentiation NCIT:C158620 MONDO:equivalentTo Endometrioid Tumor, Variant with Squamous Differentiation An endometrioid tumor exhibiting squamous differentiation. MONDO:0002480
MONDO:0854783 bladder soft tissue neoplasm NCIT:C158636 MONDO:equivalentTo Bladder Soft Tissue Neoplasm A mesenchymal neoplasm that arises from the bladder. MONDO:0006424
MONDO:0854795 early stage pancreatic ductal adenocarcinoma NCIT:C158961 MONDO:equivalentTo Early Stage Pancreatic Ductal Adenocarcinoma Pancreatic ductal adenocarcinoma that has not spread beyond the pancreas. MONDO:0005184
MONDO:0854803 kidney rhabdomyosarcoma NCIT:C159206 MONDO:equivalentTo Kidney Rhabdomyosarcoma An extremely rare rhabdomyosarcoma arising from the kidney. Most cases are of embryonal type. MONDO:0002930
MONDO:0854804 kidney ewing sarcoma NCIT:C159208 MONDO:equivalentTo Kidney Ewing Sarcoma A rare Ewing sarcoma arising from the kidney. MONDO:0018270
MONDO:0854806 kidney hemangioma NCIT:C159211 MONDO:equivalentTo Kidney Hemangioma A rare hemangioma arising from the kidney. MONDO:0002513
MONDO:0854807 kidney lymphangioma NCIT:C159214 MONDO:equivalentTo Kidney Lymphangioma A rare lymphangioma arising from the kidney. MONDO:0002013
MONDO:0854808 kidney schwannoma NCIT:C159221 MONDO:equivalentTo Kidney Schwannoma A rare schwannoma arising from the kidney. MONDO:0002513
MONDO:0854809 kidney solitary fibrous tumor NCIT:C159222 MONDO:equivalentTo Kidney Solitary Fibrous Tumor A rare solitary fibrous tumor arising from the kidney. MONDO:0016238
MONDO:0854812 kidney germ cell tumor NCIT:C159227 MONDO:equivalentTo Kidney Germ Cell Tumor A rare benign or malignant germ cell tumor that arises from the kidney. MONDO:0018201
MONDO:0854813 penile human papillomavirus-independent squamous cell carcinoma NCIT:C159244 MONDO:equivalentTo Penile Human Papillomavirus-Independent Squamous Cell Carcinoma A squamous cell carcinoma that arises from the penis and is not caused by human papillomavirus infection. Morphologic variants include pseudohyperplastic, pseudoglandular, verrucous, papillary, and sarcomatoid carcinoma. MONDO:0018352
MONDO:0854815 penile carcinoma cuniculatum NCIT:C159247 MONDO:equivalentTo Penile Carcinoma Cuniculatum A variant of verrucous carcinoma of the penis. It is characterized by a labyrinthine growth pattern. MONDO:0003698
MONDO:0854817 penile papillary-basaloid carcinoma NCIT:C159249 MONDO:equivalentTo Penile Papillary-Basaloid Carcinoma A variant of penile basaloid squamous cell carcinoma. It is characterized by a papillary exophytic or endophytic growth pattern. MONDO:0004089
MONDO:0854818 penile warty-basaloid carcinoma NCIT:C159250 MONDO:equivalentTo Penile Warty-Basaloid Carcinoma A squamous cell carcinoma that arises from the penis. It is characterized by warty (condylomatous) and basaloid features. MONDO:0004430
MONDO:0854819 penile lymphoepithelioma-like carcinoma NCIT:C159252 MONDO:equivalentTo Penile Lymphoepithelioma-Like Carcinoma A variant of penile squamous cell carcinoma characterized by the presence of islands of malignant cells with uniform vesicular nuclei and prominent nucleoli, and a dense lymphocytic infiltrate. MONDO:0003572
MONDO:0854820 borderline ovarian mucinous tumor/atypical proliferative ovarian mucinous tumor with microinvasion NCIT:C159311 MONDO:equivalentTo Borderline Ovarian Mucinous Tumor/Atypical Proliferative Ovarian Mucinous Tumor with Microinvasion A low grade ovarian epithelial neoplasm characterized by the presence of neoplastic mucinous epithelial cells, atypia, and microinvasion of the ovarian stroma. MONDO:0003756
MONDO:0854828 bladder rhabdomyosarcoma NCIT:C159667 MONDO:equivalentTo Bladder Rhabdomyosarcoma A malignant mesenchymal neoplasm with skeletal muscle differentiation arising from the bladder. MONDO:0001374
MONDO:0854831 bladder leiomyosarcoma NCIT:C159670 MONDO:equivalentTo Bladder Leiomyosarcoma A leiomyosarcoma that arises from the bladder. It is the most common type of bladder sarcoma in adults. MONDO:0001374
MONDO:0854838 bladder hemangioma NCIT:C159680 MONDO:equivalentTo Bladder Hemangioma A hemangioma that arises from the bladder. Most tumors occur in adults. MONDO:0000384
MONDO:0854839 bladder granular cell tumor NCIT:C159681 MONDO:equivalentTo Bladder Granular Cell Tumor A rare granular cell tumor arising from the bladder. Most tumors are benign. MONDO:0006235
MONDO:0854840 bladder neurofibroma NCIT:C159682 MONDO:equivalentTo Bladder Neurofibroma A plexiform or diffuse neurofibroma arising from the bladder. MONDO:0000384
MONDO:0854841 ebv-related lymphoproliferative disorder NCIT:C159717 MONDO:equivalentTo EBV-Related Lymphoproliferative Disorder A lymphoproliferative disorder associated with Epstein-Barr virus. This category includes, but is not limited to, Burkitt lymphoma, classic Hodgkin lymphoma, and lymphomas arising in immunocompromised individuals.
MONDO:0854843 platinum-sensitive ovarian carcinoma NCIT:C159902 MONDO:equivalentTo Platinum-Sensitive Ovarian Carcinoma Ovarian carcinoma that has a documented response to platinum-based chemotherapy. MONDO:0005140
MONDO:0854845 carcinoma arising in bladder diverticulum NCIT:C160158 MONDO:equivalentTo Carcinoma Arising in Bladder Diverticulum A carcinoma arising in a bladder diverticulum. Approximately one-third to half of the cases represent non-invasive, low-grade or high-grade urothelial carcinomas. Approximately half of the invasive carcinomas are urothelial. The rest include adenocarcinomas, squamous cell carcinomas, and small cell carcinomas. MONDO:0004986
MONDO:0854847 metastatic nut carcinoma NCIT:C160297 MONDO:equivalentTo Metastatic NUT Carcinoma NUT carcinoma that has spread from its original site of growth to another anatomic site. MONDO:0024879
MONDO:0854850 hematologic malignancy-associated skin squamous cell carcinoma NCIT:C160666 MONDO:equivalentTo Hematologic Malignancy-Associated Skin Squamous Cell Carcinoma A squamous cell carcinoma that arises from the skin in a patient with a history of hematologic malignancy, usually non-Hodgkin lymphoma or chronic lymphocytic leukemia. MONDO:0002529
MONDO:0854854 prostate acinar microcystic adenocarcinoma NCIT:C160817 MONDO:equivalentTo Prostate Acinar Microcystic Adenocarcinoma Acinar prostate adenocarcinoma characterized by the presence of microcystic foci in radical prostatectomy specimens. MONDO:0002493
MONDO:0854855 prostate acinar pleomorphic giant cell adenocarcinoma NCIT:C160818 MONDO:equivalentTo Prostate Acinar Pleomorphic Giant Cell Adenocarcinoma An extremely rare prostate acinar adenocarcinoma characterized by the presence of giant, bizarre anaplastic cells with pleomorphic nuclei and lack of a spindle cell component. MONDO:0002493
MONDO:0854859 platinum-sensitive primary peritoneal carcinoma NCIT:C160872 MONDO:equivalentTo Platinum-Sensitive Primary Peritoneal Carcinoma Primary peritoneal carcinoma that has a documented response to platinum-based chemotherapy. MONDO:0015686
MONDO:0854860 platinum-sensitive fallopian tube carcinoma NCIT:C160873 MONDO:equivalentTo Platinum-Sensitive Fallopian Tube Carcinoma Fallopian tube carcinoma that has a documented response to platinum-based chemotherapy. MONDO:0006206
MONDO:0854866 cribriform adenocarcinoma of minor salivary gland NCIT:C160974 MONDO:equivalentTo Cribriform Adenocarcinoma of Minor Salivary Gland A minor salivary gland adenocarcinoma characterized by a cribriform pattern. It often metastasizes to the neck lymph nodes. MONDO:0006304
MONDO:0854867 sinonasal adenocarcinoma NCIT:C160976 MONDO:equivalentTo Sinonasal Adenocarcinoma Adenocarcinomas that arises from the sinonasal tract. This category includes salivary-type and non-salivary type adenocarcinomas. The latter includes intestinal-type and non-intestinal-type adenocarcinomas. MONDO:0056819
MONDO:0854868 head and neck sebaceous carcinoma NCIT:C160978 MONDO:equivalentTo Head and Neck Sebaceous Carcinoma A sebaceous carcinoma that arises from the head and neck region. MONDO:0006962
MONDO:0854872 prostate intraductal carcinoma NCIT:C161022 MONDO:equivalentTo Prostate Intraductal Carcinoma An intra-acinar and/or intraductal neoplastic epithelial proliferation in the prostate gland that has some features of high-grade prostatic intraepithelial neoplasia but exhibits much greater architectural and/or cytological atypia, typically associated with high-grade, high-stage prostate carcinoma. (WHO 2016) MONDO:0005159
MONDO:0854873 prostate synovial sarcoma NCIT:C161034 MONDO:equivalentTo Prostate Synovial Sarcoma A rare synovial sarcoma that arises from the prostate gland. MONDO:0002854
MONDO:0854874 prostate osteosarcoma NCIT:C161035 MONDO:equivalentTo Prostate Osteosarcoma A rare osteosarcoma that arises from the prostate gland. MONDO:0002621
MONDO:0854875 prostate undifferentiated pleomorphic sarcoma NCIT:C161038 MONDO:equivalentTo Prostate Undifferentiated Pleomorphic Sarcoma A rare undifferentiated pleomorphic sarcoma that arises from the prostate gland. MONDO:0002854
MONDO:0854877 prostate soft tissue neoplasm NCIT:C161045 MONDO:equivalentTo Prostate Soft Tissue Neoplasm A mesenchymal neoplasm that arises from the prostate gland. MONDO:0006424
MONDO:0854881 prostate hemangioma NCIT:C161581 MONDO:equivalentTo Prostate Hemangioma A rare hemangioma that arises from the prostate gland. MONDO:0021510
MONDO:0854886 prostate carcinoma metastatic in the lymph nodes NCIT:C161587 MONDO:equivalentTo Prostate Carcinoma Metastatic in the Lymph Nodes A carcinoma that arises from the prostate gland and has spread to the lymph nodes. MONDO:0004956
MONDO:0854888 prostate cystadenoma NCIT:C161606 MONDO:equivalentTo Prostate Cystadenoma A rare cystadenoma affecting the prostate gland. It is characterized by the presence of multilocular prostatic cysts. MONDO:0021510
MONDO:0854889 prostate wilms tumor NCIT:C161607 MONDO:equivalentTo Prostate Wilms Tumor A rare Wilms tumor affecting the prostate gland. MONDO:0008315
MONDO:0854891 prostate melanoma NCIT:C161611 MONDO:equivalentTo Prostate Melanoma An exceptionally rare melanoma arising from the prostate gland. MONDO:0006320
MONDO:0854893 seminal vesicle mixed epithelial and stromal tumor NCIT:C161636 MONDO:equivalentTo Seminal Vesicle Mixed Epithelial and Stromal Tumor A rare biphasic neoplasm that arises from the seminal vesicle. It is characterized by the presence of stromal and benign epithelial components. Rarely, the stromal component may display atypia and mitotic activity and the tumor may behave in a malignant clinical course. MONDO:0021043
MONDO:0854895 benign seminal vesicle neoplasm NCIT:C161643 MONDO:equivalentTo Benign Seminal Vesicle Neoplasm A neoplasm that arises from the seminal vesicle and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0000625
MONDO:0854896 malignant seminal vesicle neoplasm NCIT:C161644 MONDO:equivalentTo Malignant Seminal Vesicle Neoplasm A primary or metastatic malignant neoplasm that affects the seminal vesicle. MONDO:0005836
MONDO:0854902 regressed testicular germ cell tumor NCIT:C162139 MONDO:equivalentTo Regressed Testicular Germ Cell Tumor A testicular germ cell tumor that has undergone either partial or complete regression, resulting in the creation of a fibrotic nodule in the testis. MONDO:0010108
MONDO:0854909 cervical cancer by figo stage 2018 NCIT:C162225 MONDO:equivalentTo Cervical Cancer by FIGO Stage 2018 A term that refers to the staging of cervical cancer according to the International Federation of Gynecology and Obstetrics (FIGO) staging, 2018. MONDO:0005131
MONDO:0854911 metastatic malignant digestive system neoplasm NCIT:C162255 MONDO:equivalentTo Metastatic Malignant Digestive System Neoplasm A malignant neoplasm that arises in the digestive system and has spread from its original site of growth to other anatomic sites. MONDO:0002516
MONDO:0854912 hypermutated colorectal carcinoma NCIT:C162256 MONDO:equivalentTo Hypermutated Colorectal Carcinoma A colorectal carcinoma characterized by a high mutational rate caused by DNA mismatch repair deficiency or POLE/POLD1 driver mutations. MONDO:0024331
MONDO:0854925 thymic neuroendocrine neoplasm NCIT:C162460 MONDO:equivalentTo Thymic Neuroendocrine Neoplasm A carcinoid tumor or neuroendocrine carcinoma arising from the thymus gland. MONDO:0018079
MONDO:0854927 intratubular large cell hyalinizing sertoli cell neoplasia NCIT:C162466 MONDO:equivalentTo Intratubular Large Cell Hyalinizing Sertoli Cell Neoplasia A clinically benign intratubular neoplastic proliferation of large Sertoli cells in the testis. It is associated with prominent basement membrane deposits. It occurs almost exclusively in patients with Peutz-Jeghers syndrome. MONDO:0003125
MONDO:0854928 testicular diffuse large b-cell lymphoma NCIT:C162467 MONDO:equivalentTo Testicular Diffuse Large B-Cell Lymphoma A diffuse large B-cell lymphoma that arises from the testis. It predominantly affects older men. Patients usually present with a unilateral hard painless mass. Bilateral masses have been described in a minority of patients. MONDO:0001472
MONDO:0854929 testicular nasal type extranodal nk/t-cell lymphoma NCIT:C162468 MONDO:equivalentTo Testicular Nasal Type Extranodal NK/T-Cell Lymphoma A nasal type extranodal NK/T-cell lymphoma affecting the testis. Patients usually present with unilateral testicular enlargement. Bilateral involvement is rare. The prognosis is poor. MONDO:0001472
MONDO:0854930 testicular myeloid sarcoma NCIT:C162469 MONDO:equivalentTo Testicular Myeloid Sarcoma A rare myeloid sarcoma that arises from the testis. At presentation the involvement is usually unilateral. MONDO:0005447
MONDO:0854931 testicular plasmacytoma NCIT:C162470 MONDO:equivalentTo Testicular Plasmacytoma A rare plasmacytoma that arises in the testis. At presentation the involvement is usually unilateral. MONDO:0005447
MONDO:0854936 paratesticular neoplasm NCIT:C162485 MONDO:equivalentTo Paratesticular Neoplasm A benign, borderline, or malignant neoplasm that affects the paratesticular structures. MONDO:0024582
MONDO:0854952 penile melanoma NCIT:C162547 MONDO:equivalentTo Penile Melanoma A melanoma that arises from the penis. It may be cutaneous or mucosal. The most common site of involvement is glans penis. MONDO:0001325
MONDO:0854953 penile lymphoma NCIT:C162548 MONDO:equivalentTo Penile Lymphoma A lymphoma that arises from penile skin, subcutis, corpora cavernosa, and spongiosum. Diffuse large B-cell lymphoma is the most common primary penile lymphoma. (WHO 2016) MONDO:0001325
MONDO:0854955 primary peritoneal undifferentiated carcinoma NCIT:C162562 MONDO:equivalentTo Primary Peritoneal Undifferentiated Carcinoma An extremely rare carcinoma arising from the peritoneum. It is characterized by the presence of a diffuse malignant infiltrate that is composed of epithelial cells without evidence of glandular or squamous differentiation. MONDO:0015686
MONDO:0854956 primary peritoneal transitional cell carcinoma NCIT:C162564 MONDO:equivalentTo Primary Peritoneal Transitional Cell Carcinoma An extremely rare transitional cell carcinoma that arises from the peritoneum. MONDO:0015686
MONDO:0854959 penile soft tissue neoplasm NCIT:C162574 MONDO:equivalentTo Penile Soft Tissue Neoplasm A rare mesenchymal neoplasm that arises from the penis. MONDO:0006424
MONDO:0854966 penile malignant peripheral nerve sheath tumor NCIT:C162584 MONDO:equivalentTo Penile Malignant Peripheral Nerve Sheath Tumor A rare malignant peripheral nerve sheath tumor that occurs in the penis. MONDO:0001387
MONDO:0854967 penile leiomyosarcoma NCIT:C162585 MONDO:equivalentTo Penile Leiomyosarcoma A leiomyosarcoma that occurs in the penis. MONDO:0001387
MONDO:0854968 penile schwannoma NCIT:C162586 MONDO:equivalentTo Penile Schwannoma A schwannoma that occurs in the penis. MONDO:0004820
MONDO:0854969 penile neurofibroma NCIT:C162587 MONDO:equivalentTo Penile Neurofibroma A neurofibroma that occurs in the penis. MONDO:0021458
MONDO:0854970 penile rhabdomyosarcoma NCIT:C162588 MONDO:equivalentTo Penile Rhabdomyosarcoma A rhabdomyosarcoma that occurs in the penis. It usually affects young children. Embryonal rhabdomyosarcoma is the most common type. MONDO:0001387
MONDO:0854971 penile undifferentiated pleomorphic sarcoma NCIT:C162589 MONDO:equivalentTo Penile Undifferentiated Pleomorphic Sarcoma A rare undifferentiated pleomorphic sarcoma that occurs in the penis. MONDO:0001387
MONDO:0854974 metastatic malignant neoplasm in the head and neck NCIT:C162594 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Head and Neck The spread of a malignant neoplasm to the head and neck. This may be from a primary head and neck malignant neoplasm, or from a malignant neoplasm at a distant site. MONDO:0005627
MONDO:0854984 refractory childhood malignant neoplasm NCIT:C162703 MONDO:equivalentTo Refractory Childhood Malignant Neoplasm A childhood malignant neoplasm that does not respond to treatment. MONDO:0006517
MONDO:0854998 asph-positive head and neck squamous cell carcinoma NCIT:C162770 MONDO:equivalentTo ASPH-Positive Head and Neck Squamous Cell Carcinoma A head and neck squamous cell carcinoma in which the malignant cells are positive for ASPH gene. MONDO:0010150
MONDO:0855003 parapharyngeal neoplasm NCIT:C162820 MONDO:equivalentTo Parapharyngeal Neoplasm A benign or malignant neoplasm that affects the parapharyngeal space. MONDO:0021351
MONDO:0855006 retropharyngeal neoplasm NCIT:C162825 MONDO:equivalentTo Retropharyngeal Neoplasm A benign or malignant neoplasm that affects the retropharyngeal space. MONDO:0021351
MONDO:0855015 non-invasive cribriform carcinoma NCIT:C162973 MONDO:equivalentTo Non-Invasive Cribriform Carcinoma A carcinoma characterized by the presence of a cribriform architectural pattern. There is no evidence of surrounding stromal invasion by the malignant cells. MONDO:0006176
MONDO:0855016 malignant brain glioma NCIT:C162993 MONDO:equivalentTo Malignant Brain Glioma A grade 3 or 4 glioma that arises from the brain. This category includes anaplastic astrocytoma, anaplastic ependymoma, anaplastic oligoastrocytoma, anaplastic oligodendroglioma, anaplastic pleomorphic xanthoastrocytoma (all grade 3 gliomas), and glioblastoma (grade 4 glioma). MONDO:0100342
MONDO:0855028 micropapillary carcinoma NCIT:C164144 MONDO:equivalentTo Micropapillary Carcinoma A carcinoma characterized by the presence of a predominant micropapillary pattern. MONDO:0006509
MONDO:0855034 aggressive prostate adenocarcinoma NCIT:C164185 MONDO:equivalentTo Aggressive Prostate Adenocarcinoma Prostate adenocarcinoma that metastasizes quickly to other anatomic sites. It usually has a Gleason score between 8 and 10, a PSA level higher than 20 ng/ml, and is classified as T3b or T4. MONDO:0005082
MONDO:0855035 head and neck sarcoma NCIT:C164198 MONDO:equivalentTo Head and Neck Sarcoma A sarcoma that arises from the head and neck region. MONDO:0005089
MONDO:0855040 warty carcinoma NCIT:C164248 MONDO:equivalentTo Warty Carcinoma A squamous cell carcinoma characterized by a papillary growth pattern, hyperkeratosis, and koilocytosis. MONDO:0002979
MONDO:0855041 differentiated intraepithelial neoplasia NCIT:C164249 MONDO:equivalentTo Differentiated Intraepithelial Neoplasia Intraepithelial neoplasia of the penis or vulva. It usually presents as a solitary white or pink macule or plaque that may be slightly elevated. A background of long-standing lichen sclerosus is often present. MONDO:0024474
MONDO:0855042 human papillomavirus-independent squamous cell carcinoma NCIT:C164250 MONDO:equivalentTo Human Papillomavirus-Independent Squamous Cell Carcinoma A squamous cell carcinoma not associated with human papilloma virus infection. MONDO:0005096
MONDO:0855043 invasive sarcomatoid urothelial carcinoma NCIT:C164252 MONDO:equivalentTo Invasive Sarcomatoid Urothelial Carcinoma An invasive urothelial carcinoma that exhibits spindle cell sarcomatoid features. MONDO:0040678
MONDO:0855044 mixed neuroendocrine non-neuroendocrine neoplasm NCIT:C164255 MONDO:equivalentTo Mixed Neuroendocrine Non-Neuroendocrine Neoplasm A rare neoplasm that consists of neuroendocrine and non-neuroendocrine cellular components. At least 30% of either component should be present for the diagnosis to be made. MONDO:0021043
MONDO:0855047 nf1-associated malignant peripheral nerve sheath tumor NCIT:C164313 MONDO:equivalentTo NF1-Associated Malignant Peripheral Nerve Sheath Tumor A malignant peripheral nerve sheath tumor that is associated with NF1 gene inactivation and a history of neurofibromatosis type 1. MONDO:0017827
MONDO:0855048 sporadic malignant peripheral nerve sheath tumor NCIT:C164314 MONDO:equivalentTo Sporadic Malignant Peripheral Nerve Sheath Tumor A malignant peripheral nerve sheath tumor that is not caused by inherited genetic mutations. MONDO:0017827
MONDO:0855049 radiation-induced malignant peripheral nerve sheath tumor NCIT:C164316 MONDO:equivalentTo Radiation-Induced Malignant Peripheral Nerve Sheath Tumor A malignant peripheral nerve sheath tumor that is the result of exposure to ionizing radiation. MONDO:0017827
MONDO:0855058 soft tissue sarcoma of the trunk and extremities NCIT:C165190 MONDO:equivalentTo Soft Tissue Sarcoma of the Trunk and Extremities A soft tissue sarcoma that arises from the trunk or the extremities. MONDO:0018078
MONDO:0855059 metastatic malignant mesothelioma NCIT:C165252 MONDO:equivalentTo Metastatic Malignant Mesothelioma Malignant mesothelioma that has spread from its original site of growth to another anatomic site. MONDO:0006292
MONDO:0855079 skin verrucous carcinoma NCIT:C165465 MONDO:equivalentTo Skin Verrucous Carcinoma A verrucous carcinoma that arises from the skin. It usually affects the palms, soles, and distal digits. MONDO:0002529
MONDO:0855080 skin squamous cell carcinoma with osteoclast-like giant cells NCIT:C165466 MONDO:equivalentTo Skin Squamous Cell Carcinoma with Osteoclast-Like Giant Cells A rare squamous cell carcinoma of the skin characterized by the presence of multinucleated non-neoplastic giant cells that resemble osteoclasts. MONDO:0002529
MONDO:0855081 skin lymphoepithelial carcinoma NCIT:C165467 MONDO:equivalentTo Skin Lymphoepithelial Carcinoma A rare, poorly differentiated squamous cell carcinoma of the skin. It is characterized by the presence of tumor cells islands surrounded and infiltrated by lymphocytes and plasma cells. MONDO:0002529
MONDO:0855082 skin squamous cell carcinoma with sarcomatoid differentiation NCIT:C165468 MONDO:equivalentTo Skin Squamous Cell Carcinoma with Sarcomatoid Differentiation A rare carcinoma of the skin characterized by the presence of squamous cell carcinomatous and sarcomatous components. MONDO:0002529
MONDO:0855085 lichen planus-like keratosis NCIT:C165485 MONDO:equivalentTo Lichen Planus-Like Keratosis A benign intraepidermal squamoproliferative neoplasm characterized by irregular acanthosis, hyperkeratosis, parakeratosis, and prominent chronic inflammation. MONDO:0002093
MONDO:0855094 combined nevus NCIT:C165529 MONDO:equivalentTo Combined Nevus A nevus that contains two or more melanocytic nevus components in the same lesion. The cellular components can be any combination of any nevus variants, but most frequently, a common nevus component is combined with a blue nevus, deep penetrating nevus, or Spitz nevus component. (WHO 2018) MONDO:0044794
MONDO:0855104 proximal gastric adenocarcinoma NCIT:C165628 MONDO:equivalentTo Proximal Gastric Adenocarcinoma A gastric adenocarcinoma that arises from the proximal part of the stomach. MONDO:0005036
MONDO:0855113 mixed carcinoma NCIT:C165723 MONDO:equivalentTo Mixed Carcinoma A carcinoma characterized by the presence of more than one malignant epithelial histologic pattern. MONDO:0005853
MONDO:0855116 hormone receptor-negative breast carcinoma NCIT:C165743 MONDO:equivalentTo Hormone Receptor-Negative Breast Carcinoma Breast adenocarcinoma that is negative for hormone receptors. MONDO:0004988
MONDO:0855127 musculoskeletal neoplasm NCIT:C166354 MONDO:equivalentTo Musculoskeletal Neoplasm A benign, intermediate, or malignant neoplasm that affects muscles and bones. MONDO:0002081
MONDO:0855132 pancreatobiliary carcinoma NCIT:C166418 MONDO:equivalentTo Pancreatobiliary Carcinoma A carcinoma that arises from the pancreas, bile ducts, gallbladder, or ampulla of Vater. MONDO:0006181
MONDO:0855139 acute myeloid leukemia with ram immunophenotype NCIT:C167089 MONDO:equivalentTo Acute Myeloid Leukemia with RAM Immunophenotype A high risk pediatric acute myeloid leukemia with an extremely poor prognosis. The blasts show bright CD56 expression, dim-to-negative expression of CD45 and CD38, and lack of HLA-DR expression. This immunophenotype was named after one of the pediatric patient's initials (RAM), from Children's Oncology Group (COG) clinical trial AAML0531. MONDO:0004996
MONDO:0855140 obesity-related malignant neoplasm NCIT:C167168 MONDO:equivalentTo Obesity-Related Malignant Neoplasm A malignant neoplasm that occurs in the context of obesity. MONDO:0004992
MONDO:0855143 metastatic primary peritoneal carcinoma NCIT:C167203 MONDO:equivalentTo Metastatic Primary Peritoneal Carcinoma A carcinoma that arises from the peritoneum and has metastasized to another anatomic site. MONDO:0015686
MONDO:0855150 midgut neuroendocrine tumor NCIT:C167327 MONDO:equivalentTo Midgut Neuroendocrine Tumor A neuroendocrine tumor that arises from the jejunum, ileum, proximal colon, or appendix. MONDO:0000386
MONDO:0855151 adnexal adenocarcinoma, not otherwise specified NCIT:C167341 MONDO:equivalentTo Adnexal Adenocarcinoma, Not Otherwise Specified An adnexal carcinoma with ductal/glandular differentiation lacking specific histological features that would allow further classification. (WHO 2018) MONDO:0006973
MONDO:0855152 spiradenocylindroma NCIT:C167342 MONDO:equivalentTo Spiradenocylindroma A benign adnexal neoplasm with histological features of both spiradenoma and cylindroma in a single nodular lesion. MONDO:0021489
MONDO:0855153 spiradenocylindrocarcinoma NCIT:C167344 MONDO:equivalentTo Spiradenocylindrocarcinoma A carcinoma that arises in a spiradenocylindroma. MONDO:0005524
MONDO:0855154 malignant mixed tumor of the skin NCIT:C167346 MONDO:equivalentTo Malignant Mixed Tumor of the Skin A rare malignant skin neoplasm that arises from a benign mixed tumor of the skin (chondroid syringoma). MONDO:0002206
MONDO:0855157 syringocystadenocarcinoma papilliferum NCIT:C167365 MONDO:equivalentTo Syringocystadenocarcinoma Papilliferum A sweat gland carcinoma usually arising from a pre-existing syringocystadenoma papilliferum. MONDO:0005524
MONDO:0855158 adnexal cribriform carcinoma NCIT:C167366 MONDO:equivalentTo Adnexal Cribriform Carcinoma A rare indolent adnexal carcinoma with a cribriform pattern. MONDO:0006973
MONDO:0855159 adnexal secretory carcinoma NCIT:C167368 MONDO:equivalentTo Adnexal Secretory Carcinoma A rare adnexal carcinoma that is histopathologically identical to homologous lesions in the salivary gland and breast. (WHO 2018) MONDO:0006973
MONDO:0855160 signet ring cell/histiocytoid carcinoma NCIT:C167369 MONDO:equivalentTo Signet Ring Cell/Histiocytoid Carcinoma A rare aggressive adnexal carcinoma preferentially affecting the eyelid and histopathologically resembling a metastatic lobular carcinoma of the breast and/or some adenocarcinomas arising in the gastrointestinal tract. (WHO 2018) MONDO:0006973
MONDO:0855173 resectable glioma NCIT:C168573 MONDO:equivalentTo Resectable Glioma A glioma that is amenable to surgical resection. MONDO:0021042
MONDO:0855181 phyllodes tumor of anogenital mammary-type glands NCIT:C168602 MONDO:equivalentTo Phyllodes Tumor of Anogenital Mammary-Type Glands A rare phyllodes tumor that arises from mammary-like glands in the anogenital region. MONDO:0005078
MONDO:0855182 metastatic malignant neoplasm in the digestive system NCIT:C168669 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Digestive System A malignant neoplasm that has spread to the digestive system from another anatomic site. MONDO:0024880
MONDO:0855187 unresectable round cell liposarcoma NCIT:C168724 MONDO:equivalentTo Unresectable Round Cell Liposarcoma A round cell liposarcoma that is not amenable to surgical resection. MONDO:0005238
MONDO:0855221 skin soft tissue neoplasm NCIT:C169100 MONDO:equivalentTo Skin Soft Tissue Neoplasm A mesenchymal neoplasm that arises from the skin. MONDO:0006424
MONDO:0855230 metastatic malignant head and neck neoplasm NCIT:C170467 MONDO:equivalentTo Metastatic Malignant Head and Neck Neoplasm A malignant neoplasm that arises from the head and neck region and has spread to another anatomic site. MONDO:0005627
MONDO:0855232 skin pleomorphic liposarcoma NCIT:C170473 MONDO:equivalentTo Skin Pleomorphic Liposarcoma A rare pleomorphic liposarcoma arising from the skin. MONDO:0003600
MONDO:0855235 skin angiolipoma NCIT:C170478 MONDO:equivalentTo Skin Angiolipoma An angiolipoma arising from the skin. MONDO:0000964
MONDO:0855238 benign periampullary neoplasm NCIT:C170725 MONDO:equivalentTo Benign Periampullary Neoplasm A neoplasm that arises from the periampullary region and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential.. MONDO:0006734
MONDO:0855241 metastatic malignant breast neoplasm NCIT:C170728 MONDO:equivalentTo Metastatic Malignant Breast Neoplasm A malignant breast neoplasm that has metastasized to another anatomic site. MONDO:0007254
MONDO:0855243 primary peritoneal adenocarcinoma NCIT:C170733 MONDO:equivalentTo Primary Peritoneal Adenocarcinoma A rare adenocarcinoma that arises from the lining of the peritoneum. MONDO:0015686
MONDO:0855244 appendix mucinous neoplasm NCIT:C170734 MONDO:equivalentTo Appendix Mucinous Neoplasm An appendiceal neoplasm characterized by mucinous epithelial proliferation with extracellular mucin and pushing tumour margins. (WHO 2019) MONDO:0024338
MONDO:0855245 pleomorphic fibroma NCIT:C170736 MONDO:equivalentTo Pleomorphic Fibroma A benign, often polypoid, fibroblastic neoplasm characterized by bizarre pleomorphic cells. (WHO 2018) MONDO:0005167
MONDO:0855249 non-muscle invasive bladder urothelial carcinoma NCIT:C170772 MONDO:equivalentTo Non-Muscle Invasive Bladder Urothelial Carcinoma An infiltrating urothelial carcinoma of the bladder that has not invaded into the bladder muscularis propria. MONDO:0003890
MONDO:0855250 alveolar ridge squamous cell carcinoma NCIT:C170774 MONDO:equivalentTo Alveolar Ridge Squamous Cell Carcinoma Squamous cell carcinoma arising from the upper or lower alveolar ridge. MONDO:0004958
MONDO:0855252 metastatic malignant skin neoplasm NCIT:C170811 MONDO:equivalentTo Metastatic Malignant Skin Neoplasm A malignant neoplasm of the skin that has spread to other anatomic sites. MONDO:0024880
MONDO:0855256 metastatic rhabdoid tumor NCIT:C170828 MONDO:equivalentTo Metastatic Rhabdoid Tumor A rhabdoid tumor that has spread from the original site of growth to another anatomic site. MONDO:0002728
MONDO:0855262 malignant jejunal neoplasm NCIT:C170919 MONDO:equivalentTo Malignant Jejunal Neoplasm A primary or metastatic malignant neoplasm that affects the jejunum. MONDO:0002564
MONDO:0855263 metastatic carcinosarcoma NCIT:C170924 MONDO:equivalentTo Metastatic Carcinosarcoma Carcinosarcoma that has spread from its original site of growth to another anatomic site. MONDO:0024880
MONDO:0855266 malignant fundus neoplasm NCIT:C170940 MONDO:equivalentTo Malignant Fundus Neoplasm A primary or metastatic malignant neoplasm that affects the gastric fundus. MONDO:0001056
MONDO:0855281 human papillomavirus-related mucosal head and neck squamous cell carcinoma NCIT:C171023 MONDO:equivalentTo Human Papillomavirus-Related Mucosal Head and Neck Squamous Cell Carcinoma A squamous cell carcinoma associated with human papilloma virus, arising from the mucosal sites of head and neck. MONDO:0020657
MONDO:0855283 ovarian neuroendocrine carcinoma NCIT:C171032 MONDO:equivalentTo Ovarian Neuroendocrine Carcinoma A small cell carcinoma, pulmonary-type or large cell neuroendocrine carcinoma arising from the ovary. MONDO:0002481
MONDO:0855284 endometrial neuroendocrine carcinoma NCIT:C171033 MONDO:equivalentTo Endometrial Neuroendocrine Carcinoma A small cell or large cell neuroendocrine carcinoma arising from the endometrium. MONDO:0002447
MONDO:0855285 mediastinal non-hodgkin lymphoma NCIT:C171037 MONDO:equivalentTo Mediastinal Non-Hodgkin Lymphoma Non-Hodgkin lymphoma arising from the mediastinum. MONDO:0004021
MONDO:0855297 oligometastatic prostate carcinoma NCIT:C171265 MONDO:equivalentTo Oligometastatic Prostate Carcinoma Prostate carcinoma that has metastasized to a limited number of sites. MONDO:0004956
MONDO:0855330 acute myeloid leukemia arising from previous myeloproliferative neoplasm NCIT:C172129 MONDO:equivalentTo Acute Myeloid Leukemia Arising from Previous Myeloproliferative Neoplasm An acute myeloid leukemia developing in patients with a prior history of myeloproliferative neoplasm. MONDO:0019457
MONDO:0855331 acute myeloid leukemia arising from previous myelodysplastic/myeloproliferative neoplasm NCIT:C172130 MONDO:equivalentTo Acute Myeloid Leukemia Arising from Previous Myelodysplastic/Myeloproliferative Neoplasm An acute myeloid leukemia developing in patients with a prior history of myelodysplastic/myeloproliferative neoplasm. MONDO:0019457
MONDO:0855335 progesterone receptor-positive malignant neoplasm NCIT:C172183 MONDO:equivalentTo Progesterone Receptor-Positive Malignant Neoplasm A malignant neoplasm that is positive for progesterone receptors. MONDO:0004992
MONDO:0855336 sinusoidal hemangioma NCIT:C172206 MONDO:equivalentTo Sinusoidal Hemangioma A rare hemangioma occurring mainly in middle-aged adults. The most common location is in the trunk. The lesions are small, asymptomatic, and bluish. They are composed of irregular, dilated, congested thin-walled vascular channels with scant smooth muscle in a sinusoidal or sieve-like pattern. (WHO 2018) MONDO:0006557
MONDO:0855346 refractory myeloid neoplasm NCIT:C172281 MONDO:equivalentTo Refractory Myeloid Neoplasm A myeloid neoplasm that does not respond to treatment. MONDO:0005170
MONDO:0855368 skin ewing sarcoma NCIT:C172634 MONDO:equivalentTo Skin Ewing Sarcoma A rare Ewing sarcoma that arises from the skin. MONDO:0018270
MONDO:0855377 oxyntic gland adenoma NCIT:C172655 MONDO:equivalentTo Oxyntic Gland Adenoma A benign epithelial neoplasm composed of columnar cells with differentiation to chief cells, parietal cells, or both, with a high rate of progression to adenocarcinoma (submucosal invasion). (WHO 2019) MONDO:0006221
MONDO:0855378 gastroblastoma NCIT:C172659 MONDO:equivalentTo Gastroblastoma A very rare biphasic tumor arising in the gastric muscularis propria (usually of the antrum), generally in boys and young men. It is associated with MALAT1-GLI1 gene fusion. (WHO 2019) MONDO:0001056
MONDO:0855386 colorectal conventional adenoma NCIT:C172680 MONDO:equivalentTo Colorectal Conventional Adenoma A benign, premalignant colorectal neoplasm composed of dysplastic epithelium. The descriptor "conventional" distinguishes this from lesions in the serrated pathway. (WHO 2019) MONDO:0005484
MONDO:0855389 colorectal poorly cohesive adenocarcinoma NCIT:C172694 MONDO:equivalentTo Colorectal Poorly Cohesive Adenocarcinoma An adenocarcinoma that arises from the colorectal mucosa and is characterized by the presence of isolated malignant cells or malignant cells that form small aggregates. MONDO:0005008
MONDO:0855390 colorectal adenoma-like adenocarcinoma NCIT:C172699 MONDO:equivalentTo Colorectal Adenoma-Like Adenocarcinoma A well differentiated colorectal adenocarcinoma with good prognosis. It resembles a villous adenoma on the surface. MONDO:0005008
MONDO:0855391 inflammatory bowel disease-associated colorectal adenocarcinoma NCIT:C172700 MONDO:equivalentTo Inflammatory Bowel Disease-Associated Colorectal Adenocarcinoma A colorectal adenocarcinoma that develops in patients with a history of inflammatory bowel disease. MONDO:0005008
MONDO:0855393 steatohepatitic hepatocellular carcinoma NCIT:C172709 MONDO:equivalentTo Steatohepatitic Hepatocellular Carcinoma Hepatocellular carcinoma characterized by the presence of steatohepatitis features, including macrovesicular steatosis, fibrosis, ballooning of malignant hepatocytes, Mallory bodies, and inflammation. MONDO:0007256
MONDO:0855394 macrotrabecular massive hepatocellular carcinoma NCIT:C172710 MONDO:equivalentTo Macrotrabecular Massive Hepatocellular Carcinoma Hepatocellular carcinoma characterized by more than 50% growth of macrotrabecular pattern (equal to or more than 6 to 10 cells thick). It presents with higher grade and stage compared to conventional hepatocellular carcinoma. It has poor prognosis with early recurrence and poor overall survival. MONDO:0007256
MONDO:0855395 chromophobe hepatocellular carcinoma NCIT:C172712 MONDO:equivalentTo Chromophobe Hepatocellular Carcinoma Hepatocellular carcinoma characterized by the presence of malignant cells with smooth chromophobic cytoplasm, abrupt focal nuclear anaplasia, and scattered microscopic pseudocysts. MONDO:0007256
MONDO:0855396 neutrophil-rich hepatocellular carcinoma NCIT:C172713 MONDO:equivalentTo Neutrophil-Rich Hepatocellular Carcinoma Hepatocellular carcinoma characterized by the presence of diffuse neutrophil infiltrates within the tumor. MONDO:0007256
MONDO:0855397 small hepatocellular carcinoma NCIT:C172714 MONDO:equivalentTo Small Hepatocellular Carcinoma Hepatocellular carcinoma measuring equal to or less than 2 cm in diameter. It includes early hepatocellular carcinoma and small progressed hepatocellular carcinoma. MONDO:0007256
MONDO:0855398 liver mixed adenoneuroendocrine carcinoma NCIT:C172718 MONDO:equivalentTo Liver Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the liver and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0855401 gallbladder pyloric gland adenoma NCIT:C172731 MONDO:equivalentTo Gallbladder Pyloric Gland Adenoma A grossly visible non-invasive neoplasm of the gallbladder composed of uniform back-to-back mucinous glands arranged in a tubular configuration. (WHO 2019) MONDO:0006216
MONDO:0855408 pancreatic poorly cohesive adenocarcinoma NCIT:C172811 MONDO:equivalentTo Pancreatic Poorly Cohesive Adenocarcinoma An adenocarcinoma that arises from the pancreas and is characterized by the presence of isolated malignant cells or malignant cells that form small aggregates. MONDO:0005184
MONDO:0855409 pancreatic undifferentiated carcinoma with rhabdoid cells NCIT:C172812 MONDO:equivalentTo Pancreatic Undifferentiated Carcinoma with Rhabdoid Cells An undifferentiated carcinoma that arises from the pancreas. It is characterized by the presence of rhabdoid cells. MONDO:0006478
MONDO:0855413 conventional follicular dendritic cell sarcoma NCIT:C172846 MONDO:equivalentTo Conventional Follicular Dendritic Cell Sarcoma Follicular dendritic cell sarcoma that is not associated with Epstein-Barr virus. MONDO:0005764
MONDO:0855418 digestive system soft tissue neoplasm NCIT:C172852 MONDO:equivalentTo Digestive System Soft Tissue Neoplasm A benign, intermediate, or malignant mesenchymal neoplasm that arises from the digestive system. MONDO:0006424
MONDO:0855432 sinonasal spindle cell squamous carcinoma NCIT:C173079 MONDO:equivalentTo Sinonasal Spindle Cell Squamous Carcinoma A poorly differentiated squamous cell carcinoma arising from the sinonasal tract. It is characterized by the presence of malignant cells with spindle cell features. MONDO:0021663
MONDO:0855433 sinonasal lymphoepithelial carcinoma NCIT:C173080 MONDO:equivalentTo Sinonasal Lymphoepithelial Carcinoma A nonkeratinizing squamous cell carcinoma arising from the sinonasal tract. It is characterized by the presence of large cells with vesicular nuclei and prominent nucleoli, a syncytial growth pattern, and a lymphoplasmacytic infiltrate. MONDO:0002831
MONDO:0855435 head and neck nut carcinoma NCIT:C173087 MONDO:equivalentTo Head and Neck NUT Carcinoma A highly aggressive, poorly differentiated carcinoma that arises from the head and neck. Most cases are in the nasal cavity and paranasal sinuses. It is characterized by mutations and rearrangement of the NUT gene. MONDO:0005563
MONDO:0855439 malignant sinonasal neoplasm NCIT:C173097 MONDO:equivalentTo Malignant Sinonasal Neoplasm A primary or metastatic malignant neoplasm involving the nasal cavity and paranasal sinuses. MONDO:0056820
MONDO:0855471 peritoneal implant NCIT:C173164 MONDO:equivalentTo Peritoneal Implant Deposits of borderline, malignant, and rarely benign tumors, usually from the ovary, on the peritoneal surface. MONDO:0006901
MONDO:0855472 sinonasal ameloblastoma NCIT:C173166 MONDO:equivalentTo Sinonasal Ameloblastoma A locally aggressive, primarily gnathic (jaw) tumor with a high propensity for recurrence. It originates wholly within the sinonasal tract, without connection to gnathic sites, arising from sinonasal epithelium and showing histological features identical to those of its counterpart originating in the jaw. (WHO 2017) MONDO:0056820
MONDO:0855481 microsatellite stable colorectal carcinoma NCIT:C173324 MONDO:equivalentTo Microsatellite Stable Colorectal Carcinoma Colorectal carcinoma characterized by the absence of microsatellite instability. MONDO:0024331
MONDO:0855487 nasopharyngeal adenoid cystic carcinoma NCIT:C173340 MONDO:equivalentTo Nasopharyngeal Adenoid Cystic Carcinoma An adenoid cystic carcinoma that arises from the nasopharynx. MONDO:0006367
MONDO:0855489 ectopic pituitary neuroendocrine tumor NCIT:C173345 MONDO:equivalentTo Ectopic Pituitary Neuroendocrine Tumor A pituitary neuroendocrine tumor that does not involve the sella turcica. MONDO:0006373
MONDO:0855495 cutaneous merkel cell carcinoma NCIT:C173385 MONDO:equivalentTo Cutaneous Merkel Cell Carcinoma A rare aggressive neuroendocrine carcinoma that arises from the skin and most often affects older individuals. It is usually located in the head, neck, and extremities. The tumor is composed of small round cells with scanty cytoplasm. Merkel cell polyomavirus is implicated in the majority of cases. MONDO:0002656
MONDO:0855506 laryngeal chondroma NCIT:C173406 MONDO:equivalentTo Laryngeal Chondroma A benign neoplasm arising from hyaline cartilage of the larynx. It is characterized by the presence of chondrocytes, a lobulated growth pattern, and calcification. MONDO:0002360
MONDO:0855507 laryngeal chondrosarcoma NCIT:C173407 MONDO:equivalentTo Laryngeal Chondrosarcoma A chondrosarcoma that arises from hyaline cartilage of the larynx. MONDO:0002448
MONDO:0855526 head and neck melanocytic neoplasm NCIT:C173488 MONDO:equivalentTo Head and Neck Melanocytic Neoplasm A melanocytic neoplasm that arises from the skin or mucosal sites in the head and neck region. MONDO:0021143
MONDO:0855532 refractory primitive neuroectodermal tumor NCIT:C173565 MONDO:equivalentTo Refractory Primitive Neuroectodermal Tumor Primitive neuroectodermal tumor that does not respond to treatment. MONDO:0005462
MONDO:0855540 head and neck heterotopia-associated carcinoma NCIT:C173588 MONDO:equivalentTo Head and Neck Heterotopia-Associated Carcinoma A head and neck carcinoma arising from heterotopic tissue elements (i.e. histologically normal tissue of a particular type that is present at an abnormal anatomical site). (WHO 2017) MONDO:0002038
MONDO:0855551 salivary gland poorly differentiated carcinoma NCIT:C173649 MONDO:equivalentTo Salivary Gland Poorly Differentiated Carcinoma A high-grade carcinoma that arises from the salivary glands. This category includes large and small cell types with or without neuroendocrine differentiation. MONDO:0000521
MONDO:0855553 salivary gland lymphadenoma NCIT:C173659 MONDO:equivalentTo Salivary Gland Lymphadenoma A rare benign salivary gland tumor that consists of a well-circumscribed biphasic proliferation of epithelial cells and reactive lymphoid tissue. Sebaceous and non-sebaceous forms can be distinguished. (WHO 2017) MONDO:0021460
MONDO:0855558 sialolipoma NCIT:C173682 MONDO:equivalentTo Sialolipoma A benign salivary gland neoplasm composed of mature adipose tissue and epithelial tissue. It usually occurs in the parotid gland. MONDO:0021460
MONDO:0855575 appendix disorder NCIT:C173799 MONDO:equivalentTo Appendix Disorder A non-neoplastic or neoplastic disorder that affects the appendix.
MONDO:0855576 retroperitoneal undifferentiated pleomorphic sarcoma NCIT:C173808 MONDO:equivalentTo Retroperitoneal Undifferentiated Pleomorphic Sarcoma A rare undifferentiated pleomorphic sarcoma that arises from the retroperitoneum. MONDO:0001501
MONDO:0855577 lung alveolar soft part sarcoma NCIT:C173809 MONDO:equivalentTo Lung Alveolar Soft Part Sarcoma An exceptionally rare alveolar soft part sarcoma that arises from the lung. MONDO:0002426
MONDO:0855584 maxillofacial neoplasm NCIT:C173845 MONDO:equivalentTo Maxillofacial Neoplasm A neoplasm that arises in a maxillofacial bone. MONDO:0019060
MONDO:0855590 craniofacial fibrous dysplasia NCIT:C173926 MONDO:equivalentTo Craniofacial Fibrous Dysplasia Fibrous dysplasia affecting the craniofacial bones. MONDO:0000845
MONDO:0855591 benign head and neck neoplasm NCIT:C173932 MONDO:equivalentTo Benign Head and Neck Neoplasm A neoplasm that arises from the head and neck and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0005165
MONDO:0855593 aggressive papillary tumor NCIT:C174022 MONDO:equivalentTo Aggressive Papillary Tumor A locally invasive, papillary epithelial neoplasm arising in any area of the middle ear, including the mastoid process and air cells, and may fill the tympanic cavity. It is characterized by the presence of a papillary glandular pattern, with complex interdigitating papillae lying loosely or infiltrating fibrous connective tissue. (WHO 2017) MONDO:0021366
MONDO:0855594 benign inner ear neoplasm NCIT:C174023 MONDO:equivalentTo Benign Inner Ear Neoplasm A neoplasm that arises from the inner ear and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. Representative examples include vestibular schwannoma and lipoma. MONDO:0021474
MONDO:0855597 malignant inner ear neoplasm NCIT:C174026 MONDO:equivalentTo Malignant Inner Ear Neoplasm A malignant neoplasm that affects the inner ear. MONDO:0003277
MONDO:0855616 conjunctival oncocytoma NCIT:C174388 MONDO:equivalentTo Conjunctival Oncocytoma A benign epithelial neoplasm that arises from the conjunctiva. It is characterized by the presence of oncocytic cells with abundant eosinophilic and granular cytoplasm. MONDO:0010795
MONDO:0855617 conjunctival keratoacanthoma NCIT:C174390 MONDO:equivalentTo Conjunctival Keratoacanthoma A rapidly growing neoplasm that arises from the conjunctiva. It is characterized by a proliferation of squamous cells, acanthosis, keratinization, dysplasia, increased mitotic activity, and a central crater filled with keratinocytes. It is considered a variant of well-differentiated squamous cell carcinoma with distinct clinical behavior. MONDO:0006173
MONDO:0855618 conjunctival spindle cell carcinoma NCIT:C174398 MONDO:equivalentTo Conjunctival Spindle Cell Carcinoma A variant of conjunctival squamous cell carcinoma characterized by the presence of malignant spindle cells and/or pleomorphic cells. MONDO:0006173
MONDO:0855620 conjunctival carcinoma NCIT:C174403 MONDO:equivalentTo Conjunctival Carcinoma A carcinoma that arises from the conjunctiva. MONDO:0002466
MONDO:0855625 conjunctival subepithelial (stromal) nevus NCIT:C174426 MONDO:equivalentTo Conjunctival Subepithelial (Stromal) Nevus A conjunctival nevus characterized by an intrastromal proliferation of predominantly type B nevus cells. MONDO:0006172
MONDO:0855630 conjunctival blue nevus NCIT:C174452 MONDO:equivalentTo Conjunctival Blue Nevus A benign melanocytic neoplasm that arises from the conjunctiva. It is characterized by the presence of dendritic and spindle-shaped melanocytes in the subepithelial connective tissue. It presents as a dark brown or black, slightly elevated conjunctival lesion. MONDO:0006172
MONDO:0855631 atypical ewing sarcoma NCIT:C174456 MONDO:equivalentTo Atypical Ewing Sarcoma Ewing sarcoma characterized by the presence of large malignant cells with prominent nucleoli and irregular contours. MONDO:0012817
MONDO:0855633 conjunctival spitz nevus NCIT:C174493 MONDO:equivalentTo Conjunctival Spitz Nevus A rare nevus that arises from the conjunctiva. It is characterized by the presence of large spindle-shaped or epithelioid melanocytes. MONDO:0006172
MONDO:0855634 metastatic malignant neoplasm in the conjunctiva NCIT:C174496 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Conjunctiva A malignant neoplasm that has spread to the conjunctiva from another anatomic site. MONDO:0044913
MONDO:0855635 iris epithelioid cell melanoma NCIT:C174498 MONDO:equivalentTo Iris Epithelioid Cell Melanoma An iris melanoma characterized by the presence of malignant large epithelioid melanocytes. MONDO:0004064
MONDO:0855640 iris mixed epithelioid and spindle cell melanoma NCIT:C174506 MONDO:equivalentTo Iris Mixed Epithelioid and Spindle Cell Melanoma A melanoma arising from the iris. It is characterized by the presence of a mixture of spindle A melanoma cells, spindle B melanoma cells, and epithelioid melanoma cells. MONDO:0004064
MONDO:0855641 metastatic malignant neoplasm in the uvea NCIT:C174507 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Uvea A malignant neoplasm that has spread to the uvea from another anatomic site. MONDO:0002659
MONDO:0855646 retinal astrocytoma NCIT:C174539 MONDO:equivalentTo Retinal Astrocytoma An astrocytoma that arises from the retina. It is often found in association with the tuberous sclerosis complex. MONDO:0021231
MONDO:0855649 adenoma of the retinal pigment epithelium NCIT:C174550 MONDO:equivalentTo Adenoma of the Retinal Pigment Epithelium A benign neoplasm that arises from the retinal pigment epithelium. It consists of cords and tubules of variably pigmented proliferating retinal pigment epithelium cells, separated by fibrous stroma. Malignant transformation is rare. (WHO 2018) MONDO:0021453
MONDO:0855650 retinal pigment epithelium adenocarcinoma NCIT:C174551 MONDO:equivalentTo Retinal Pigment Epithelium Adenocarcinoma An adenocarcinoma that arises from the retinal pigment epithelium. The prognosis is good if the tumor has not extended extraocularly. MONDO:0002466
MONDO:0855653 ciliary body adenoma NCIT:C174560 MONDO:equivalentTo Ciliary Body Adenoma A benign neoplasm of the pigmented ciliary epithelium (pigmented epithelial adenoma) and/ or the non-pigmented ciliary epithelium (non-pigmented epithelial adenoma). (WHO 2018) MONDO:0021486
MONDO:0855654 ciliary body adenocarcinoma NCIT:C174561 MONDO:equivalentTo Ciliary Body Adenocarcinoma An adenocarcinoma arising from the pigmented or non-pigmented ciliary epithelium. MONDO:0002466
MONDO:0855667 incidental gallbladder carcinoma NCIT:C175214 MONDO:equivalentTo Incidental Gallbladder Carcinoma Gallbladder carcinoma that is discovered incidental to gallbladder surgery for another indication. MONDO:0003220
MONDO:0855668 metastatic malignant neoplasm in the regional lymph nodes NCIT:C175222 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Regional Lymph Nodes The spread of a malignant neoplasm from its original site of growth to nearby lymph nodes. MONDO:0005438
MONDO:0855669 lacrimal gland oncocytoma NCIT:C175264 MONDO:equivalentTo Lacrimal Gland Oncocytoma A benign epithelial neoplasm that arises from the lacrimal gland. It is characterized by the presence of oncocytic cells with abundant eosinophilic and granular cytoplasm. MONDO:0010795
MONDO:0855671 lacrimal gland myoepithelial carcinoma NCIT:C175274 MONDO:equivalentTo Lacrimal Gland Myoepithelial Carcinoma A carcinoma that arises from the lacrimal gland. It is characterized by the presence of a malignant cellular infiltrate exhibiting myoepithelial differentiation. MONDO:0003158
MONDO:0855672 lacrimal gland carcinosarcoma NCIT:C175279 MONDO:equivalentTo Lacrimal Gland Carcinosarcoma An aggressive, high grade malignant neoplasm that arises from the lacrimal gland. It is characterized by the presence of a malignant epithelial and a sarcomatous component. MONDO:0002464
MONDO:0855673 lacrimal gland epithelial-myoepithelial carcinoma NCIT:C175288 MONDO:equivalentTo Lacrimal Gland Epithelial-Myoepithelial Carcinoma A rare, slow-growing carcinoma that arises from the lacrimal gland. It is characterized by the presence of duct-like structures lined by two layers of cells, an inner layer composed of epithelial-type cells and an outer layer composed of clear, myoepithelial-type cells. MONDO:0002463
MONDO:0855674 lacrimal gland acinic cell carcinoma NCIT:C175290 MONDO:equivalentTo Lacrimal Gland Acinic Cell Carcinoma An extremely rare, low-grade, salivary gland-type carcinoma that arises from the lacrimal gland. It exhibits acinar differentiation. MONDO:0002475
MONDO:0855675 lacrimal gland warthin tumor NCIT:C175291 MONDO:equivalentTo Lacrimal Gland Warthin Tumor A rare benign tumor that arises from the lacrimal gland. It is characterized by an oncocytic epithelial component and dense lymphoid stroma. MONDO:0021488
MONDO:0855677 benign lacrimal system neoplasm NCIT:C175307 MONDO:equivalentTo Benign Lacrimal System Neoplasm A neoplasm that arises from the lacrimal gland or lacrimal drainage system and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0002460
MONDO:0855678 malignant lacrimal system neoplasm NCIT:C175308 MONDO:equivalentTo Malignant Lacrimal System Neoplasm A primary or metastatic malignant neoplasm affecting the lacrimal gland or the lacrimal drainage system. MONDO:0002460
MONDO:0855679 lacrimal drainage system neoplasm NCIT:C175316 MONDO:equivalentTo Lacrimal Drainage System Neoplasm A benign or malignant neoplasm that affects the lacrimal drainage system. MONDO:0002460
MONDO:0855684 lacrimal drainage system non-keratinizing squamous cell carcinoma NCIT:C175335 MONDO:equivalentTo Lacrimal Drainage System Non-Keratinizing Squamous Cell Carcinoma A squamous cell carcinoma of the lacrimal drainage system characterized by a plexiform or ribbon-like growth pattern, cytological atypia, and lack of histological evidence of keratinization. MONDO:0003492
MONDO:0855694 conjunctival non-hodgkin lymphoma NCIT:C175432 MONDO:equivalentTo Conjunctival Non-Hodgkin Lymphoma A non-Hodgkin lymphoma that arises from the conjunctiva. MONDO:0004034
MONDO:0855700 primary uveal non-hodgkin lymphoma NCIT:C175451 MONDO:equivalentTo Primary Uveal Non-Hodgkin Lymphoma An indolent, low-grade B-cell non-Hodgkin lymphoma that arises from the choroid, iris, or ciliary body. It is characterized by the presence of a diffuse infiltrate of small, round lymphocytes. Lymphoid follicles with germinal centers may be present. In the past these tumors were termed 'reactive lymphoid hyperplasia'. Now they are considered low-grade B-cell lymphomas, most commonly extranodal marginal zone lymphomas of mucosa-associated lymphoid tissue. MONDO:0004351
MONDO:0855708 conjunctival myxoma NCIT:C175495 MONDO:equivalentTo Conjunctival Myxoma A rare myxoma arising from the bulbar conjunctiva. MONDO:0044784
MONDO:0855710 conjunctival hemangioma NCIT:C175497 MONDO:equivalentTo Conjunctival Hemangioma A hemangioma that arises from the conjunctiva. MONDO:0006105
MONDO:0855711 conjunctival lymphangioma NCIT:C175498 MONDO:equivalentTo Conjunctival Lymphangioma A lymphangioma that arises from the conjunctiva. MONDO:0002013
MONDO:0855715 conjunctival sarcoma NCIT:C175502 MONDO:equivalentTo Conjunctival Sarcoma A sarcoma that arises from the conjunctiva. MONDO:0018078
MONDO:0855718 malignant hypothalamic neoplasm NCIT:C175539 MONDO:equivalentTo Malignant Hypothalamic Neoplasm A primary or metastatic malignant neoplasm that affects the hypothalamus. MONDO:0002786
MONDO:0855721 breast polymorphous adenocarcinoma NCIT:C175604 MONDO:equivalentTo Breast Polymorphous Adenocarcinoma A rare, low grade malignant epithelial neoplasm arising from the breast. It is characterized by the presence of uniform, small to medium size malignant epithelial cells and an infiltrating pattern. MONDO:0006256
MONDO:0855722 breast tall cell carcinoma with reversed polarity NCIT:C175607 MONDO:equivalentTo Breast Tall Cell Carcinoma with Reversed Polarity A rare subtype of invasive breast carcinoma characterized by tall columnar cells with reversed nuclear polarity, arranged in solid and solid papillary patterns, most commonly associated with IDH2 p.Arg172 hotspot mutations. (WHO 2019) MONDO:0006256
MONDO:0855725 metastatic malignant glomus tumor NCIT:C175662 MONDO:equivalentTo Metastatic Malignant Glomus Tumor A malignant glomus tumor that has spread from its original site of growth to another anatomic site. MONDO:0003340
MONDO:0855727 locally invasive desmoid-type fibromatosis NCIT:C175667 MONDO:equivalentTo Locally Invasive Desmoid-Type Fibromatosis Desmoid-type fibromatosis that has invaded the surrounding tissues. MONDO:0007608
MONDO:0855734 metastatic malignant neoplasm in the supraclavicular lymph nodes NCIT:C175934 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Supraclavicular Lymph Nodes The spread of a malignant neoplasm from its original site of growth to supraclavicular lymph nodes. MONDO:0005438
MONDO:0855737 breast classic lobular carcinoma in situ NCIT:C175949 MONDO:equivalentTo Breast Classic Lobular Carcinoma In Situ Breast lobular carcinoma in situ characterized by the presence of dyscohesive proliferations of type A and/or type B epithelial cells. Type A cells are small cells with uniform hyperchromatic nuclei, whereas type B cells have slightly larger vesicular nuclei, with mild variability in size and shape and with small nucleoli. The cell populations may be mixed in individual proliferations. (WHO 2019) MONDO:0006270
MONDO:0855738 breast florid lobular carcinoma in situ NCIT:C175950 MONDO:equivalentTo Breast Florid Lobular Carcinoma In Situ Breast lobular carcinoma in situ characterized by the presence of neoplastic cells with cytological features identical to classic lobular carcinoma in situ, but with marked distention of terminal ductal lobular units or ducts. MONDO:0006270
MONDO:0855740 breast ductal carcinoma in situ, comedo type NCIT:C176005 MONDO:equivalentTo Breast Ductal Carcinoma In Situ, Comedo Type Breast ductal carcinoma in situ characterized by the presence of sheets of tumor cells with evidence of central necrosis and associated karyorrhectic/nuclear debris. MONDO:0003575
MONDO:0855747 ocular surface squamous neoplasia NCIT:C176043 MONDO:equivalentTo Ocular Surface Squamous Neoplasia An umbrella term that comprises the spectrum of squamous neoplasms of the conjunctiva, ranging from low-grade squamous intraepithelial neoplasia to invasive conjunctival squamous cell carcinoma. MONDO:0020204
MONDO:0855748 breast cellular fibroadenoma NCIT:C176045 MONDO:equivalentTo Breast Cellular Fibroadenoma A fibroadenoma characterized by the presence of a pericanalicular growth pattern, increased stromal cellularity, and less than 2 mitoses per 10 high-power fields. MONDO:0002056
MONDO:0855749 primary breast angiosarcoma NCIT:C176251 MONDO:equivalentTo Primary Breast Angiosarcoma An angiosarcoma that arises from the breast parenchyma and is not associated with radiation exposure. MONDO:0003024
MONDO:0855751 breast angiolipoma NCIT:C176255 MONDO:equivalentTo Breast Angiolipoma An angiolipoma that arises from the breast. The majority are located in the subcutaneous tissue overlying the breast parenchyma, rather than in breast parenchyma. MONDO:0000970
MONDO:0855753 breast schwannoma NCIT:C176414 MONDO:equivalentTo Breast Schwannoma A schwannoma that arises from the breast. MONDO:0000620
MONDO:0855754 breast neurofibroma NCIT:C176415 MONDO:equivalentTo Breast Neurofibroma A neurofibroma that arises from the breast. MONDO:0000620
MONDO:0855756 synovial chondrosarcoma NCIT:C176467 MONDO:equivalentTo Synovial Chondrosarcoma An extremely rare chondrosarcoma arising from the synovium either as a de novo neoplasm or secondary to synovial chondromatosis. MONDO:0018078
MONDO:0855757 male breast carcinoma in situ NCIT:C176503 MONDO:equivalentTo Male Breast Carcinoma In Situ A proliferation of atypical neoplastic epithelial cells confined to the mammary ducts of the male breast. It includes the entire spectrum of carcinoma in situ observed in the female breast. It usually develops in the retroareolar region. MONDO:0005628
MONDO:0855758 invasive male breast carcinoma NCIT:C176504 MONDO:equivalentTo Invasive Male Breast Carcinoma A rare invasive carcinoma that arises from the male breast. Morphologically, it is similar to the invasive carcinomas that arise from the female breast. It usually develops in the retroareolar region. MONDO:0006256
MONDO:0855763 invasive female breast carcinoma NCIT:C176579 MONDO:equivalentTo Invasive Female Breast Carcinoma An invasive carcinoma that arises from the breast in females. MONDO:0006256
MONDO:0855764 female breast carcinoma in situ NCIT:C176580 MONDO:equivalentTo Female Breast Carcinoma In Situ A proliferation of atypical neoplastic epithelial cells confined to the mammary ducts of the female breast. MONDO:0004658
MONDO:0855783 functioning lung neuroendocrine tumor NCIT:C176705 MONDO:equivalentTo Functioning Lung Neuroendocrine Tumor A lung neuroendocrine tumor that is associated with carcinoid syndrome. MONDO:0021120
MONDO:0855784 non-functioning lung neuroendocrine tumor NCIT:C176706 MONDO:equivalentTo Non-Functioning Lung Neuroendocrine Tumor A lung neuroendocrine tumor that is not associated with carcinoid syndrome. MONDO:0021119
MONDO:0855809 metastatic malignant thoracic neoplasm NCIT:C176862 MONDO:equivalentTo Metastatic Malignant Thoracic Neoplasm A malignant thoracic neoplasm that has spread from its original site of growth to another anatomic site. MONDO:0024880
MONDO:0855811 psammocarcinoma NCIT:C176887 MONDO:equivalentTo Psammocarcinoma An extremely rare variant of serous carcinoma arising from the ovary or peritoneum. It is characterized by extensive formation of psammoma bodies, low-grade cytological features, and invasion of surrounding structures. MONDO:0004970
MONDO:0855859 infantile myofibromatosis 1 NCIT:C176943 MONDO:equivalentTo Infantile Myofibromatosis 1 A rare inherited form of myofibromatosis caused by autosomal dominant mutation(s) in the PDGFRB gene, encoding platelet-derived growth factor receptor beta. The condition is characterized by the onset of solitary or multicentric benign tumors in the skin, striated muscles, bones, and viscera. The lesions may be present at birth or become apparent in early infancy or even occasionally in adult life. MONDO:0016824
MONDO:0855860 infantile myofibromatosis 2 NCIT:C176944 MONDO:equivalentTo Infantile Myofibromatosis 2 A rare inherited form of myofibromatosis caused by autosomal dominant mutation(s) in the NOTCH3 gene, encoding neurogenic locus notch homolog protein 3. The condition is characterized by the onset of solitary or multicentric benign tumors in the skin, striated muscles, bones, and viscera. Soft tissue lesions may regress spontaneously whereas visceral lesions are associated with high morbidity and mortality. MONDO:0016824
MONDO:0855861 lipoma-like atypical lipomatous tumor/well differentiated liposarcoma NCIT:C176979 MONDO:equivalentTo Lipoma-Like Atypical Lipomatous Tumor/Well Differentiated Liposarcoma An atypical lipomatous tumor/well differentiated liposarcoma composed of mature adipocytes in which, unlike in benign lipoma, substantial variation in cell size is appreciated alongside nuclear atypia in fat cells or stromal spindle cells. (WHO 2020) MONDO:0006097
MONDO:0855862 superficial atypical lipomatous tumor/well differentiated liposarcoma NCIT:C176980 MONDO:equivalentTo Superficial Atypical Lipomatous Tumor/Well Differentiated Liposarcoma An atypical lipomatous tumor/well differentiated liposarcoma that occurs in a superficial body structure. MONDO:0006097
MONDO:0855863 atypical lipomatous tumor/well differentiated liposarcoma of deep soft tissue NCIT:C176981 MONDO:equivalentTo Atypical Lipomatous Tumor/Well Differentiated Liposarcoma of Deep Soft Tissue An atypical lipomatous tumor/well differentiated liposarcoma that occurs in deep soft tissue. MONDO:0006097
MONDO:0855864 myxoid pleomorphic liposarcoma NCIT:C176989 MONDO:equivalentTo Myxoid Pleomorphic Liposarcoma An exceptionally rare, aggressive adipocytic neoplasm, typically occurring in children and adolescents. Myxoid pleomorphic liposarcoma shows mixed histological features of conventional myxoid liposarcoma and pleomorphic liposarcoma and lacks the gene fusions and amplifications of myxoid liposarcoma, atypical lipomatous tumor, and dedifferentiated liposarcoma. (WHO 2020) MONDO:0005060
MONDO:0855883 plaque-like dermatofibrosarcoma protuberans NCIT:C177325 MONDO:equivalentTo Plaque-Like Dermatofibrosarcoma Protuberans A rare variant of dermatofibrosarcoma protuberans characterized by plaque-like growth, resembling plaque-like CD34-positive dermal fibroma. MONDO:0011934
MONDO:0855884 somatic-type malignancy NCIT:C177364 MONDO:equivalentTo Somatic-Type Malignancy A malignant non-germ cell component that typically develops secondarily within a germ cell tumor. The malignant cellular component is usually sarcomatous or carcinomatous. MONDO:0004992
MONDO:0855885 epithelioid myxofibrosarcoma NCIT:C177414 MONDO:equivalentTo Epithelioid Myxofibrosarcoma A rare subtype of myxofibrosarcoma composed predominantly of malignant epithelioid cells with abundant eosinophilic cytoplasm. MONDO:0019202
MONDO:0855891 bladder flat urothelial carcinoma NCIT:C177531 MONDO:equivalentTo Bladder Flat Urothelial Carcinoma An in situ or invasive urothelial carcinoma that arises from the bladder wall and does not grow toward the hollow part of the bladder. MONDO:0005611
MONDO:0855897 epithelioid hemangioendothelioma with wwtr1-camta1 gene fusion NCIT:C177552 MONDO:equivalentTo Epithelioid Hemangioendothelioma with WWTR1-CAMTA1 Gene Fusion Epithelioid hemangioendothelioma characterized by a t(1;3)(p36;q23-q25) translocation, resulting in a WWTR1-CAMTA1 gene fusion. This translocation and associated gene fusion occur in more than 90% of epithelioid hemangioendotheliomas. MONDO:0015523
MONDO:0855898 epithelioid hemangioendothelioma with yap1-tfe3 gene fusion NCIT:C177553 MONDO:equivalentTo Epithelioid Hemangioendothelioma with YAP1-TFE3 Gene Fusion Epithelioid hemangioendothelioma characterized by a YAP1-TFE3 gene fusion. This gene fusion occurs in a subset of epithelioid hemangioendotheliomas characterized by the presence of well-formed vessels lined by epithelioid endothelial cells with abundant eosinophilic cytoplasm. Patients with YAP1-TFE3 gene fusion tumors tend to be younger than those with a WWTR1-CAMTA1 gene fusion. MONDO:0015523
MONDO:0855909 who grade 1 glioma NCIT:C177797 MONDO:equivalentTo WHO Grade 1 Glioma A category of low grade gliomas that includes subependymal giant cell astrocytoma, pilocytic astrocytoma, angiocentric glioma, and subependymoma. MONDO:0021637
MONDO:0855911 poorly differentiated chordoma NCIT:C177898 MONDO:equivalentTo Poorly Differentiated Chordoma A rare, aggressive type of chordoma characterized by loss of SMARCB1 expression. It affects children and occasionally young adults. Females are affected twice as frequently as males. It usually arises in the axial skeleton. It is composed of sheets or nests of malignant epithelioid cells with abundant eosinophilic cytoplasm. The prognosis is poor. MONDO:0008978
MONDO:0855914 ebv-associated smooth muscle tumor NCIT:C178217 MONDO:equivalentTo EBV-Associated Smooth Muscle Tumor A rare smooth muscle neoplasm of uncertain biological potential. It is associated with Epstein-Barr virus infection and seen in patients with immunodeficiency, including primary immunodeficiency, HIV/AIDS infection, and post-transplant immunosuppression. MONDO:0006975
MONDO:0855915 pleomorphic leiomyosarcoma NCIT:C178220 MONDO:equivalentTo Pleomorphic Leiomyosarcoma A leiomyosarcoma characterized by the presence of poorly differentiated areas with pleomorphic appearance, in addition to areas with typical morphologic features. MONDO:0005058
MONDO:0855916 epithelioid schwannoma NCIT:C178245 MONDO:equivalentTo Epithelioid Schwannoma A schwannoma characterized by the presence of epithelioid cells with eosinophilic cytoplasm, within a myxoid and/or hyalinized stroma. MONDO:0002546
MONDO:0855929 round cell sarcoma with ewsr1-non-ets fusion NCIT:C178459 MONDO:equivalentTo Round Cell Sarcoma with EWSR1-non-ETS Fusion A group of rare round and spindle cell sarcomas characterized by the presence of EWSR1 or FUS fusions involving partners unrelated to the ETS gene family. This category includes EWSR1-NFATC2, EWSR1-PATZ1, and FUS-NFATC2 sarcomas. MONDO:0006974
MONDO:0855930 sarcoma with bcor genetic alterations NCIT:C178465 MONDO:equivalentTo Sarcoma with BCOR Genetic Alterations A group of rare primitive round cell sarcomas characterized by the presence of BCOR genetic alterations. This category includes sarcomas with BCOR-related gene fusions, most frequently BCOR-CCNB3, and sarcomas showing internal tandem duplication (BCOR-ITD). MONDO:0006974
MONDO:0855935 gastric melanoma NCIT:C178519 MONDO:equivalentTo Gastric Melanoma A melanoma that arises from mucosa of the stomach. MONDO:0001056
MONDO:0855938 yolk sac tumor with somatic-type malignancy NCIT:C178523 MONDO:equivalentTo Yolk Sac Tumor with Somatic-Type Malignancy A yolk sac tumor that is characterized by morphologic transformation to somatic-type malignancy. The somatic-type malignant component most often is sarcomatous or carcinomatous. MONDO:0005744
MONDO:0855939 conventional chordoma NCIT:C178563 MONDO:equivalentTo Conventional Chordoma A malignant bone tumor arising from the remnants of the fetal notochord. It is characterized by the presence of large epithelioid cells with clear to light eosinophilic cytoplasm. Some of the cells are large with bubbly, vacuolated cytoplasm (physaliphorous cells). The cells form cords and nests that are embedded within an extracellular myxoid matrix. MONDO:0008978
MONDO:0855941 bone langerhans cell histiocytosis NCIT:C178607 MONDO:equivalentTo Bone Langerhans Cell Histiocytosis Langerhans cell histiocytosis affecting the bone. MONDO:0019060
MONDO:0855942 bone erdheim-chester disease NCIT:C178609 MONDO:equivalentTo Bone Erdheim-Chester Disease Erdheim-Chester disease affecting the bone. MONDO:0019060
MONDO:0855961 b-cell lymphoproliferative disorder NCIT:C179052 MONDO:equivalentTo B-Cell Lymphoproliferative Disorder A non-neoplastic or neoplastic proliferation of B-lymphocytes.
MONDO:0855962 t/nk-cell lymphoproliferative disorder NCIT:C179053 MONDO:equivalentTo T/NK-Cell Lymphoproliferative Disorder A non-neoplastic or neoplastic proliferation of T-lymphocytes and/or NK-cells.
MONDO:0855976 ovarian signet ring cell carcinoma NCIT:C179208 MONDO:equivalentTo Ovarian Signet Ring Cell Carcinoma An extremely rare adenocarcinoma that arises from the ovary. It is characterized by the presence of signet ring malignant epithelial cells. MONDO:0005092
MONDO:0855982 myxoid glioneuronal tumor NCIT:C179229 MONDO:equivalentTo Myxoid Glioneuronal Tumor A rare, low-grade glioneuronal neoplasm characterized by a dinucleotide mutation at codon 385 of the PDGFR gene. It usually occurs in the septum pellucidum. It has also been described in the corpus callosum and periventricular white matter of the lateral ventricle. It has histologic features reminiscent of either dysembryoplastic neuroepithelial tumor or rosette-forming glioneuronal tumor. It is composed of oligodendrocyte-like cells in a prominent myxoid stroma. MONDO:0016729
MONDO:0855983 borderline ovarian seromucinous tumor NCIT:C179259 MONDO:equivalentTo Borderline Ovarian Seromucinous Tumor A low grade ovarian epithelial neoplasm characterized by the presence of atypical neoplastic serous and mucinous cells. MONDO:0016093
MONDO:0855987 mesonephric-like adenocarcinoma NCIT:C179320 MONDO:equivalentTo Mesonephric-Like Adenocarcinoma An exceedingly rare adenocarcinoma that arises from the uterine corpus and ovary and displays mesonephric differentiation. Some tumors are thought to derive from mesonephric duct (Wolffian duct) remnants. Others may have a Mullerian duct lineage. MONDO:0001416
MONDO:0855990 ovarian dedifferentiated carcinoma NCIT:C179334 MONDO:equivalentTo Ovarian Dedifferentiated Carcinoma An aggressive carcinoma arising from the ovary. Most patients present with advanced disease. Microscopically, it is characterized by the presence of an undifferentiated carcinomatous component and a second component of either endometrioid carcinoma or, rarely, serous carcinoma. MONDO:0005140
MONDO:0855991 ovarian mixed cell adenocarcinoma NCIT:C179339 MONDO:equivalentTo Ovarian Mixed Cell Adenocarcinoma An adenocarcinoma that arises from the ovary and is characterized by the presence of two or more adenocarcinoma components, most often endometrioid and clear cell. MONDO:0002752
MONDO:0855993 giant cell-rich osteosarcoma NCIT:C179410 MONDO:equivalentTo Giant Cell-Rich Osteosarcoma An exceedingly rare, high-grade variant of conventional osteosarcoma characterized by the presence of numerous osteoclast-like giant cells and variable amount of tumor osteoid. MONDO:0002631
MONDO:0855995 unresectable plexiform neurofibroma NCIT:C179423 MONDO:equivalentTo Unresectable Plexiform Neurofibroma Plexiform neurofibroma that is not amenable to surgical resection. MONDO:0003304
MONDO:0855999 ovarian neuroectodermal-type tumor NCIT:C179474 MONDO:equivalentTo Ovarian Neuroectodermal-Type Tumor A rare ovarian malignant tumor with neuroectodermal differentiation. It is characterized either by a small round cell proliferation or by neuronal or glial differentiation. MONDO:0008170
MONDO:0856000 ovarian wolffian tumor NCIT:C179548 MONDO:equivalentTo Ovarian Wolffian Tumor An epithelial neoplasm of Wolffian (mesonephric) origin arising from the ovarian hilum. Most tumors behave in a benign fashion. MONDO:0002229
MONDO:0856002 her2-low breast carcinoma NCIT:C179553 MONDO:equivalentTo HER2-Low Breast Carcinoma A breast adenocarcinoma defined by low expression of HER2 (IHC1+ or IHC2+; FISH negative). MONDO:0004988
MONDO:0856003 peritoneal calcifying fibrous tumor NCIT:C179560 MONDO:equivalentTo Peritoneal Calcifying Fibrous Tumor A benign well-circumscribed lesion arising from the mesentery. It is characterized by the presence of fibroblasts, lymphoplasmacytic infiltrates, collagenous stroma formation, psammoma bodies, and dystrophic calcifications. MONDO:0000650
MONDO:0856016 basal ganglia neoplasm NCIT:C179882 MONDO:equivalentTo Basal Ganglia Neoplasm A benign or malignant neoplasm that affects the basal ganglia. MONDO:0021374
MONDO:0856017 cerebellar peduncle neoplasm NCIT:C179883 MONDO:equivalentTo Cerebellar Peduncle Neoplasm A benign or malignant neoplasm that affects the cerebellar peduncle. MONDO:0002913
MONDO:0856018 corpus callosum neoplasm NCIT:C179884 MONDO:equivalentTo Corpus Callosum Neoplasm A benign or malignant neoplasm that affects the corpus callosum. MONDO:0021374
MONDO:0856019 oral cavity carcinoma cuniculatum NCIT:C179894 MONDO:equivalentTo Oral Cavity Carcinoma Cuniculatum A variant of well-differentiated squamous cell carcinoma arising from the oral cavity. It is characterized by the presence of minimal cytological atypia, multiple keratin-filled crypts, and intraepithelial neutrophils. MONDO:0021538
MONDO:0856021 uterine ligament leiomyoma NCIT:C179923 MONDO:equivalentTo Uterine Ligament Leiomyoma A leiomyoma that arises from the broad or other uterine ligaments. MONDO:0001572
MONDO:0856022 uterine ligament adenomyoma NCIT:C179925 MONDO:equivalentTo Uterine Ligament Adenomyoma A benign neoplasm that arises from the broad or other uterine ligaments. It is characterized by the presence of a glandular and a mesenchymal component. MONDO:0005635
MONDO:0856024 uterine ligament wolffian tumor NCIT:C179927 MONDO:equivalentTo Uterine Ligament Wolffian Tumor An epithelial neoplasm of Wolffian (mesonephric) origin arising from a uterine ligament. Most tumors behave in a benign fashion. MONDO:0004255
MONDO:0856025 uterine ligament ependymoma NCIT:C179928 MONDO:equivalentTo Uterine Ligament Ependymoma A rare neoplasm that arises from the broad or other uterine ligaments and shows ependymal differentiation. MONDO:0021629
MONDO:0856026 broad ligament neoplasm NCIT:C179931 MONDO:equivalentTo Broad Ligament Neoplasm A benign, borderline, or malignant neoplasm that affects the broad ligament. MONDO:0021629
MONDO:0856027 microsatellite stable ovarian carcinoma NCIT:C180332 MONDO:equivalentTo Microsatellite Stable Ovarian Carcinoma Ovarian carcinoma characterized by the absence of microsatellite instability. MONDO:0005140
MONDO:0856028 microsatellite stable endometrial carcinoma NCIT:C180335 MONDO:equivalentTo Microsatellite Stable Endometrial Carcinoma Endometrial carcinoma characterized by the absence of microsatellite instability. MONDO:0002447
MONDO:0856030 polymorphous low grade neuroepithelial tumor of the young NCIT:C180378 MONDO:equivalentTo Polymorphous Low Grade Neuroepithelial Tumor of the Young A low-grade cerebral tumor associated with seizures and in many cases refractory epilepsy. It usually occurs in the second and third decades of life. It is characterized by the presence of oligodendroglioma-like components. It may also contain astrocytic components. MAPK pathway-activating genetic alterations play a role in the development of this tumor. Causative gene alterations include mutations resulting in the expression of BRAF p.V600E and gene fusions involving FGFR2 or FGFR3 genes. IDH gene mutations and 1p/19q codeletion are not present. MONDO:0016729
MONDO:0856033 tectal glioma NCIT:C180407 MONDO:equivalentTo Tectal Glioma A glioma that arises from the tectum mesenchephali. MONDO:0021042
MONDO:0856035 pole-ultramutated endometrial endometrioid adenocarcinoma NCIT:C180512 MONDO:equivalentTo POLE-Ultramutated Endometrial Endometrioid Adenocarcinoma An endometrial endometrioid adenocarcinoma characterized by mutations in the exonuclease domain of the DNA polymerase epsilon (POLE) gene that result in an ultra-mutated tumor phenotype. MONDO:0006192
MONDO:0856036 mismatch repair-deficient endometrial endometrioid adenocarcinoma NCIT:C180514 MONDO:equivalentTo Mismatch Repair-Deficient Endometrial Endometrioid Adenocarcinoma An endometrial endometrioid adenocarcinoma characterized by mismatch repair (MMR) deficiency caused by inactivating methylation or less frequently mutation of an MMR gene (MLH1, PMS2, MSH2, or MSH6). MONDO:0006192
MONDO:0856037 p53-mutant endometrial endometrioid adenocarcinoma NCIT:C180515 MONDO:equivalentTo p53-Mutant Endometrial Endometrioid Adenocarcinoma An endometrial endometrioid adenocarcinoma characterized by the presence of p53 gene mutations. MONDO:0006192
MONDO:0856038 no specific molecular profile endometrial endometrioid adenocarcinoma NCIT:C180516 MONDO:equivalentTo No Specific Molecular Profile Endometrial Endometrioid Adenocarcinoma An endometrial endometrioid adenocarcinoma characterized by the absence of POLE gene mutations, mismatch repair (MMR) deficiency, and p53 gene mutations. MONDO:0006192
MONDO:0856040 dysembryoplastic neuroepithelial-like tumor of the septum pellucidum NCIT:C180532 MONDO:equivalentTo Dysembryoplastic Neuroepithelial-Like Tumor of the Septum Pellucidum A very rare, low-grade midline brain neoplasm that affects the septum pellucidum. It is characterized by similar histological features to those found in dysembryoplastic neuroepithelial tumor, but does not display multinodularity. It usually manifests with symptoms related to increased intracranial pressure. Epilepsy has been reported in approximately one third of patients. PDGFRA gene mutations have been identified in the majority of patients. Alterations in FGFR1 and NF1 genes have also been reported. BRAF mutations which represent the most common molecular alteration found in cortical dysembryoplastic neuroepithelial tumor, were absent in this rare group of midline tumors. MONDO:0016729
MONDO:0856041 endometrial mucinous adenocarcinoma, intestinal-type NCIT:C180536 MONDO:equivalentTo Endometrial Mucinous Adenocarcinoma, Intestinal-Type A rare mucinous adenocarcinoma arising from intestinal metaplasia of the endometrium. MONDO:0005461
MONDO:0856042 endometrial mucinous adenocarcinoma, gastric-type NCIT:C180537 MONDO:equivalentTo Endometrial Mucinous Adenocarcinoma, Gastric-Type A rare mucinous adenocarcinoma arising from gastric metaplasia of the endometrium. MONDO:0005461
MONDO:0856044 uterine corpus central primitive neuroectodermal tumor NCIT:C180546 MONDO:equivalentTo Uterine Corpus Central Primitive Neuroectodermal Tumor A rare uterine corpus malignant small round cell tumor with neuroglial differentiation. The prognosis is poor. MONDO:0005210
MONDO:0856048 urothelial carcinoma, high grade NCIT:C180606 MONDO:equivalentTo Urothelial Carcinoma, High Grade Urothelial carcinoma characterized by the presence of neoplastic epithelial cells with high grade features. MONDO:0040679
MONDO:0856052 gestational trophoblastic disorder NCIT:C180633 MONDO:equivalentTo Gestational Trophoblastic Disorder A group of pregnancy-related proliferative disorders. It includes non-neoplastic disorders (complete hydatidiform mole, partial hydatidiform mole, placental site nodule and plaque, and exaggerated placental site reaction) and neoplasms (invasive hydatidiform mole and trophoblastic tumors). Trophoblastic tumors include gestational choriocarcinoma, epithelioid trophoblastic tumor, placental-site trophoblastic tumor, and mixed trophoblastic tumor.
MONDO:0856053 mixed trophoblastic tumor NCIT:C180634 MONDO:equivalentTo Mixed Trophoblastic Tumor A gestational trophoblastic tumor characterized by the presence of two or three histological types of gestational trophoblastic tumor, including choriocarcinoma, placental site trophoblastic tumor, and epithelioid trophoblastic tumor. MONDO:0018944
MONDO:0856054 metastatic hydatidiform mole NCIT:C180635 MONDO:equivalentTo Metastatic Hydatidiform Mole The spread of abnormal molar chorionic villi from an invasive hydatidiform mole in the uterine cavity to other anatomic sites, usually the vaginal wall and pelvis. MONDO:0020549
MONDO:0856055 low grade papillary schneiderian carcinoma NCIT:C180670 MONDO:equivalentTo Low Grade Papillary Schneiderian Carcinoma A rare sinonasal carcinoma characterized by the presence of a papillary architecture and bland morphological features similar to the Schneiderian papilloma, a pushing pattern of stromal invasion, and an increased risk of local recurrence. MONDO:0056819
MONDO:0856057 cervical squamous cell carcinoma, not otherwise specified NCIT:C180839 MONDO:equivalentTo Cervical Squamous Cell Carcinoma, Not Otherwise Specified Cervical squamous cell carcinoma in which information on the p16 immunohistochemistry or HPV testing status is not available. MONDO:0006143
MONDO:0856060 human papillomavirus-independent cervical adenocarcinoma NCIT:C180848 MONDO:equivalentTo Human Papillomavirus-Independent Cervical Adenocarcinoma Cervical adenocarcinoma not associated with human papillomavirus infection. MONDO:0005153
MONDO:0856067 cervical adenocarcinoma, not otherwise specified NCIT:C180870 MONDO:equivalentTo Cervical Adenocarcinoma, Not Otherwise Specified A cervical adenocarcinoma that cannot be classified by WHO criteria or International Endocervical Adenocarcinoma Criteria and Classification (IECC). MONDO:0005153
MONDO:0856070 cervical mucoepidermoid carcinoma NCIT:C180878 MONDO:equivalentTo Cervical Mucoepidermoid Carcinoma A rare carcinoma that arises from the cervix. It is characterized by the presence of squamous cells, mucus producing cells, and cells of intermediate type. MONDO:0005131
MONDO:0856071 cervical germ cell tumor NCIT:C180879 MONDO:equivalentTo Cervical Germ Cell Tumor A rare germ cell tumor that arises from the cervix. Examples include mature cystic teratoma, yolk sac tumor, and choriocarcinoma. MONDO:0005040
MONDO:0856072 minor salivary gland intraductal papillary neoplasm NCIT:C180880 MONDO:equivalentTo Minor Salivary Gland Intraductal Papillary Neoplasm A rare papillary neoplasm that grows within and is limited to the duct system of the minor salivary glands. This category includes papillary cystadenoma, ductal papilloma (including the intraductal and inverted variants), sialadenoma papilliferum, and intraductal papillary mucinous neoplasm. MONDO:0021370
MONDO:0856074 adult myofibroma NCIT:C180888 MONDO:equivalentTo Adult Myofibroma A rare myofibroma that occurs in adults. MONDO:0006312
MONDO:0856077 human papillomavirus-related vaginal squamous cell carcinoma NCIT:C180917 MONDO:equivalentTo Human Papillomavirus-Related Vaginal Squamous Cell Carcinoma A squamous cell carcinoma that arises from the vagina and is caused by human papillomavirus infection. MONDO:0020657
MONDO:0856083 vaginal adenocarcinoma of skene gland origin NCIT:C180947 MONDO:equivalentTo Vaginal Adenocarcinoma of Skene Gland Origin A rare vaginal adenocarcinoma arising from the Skene gland. It is characterized by morphological and immunohistochemical features similar to prostate adenocarcinoma. MONDO:0020653
MONDO:0856100 hybrid salivary gland tumor NCIT:C181078 MONDO:equivalentTo Hybrid Salivary Gland Tumor A rare neoplasm that arises from the salivary gland and consists of at least two histologically distinct types of tumor within the same topographic location. The tumor components can be either benign or malignant. MONDO:0021043
MONDO:0856104 eyelid basal cell carcinoma NCIT:C181159 MONDO:equivalentTo Eyelid Basal Cell Carcinoma A basal cell carcinoma that arises from the eyelid. MONDO:0003876
MONDO:0856106 major salivary gland squamous cell carcinoma NCIT:C181161 MONDO:equivalentTo Major Salivary Gland Squamous Cell Carcinoma A squamous cell carcinoma that arises from the parotid or submandibular gland. MONDO:0044740
MONDO:0856110 lung rhabdomyosarcoma NCIT:C181201 MONDO:equivalentTo Lung Rhabdomyosarcoma A rare rhabdomyosarcoma that arises from the lung. MONDO:0002426
MONDO:0856111 lung hodgkin lymphoma NCIT:C181205 MONDO:equivalentTo Lung Hodgkin Lymphoma A rare Hodgkin lymphoma that arises in and is confined to the lung at the time of diagnosis. MONDO:0003987
MONDO:0856112 primary bone hodgkin lymphoma NCIT:C181207 MONDO:equivalentTo Primary Bone Hodgkin Lymphoma An exceedingly rare Hodgkin lymphoma that arises from the bone, without lymph node or other extranodal involvement. MONDO:0004952
MONDO:0856114 cervical cancer by ajcc v9 stage NCIT:C181562 MONDO:equivalentTo Cervical Cancer by AJCC v9 Stage A term that refers to the staging of cervical cancer according to the American Joint Committee on Cancer, 9th edition. This staging system applies to carcinomas and carcinosarcomas. It does not apply to sarcomas, lymphomas, and melanomas. Sarcomas are staged according to the corpus uteri classification for sarcomas. Lymphomas are staged according to Hodgkin and non-Hodgkin lymphoma classification. Melanomas are not staged. (from AJCC 9th Ed.) MONDO:0005131
MONDO:0856117 epiglottic squamous cell carcinoma NCIT:C181714 MONDO:equivalentTo Epiglottic Squamous Cell Carcinoma A squamous cell carcinoma of the larynx that arises from the epiglottis. MONDO:0004293
MONDO:0856124 vulvar squamous cell carcinoma, not otherwise specified NCIT:C181902 MONDO:equivalentTo Vulvar Squamous Cell Carcinoma, Not Otherwise Specified Vulvar squamous cell carcinoma in which information on the p16 immunohistochemistry or HPV testing status is not available. MONDO:0024609
MONDO:0856128 endometrial mucosa-associated lymphoid tissue lymphoma NCIT:C181910 MONDO:equivalentTo Endometrial Mucosa-Associated Lymphoid Tissue Lymphoma A rare extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue affecting the endometrium. MONDO:0007650
MONDO:0856134 vulvar kaposi sarcoma NCIT:C181938 MONDO:equivalentTo Vulvar Kaposi Sarcoma A Kaposi sarcoma arising from the vulva. MONDO:0005055
MONDO:0856136 vulvar rhabdomyosarcoma NCIT:C181944 MONDO:equivalentTo Vulvar Rhabdomyosarcoma A malignant mesenchymal neoplasm with skeletal muscle differentiation arising from the vulva. MONDO:0005214
MONDO:0856137 vulvar epithelioid sarcoma NCIT:C181971 MONDO:equivalentTo Vulvar Epithelioid Sarcoma An epithelioid sarcoma that arises from the vulva. MONDO:0005214
MONDO:0856139 vulvar ewing sarcoma NCIT:C181977 MONDO:equivalentTo Vulvar Ewing Sarcoma Ewing sarcoma arising from the vulva. MONDO:0018270
MONDO:0856154 bronchiolar adenoma/ciliated muconodular papillary tumor NCIT:C183045 MONDO:equivalentTo Bronchiolar Adenoma/Ciliated Muconodular Papillary Tumor A rare, benign, circumscribed nodule arising from the bronchioles. It is usually seen in middle-aged to elderly patients. It is characterized by the presence a two-layer cellular structure composed of a basal and luminal layer. MONDO:0003422
MONDO:0856155 invasive lung non-mucinous adenocarcinoma NCIT:C183109 MONDO:equivalentTo Invasive Lung Non-Mucinous Adenocarcinoma An invasive adenocarcinoma that arises from the lung. It is characterized by the absence of tall columnar cells and mucin production. This category includes lepidic adenocarcinoma, acinar adenocarcinoma, papillary adenocarcinoma, micropapillary adenocarcinoma, and solid adenocarcinoma. MONDO:0040677
MONDO:0856156 thoracic smarca4-deficient undifferentiated tumor NCIT:C183115 MONDO:equivalentTo Thoracic SMARCA4-Deficient Undifferentiated Tumor An aggressive, high-grade malignant neoplasm characterized by biallelic inactivation of SMARCA4 gene. It affects adults, usually heavy smokers, and involves the thorax (lung, pulmonary hilum, mediastinum, and/or pleura) with or without chest wall invasion. It is composed of sheets of malignant large round to epithelioid cells. Rhabdoid cells may be present. Increased number of mitoses and necrosis are frequently seen. The prognosis is poor. MONDO:0003274
MONDO:0856158 lung intravascular large b-cell lymphoma NCIT:C183121 MONDO:equivalentTo Lung Intravascular Large B-Cell Lymphoma An aggressive extranodal B-cell non-Hodgkin lymphoma that affects the lung. It is characterized by the presence of large neoplastic lymphocytes exclusively in the lumina of small vessels, particularly capillaries. MONDO:0020324
MONDO:0856161 pleural mesothelioma in situ NCIT:C183134 MONDO:equivalentTo Pleural Mesothelioma In Situ A non-invasive mesothelial neoplasm that arises from the pleura. It is characterized by the proliferation of a single-layer of flat or cuboidal neoplastic mesothelial cells. Cytological atypia is absent or minimal. Mitoses are absent. BAP1 gene inactivation and/or CDKN2A gene homozygous deletion are present. Patients present with non-resolving pleural effusion. It may progress to invasive epithelioid mesothelioma. MONDO:0003308
MONDO:0856165 cardiac diffuse large b-cell lymphoma NCIT:C183146 MONDO:equivalentTo Cardiac Diffuse Large B-Cell Lymphoma A diffuse large B-cell lymphoma that arises from the heart. MONDO:0003917
MONDO:0856172 pleural calcifying fibrous tumor NCIT:C183277 MONDO:equivalentTo Pleural Calcifying Fibrous Tumor A rare, benign, well-circumscribed lesion arising from the pleura. It is characterized by the presence of fibroblasts, lymphoplasmacytic infiltrates, collagenous stroma formation, and dystrophic calcifications. Patients may present with chest pain, dyspnea, cough, or may be asymptomatic. MONDO:0006121
MONDO:0856178 thymic carcinoma with adenoid cystic carcinoma-like features NCIT:C183313 MONDO:equivalentTo Thymic Carcinoma with Adenoid Cystic Carcinoma-Like Features A very rare primary thymic carcinoma that resembles adenoid cystic carcinoma of the salivary gland. MONDO:0006451
MONDO:0856179 thymic enteric-type adenocarcinoma NCIT:C183314 MONDO:equivalentTo Thymic Enteric-Type Adenocarcinoma A primary thymic adenocarcinoma characterized by morphological and immunohistochemical features seen in colorectal adenocarcinoma. MONDO:0003209
MONDO:0856180 thymic adenocarcinoma, not otherwise specified NCIT:C183315 MONDO:equivalentTo Thymic Adenocarcinoma, Not Otherwise Specified A primary thymic adenocarcinoma that does not conform to either low-grade papillary adenocarcinoma or enteric-type adenocarcinoma. MONDO:0003209
MONDO:0856181 thymic carcinoma, not otherwise specified NCIT:C183316 MONDO:equivalentTo Thymic Carcinoma, Not Otherwise Specified A primary thymic carcinoma that cannot be defined as one of the thymic carcinomas with specific morphologic characteristics. MONDO:0006451
MONDO:0856182 mediastinal follicular dendritic cell sarcoma NCIT:C183374 MONDO:equivalentTo Mediastinal Follicular Dendritic Cell Sarcoma A rare follicular dendritic cell sarcoma that affects the structures of the mediastinum. MONDO:0005764
MONDO:0856183 metastatic malignant neoplasm in the mediastinal lymph nodes NCIT:C183510 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Mediastinal Lymph Nodes The spread of a malignant neoplasm to the mediastinal lymph nodes from an adjacent or distant anatomic site. MONDO:0005438
MONDO:0856191 salivary gland adenoma NCIT:C184295 MONDO:equivalentTo Salivary Gland Adenoma A benign adenoma that arises from the salivary gland. This group includes pleomorphic adenoma, canalicular adenoma, basal cell adenoma, and sebaceous adenoma. MONDO:0021460
MONDO:0856197 multiple solitary plasmacytoma of bone NCIT:C185035 MONDO:equivalentTo Multiple Solitary Plasmacytoma of Bone The presence of more than one plasmacytoma arising in the bone, concurrently or sequentially, in the absence of bone marrow involvement by plasma cell myeloma. MONDO:0002755
MONDO:0856199 splenic plasmacytoma NCIT:C185041 MONDO:equivalentTo Splenic Plasmacytoma A plasmacytoma that arises in the spleen. MONDO:0002754
MONDO:0856204 extramedullary disease in multiple myeloma NCIT:C185149 MONDO:equivalentTo Extramedullary Disease in Multiple Myeloma Infiltration of organs and soft tissues by malignant (clonal) plasma cells in patients with history of multiple myeloma. Skin, liver, lymph nodes, pleura, and central nervous system are the most frequently affected sites. MONDO:0009693
MONDO:0856206 astrocytoma, idh-mutant NCIT:C185167 MONDO:equivalentTo Astrocytoma, IDH-Mutant An astrocytoma associated with IDH1 or IDH2 gene mutations and absence of 1p/19q codeletion. It is classified as grade 2, 3, or 4. MONDO:0019781
MONDO:0856207 astrocytoma, idh-wildtype NCIT:C185184 MONDO:equivalentTo Astrocytoma, IDH-Wildtype Astrocytoma lacking mutations in IDH1 or IDH2 genes. It includes diffuse astrocytoma, IDH-wildtype and anaplastic astrocytoma, IDH-wildtype. MONDO:0019781
MONDO:0856208 astrocytoma, not otherwise specified NCIT:C185185 MONDO:equivalentTo Astrocytoma, Not Otherwise Specified A central nervous system tumor with morphological features of astrocytoma in which there is insufficient information on the IDH genes status. MONDO:0019781
MONDO:0856216 extranodal lymphoma NCIT:C185752 MONDO:equivalentTo Extranodal Lymphoma A non-Hodgkin or Hodgkin lymphoma that arises from an anatomic site other than a lymph node. MONDO:0017207
MONDO:0856218 high grade astrocytoma with piloid features NCIT:C185879 MONDO:equivalentTo High Grade Astrocytoma with Piloid Features An astrocytoma characterized by high-grade piloid and/or glioblastoma-like histological features. It may occur anywhere in the central nervous system but most often arises in the posterior fossa. Alterations in the following three pathways are responsible for the pathogenesis of this tumor: MAPK pathway, retinoblastoma tumor suppressor protein cell-cycle pathway, and telomere maintenance pathway. MONDO:0016684
MONDO:0856232 spinal cord ependymoma, mycn amplified NCIT:C186494 MONDO:equivalentTo Spinal Cord Ependymoma, MYCN Amplified A rare, aggressive ependymoma that arises from the spinal cord. It displays microvascular proliferation, necrosis, and high mitotic rate. It is characterized by high-level MYCN amplification. Cytogenetic abnormalities include loss of chromosome 10 and focal losses on chromosome 11q. The prognosis is poor. MONDO:0002542
MONDO:0856233 childhood spinal cord ependymoma NCIT:C186495 MONDO:equivalentTo Childhood Spinal Cord Ependymoma An ependymoma of the spinal cord not associated with MYCN amplification and occurring in children. MONDO:0002716
MONDO:0856234 central nervous system neuroblastoma, foxr2-activated NCIT:C186547 MONDO:equivalentTo Central Nervous System Neuroblastoma, FOXR2-Activated A rare central nervous system neoplasm with neuroblastic and/or neuronal differentiation. It is characterized by the presence of structural rearrangements of FOXR2 gene that result in the activation of the transcription factor FOXR2. MONDO:0002900
MONDO:0856238 primary intracranial sarcoma, dicer1-mutant NCIT:C186610 MONDO:equivalentTo Primary Intracranial Sarcoma, DICER1-Mutant A primary intracranial sarcoma composed of malignant pleomorphic or spindle neoplastic cells typically demonstrating myogenic and/or chondroid differentiation. Cytoplasmic eosinophilic globules and myxoid stroma formation are usually present. It is associated with mutations in the DICER1 gene. MONDO:0002216
MONDO:0856239 central nervous system ewing sarcoma NCIT:C186611 MONDO:equivalentTo Central Nervous System Ewing Sarcoma Ewing sarcoma that arises in the central nervous system. MONDO:0018270
MONDO:0856240 intracranial mesenchymal tumor, fet-creb fusion-positive NCIT:C186614 MONDO:equivalentTo Intracranial Mesenchymal Tumor, FET-CREB Fusion-Positive A provisional entity that refers to a group of neoplasms with a broad morphological spectrum, characterized by fusion of a FET family gene (usually EWSR1 and rarely FUS) with a member of the CREB family of transcription factors (CREB1, ATF1, or CREM). It includes entities previously termed intracranial angiomatoid fibrous histiocytoma or intracranial myxoid mesenchymal tumor. It is usually located in the supratentorial brain and mostly affects children and young adults. There is a spectrum of clinical behaviors ranging from slowly growing tumors to rapid recurrences, and rarely metastases. MONDO:0003244
MONDO:0856241 cervical cancer by figo stage 2009 NCIT:C186619 MONDO:equivalentTo Cervical Cancer by FIGO Stage 2009 A term that refers to the staging of cervical cancer according to the International Federation of Gynecology and Obstetrics (FIGO) staging, 2009. MONDO:0005131
MONDO:0856244 central nervous system lymphomatoid granulomatosis NCIT:C186662 MONDO:equivalentTo Central Nervous System Lymphomatoid Granulomatosis Lymphomatoid granulomatosis that affects the brain, spinal cord, and leptomeninges. MONDO:0019466
MONDO:0856246 smarcb1 schwannomatosis 1 NCIT:C186703 MONDO:equivalentTo SMARCB1 Schwannomatosis 1 Schwannomatosis caused by germline mutations in the SMARCB1 gene. MONDO:0008075
MONDO:0856247 lztr1 schwannomatosis 2 NCIT:C186704 MONDO:equivalentTo LZTR1 Schwannomatosis 2 Schwannomatosis caused by germline mutations in the LZTR1 gene. MONDO:0008075
MONDO:0856253 childhood acute leukemia NCIT:C187056 MONDO:equivalentTo Childhood Acute Leukemia An acute leukemia that occurs during childhood. MONDO:0010643
MONDO:0856254 pituitary neuroendocrine tumor of pit1-lineage NCIT:C187086 MONDO:equivalentTo Pituitary Neuroendocrine Tumor of PIT1-Lineage A pituitary neuroendocrine tumor arising from PIT1-lineage adenohypophysial cells. MONDO:0006373
MONDO:0856255 pituitary neuroendocrine tumor of tpit-lineage NCIT:C187087 MONDO:equivalentTo Pituitary Neuroendocrine Tumor of TPIT-Lineage A pituitary neuroendocrine tumor arising from TPIT-lineage adenohypophysial cells. MONDO:0006373
MONDO:0856256 pituitary neuroendocrine tumor of sf1-lineage NCIT:C187088 MONDO:equivalentTo Pituitary Neuroendocrine Tumor of SF1-Lineage A pituitary neuroendocrine tumor arising from SF1-lineage adenohypophysial cells. MONDO:0006373
MONDO:0856257 pituitary neuroendocrine tumor without distinct lineage differentiation NCIT:C187096 MONDO:equivalentTo Pituitary Neuroendocrine Tumor without Distinct Lineage Differentiation A pituitary neuroendocrine tumor that belongs to more than one adenohypophysial cell lineage or does not show evidence of adenohypophysial hormonal immunoreactivity and specific adenohypophysial cell derivation. MONDO:0006373
MONDO:0856258 pituitary neuroendocrine tumor, not otherwise specified NCIT:C187135 MONDO:equivalentTo Pituitary Neuroendocrine Tumor, Not Otherwise Specified A pituitary neuroendocrine tumor in which further characterization regarding subtyping is not available. MONDO:0006373
MONDO:0856267 thyroid gland follicular adenoma with papillary architecture NCIT:C187261 MONDO:equivalentTo Thyroid Gland Follicular Adenoma with Papillary Architecture A benign, encapsulated thyroid gland neoplasm characterized by the presence of large follicles with intrafollicular papillary architecture. The cells lining the papillae are usually columnar. It is usually a cystic neoplasm and lacks nuclear atypia and capsular invasion. Psammoma bodies are not present. Activating TSHR mutations have been described in the majority of cases. In a small number of cases GNAS mutations have been identified. MONDO:0005032
MONDO:0856268 low risk thyroid gland neoplasm NCIT:C187273 MONDO:equivalentTo Low Risk Thyroid Gland Neoplasm A thyroid gland neoplasm in which the incidence of metastatic spread is extremely low. This category includes thyroid gland noninvasive follicular neoplasm with papillary-like nuclear features, thyroid gland hyalinizing trabecular tumor, and thyroid gland tumors of uncertain malignant potential. MONDO:0015074
MONDO:0856272 invasive breast lobular carcinoma with extracellular mucin NCIT:C187405 MONDO:equivalentTo Invasive Breast Lobular Carcinoma with Extracellular Mucin A rare variant of invasive breast lobular carcinoma characterized by the presence of pools of extracellular mucin in which groups of floating lobular carcinoma cells are identified. MONDO:0005051
MONDO:0856275 thyroid gland follicular carcinoma, signet ring cell variant NCIT:C187643 MONDO:equivalentTo Thyroid Gland Follicular Carcinoma, Signet Ring Cell Variant A morphologic variant of follicular carcinoma of the thyroid gland characterized by the presence of malignant follicular cells with cytoplasmic vacuoles and eccentrically placed nuclei. MONDO:0005034
MONDO:0856276 classic thyroid gland papillary carcinoma NCIT:C187644 MONDO:equivalentTo Classic Thyroid Gland Papillary Carcinoma A thyroid gland papillary carcinoma characterized by the presence of thin cores of fibrovascular tissue lined by one or occasionally several layers of malignant cells with distinct nuclear features that include nuclear pseudoinclusions, nuclear grooves, and ground glass nuclear inclusions. MONDO:0005075
MONDO:0856277 high grade follicular cell-derived non-anaplastic thyroid gland carcinoma NCIT:C187645 MONDO:equivalentTo High Grade Follicular Cell-Derived Non-Anaplastic Thyroid Gland Carcinoma A thyroid gland carcinoma that arises from follicular cells and is characterized by the presence of high mitotic activity and necrotic changes in the absence of anaplastic histological features. This category includes poorly differentiated thyroid gland carcinoma and differentiated high-grade thyroid gland carcinoma. MONDO:0024622
MONDO:0856285 thyroid gland secretory carcinoma NCIT:C187994 MONDO:equivalentTo Thyroid Gland Secretory Carcinoma An invasive adenocarcinoma of the thyroid gland characterized by the presence of cells that secrete eosinophilic material. It is composed of cystic spaces, tubular structures, and solid areas. ETV6 translocations and ETV6-NTRK3 fusion are present. MONDO:0024622
MONDO:0856286 thyroblastoma NCIT:C187995 MONDO:equivalentTo Thyroblastoma A high-grade, rapidly growing malignant embryonal neoplasm that arises from the thyroid gland. It is characterized by the presence of primitive follicular-like structures surrounded by primitive small cells and primitive spindle cell mesenchymal stroma. It is associated with DICER1 gene mutations. The prognosis is poor. MONDO:0002108
MONDO:0856287 teratoma with endocrine differentiation NCIT:C188013 MONDO:equivalentTo Teratoma with Endocrine Differentiation A teratoma that arises outside an endocrine organ and shows endocrine differentiation. The endocrine component ranges from benign endocrine tissue to malignant endocrine neoplasms. This category includes struma ovarii, thyroid carcinoma arising in struma ovarii, and carcinoid tumor arising in ovarian teratoma. MONDO:0002601
MONDO:0856289 b-cell malignant neoplasm NCIT:C188021 MONDO:equivalentTo B-Cell Malignant Neoplasm A clonal lymphoproliferative disorder composed of neoplastic B-cells. It includes B-cell non-Hodgkin lymphomas, B-cell leukemias, and plasma cell myeloma. MONDO:0004992
MONDO:0856293 mast cell leukemia with an associated myeloid neoplasm NCIT:C188031 MONDO:equivalentTo Mast Cell Leukemia with an Associated Myeloid Neoplasm Mast cell leukemia associated with another clonal non-mast cell myeloid neoplasm (e.g., myelodysplastic syndrome, myeloproliferative neoplasm, and acute myeloid leukemia). MONDO:0020332
MONDO:0856298 refractory wilms tumor NCIT:C188038 MONDO:equivalentTo Refractory Wilms Tumor Wilms tumor that is resistant to treatment. MONDO:0006058
MONDO:0856302 pleural proximal-type epithelioid sarcoma NCIT:C188055 MONDO:equivalentTo Pleural Proximal-Type Epithelioid Sarcoma A rare epithelioid sarcoma of the proximal type that arises from the pleura. MONDO:0004244
MONDO:0856303 lung osteosarcoma NCIT:C188061 MONDO:equivalentTo Lung Osteosarcoma A rare extraskeletal osteosarcoma that arises from the lung parenchyma. MONDO:0002621
MONDO:0856304 pleural leiomyosarcoma NCIT:C188063 MONDO:equivalentTo Pleural Leiomyosarcoma A rare leiomyosarcoma that arises from the pleural cavity. MONDO:0006294
MONDO:0856305 bone malignant peripheral nerve sheath tumor NCIT:C188064 MONDO:equivalentTo Bone Malignant Peripheral Nerve Sheath Tumor An exceedingly rare malignant peripheral nerve sheath tumor that arises from the bone. MONDO:0021054
MONDO:0856308 lung secretory carcinoma NCIT:C188068 MONDO:equivalentTo Lung Secretory Carcinoma A rare carcinoma that arises from the lung and has histopathological, immunohistochemical, and genetic features identical to those described in breast and salivary gland secretory carcinomas. MONDO:0005138
MONDO:0856309 prostate alveolar rhabdomyosarcoma NCIT:C188070 MONDO:equivalentTo Prostate Alveolar Rhabdomyosarcoma A rare alveolar rhabdomyosarcoma arising from the prostate gland. MONDO:0006389
MONDO:0856310 retroperitoneal rhabdomyosarcoma NCIT:C188071 MONDO:equivalentTo Retroperitoneal Rhabdomyosarcoma A rhabdomyosarcoma arising from the retroperitoneum. MONDO:0005212
MONDO:0856312 retroperitoneal malignant peripheral nerve sheath tumor NCIT:C188073 MONDO:equivalentTo Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Malignant peripheral nerve sheath tumor that arises in the retroperitoneum. MONDO:0001501
MONDO:0856313 rectal epithelioid cell melanoma NCIT:C188079 MONDO:equivalentTo Rectal Epithelioid Cell Melanoma An epithelioid cell melanoma arising from the rectum. MONDO:0002167
MONDO:0856316 lung anaplastic large cell lymphoma NCIT:C188082 MONDO:equivalentTo Lung Anaplastic Large Cell Lymphoma A rare anaplastic large cell lymphoma that arises in the lung parenchyma. MONDO:0020644
MONDO:0856325 adrenal cortical myxoid carcinoma NCIT:C188182 MONDO:equivalentTo Adrenal Cortical Myxoid Carcinoma A carcinoma that arises from the adrenal cortex and is characterized by the presence of abundant extracellular connective tissue mucin. MONDO:0006639
MONDO:0856326 adrenal cortical high grade carcinoma NCIT:C188183 MONDO:equivalentTo Adrenal Cortical High Grade Carcinoma A carcinoma that arises from the adrenal cortex and is characterized by the presence of more than twenty mitoses per ten square millimeters. MONDO:0006639
MONDO:0856327 adrenal cortical melanoma NCIT:C188185 MONDO:equivalentTo Adrenal Cortical Melanoma A rare melanoma that arises within the adrenal cortex. MONDO:0021312
MONDO:0856335 neuroendocrine tumor NCIT:C188218 MONDO:equivalentTo Neuroendocrine Tumor A well-differentiated neuroendocrine neoplasm of low, intermediate, or high grade. MONDO:0019496
MONDO:0856336 head and neck neuroendocrine neoplasm NCIT:C188222 MONDO:equivalentTo Head and Neck Neuroendocrine Neoplasm A neoplasm with neuroendocrine differentiation that arises from the head and neck. This category includes neuroendocrine tumors, neuroendocrine carcinomas, and paragangliomas. MONDO:0019496
MONDO:0856338 adrenal gland lipoma NCIT:C188250 MONDO:equivalentTo Adrenal Gland Lipoma A rare lipoma that arises from the adrenal gland. MONDO:0021511
MONDO:0856339 adrenal gland hemangioma NCIT:C188251 MONDO:equivalentTo Adrenal Gland Hemangioma A rare hemangioma that arises from the adrenal gland. MONDO:0021511
MONDO:0856340 adrenal gland lymphangioma NCIT:C188252 MONDO:equivalentTo Adrenal Gland Lymphangioma A rare lymphangioma that arises from the adrenal gland. MONDO:0002013
MONDO:0856341 adrenal gland leiomyoma NCIT:C188253 MONDO:equivalentTo Adrenal Gland Leiomyoma A rare leiomyoma that arises from the adrenal gland. MONDO:0021511
MONDO:0856343 multiple endocrine neoplasia type 5 NCIT:C188257 MONDO:equivalentTo Multiple Endocrine Neoplasia Type 5 An inherited neoplastic syndrome caused by mutations in the MYC-associated factor X (MAX) gene. It is associated with the development of paragangliomas/pheochromocytomas, pituitary neuroendocrine tumors, and parathyroid adenomas. Renal cell carcinomas, squamous cell carcinomas, breast carcinomas, lung carcinomas, and endometrial carcinomas have also been reported. MONDO:0017169
MONDO:0856349 chronic phase primary myelofibrosis NCIT:C188314 MONDO:equivalentTo Chronic Phase Primary Myelofibrosis Primary myelofibrosis characterized by the presence of less than 10% blasts in the peripheral blood or bone marrow. MONDO:0009692
MONDO:0856350 accelerated phase myeloproliferative neoplasm NCIT:C188315 MONDO:equivalentTo Accelerated Phase Myeloproliferative Neoplasm Rapid progression of a myeloproliferative neoplasm, characterized by the presence of myeloblasts accounting for 10-19% of the peripheral blood white cells or the nucleated cells in the bone marrow. MONDO:0020076
MONDO:0856351 blast phase myeloproliferative neoplasm NCIT:C188316 MONDO:equivalentTo Blast Phase Myeloproliferative Neoplasm Transformation of a myeloproliferative neoplasm into acute myeloid leukemia, typically via accelerated phase myeloproliferative neoplasm. Myeloblasts account for 20% or more of the peripheral blood white cells or the nucleated cells in the bone marrow. MONDO:0020076
MONDO:0856357 intraductal hyperplasia NCIT:C26458 MONDO:equivalentTo Intraductal Hyperplasia A hyperplasia of the intraductal cells.
MONDO:0856375 reticulosarcoma involving spleen NCIT:C26959 MONDO:equivalentTo Reticulosarcoma Involving Spleen An antiquated term that refers to a non-Hodgkin lymphoma composed of diffuse infiltrates of large, often anaplastic lymphocytes affecting the spleen. MONDO:0009975
MONDO:0856376 lymphosarcoma involving spleen NCIT:C26960 MONDO:equivalentTo Lymphosarcoma Involving Spleen An antiquated term that refers to a non-Hodgkin lymphoma composed of small and medium sized lymphocytes affecting the spleen. MONDO:0004638
MONDO:0856398 nonpigmented nevus NCIT:C27095 MONDO:equivalentTo Nonpigmented Nevus A benign nevus characterized by the absence of melanin pigment in the melanocytes. MONDO:0044794
MONDO:0856421 transplant-related disorder NCIT:C27233 MONDO:equivalentTo Transplant-Related Disorder
MONDO:0856422 familial adenomatous polyposis associated medulloblastoma NCIT:C27237 MONDO:equivalentTo Familial Adenomatous Polyposis Associated Medulloblastoma A medulloblastoma developing in patients with familiar adenomatous polyposis syndrome. It is observed in patients with Turcot syndrome, type 2. MONDO:0007959
MONDO:0856423 lymphoma by stage NCIT:C27268 MONDO:equivalentTo Lymphoma by Stage MONDO:0005062
MONDO:0856424 glandular cell intraepithelial neoplasia NCIT:C27269 MONDO:equivalentTo Glandular Cell Intraepithelial Neoplasia MONDO:0024474
MONDO:0856425 secondary myelodysplastic syndrome NCIT:C27280 MONDO:equivalentTo Secondary Myelodysplastic Syndrome A myelodysplastic syndrome resulting from chemotherapy or radiation therapy for cancer or exposure to certain chemicals. MONDO:0018881
MONDO:0856428 metastatic ewing sarcoma/peripheral primitive neuroectodermal tumor NCIT:C27292 MONDO:equivalentTo Metastatic Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor A small round cell tumor with or without neural differentiation that has spread from its original site of growth to another anatomic site. MONDO:0021038
MONDO:0856443 unresectable malignant neoplasm NCIT:C27359 MONDO:equivalentTo Unresectable Malignant Neoplasm A malignant neoplasm which is not amenable to surgical resection. MONDO:0004992
MONDO:0856447 mucin-producing adenocarcinoma NCIT:C27379 MONDO:equivalentTo Mucin-Producing Adenocarcinoma An invasive adenocarcinoma composed of malignant glandular cells which produce mucin. MONDO:0020596
MONDO:0856451 extraosseous/peripheral ameloblastoma NCIT:C27396 MONDO:equivalentTo Extraosseous/Peripheral Ameloblastoma An ameloblastoma that arises from the soft tissues in the gingiva or alveolar mucosa. It presents as a painless exophytic mass. MONDO:0017795
MONDO:0856452 ampulla of vater intestinal-type adenocarcinoma NCIT:C27415 MONDO:equivalentTo Ampulla of Vater Intestinal-Type Adenocarcinoma An invasive adenocarcinoma arising from the ampulla of Vater. Morphologically, it is characterized by the presence of intestinal-type malignant epithelial cells. MONDO:0002670
MONDO:0856453 ampulla of vater undifferentiated carcinoma NCIT:C27419 MONDO:equivalentTo Ampulla of Vater Undifferentiated Carcinoma An aggressive carcinoma arising from the ampulla of Vater. Morphologically, it is characterized by the presence of malignant epithelial cells without evidence of glandular or squamous differentiation. Signs and symptoms include jaundice, abdominal pain, anorexia, nausea, vomiting, and weight loss. MONDO:0017590
MONDO:0856456 small intestinal gastrin-producing neuroendocrine tumor NCIT:C27450 MONDO:equivalentTo Small Intestinal Gastrin-Producing Neuroendocrine Tumor A gastrin-producing neuroendocrine tumor that arises from the small intestine. It is characterized by the presence of uniform cells that form pseudorosettes. The neoplastic cells have uniform nuclei and small amount of eosinophilic cytoplasm. MONDO:0002995
MONDO:0856457 small intestinal enterochromaffin cell serotonin-producing neuroendocrine tumor NCIT:C27451 MONDO:equivalentTo Small Intestinal Enterochromaffin Cell Serotonin-Producing Neuroendocrine Tumor A well differentiated neuroendocrine tumor that arises from the small intestine and produces serotonin. MONDO:0002995
MONDO:0856458 small intestinal somatostatin-producing neuroendocrine tumor NCIT:C27453 MONDO:equivalentTo Small Intestinal Somatostatin-Producing Neuroendocrine Tumor A somatostatin-producing neuroendocrine tumor that arises from the small intestine. MONDO:0002995
MONDO:0856460 colorectal adenoma with moderate dysplasia NCIT:C27457 MONDO:equivalentTo Colorectal Adenoma with Moderate Dysplasia An adenoma that arises from the colon or rectum. It is characterized by the presence of moderate epithelial dysplasia. MONDO:0005484
MONDO:0856461 colorectal adenoma with mild dysplasia NCIT:C27458 MONDO:equivalentTo Colorectal Adenoma with Mild Dysplasia An adenoma that arises from the colon or rectum. It is characterized by the presence of mild epithelial dysplasia. MONDO:0005484
MONDO:0856463 disseminated malignant neoplasm NCIT:C27470 MONDO:equivalentTo Disseminated Malignant Neoplasm Cancer that is spread throughout the body, a metastatic phenomenon. MONDO:0024880
MONDO:0856464 bone lipoma NCIT:C27475 MONDO:equivalentTo Bone Lipoma A benign neoplasm which is composed of adipocytes and arises from the surface of the bone or the medullary cavity. MONDO:0000631
MONDO:0856465 bone schwannoma NCIT:C27476 MONDO:equivalentTo Bone Schwannoma A very rare schwannoma of the bone. It is often located in the mandible and is well circumscribed. MONDO:0004820
MONDO:0856468 secondary chondrosarcoma NCIT:C27482 MONDO:equivalentTo Secondary Chondrosarcoma A chondrosarcoma that arises either in a pre-existing enchondroma or within the cartilaginous cap of a pre-existing osteochondroma. MONDO:0021054
MONDO:0856469 conventional alveolar rhabdomyosarcoma NCIT:C27492 MONDO:equivalentTo Conventional Alveolar Rhabdomyosarcoma An alveolar rhabdomyosarcoma characterized by the presence of large striated muscle cells with clear cytoplasm, giant cells with myoblastic differentiation, and fibrovascular septa. MONDO:0009994
MONDO:0856470 solid alveolar rhabdomyosarcoma NCIT:C27493 MONDO:equivalentTo Solid Alveolar Rhabdomyosarcoma A morphologic variant of alveolar rhabdomyosarcoma. It is characterized by the presence of a solid growth pattern and the absence of fibrovascular stroma. MONDO:0009994
MONDO:0856471 lymphadenopathic kaposi sarcoma NCIT:C27500 MONDO:equivalentTo Lymphadenopathic Kaposi Sarcoma A Kaposi sarcoma affecting the lymph nodes. MONDO:0001082
MONDO:0856472 conventional extraskeletal myxoid chondrosarcoma NCIT:C27501 MONDO:equivalentTo Conventional Extraskeletal Myxoid Chondrosarcoma A well differentiated extraskeletal myxoid chondrosarcoma. MONDO:0012825
MONDO:0856473 intra-abdominal lymphangioma NCIT:C27508 MONDO:equivalentTo Intra-Abdominal Lymphangioma A lymphangioma arising from the organs of the abdominal cavity. MONDO:0002013
MONDO:0856474 angiosarcoma associated with lymphedema NCIT:C27512 MONDO:equivalentTo Angiosarcoma Associated with Lymphedema An angiosarcoma that develops in association with long standing lymphedema. MONDO:0016982
MONDO:0856475 desmoplastic fibroblastoma NCIT:C27515 MONDO:equivalentTo Desmoplastic Fibroblastoma A rare benign soft tissue neoplasm characterized by the presence of an abundant collagenous or myxocollagenous matrix, spindle-shaped, and stellate-shaped fibroblasts. It usually presents as an asymptomatic, slowly growing subcutaneous mass. The most common sites of involvement are the upper arm, shoulder, and lower limb. MONDO:0005167
MONDO:0856477 columnar trichoblastoma NCIT:C27524 MONDO:equivalentTo Columnar Trichoblastoma A benign adnexal tumor occurring in the face of young female subjects. It is characterized by the presence of epithelial neoplastic cells and keratinous cysts in a desmoplastic stroma. MONDO:0020593
MONDO:0856478 tubular apocrine adenoma NCIT:C27527 MONDO:equivalentTo Tubular Apocrine Adenoma A benign dermal adnexal neoplasm with apocrine differentiation. It usually occurs in the scalp and has a female predilection. It presents as an asymptomatic solitary nodule. It is characterized by a lobular architecture. The lobules are composed by tubular structures lined by epithelial cells. There is no cytologic atypia or mitotic figures present. MONDO:0002804
MONDO:0856479 primary cutaneous mucinous carcinoma NCIT:C27533 MONDO:equivalentTo Primary Cutaneous Mucinous Carcinoma A rare low-grade carcinoma of the sweat glands. The most common sites are eyelids, scalp, axilla, face and trunk. It is histologically characterized by proliferating ducts until the overproduction of mucin creates islands of tumor cells, essentially floating in mucinous pools (Rosai J. Ackerman's Surgical Pathology). MONDO:0005524
MONDO:0856501 oral cavity disorder NCIT:C27641 MONDO:equivalentTo Oral Cavity Disorder A non-neoplastic or neoplastic disorder affecting the oral cavity.
MONDO:0856504 sinonasal disorder NCIT:C27647 MONDO:equivalentTo Sinonasal Disorder A non-neoplastic or neoplastic disorder that affects the nasal cavity or paranasal sinuses. Representative examples include inflammatory disorders, papillomas, and carcinomas.
MONDO:0856509 human papillomavirus-related verrucous carcinoma NCIT:C27678 MONDO:equivalentTo Human Papillomavirus-Related Verrucous Carcinoma A verrucous carcinoma that is associated with human papillomavirus infection. MONDO:0020657
MONDO:0856510 human papillomavirus-related vulvar squamous cell carcinoma NCIT:C27679 MONDO:equivalentTo Human Papillomavirus-Related Vulvar Squamous Cell Carcinoma A squamous cell carcinoma that arises from the vulva and is caused by human papillomavirus infection. MONDO:0020657
MONDO:0856511 human papillomavirus-related esophageal squamous cell carcinoma NCIT:C27680 MONDO:equivalentTo Human Papillomavirus-Related Esophageal Squamous Cell Carcinoma An esophageal squamous cell carcinoma that arises from squamous epithelial cells infected with human papillomavirus. MONDO:0005580
MONDO:0856512 human papillomavirus-related anal squamous cell carcinoma NCIT:C27681 MONDO:equivalentTo Human Papillomavirus-Related Anal Squamous Cell Carcinoma An anal squamous cell carcinoma related to infection with sexually transmittable human papillomavirus. MONDO:0020657
MONDO:0856518 ebv-related post-transplant lymphoproliferative disorder NCIT:C27696 MONDO:equivalentTo EBV-Related Post-Transplant Lymphoproliferative Disorder A lymphoproliferative disorder that develops following organ transplantation and is associated with Epstein-Barr virus infection.
MONDO:0856523 extragastrointestinal gastrointestinal stromal tumor NCIT:C27716 MONDO:equivalentTo Extragastrointestinal Gastrointestinal Stromal Tumor A rare gastrointestinal stromal tumor that presents as a solitary mass outside the gastrointestinal tract. MONDO:0011719
MONDO:0856526 myelodysplastic syndrome with ring sideroblasts and multilineage dysplasia NCIT:C27726 MONDO:equivalentTo Myelodysplastic Syndrome with Ring Sideroblasts and Multilineage Dysplasia A myelodysplastic syndrome characterized by bi-cytopenia or pancytopenia, dysplastic changes in 10% or more of the cells in two or more of the myeloid cell lines, and 15% or more ring sideroblasts in the bone marrow. (WHO, 2001) MONDO:0019157
MONDO:0856529 typical acute promyelocytic leukemia NCIT:C27756 MONDO:equivalentTo Typical Acute Promyelocytic Leukemia Acute Promyelocytic leukemia characterized by the presence of hypergranular promyelocytes and characteristic cells that contain bundles of Auer rods. MONDO:0012883
MONDO:0856530 microgranular acute promyelocytic leukemia NCIT:C27757 MONDO:equivalentTo Microgranular Acute Promyelocytic Leukemia Acute promyelocytic leukemia in which the promyelocytes in the peripheral blood have paucity or absence of cytoplasmic granules and characteristic bilobed nuclei. MONDO:0012883
MONDO:0856539 myelodysplastic/myeloproliferative neoplasm, not otherwise specified NCIT:C27780 MONDO:equivalentTo Myelodysplastic/Myeloproliferative Neoplasm, Not Otherwise Specified A myelodysplastic/myeloproliferative neoplasm that does not meet the criteria of other myelodysplastic/myeloproliferative neoplasms, myelodysplastic syndromes, and myeloproliferative neoplasms. It is associated with cytopenia, blasts less than 20% in bone marrow and peripheral blood, thrombocytosis, and absence of genetic abnormalities associated with myeloid/lymphoid neoplasms with eosinophilia and tyrosine kinase gene fusions. MONDO:0006311
MONDO:0856541 spindle cell type gastrointestinal stromal tumor NCIT:C27792 MONDO:equivalentTo Spindle Cell Type Gastrointestinal Stromal Tumor A gastrointestinal stromal tumor composed of neoplastic spindle cells. MONDO:0011719
MONDO:0856542 mixed cell type gastrointestinal stromal tumor NCIT:C27793 MONDO:equivalentTo Mixed Cell Type Gastrointestinal Stromal Tumor A gastrointestinal stromal tumor composed of a mixture of neoplastic epithelioid and spindle cells. MONDO:0011719
MONDO:0856545 nodular sclerosis classic hodgkin lymphoma, syncytial variant NCIT:C27807 MONDO:equivalentTo Nodular Sclerosis Classic Hodgkin Lymphoma, Syncytial Variant MONDO:0004665
MONDO:0856546 pigmented nevus NCIT:C27816 MONDO:equivalentTo Pigmented Nevus A nevus characterised by the presence of excessive pigment. MONDO:0044794
MONDO:0856549 invasive breast carcinoma by histologic grade NCIT:C27829 MONDO:equivalentTo Invasive Breast Carcinoma by Histologic Grade MONDO:0006256
MONDO:0856551 endometrial endometrioid adenocarcinoma with clear cell change NCIT:C27843 MONDO:equivalentTo Endometrial Endometrioid Adenocarcinoma with Clear Cell Change A morphologic variant of endometrioid adenocarcinoma characterized by the presence of large multinucleated clear cells. MONDO:0006192
MONDO:0856552 endometrial endometrioid adenocarcinoma with a poorly differentiated carcinomatous component NCIT:C27844 MONDO:equivalentTo Endometrial Endometrioid Adenocarcinoma with a Poorly Differentiated Carcinomatous Component A primary endometrioid adenocarcinoma of the endometrium characterized by the presence of a component with poorly differentiated carcinoma cells. MONDO:0006192
MONDO:0856553 endometrial endometrioid adenocarcinoma with an undifferentiated carcinomatous component NCIT:C27845 MONDO:equivalentTo Endometrial Endometrioid Adenocarcinoma with an Undifferentiated Carcinomatous Component A primary endometrioid adenocarcinoma of the endometrium characterized by the presence of a component with undifferentiated malignant cells. MONDO:0006192
MONDO:0856554 endometrial endometrioid adenocarcinoma, ciliated variant NCIT:C27848 MONDO:equivalentTo Endometrial Endometrioid Adenocarcinoma, Ciliated Variant An endometrioid adenocarcinoma arising from the endometrium, in which ciliated cells line the majority of the malignant glands. MONDO:0006192
MONDO:0856567 transitional cell intraepithelial neoplasia NCIT:C27881 MONDO:equivalentTo Transitional Cell Intraepithelial Neoplasia MONDO:0024474
MONDO:0856569 type 1 papillary renal cell carcinoma NCIT:C27886 MONDO:equivalentTo Type 1 Papillary Renal Cell Carcinoma A papillary renal cell carcinoma characterized by the presence of papillae covered by small cells with scant amount of cytoplasm. The cells are arranged in a single layer on the basement membrane of the papillae. MONDO:0017884
MONDO:0856570 type 2 papillary renal cell carcinoma NCIT:C27887 MONDO:equivalentTo Type 2 Papillary Renal Cell Carcinoma A papillary renal cell carcinoma characterized by the presence of papillae covered by cells of a higher nuclear grade as compared to type 1 papillary renal cell carcinoma. The cells have eosinophilic cytoplasm and pseudostratified nuclei. MONDO:0017884
MONDO:0856571 sporadic papillary renal cell carcinoma NCIT:C27890 MONDO:equivalentTo Sporadic Papillary Renal Cell Carcinoma A papillary renal cell carcinoma that occurs in a patient who does not have a family history of papillary renal cell carcinoma nor is a carrier of an inherited DNA change that would increase the risk of developing this carcinoma. MONDO:0017884
MONDO:0856577 well differentiated prostate adenocarcinoma NCIT:C27905 MONDO:equivalentTo Well Differentiated Prostate Adenocarcinoma An invasive prostate adenocarcinoma characterized by the presence of well differentiated malignant glandular epithelial components. MONDO:0005082
MONDO:0856578 moderately differentiated prostate adenocarcinoma NCIT:C27906 MONDO:equivalentTo Moderately Differentiated Prostate Adenocarcinoma An invasive prostate adenocarcinoma characterized by the presence of malignant cells exhibiting moderate differentiation. MONDO:0005082
MONDO:0856579 alkylating agent-related acute myeloid leukemia and myelodysplastic syndrome NCIT:C27913 MONDO:equivalentTo Alkylating Agent-Related Acute Myeloid Leukemia and Myelodysplastic Syndrome Acute myeloid leukemias and myelodysplastic syndromes arising as a result of the mutagenic effect of alkylating agents that are used for the treatment of malignant tumors. Patients usually develop a myelodysplastic syndrome which may evolve to a higher grade myelodysplastic syndrome or acute myeloid leukemia. A minority of patients present with an acute myeloid leukemia. Clonal cytogenetic abnormalities are frequently present and usually are unbalanced translocations or deletions of chromosomes 5 and 7. Patients with acute myeloid leukemia usually do not respond to treatment and have an unfavorable clinical outcome. MONDO:0006450
MONDO:0856580 sporadic burkitt lymphoma NCIT:C27914 MONDO:equivalentTo Sporadic Burkitt Lymphoma A clinical variant of Burkitt lymphoma that occurs throughout the world. It affects both children and adults and is more frequently seen in males. MONDO:0007243
MONDO:0856582 poorly differentiated prostate adenocarcinoma NCIT:C27916 MONDO:equivalentTo Poorly Differentiated Prostate Adenocarcinoma An invasive prostate adenocarcinoma characterized by the presence of poorly differentiated malignant cells. MONDO:0005082
MONDO:0856592 metaplastic carcinoma NCIT:C27949 MONDO:equivalentTo Metaplastic Carcinoma A general term used to describe carcinomas arising from epithelial cells that have been transformed into another cells type (metaplastic epithelial cells). A representative example is the adenocarcinoma arising in Barrett esophagus. This term is also used to describe carcinomas in which the malignant epithelial cells show differentiation towards another cell type. A representative example of the latter is the metaplastic breast carcinoma in which the malignant glandular cells show squamous, spindle cell, or chondroid/osseous differentiation. MONDO:0004993
MONDO:0856593 squamous cell carcinoma in situ of the nipple NCIT:C28292 MONDO:equivalentTo Squamous Cell Carcinoma In Situ of the Nipple An intraepidermal squamous cell carcinoma involving the area of the nipple. MONDO:0004693
MONDO:0856599 biliary system disorder NCIT:C2899 MONDO:equivalentTo Biliary System Disorder A non-neoplastic or neoplastic disorder that affects the intrahepatic or extrahepatic bile ducts or the gallbladder. Representative examples of non-neoplastic disorders include cholangitis and cholecystitis. Representative examples of neoplastic disorders include extrahepatic bile duct adenoma, intrahepatic and extrahepatic cholangiocarcinoma, and gallbladder carcinoma.
MONDO:0856602 enchondroma NCIT:C3007 MONDO:equivalentTo Enchondroma A common benign hyaline cartilage neoplasm arising in the intramedullary bone. It is characterized by the presence of chondrocytes, low mitotic activity, and in some cases, a nodular pattern and calcification. The small bones of the hands and feet are the most frequently affected sites. MONDO:0000631
MONDO:0856604 pancreatic glucagon-producing neuroendocrine tumor NCIT:C3062 MONDO:equivalentTo Pancreatic Glucagon-Producing Neuroendocrine Tumor A usually malignant, glucagon-producing neuroendocrine tumor arising from the pancreatic alpha cells. It may or may not be associated with inappropriate secretion of glucagon and an associated clinical syndrome. MONDO:0019954
MONDO:0856606 chronic phase chronic myeloid leukemia, bcr-abl1 positive NCIT:C3175 MONDO:equivalentTo Chronic Phase Chronic Myeloid Leukemia, BCR-ABL1 Positive A phase of chronic myeloid leukemia, BCR-ABL1 positive in which the peripheral blood smear shows leukocytosis with neutrophils in different stages of maturation, less than 2% blasts, and normal or increased platelet count. Most patients have mild anemia. The bone marrow is hypercellular due to increased numbers of neutrophils and their precursors, and blasts usually account for fewer than 5% of the marrow cells. Megakaryocytes are smaller than normal and have hypolobated nuclei. The spleen is enlarged due to infiltration of the cords of the red pulp by granulocytes. MONDO:0001014
MONDO:0856607 myeloid leukemia, philadelphia-negative NCIT:C3176 MONDO:equivalentTo Myeloid Leukemia, Philadelphia-Negative Myeloid leukemia characterized by the absence of Philadelphia chromosome. MONDO:0004643
MONDO:0856608 neoplasm by site NCIT:C3263 MONDO:equivalentTo Neoplasm by Site A term that refers to the classification of a neoplastic process according to the anatomic site that is involved. MONDO:0005070
MONDO:0856610 osteochondroma NCIT:C3295 MONDO:equivalentTo Osteochondroma A common, benign cartiliginous neoplasm arising from the metaphysis of bone. The tumor grows on the surface of the bone; it may be pedunculated or sessile. It is characterized by the presence of chondrocytes, a cartilage cap, and a fibrous perichondrium that extends to the periosteum of the bone. In some cases, there is deletion of 8q24.1 chromosome locus. MONDO:0000631
MONDO:0856611 extra-adrenal paraganglioma NCIT:C3309 MONDO:equivalentTo Extra-Adrenal Paraganglioma A paraganglioma arising from sympathetic or parasympathetic paraganglia outside the adrenal gland. MONDO:0000448
MONDO:0856614 supratentorial neoplasm NCIT:C3397 MONDO:equivalentTo Supratentorial Neoplasm A benign or malignant neoplasm that occurs within the intracranial cavity above the tentorium cerebelli. MONDO:0021211
MONDO:0856615 thyroid gland nodule NCIT:C3415 MONDO:equivalentTo Thyroid Gland Nodule A nodular lesion that develops in the thyroid gland. Causes include adenoma, thyroiditis, fluid-filled cyst, multinodular goiter, and carcinoma.
MONDO:0856638 grade 3 follicular lymphoma NCIT:C3460 MONDO:equivalentTo Grade 3 Follicular Lymphoma A follicular lymphoma which contains more than 15 centroblasts per 40X high-power microscopic field. MONDO:0018906
MONDO:0856655 lobular capillary hemangioma NCIT:C3480 MONDO:equivalentTo Lobular Capillary Hemangioma MONDO:0002407
MONDO:0856661 epithelioid cell type gastrointestinal stromal tumor NCIT:C3486 MONDO:equivalentTo Epithelioid Cell Type Gastrointestinal Stromal Tumor A benign or malignant gastrointestinal stromal tumor with epithelioid morphology. MONDO:0011719
MONDO:0856691 uterine corpus degenerated leiomyoma NCIT:C3511 MONDO:equivalentTo Uterine Corpus Degenerated Leiomyoma A morphologic variant of uterine corpus leiomyoma characterized by the presence of hyalinized or myxoid stroma, edema, cystic changes, hemorrhage, and calcifications. MONDO:0007886
MONDO:0856703 eyelid vascular disorder NCIT:C35198 MONDO:equivalentTo Eyelid Vascular Disorder Any non-neoplastic or neoplastic disorder affecting the arteries, veins, or lymphatic vessels of the eyelid.
MONDO:0856706 placental polyp NCIT:C3521 MONDO:equivalentTo Placental Polyp A polyp in the uterine cavity that is formed by placenta remnants. MONDO:0021498
MONDO:0856715 chondromatosis NCIT:C35259 MONDO:equivalentTo Chondromatosis A multifocal benign neoplasm arising from bone or soft tissue. It is characterized by the presence of chondrocytes and is composed of hyaline cartilage. MONDO:0024470
MONDO:0856716 malignant submandibular gland neoplasm NCIT:C3526 MONDO:equivalentTo Malignant Submandibular Gland Neoplasm A malignant neoplasm that arises from the submandibular gland. The majority are carcinomas. MONDO:0021244
MONDO:0856723 malignant palate neoplasm NCIT:C3530 MONDO:equivalentTo Malignant Palate Neoplasm A primary or metastatic malignant neoplasm that affects the hard palate, soft palate, or uvula. MONDO:0005515
MONDO:0856758 malignant neoplasm of multiple primary sites NCIT:C35427 MONDO:equivalentTo Malignant Neoplasm of Multiple Primary Sites A malignant neoplasm arising in multiple primary sites. MONDO:0004992
MONDO:0856764 behavioral disorder NCIT:C35470 MONDO:equivalentTo Behavioral Disorder A specific behavioral problem that occurs in persistent patterns and characteristic clusters and that causes clinically significant impairment.
MONDO:0856772 lung kaposi sarcoma NCIT:C3551 MONDO:equivalentTo Lung Kaposi Sarcoma A Kaposi sarcoma arising from the lung. MONDO:0002426
MONDO:0856784 malignant exocervical neoplasm NCIT:C3554 MONDO:equivalentTo Malignant Exocervical Neoplasm A malignant neoplasm that affects the exocervix. MONDO:0002974
MONDO:0856786 malignant uterine corpus neoplasm NCIT:C3556 MONDO:equivalentTo Malignant Uterine Corpus Neoplasm A malignant neoplasm that affects the uterine corpus. Representative examples include endometrial carcinoma, carcinosarcoma, leiomyosarcoma, and adenosarcoma. MONDO:0021254
MONDO:0856787 complex endometrial hyperplasia with atypia NCIT:C35560 MONDO:equivalentTo Complex Endometrial Hyperplasia with Atypia A hyperplasia characterized by excessive proliferation of endometrial cells, resulting in the formation of complex epithelial structures. It is associated with cytologic atypia and an increased risk of endometrial adenocarcinoma. MONDO:0006169
MONDO:0856810 mixed tumor of the salivary gland NCIT:C35691 MONDO:equivalentTo Mixed Tumor of the Salivary Gland A benign or malignant neoplasm that arises from the salivary glands. It is characterized by the presence of epithelial and mesenchymal elements. This category includes pleomorphic adenoma, carcinoma ex pleomorphic adenoma, and carcinosarcoma. MONDO:0021043
MONDO:0856811 posterior pharyngeal wall carcinoma NCIT:C35692 MONDO:equivalentTo Posterior Pharyngeal Wall Carcinoma A carcinoma that arises from the posterior wall of the pharynx. MONDO:0021345
MONDO:0856812 benign uvula neoplasm NCIT:C35698 MONDO:equivalentTo Benign Uvula Neoplasm A non-metastasizing neoplasm that arises from the uvula. MONDO:0021480
MONDO:0856814 testicular teratoma with somatic-type malignancy NCIT:C35711 MONDO:equivalentTo Testicular Teratoma with Somatic-Type Malignancy A testicular teratoma associated with a distinct secondary component that resembles a somatic-type malignant neoplasm (e.g., carcinoma or sarcoma). MONDO:0003403
MONDO:0856818 salivary gland lymphoepithelial carcinoma NCIT:C35736 MONDO:equivalentTo Salivary Gland Lymphoepithelial Carcinoma A rare carcinoma that arises from the salivary glands, most often the parotid gland. It is characterized by the presence of an undifferentiated carcinomatous component associated with a prominent reactive lymphoplasmacytic infiltrate. MONDO:0000521
MONDO:0856830 metastatic malignant neoplasm in the bone NCIT:C3580 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Bone The spread of a malignant neoplasm from a primary site to the skeletal system. The majority of metastatic neoplasms to the bone are carcinomas. MONDO:0002129
MONDO:0856835 monoblastic sarcoma NCIT:C35816 MONDO:equivalentTo Monoblastic Sarcoma A less common form of myeloid sarcoma composed of monoblasts. Monoblastic sarcoma may precede or occur simultaneously with acute monoblastic leukemia. (WHO 2001) MONDO:0006861
MONDO:0856836 blastic granulocytic sarcoma NCIT:C35817 MONDO:equivalentTo Blastic Granulocytic Sarcoma A granulocytic sarcoma composed primarily of myeloblasts (WHO 2001). MONDO:0006237
MONDO:0856837 immature granulocytic sarcoma NCIT:C35818 MONDO:equivalentTo Immature Granulocytic Sarcoma A granulocytic sarcoma composed of myeloblasts and promyelocytes (WHO 2001). MONDO:0006237
MONDO:0856838 differentiated granulocytic sarcoma NCIT:C35819 MONDO:equivalentTo Differentiated Granulocytic Sarcoma A granulocytic sarcoma composed of promyelocytes and more mature neutrophils (WHO 2001). MONDO:0006237
MONDO:0856840 salivary gland cystadenoma NCIT:C35833 MONDO:equivalentTo Salivary Gland Cystadenoma An uncommon benign epithelial tumor, characterized by predominantly unicystic or multicystic growth; there is focal intraluminal papillary proliferation of the lining epithelium. Nearly half occur in the parotid gland. In the minor salivary glands, women are affected more than men. In the major salivary glands, cystadenomas present as slowly enlarging, asymptomatic masses that may be slightly compressible. Cystadenocarcinoma is the malignant counterpart. MONDO:0021460
MONDO:0856844 salivary gland ductal papilloma NCIT:C35839 MONDO:equivalentTo Salivary Gland Ductal Papilloma A benign papillary neoplasm that arises from the salivary glands. This category includes intraductal papilloma, inverted ductal papilloma, and sialadenoma papilliferum. MONDO:0002363
MONDO:0856847 grade 1 clear cell renal cell carcinoma NCIT:C35851 MONDO:equivalentTo Grade 1 Clear Cell Renal Cell Carcinoma A clear cell renal cell carcinoma characterized by absent or inconspicuous and basophilic nucleoli at x 400 magnification. (WHO 1982 /ISUP 2014) MONDO:0005005
MONDO:0856848 grade 2 clear cell renal cell carcinoma NCIT:C35852 MONDO:equivalentTo Grade 2 Clear Cell Renal Cell Carcinoma A clear cell renal cell carcinoma characterized by nucleoli conspicuous and eosinophilic at x 400 magnification, and visible but not prominent at x 100 magnification. (WHO 1982 /ISUP 2014) MONDO:0005005
MONDO:0856849 grade 3 clear cell renal cell carcinoma NCIT:C35853 MONDO:equivalentTo Grade 3 Clear Cell Renal Cell Carcinoma A clear cell renal cell carcinoma characterized by nucleoli conspicuous and eosinophilic at x 100 magnification. (WHO 1982 /ISUP 2014) MONDO:0005005
MONDO:0856850 grade 4 clear cell renal cell carcinoma NCIT:C35854 MONDO:equivalentTo Grade 4 Clear Cell Renal Cell Carcinoma A clear cell renal cell carcinoma characterized by extreme nuclear pleomorphism and/or sarcomatoid and/or rhabdoid differentiation and/or tumor giant cells. (WHO, 1982 /ISUP 2014) MONDO:0005005
MONDO:0856855 endemic african kaposi sarcoma NCIT:C35874 MONDO:equivalentTo Endemic African Kaposi Sarcoma A Kaposi sarcoma that occurs in adults and children in Equatorial Africa. MONDO:0005055
MONDO:0856856 distantly metastatic malignant neoplasm NCIT:C35933 MONDO:equivalentTo Distantly Metastatic Malignant Neoplasm A malignant tumor that has spread from its original (primary) site of growth to another site distant from the primary site. MONDO:0024880
MONDO:0856857 malignant neoplasm by grade NCIT:C36041 MONDO:equivalentTo Malignant Neoplasm by Grade A term that refers to the categorization of malignant neoplasm by histologic grade. MONDO:0004992
MONDO:0856858 moderately differentiated malignant neoplasm NCIT:C36049 MONDO:equivalentTo Moderately Differentiated Malignant Neoplasm A neoplasm whose histologic characteristics are intermediate between poorly differentiated and well differentiated. MONDO:0004992
MONDO:0856859 poorly differentiated malignant neoplasm NCIT:C36050 MONDO:equivalentTo Poorly Differentiated Malignant Neoplasm A neoplasm whose histologic characteristics have regressed and are more similar to stem cells. MONDO:0004992
MONDO:0856860 undifferentiated malignant neoplasm NCIT:C36051 MONDO:equivalentTo Undifferentiated Malignant Neoplasm A neoplasm that has minimal to no differentiating features. MONDO:0004992
MONDO:0856861 well differentiated malignant neoplasm NCIT:C36052 MONDO:equivalentTo Well Differentiated Malignant Neoplasm A malignant neoplasm with morphological features reminiscent of the tissue from which it arose. MONDO:0004992
MONDO:0856862 acute myeloid leukemia with t(11;17)(q23;q21); zbtb16-rara NCIT:C36056 MONDO:equivalentTo Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16-RARA Acute myeloid leukemia with the variant RARA t(11;17)(q23;q21) and the expression of ZBTB16-RARA fusion protein. It lacks differentiation response to retinoids treatment. MONDO:0100375
MONDO:0856863 acute myeloid leukemia with t(5;17)(q35;q21); npm1-rara NCIT:C36057 MONDO:equivalentTo Acute Myeloid Leukemia with t(5;17)(q35;q21); NPM1-RARA Acute myeloid leukemia with the variant RARA t(5;17)(q35;q21) and the expression of NPM1-RARA fusion protein. MONDO:0100375
MONDO:0856864 acute myeloid leukemia with t(11;17)(q13;q21); numa1-rara NCIT:C36058 MONDO:equivalentTo Acute Myeloid Leukemia with t(11;17)(q13;q21); NUMA1-RARA Acute myeloid leukemia with the variant RARA t(11;17)(q13;q21) and the expression of NUMA1-RARA fusion protein. MONDO:0100375
MONDO:0856865 chronic myelomonocytic leukemia with eosinophilia NCIT:C36060 MONDO:equivalentTo Chronic Myelomonocytic Leukemia with Eosinophilia A chronic myelomonocytic leukemia characterized by a peripheral blood eosinophil count of equal or greater than 1.5x10E9/L, and absence of PDGFRA or PDGFRB gene abnormalities. MONDO:0020311
MONDO:0856866 chronic myelomonocytic leukemia-1 NCIT:C36061 MONDO:equivalentTo Chronic Myelomonocytic Leukemia-1 A chronic myelomonocytic leukemia characterized by the presence of less than 10 percent blasts in the bone marrow and less than 5 percent blasts in the peripheral blood. MONDO:0020311
MONDO:0856867 chronic myelomonocytic leukemia-2 NCIT:C36062 MONDO:equivalentTo Chronic Myelomonocytic Leukemia-2 A chronic myelomonocytic leukemia characterized by the presence of 10-19 percent blasts in the bone marrow and 5-19 percent blasts in the peripheral blood or by the presence of Auer rods regardless of the blasts count. MONDO:0020311
MONDO:0856875 hereditary male breast carcinoma NCIT:C36106 MONDO:equivalentTo Hereditary Male Breast Carcinoma Breast carcinoma that has developed in male relatives of patients with history of breast carcinoma. MONDO:0016419
MONDO:0856876 hereditary female breast carcinoma NCIT:C36107 MONDO:equivalentTo Hereditary Female Breast Carcinoma Breast carcinoma that has developed in female relatives of patients with history of breast carcinoma. MONDO:0016419
MONDO:0856880 non-hereditary clear cell renal cell carcinoma NCIT:C36261 MONDO:equivalentTo Non-Hereditary Clear Cell Renal Cell Carcinoma The most common type of renal cell carcinoma, characterized by a loss of genetic material of the short arm of chromosome 3. The most common symptom at the time of diagnosis is hematuria. The tumor has a golden-yellow color because of the abundance of intracytoplasmic lipid. This is a clinically aggressive type of renal cell carcinoma. The tumor usually metastasizes to unusual sites and late metastasis is common. MONDO:0005005
MONDO:0856882 metastatic benign neoplasm NCIT:C36264 MONDO:equivalentTo Metastatic Benign Neoplasm A very rare benign neoplasm that metastasizes inexplicably. This category includes metastasizing pleomorphic adenoma of the salivary gland and uterine corpus metastasizing leiomyoma. MONDO:0005165
MONDO:0856883 lymphomatous adult t-cell leukemia/lymphoma NCIT:C36266 MONDO:equivalentTo Lymphomatous Adult T-Cell Leukemia/Lymphoma An adult T-cell leukemia/lymphoma characterized by generalized lymphadenopathy without peripheral blood involvement. Most patients have advanced disease, however hypercalcemia is not frequently present. MONDO:0019471
MONDO:0856884 hodgkin-like adult t-cell leukemia/lymphoma NCIT:C36268 MONDO:equivalentTo Hodgkin-Like Adult T-Cell Leukemia/Lymphoma A rare morphologic variant of adult T-cell leukemia/lymphoma characterized by the presence of Hodgkin-like and Reed-Sternberg-like cells. MONDO:0019471
MONDO:0856885 t-cell prolymphocytic leukemia, small cell variant NCIT:C36270 MONDO:equivalentTo T-Cell Prolymphocytic Leukemia, Small Cell Variant A T-cell prolymphocytic leukemia characterized by the presence of small neoplastic prolymphocytes often with invisible nucleolus by light microscopy. MONDO:0019468
MONDO:0856886 t-cell prolymphocytic leukemia, cerebriform cell variant NCIT:C36271 MONDO:equivalentTo T-Cell Prolymphocytic Leukemia, Cerebriform Cell Variant A T-cell prolymphocytic leukemia characterized by the presence of neoplastic prolymphocytes with irregular or cerebriform nuclear outline. MONDO:0019468
MONDO:0856887 chronic lymphocytic leukemia with plasmacytoid differentiation NCIT:C36272 MONDO:equivalentTo Chronic Lymphocytic Leukemia with Plasmacytoid Differentiation A chronic lymphocytic leukemia characterized by the presence of neoplastic lymphocytes with plasmacytoid morphology. MONDO:0004948
MONDO:0856891 prostate carcinoma metastatic in the bone NCIT:C36308 MONDO:equivalentTo Prostate Carcinoma Metastatic in the Bone A carcinoma that arises from the prostate gland and has spread to the bone. MONDO:0004956
MONDO:0856897 oncocytic adenocarcinoma NCIT:C3679 MONDO:equivalentTo Oncocytic Adenocarcinoma An adenocarcinoma characterized by the presence of large malignant epithelial cells with abundant granular eosinophilic cytoplasm (oncocytes). Representative examples include thyroid gland oncocytic follicular carcinoma, oncocytic breast carcinoma, and salivary gland oncocytic carcinoma. MONDO:0004970
MONDO:0856898 sweat gland tubular carcinoma NCIT:C3682 MONDO:equivalentTo Sweat Gland Tubular Carcinoma An aggressive adenocarcinoma that arises from the sweat glands. It usually presents as a firm, erythematous nodular lesion in the axilla. Morphologically, it is characterized by the presence of tubular structures and apocrine differentiation. MONDO:0005524
MONDO:0856899 trabecular adenoma NCIT:C3688 MONDO:equivalentTo Trabecular Adenoma A benign epithelial neoplasm characterized by the presence of a trabecular glandular architectural pattern. MONDO:0004972
MONDO:0856900 carcinomatosis NCIT:C3693 MONDO:equivalentTo Carcinomatosis Carcinoma that has spread diffusely to an anatomic site or throughout the body. MONDO:0024879
MONDO:0856901 papillary fibroelastoma NCIT:C3695 MONDO:equivalentTo Papillary Fibroelastoma A rare benign neoplasm of the endocardium. The vast majority of cases arise in the heart valves. Histopathologic examination reveals a papilloma lined by endothelial cells with a central avascular core which contains fibroblasts and elastic fibers. Patients may be asymptomatic or present with ischemic or embolic events. MONDO:0021505
MONDO:0856902 meningiomatosis NCIT:C3707 MONDO:equivalentTo Meningiomatosis The presence of multiple meningiomas in the leptomeninges. MONDO:0016642
MONDO:0856905 chronic lymphocytic leukemia with immunoglobulin heavy chain variable-region gene somatic hypermutation NCIT:C37202 MONDO:equivalentTo Chronic Lymphocytic Leukemia with Immunoglobulin Heavy Chain Variable-Region Gene Somatic Hypermutation Chronic lymphocytic leukemia characterized by the presence of somatic hypermutation within the immunoglobulin heavy chain gene variable region of neoplastic clones. Patients have a better prognosis as compared to those with unmutated immunoglobulin heavy chain gene variable region rearrangements. MONDO:0004948
MONDO:0856906 chronic lymphocytic leukemia with unmutated immunoglobulin heavy chain variable-region gene NCIT:C37205 MONDO:equivalentTo Chronic Lymphocytic Leukemia with Unmutated Immunoglobulin Heavy Chain Variable-Region Gene Chronic lymphocytic leukemia characterized by the absence of somatic hypermutation within the immunoglobulin heavy chain gene variable region of neoplastic clones. Patients have a significantly worse prognosis as compared to those with mutated immunoglobulin heavy chain gene variable region rearrangements. MONDO:0004478
MONDO:0856907 high grade b-cell lymphoma with blastoid morphologic features NCIT:C37209 MONDO:equivalentTo High Grade B-Cell Lymphoma with Blastoid Morphologic Features A high-grade B-cell lymphoma characterized by the presence of medium-size neoplastic lymphocytes with a scant amount of cytoplasm and inconspicuous nucleoli, resembling lymphoblasts. MONDO:0044889
MONDO:0856911 benign kidney mixed epithelial and stromal tumor NCIT:C37264 MONDO:equivalentTo Benign Kidney Mixed Epithelial and Stromal Tumor A rare, benign neoplasm that most often manifests as a multiloculated cystic renal mass. It is characterized by the presence of solid and cystic components. The solid components contain a mixture of epithelial and stromal elements. MONDO:0002513
MONDO:0856912 atypical small acinar proliferation of the prostate gland NCIT:C37268 MONDO:equivalentTo Atypical Small Acinar Proliferation of the Prostate Gland Focal proliferation of small acinar glandular cells in the prostate gland with cytologic changes ranging from atypia to highly suggestive of malignancy. MONDO:0021259
MONDO:0856914 head and neck basaloid squamous cell carcinoma NCIT:C37290 MONDO:equivalentTo Head and Neck Basaloid Squamous Cell Carcinoma A high-grade, aggressive variant of squamous cell carcinoma that arises from the head and neck region. The most common sites of origin are pyriform sinus, epiglottis, and base of tongue. It is characterized by the presence of small malignant cells with hyperchromatic nuclei and scant amount of cytoplasm forming lobules with peripheral palisading. Comedonecrosis may be present. MONDO:0010150
MONDO:0856915 mixed mesodermal (mullerian) tumor NCIT:C3730 MONDO:equivalentTo Mixed Mesodermal (Mullerian) Tumor A group of tumors affecting the female reproductive system, characterized by the presence of epithelial and stromal elements. It includes the following clinicopathological entities: adenofibroma, adenomyoma, Mullerian adenosarcoma, and malignant mixed mesodermal (Mullerian) tumor. MONDO:0021148
MONDO:0856917 abdominal (mesenteric) fibromatosis NCIT:C3741 MONDO:equivalentTo Abdominal (Mesenteric) Fibromatosis An insidious poorly circumscribed neoplasm arising from the deep soft tissues of the abdomen. It is characterized by the presence of elongated spindle-shaped fibroblasts, collagenous stroma formation, and an infiltrative growth pattern. MONDO:0007608
MONDO:0856918 adenomatous polyp NCIT:C3764 MONDO:equivalentTo Adenomatous Polyp A polypoid neoplasm arising from the glandular epithelium of the gastrointestinal tract. There is proliferation of glandular cells which may display dysplastic cytologic features. Representative examples include the adenomatous polyps of the colon and rectum.. MONDO:0006180
MONDO:0856920 giant cell carcinoma NCIT:C3779 MONDO:equivalentTo Giant Cell Carcinoma A malignant epithelial neoplasm composed of giant, pleomorphic cells. MONDO:0005232
MONDO:0856923 renal cell carcinoma associated with t(x;1)(p11.2;q21) NCIT:C37872 MONDO:equivalentTo Renal Cell Carcinoma Associated with t(X;1)(p11.2;q21) A renal cell carcinoma with papillary architecture comprised of clear cells. It is characterized by the t(X;1)(p11.2;q21) resulting in fusion of the PRCC and TFE3 genes. MONDO:0006397
MONDO:0856924 renal cell carcinoma associated with t(x;1)(p11.2;p34) NCIT:C37874 MONDO:equivalentTo Renal Cell Carcinoma Associated with t(X;1)(p11.2;p34) A renal cell carcinoma with papillary architecture comprised of clear cells. It is characterized by the t(X;1)(p11.2;p34) resulting in fusion of the PSF and TFE3 genes. MONDO:0006397
MONDO:0856925 renal cell carcinoma associated with t(x;17)(p11.2;q25) NCIT:C37876 MONDO:equivalentTo Renal Cell Carcinoma Associated with t(X;17)(p11.2;q25) A renal cell carcinoma with papillary architecture comprised of clear cells. It is characterized by the t(X;1)(p11.2;q25) resulting in fusion of the ASPL and TFE3 genes. MONDO:0006397
MONDO:0856927 angiofibroma NCIT:C3799 MONDO:equivalentTo Angiofibroma A morphologic variant of fibroma characterized by the presence of numerous dilated vascular channels. MONDO:0005167
MONDO:0856930 dermatofibrosarcoma protuberans with myoid differentiation NCIT:C38105 MONDO:equivalentTo Dermatofibrosarcoma Protuberans with Myoid Differentiation A morphologic variant of dermatofibrosarcoma protuberans characterized by the presence of areas of myofibroblastic differentiation. MONDO:0011934
MONDO:0856931 myxoid dermatofibrosarcoma protuberans NCIT:C38106 MONDO:equivalentTo Myxoid Dermatofibrosarcoma Protuberans A morphologic variant of dermatofibrosarcoma protuberans characterized by the presence of extensive myxoid stroma formation and a storiform growth pattern. MONDO:0011934
MONDO:0856932 dedifferentiated dermatofibrosarcoma protuberans NCIT:C38107 MONDO:equivalentTo Dedifferentiated Dermatofibrosarcoma Protuberans A morphologic variant of dermatofibrosarcoma protuberans characterized by the presence of poorly differentiated sarcomatous components. MONDO:0011934
MONDO:0856933 dermatofibrosarcoma protuberans with giant cell fibroblastoma-like differentiation NCIT:C38108 MONDO:equivalentTo Dermatofibrosarcoma Protuberans with Giant Cell Fibroblastoma-Like Differentiation A morphologic variant of dermatofibrosarcoma protuberans characterized by areas of fibroblastoma like-differentiation, and the presence of giant cells. MONDO:0011934
MONDO:0856934 skin basal cell carcinoma with adnexal differentiation NCIT:C38109 MONDO:equivalentTo Skin Basal Cell Carcinoma with Adnexal Differentiation A basal cell carcinoma of the skin that is characterized by adnexal differentiation. MONDO:0005341
MONDO:0856938 clear cell myomelanocytic tumor of the falciform ligament/ligamentum teres NCIT:C38154 MONDO:equivalentTo Clear Cell Myomelanocytic Tumor of the Falciform Ligament/Ligamentum Teres A very rare, usually benign neoplasm with perivascular epithelioid cell differentiation characterized by the presence of clear spindle cells arranged in fascicles and nests that usually affects young girls. Patients usually present with a painful abdominal mass. MONDO:0006359
MONDO:0856939 metachronous malignant neoplasm NCIT:C38156 MONDO:equivalentTo Metachronous Malignant Neoplasm A malignant tumor that arises at a site separate from another, primary malignant tumor in the same anatomic system. It is not clear if metachronous malignant neoplasms represent new primary tumors or metastatic disease. Examples include metachronous osteosarcoma of the bones that develops in patients with known primary bone osteosarcoma, and metachronous Wilms' tumor that affects the opposite kidney in patients with a history of Wilms' tumor. MONDO:0004992
MONDO:0856940 plasmablastic lymphoma of mucosa site NCIT:C38159 MONDO:equivalentTo Plasmablastic Lymphoma of Mucosa Site A plasmablastic lymphoma that arises from a mucosal site. MONDO:0017347
MONDO:0856941 digestive system non-hodgkin lymphoma NCIT:C38161 MONDO:equivalentTo Digestive System Non-Hodgkin Lymphoma A non-Hodgkin lymphoma that arises from any part of the digestive system, with the bulk of the disease localized to that site. MONDO:0018908
MONDO:0856942 digestive system hodgkin lymphoma NCIT:C38163 MONDO:equivalentTo Digestive System Hodgkin Lymphoma A Hodgkin lymphoma that arises from any part of the digestive system, with the bulk of the disease localized to that site. MONDO:0004699
MONDO:0856943 acute myeloid leukemia with stat5b-rara NCIT:C38377 MONDO:equivalentTo Acute Myeloid Leukemia with STAT5B-RARA Acute myeloid leukemia with variant RARA rearrangement and expression of STAT5B-RARA fusion protein. MONDO:0100375
MONDO:0856945 traditional serrated adenoma NCIT:C38458 MONDO:equivalentTo Traditional Serrated Adenoma An adenoma that arises from the large intestine and the appendix. It is characterized by prominent serration of the glands. MONDO:0006180
MONDO:0856947 benign female breast neoplasm NCIT:C3848 MONDO:equivalentTo Benign Female Breast Neoplasm A neoplasm that arises from the breast in females and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0000620
MONDO:0856948 aggravated malignant neoplasm NCIT:C3851 MONDO:equivalentTo Aggravated Malignant Neoplasm A malignant neoplasm that shows clinical and/or pathologic progression. MONDO:0004992
MONDO:0856949 thyroid gland sclerosing mucoepidermoid carcinoma with eosinophilia NCIT:C38763 MONDO:equivalentTo Thyroid Gland Sclerosing Mucoepidermoid Carcinoma with Eosinophilia A rare type of mucoepidermoid carcinoma of the thyroid gland, usually associated with chronic lymphocytic thyroiditis. It exhibits a unique morphologic appearance consisting of a squamoid, nested growth pattern, dense fibrosis, and mucinous differentiation. The histogenesis of this unusual carcinoma has been debated, and it is unclear if it arises from remnants of the ultimobranchial body or from the follicular epithelial cells. MONDO:0006463
MONDO:0856951 grade 1 meningioma NCIT:C38936 MONDO:equivalentTo Grade 1 Meningioma A benign meningioma which may recur in approximately 7-20% of the cases. This category includes the angiomatous meningioma, fibrous meningioma, lymphoplasmacyte-rich meningioma, meningothelial meningioma, metaplastic meningioma, microcystic meningioma, psammomatous meningioma, secretory meningioma, and transitional meningioma. MONDO:0016642
MONDO:0856952 compound nevus NCIT:C3901 MONDO:equivalentTo Compound Nevus A nevus composed of neoplastic melanocytes that infiltrate both the epidermis and the dermis. MONDO:0005073
MONDO:0856963 t-cell large granular lymphocyte leukemia, common variant NCIT:C39584 MONDO:equivalentTo T-Cell Large Granular Lymphocyte Leukemia, Common Variant T-cell large granular lymphocyte leukemia defined by the presence of CD3-positive, CD8-positive, and T-cell receptor alpha-beta-positive cytotoxic T-cells. MONDO:0019469
MONDO:0856964 t-cell large granular lymphocyte leukemia expressing the t-cell receptor gamma-delta NCIT:C39586 MONDO:equivalentTo T-Cell Large Granular Lymphocyte Leukemia Expressing the T-Cell Receptor Gamma-Delta An uncommon variant of T-cell large granular lymphocyte leukemia expressing the gamma-delta T-cell receptor. Approximately 60% of these cases are CD8-positive and the remainder are CD4/CD8-negative. MONDO:0019469
MONDO:0856966 anaplastic large cell lymphoma, giant cell rich subtype NCIT:C39674 MONDO:equivalentTo Anaplastic Large Cell Lymphoma, Giant Cell Rich Subtype An anaplastic large cell lymphoma characterized by the presence of numerous giant cells. MONDO:0020325
MONDO:0856967 anaplastic large cell lymphoma, sarcomatoid subtype NCIT:C39675 MONDO:equivalentTo Anaplastic Large Cell Lymphoma, Sarcomatoid Subtype A are variant of anaplastic large cell lymphoma. It is characterized by presence of large spindle shaped cells resembling a soft tissue sarcoma. MONDO:0020325
MONDO:0856968 anaplastic large cell lymphoma, signet ring-like subtype NCIT:C39676 MONDO:equivalentTo Anaplastic Large Cell Lymphoma, Signet Ring-Like Subtype An anaplastic large cell lymphoma, characterized by lymphoid cells with signet ring nuclei. MONDO:0020325
MONDO:0856969 pleomorphic variant mantle cell lymphoma NCIT:C39747 MONDO:equivalentTo Pleomorphic Variant Mantle Cell Lymphoma An aggressive mantle cell lymphoma characterized by the presence of pleomorphic neoplastic B-lymphocytes. MONDO:0018876
MONDO:0856970 type ii endometrial adenocarcinoma NCIT:C39749 MONDO:equivalentTo Type II Endometrial Adenocarcinoma A classification of primary endometrial adenocarcinomas that refers to clear cell adenocarcinoma, serous adenocarcinoma, and serous endometrial intraepithelial carcinoma. MONDO:0005461
MONDO:0856971 glioblastoma, idh-wildtype NCIT:C39750 MONDO:equivalentTo Glioblastoma, IDH-Wildtype A glioblastoma that arises de novo. It is more commonly seen in older patients. Mutations in IDH1 or IDH2 genes are not present. MONDO:0018177
MONDO:0856972 secondary glioblastoma NCIT:C39751 MONDO:equivalentTo Secondary Glioblastoma A glioblastoma arising from a lower grade astrocytoma. MONDO:0018177
MONDO:0856973 conventional ameloblastoma NCIT:C39755 MONDO:equivalentTo Conventional Ameloblastoma An intraosseous ameloblastoma that arises from the jaw, usually the mandible. It grows slowly, invades locally, and recurs frequently. It presents with swelling of the jaw. MONDO:0017795
MONDO:0856974 unicystic ameloblastoma NCIT:C39756 MONDO:equivalentTo Unicystic Ameloblastoma An ameloblastoma that presents as a unilocular cyst. It usually arises from the mandible. MONDO:0021077
MONDO:0856975 renal cell carcinoma with constitutional chromosome 3 translocations NCIT:C39790 MONDO:equivalentTo Renal Cell Carcinoma with Constitutional Chromosome 3 Translocations A renal cell carcinoma with constitutional chromosome 3 translocations. MONDO:0003008
MONDO:0856976 renal cell carcinoma associated with inv(x)(p11;q12) NCIT:C39802 MONDO:equivalentTo Renal Cell Carcinoma Associated with inv(X)(p11;q12) A renal cell carcinoma with papillary architecture comprised of clear cells. It is characterized by the inv(X)(p11;q12) resulting in fusion of the NONO (p54nrb) and TFE3 genes. MONDO:0006397
MONDO:0856980 invasive bladder sarcomatoid urothelial carcinoma with heterologous elements NCIT:C39825 MONDO:equivalentTo Invasive Bladder Sarcomatoid Urothelial Carcinoma with Heterologous Elements Invasive bladder sarcomatoid urothelial carcinoma characterized by the presence of heterologous elements. MONDO:0004278
MONDO:0856981 invasive bladder sarcomatoid urothelial carcinoma without heterologous elements NCIT:C39826 MONDO:equivalentTo Invasive Bladder Sarcomatoid Urothelial Carcinoma without Heterologous Elements Invasive bladder sarcomatoid urothelial carcinoma characterized by the absence of heterologous elements. MONDO:0004278
MONDO:0856984 bladder adenocarcinoma, not otherwise specified NCIT:C39836 MONDO:equivalentTo Bladder Adenocarcinoma, Not Otherwise Specified An adenocarcinoma, not otherwise specified, arising from the bladder. MONDO:0002751
MONDO:0856986 human papillomavirus-related urethral squamous cell carcinoma NCIT:C39862 MONDO:equivalentTo Human Papillomavirus-Related Urethral Squamous Cell Carcinoma A rare urethral squamous cell carcinoma that is related to human papilloma virus (HPV) infection of the urinary tract. MONDO:0002764
MONDO:0856987 bladder mucosa-associated lymphoid tissue lymphoma NCIT:C39878 MONDO:equivalentTo Bladder Mucosa-Associated Lymphoid Tissue Lymphoma A rare mucosa-associated lymphoid tissue lymphoma affecting the bladder. MONDO:0001381
MONDO:0856988 prostate acinar adenocarcinoma, atrophic pattern NCIT:C39880 MONDO:equivalentTo Prostate Acinar Adenocarcinoma, Atrophic Pattern An unusual variant of acinar prostate adenocarcinoma characterized by the presence of neoplastic small atrophic glands that contain malignant cells with scant cytoplasm. MONDO:0002493
MONDO:0856989 prostate acinar pseudohyperplastic adenocarcinoma NCIT:C39881 MONDO:equivalentTo Prostate Acinar Pseudohyperplastic Adenocarcinoma Acinar prostate adenocarcinoma characterized by the presence of neoplastic large glands that resemble the benign, non-neoplastic prostate glands. MONDO:0002493
MONDO:0856991 prostatic duct urothelial carcinoma NCIT:C39901 MONDO:equivalentTo Prostatic Duct Urothelial Carcinoma An urothelial carcinoma that arises from the urothelial lining of the prostatic ducts. MONDO:0002834
MONDO:0856992 testicular seminoma with syncytiotrophoblastic cells NCIT:C39919 MONDO:equivalentTo Testicular Seminoma with Syncytiotrophoblastic Cells A testicular seminoma characterized by the presence of syncytiotrophoblastic giant cells. MONDO:0003669
MONDO:0856994 testicular seminoma with high mitotic index NCIT:C39920 MONDO:equivalentTo Testicular Seminoma with High Mitotic Index A seminoma of the testis characterized by increased cellular pleomorphism, high mitotic activity, and a non-prominent stromal lymphocytic infiltrate. MONDO:0020633
MONDO:0856995 testicular spermatocytic tumor with sarcoma NCIT:C39922 MONDO:equivalentTo Testicular Spermatocytic Tumor with Sarcoma A malignant germ cell tumor that arises from the testis and is characterized by the presence of a spermatocytic tumor component that is contiguous with an undifferentiated or differentiated sarcomatous component. It usually presents as a slowly growing mass that enlarges very rapidly soon after the initial diagnosis. MONDO:0020513
MONDO:0856996 monodermal testicular teratoma NCIT:C39936 MONDO:equivalentTo Monodermal Testicular Teratoma A teratoma that arises from the testis. It is composed exclusively of one of the following tissue types: endoderm, ectoderm, or mesoderm. MONDO:0018193
MONDO:0856997 testicular sertoli cell tumor, lipid rich variant NCIT:C39943 MONDO:equivalentTo Testicular Sertoli Cell Tumor, Lipid Rich Variant A testicular Sertoli cell tumor in which the neoplastic cells have clear and vacuolated cytoplasm due to accumulation of intracytoplasmic lipids. MONDO:0020813
MONDO:0856998 testicular large cell calcifying sertoli cell tumor NCIT:C39944 MONDO:equivalentTo Testicular Large Cell Calcifying Sertoli Cell Tumor A testicular Sertoli cell tumor characterized by the presence of large polygonal cells with eosinophilic cytoplasm in a myxoid and hyalinized stroma. Calcifications may be present in the stroma. Malignant behavior is uncommon. MONDO:0020808
MONDO:0856999 testicular sclerosing sertoli cell tumor NCIT:C39945 MONDO:equivalentTo Testicular Sclerosing Sertoli Cell Tumor A rare testicular Sertoli cell tumor characterized by the presence of neoplastic tubules that are surrounded by a dense fibrotic stroma. MONDO:0020813
MONDO:0857002 tumor of the thecoma/fibroma group NCIT:C39950 MONDO:equivalentTo Tumor of the Thecoma/Fibroma Group A sex cord-stromal tumor that arises from the ovary or the testis. Representative examples include fibroma, fibrosarcoma, and thecoma. MONDO:0006055
MONDO:0857004 moderately differentiated ovarian sertoli-leydig cell tumor NCIT:C39968 MONDO:equivalentTo Moderately Differentiated Ovarian Sertoli-Leydig Cell Tumor A Sertoli-Leydig cell tumor of the ovary characterized by the presence of spindle-shaped gonadal stromal cells and Sertoli cells, some of which are atypical. Leydig cells are also present forming clusters at the periphery of the cellular aggregates. Metastases have been reported in a minority of patients. MONDO:0036595
MONDO:0857005 ovarian sertoli-leydig cell tumor with heterologous elements NCIT:C39970 MONDO:equivalentTo Ovarian Sertoli-Leydig Cell Tumor with Heterologous Elements A Sertoli-Leydig cell tumor that arises from the ovary. It is characterized by the presence of epithelial and/or mesenchymal components and neoplasms that arise from these components. MONDO:0036595
MONDO:0857006 ovarian retiform sertoli-leydig cell tumor NCIT:C39971 MONDO:equivalentTo Ovarian Retiform Sertoli-Leydig Cell Tumor A Sertoli-Leydig cell tumor of the ovary in which anastomosing, slit-like spaces resembling rete testis constitute at least 90% of the tumor elements. It may present with estrogenic and less often androgenic manifestations. It usually follows a benign clinical course. MONDO:0036595
MONDO:0857007 ovarian sertoli-leydig cell tumor with retiform elements NCIT:C39974 MONDO:equivalentTo Ovarian Sertoli-Leydig Cell Tumor with Retiform Elements A Sertoli-Leydig cell tumor characterized by the presence of spaces that resemble rete testis (retiform elements). These spaces form anastomosing patterns and comprise at least ten percent but less than ninety percent of the tumor. When the retiform elements comprise ninety percent or more of the tumor, the term retiform Sertoli-Leydig cell tumor is used. A minority of patients may have an aggressive clinical course. MONDO:0036595
MONDO:0857008 ovarian stromal-leydig cell tumor NCIT:C39977 MONDO:equivalentTo Ovarian Stromal-Leydig Cell Tumor A rare, benign and well circumscribed stromal tumor of the ovary. It is characterized by the presence of a fibrotic stroma with clusters of Leydig cells. The Leydig cells contain crystals of Reinke. Patients may present with virilization. MONDO:0024387
MONDO:0857009 ovarian sex cord-stromal tumor, not otherwise specified NCIT:C39978 MONDO:equivalentTo Ovarian Sex Cord-Stromal Tumor, Not Otherwise Specified A sex cord-stromal tumor that arises from the ovary and lacks the morphologic features that belong to the categories of granulosa-stromal tumors, Sertoli-stromal tumors, or steroid cell tumors. MONDO:0021657
MONDO:0857012 malignant ovarian teratoma NCIT:C39995 MONDO:equivalentTo Malignant Ovarian Teratoma A teratoma that arises from the ovary. It is composed exclusively of immature tissue elements. MONDO:0003514
MONDO:0857014 borderline ovarian serous tumor/atypical proliferative ovarian serous tumor with microinvasion NCIT:C40027 MONDO:equivalentTo Borderline Ovarian Serous Tumor/Atypical Proliferative Ovarian Serous Tumor with Microinvasion A low grade ovarian epithelial neoplasm characterized by the presence of neoplastic serous epithelial cells, atypia, and microinvasion of the ovarian stroma. MONDO:0037255
MONDO:0857015 borderline ovarian serous adenofibroma NCIT:C40028 MONDO:equivalentTo Borderline Ovarian Serous Adenofibroma A low malignant potential adenofibroma arising from the ovary. It is characterized by an atypical epithelial hyperplasia. The epithelial cells are of serous type. There is no evidence of stromal destructive invasion. MONDO:0024886
MONDO:0857016 borderline ovarian mucinous tumor NCIT:C40036 MONDO:equivalentTo Borderline Ovarian Mucinous Tumor A low grade mucinous epithelial neoplasm arising from the ovary. It is characterized by an atypical proliferation of mucinous-type epithelial cells without evidence of stromal invasion. The mucinous epithelial cells may be of intestinal or endocervical type. MONDO:0003756
MONDO:0857017 ovarian mucinous cystic tumor with mural nodules NCIT:C40042 MONDO:equivalentTo Ovarian Mucinous Cystic Tumor with Mural Nodules A mucinous cystic tumor of the ovary characterized by the presence of one or more well circumscribed solid nodules in the wall of the cysts (mural nodules) that protrude into the lumen. The mural nodules may be benign (sarcoma-like) or malignant. The malignant mural nodules histologically are anaplastic carcinomas, carcinosarcomas, or sarcomas. The clinical course depends on the histology of the mural nodules. The prognosis of mucinous cystic tumors with benign mural nodules is the same as the corresponding types of mucinous cystic tumors without the mural nodules. Mucinous cystic tumors with malignant mural nodules may follow a malignant clinical course. MONDO:0003756
MONDO:0857018 ovarian mucinous cystic tumor associated with pseudomyxoma peritonei NCIT:C40043 MONDO:equivalentTo Ovarian Mucinous Cystic Tumor Associated with Pseudomyxoma Peritonei The presence of abundant mucoid or gelatinous, cellular or acellular material in the pelvis and abdominal cavity (pseudomyxoma peritonei) that is associated with the presence of an ovarian mucinous cystic tumor. In the vast majority of cases, the presence of pseudomyxoma peritonei is the result of metastasis from a primary appendiceal or gastrointestinal tumor site, and the ovarian mucinous tumor is metastatic rather than primary. MONDO:0003756
MONDO:0857022 borderline ovarian clear cell tumor NCIT:C40080 MONDO:equivalentTo Borderline Ovarian Clear Cell Tumor An epithelial neoplasm with low malignant potential affecting the ovary. It is characterized by the presence of clear or hobnail cells. In some cases, the cells may display nuclear atypia and prominent nucleoli. When such cells are present, they remain confined to the glands. There is no evidence of stromal invasion. MONDO:0021144
MONDO:0857025 fallopian tube serous neoplasm NCIT:C40102 MONDO:equivalentTo Fallopian Tube Serous Neoplasm A benign, borderline, or malignant epithelial tumor of the fallopian tube characterized by the presence of neoplastic serous epithelial cells. MONDO:0037256
MONDO:0857028 fallopian tube endometrioid polyp NCIT:C40115 MONDO:equivalentTo Fallopian Tube Endometrioid Polyp An adenomatous polyp that arises from the interstitial portion of the fallopian tube and is characterized by the presence of endometrial epithelium. It may obstruct the lumen of the fallopian tube and result in infertility or tubal pregnancy. MONDO:0021075
MONDO:0857029 fallopian tube metaplastic papillary tumor NCIT:C40116 MONDO:equivalentTo Fallopian Tube Metaplastic Papillary Tumor A rare metaplastic lesion that arises from the fallopian tube. It is characterized by the presence of an intraluminal papillary proliferation composed of atypical epithelial cells with abundant eosinophilic cytoplasm. In the vast majority of cases, it is an incidental finding during microscopic examination of a fallopian tube in the postpartum period. MONDO:0021096
MONDO:0857030 fallopian tube soft tissue neoplasm NCIT:C40126 MONDO:equivalentTo Fallopian Tube Soft Tissue Neoplasm A benign or malignant mesenchymal neoplasm of the fallopian tube. Representative examples include leiomyoma and leiomyosarcoma. MONDO:0006424
MONDO:0857031 type i endometrial adenocarcinoma NCIT:C40145 MONDO:equivalentTo Type I Endometrial Adenocarcinoma A classification of primary endometrial adenocarcinomas that refers to endometrioid adenocarcinoma and mucinous adenocarcinoma. MONDO:0005461
MONDO:0857033 figo grade 1 endometrial mucinous adenocarcinoma NCIT:C40149 MONDO:equivalentTo FIGO Grade 1 Endometrial Mucinous Adenocarcinoma A primary mucinous adenocarcinoma of the endometrium that contains equal to or less than 5% non-squamous solid areas. MONDO:0002747
MONDO:0857034 figo grade 2 endometrial mucinous adenocarcinoma NCIT:C40150 MONDO:equivalentTo FIGO Grade 2 Endometrial Mucinous Adenocarcinoma A primary mucinous adenocarcinoma of the endometrium that contains 6-50% non-squamous solid areas. MONDO:0002747
MONDO:0857035 figo grade 3 endometrial mucinous adenocarcinoma NCIT:C40151 MONDO:equivalentTo FIGO Grade 3 Endometrial Mucinous Adenocarcinoma A primary mucinous adenocarcinoma of the endometrium that contains more than 50% non-squamous solid areas. MONDO:0002747
MONDO:0857036 uterine corpus leiomyoma, mitotically active variant NCIT:C40162 MONDO:equivalentTo Uterine Corpus Leiomyoma, Mitotically Active Variant A morphologic variant of uterine corpus leiomyoma characterized by an increased number of mitoses (up to 19 mitoses per 10 high-powered fields). MONDO:0007886
MONDO:0857037 uterine corpus soft tissue neoplasm NCIT:C40179 MONDO:equivalentTo Uterine Corpus Soft Tissue Neoplasm A benign or malignant mesenchymal neoplasm of the uterine corpus. Representative examples include leiomyoma, leiomyosarcoma, and endometrial stromal sarcoma. MONDO:0021254
MONDO:0857039 cervical squamous neoplasm NCIT:C40195 MONDO:equivalentTo Cervical Squamous Neoplasm A benign, precancerous, or malignant neoplasm that arises from the squamous epithelium of the cervix. Representative examples include condyloma acuminatum, cervical intraepithelial neoplasia, and squamous cell carcinoma. MONDO:0002532
MONDO:0857040 cervical glandular neoplasm NCIT:C40210 MONDO:equivalentTo Cervical Glandular Neoplasm A benign, malignant, or precancerous neoplasm that arises from the glandular epithelium of the cervix. Representative examples include endocervical polyp, cervical adenocarcinoma, and cervical glandular intraepithelial neoplasia. MONDO:0024276
MONDO:0857041 cervical soft tissue neoplasm NCIT:C40216 MONDO:equivalentTo Cervical Soft Tissue Neoplasm A benign or malignant mesenchymal neoplasm of the cervix. Representative examples include rhabdomyoma, alveolar soft part sarcoma, and AIDS-related Kaposi sarcoma. MONDO:0006424
MONDO:0857043 cervical mixed epithelial and mesenchymal neoplasm NCIT:C40226 MONDO:equivalentTo Cervical Mixed Epithelial and Mesenchymal Neoplasm A benign or malignant neoplasm that arises from the cervix and is characterized by the presence of epithelial and mesenchymal elements. This category includes adenofibroma, adenomyoma, adenosarcoma, and carcinosarcoma. MONDO:0021043
MONDO:0857045 vaginal keratinizing squamous cell carcinoma NCIT:C40243 MONDO:equivalentTo Vaginal Keratinizing Squamous Cell Carcinoma A squamous cell carcinoma that arises from the vagina and is characterized by the presence of keratin pearls. Intercellular bridges and cytoplasmic keratinization are usually present. MONDO:0005056
MONDO:0857046 vaginal basaloid squamous cell carcinoma NCIT:C40245 MONDO:equivalentTo Vaginal Basaloid Squamous Cell Carcinoma A squamous cell carcinoma that arises from the vagina and is characterized by the presence of nests of malignant basaloid squamous cells with scant amounts of cytoplasm. MONDO:0003486
MONDO:0857047 vaginal endometrioid adenocarcinoma NCIT:C40251 MONDO:equivalentTo Vaginal Endometrioid Adenocarcinoma A rare adenocarcinoma that arises from the vagina with histologic features resembling the endometrioid adenocarcinoma of the endometrium. MONDO:0020653
MONDO:0857048 vaginal mucinous adenocarcinoma NCIT:C40252 MONDO:equivalentTo Vaginal Mucinous Adenocarcinoma A rare adenocarcinoma that arises from the vagina with histologic features resembling cervical mucinous adenocarcinoma. MONDO:0020653
MONDO:0857049 vaginal mesonephric adenocarcinoma NCIT:C40253 MONDO:equivalentTo Vaginal Mesonephric Adenocarcinoma Vaginal adenocarcinoma that derives from Wolffian duct remnants and shows mesonephric differentiation. MONDO:0020653
MONDO:0857050 vaginal adenosquamous carcinoma NCIT:C40260 MONDO:equivalentTo Vaginal Adenosquamous Carcinoma A carcinoma that arises from the vagina and is characterized by the presence of malignant glandular and malignant squamous epithelial components. MONDO:0006074
MONDO:0857051 vaginal adenoid basal carcinoma NCIT:C40262 MONDO:equivalentTo Vaginal Adenoid Basal Carcinoma A carcinoma that arises from the vagina and is characterized by the presence of nests of basaloid cells with focal glandular formations. MONDO:0015867
MONDO:0857052 vaginal undifferentiated carcinoma NCIT:C40264 MONDO:equivalentTo Vaginal Undifferentiated Carcinoma A carcinoma that arises from the vagina and is characterized by the lack of specific cellular differentiation. MONDO:0015867
MONDO:0857053 vaginal soft tissue neoplasm NCIT:C40265 MONDO:equivalentTo Vaginal Soft Tissue Neoplasm A benign or malignant mesenchymal neoplasm that arises from the vagina. Representative examples include leiomyoma, rhabdomyoma, leiomyosarcoma, endometrioid stromal sarcoma, and botryoid-type embryonal rhabdomyosarcoma. MONDO:0021050
MONDO:0857056 vaginal mixed epithelial and mesenchymal neoplasm NCIT:C40274 MONDO:equivalentTo Vaginal Mixed Epithelial and Mesenchymal Neoplasm A benign or malignant neoplasm that arises from the vagina and is characterized by the presence of epithelial and mesenchymal elements. This category includes benign mixed tumor, adenosarcoma, carcinosarcoma, and malignant mixed tumor resembling synovial sarcoma. MONDO:0021043
MONDO:0857057 malignant vaginal mixed tumor resembling synovial sarcoma NCIT:C40279 MONDO:equivalentTo Malignant Vaginal Mixed Tumor Resembling Synovial Sarcoma A very rare malignant mixed epithelial and mesenchymal neoplasm that arises from the vagina and resembles synovial sarcoma. It is characterized by a biphasic pattern and is composed of gland-like structures that are lined by epithelial cells and a cellular mesenchymal component. MONDO:0037746
MONDO:0857058 vulvar squamous cell carcinoma with tumor giant cells NCIT:C40289 MONDO:equivalentTo Vulvar Squamous Cell Carcinoma with Tumor Giant Cells An aggressive squamous cell carcinoma that arises from the vulva and is characterized by the prominence of malignant giant cells. MONDO:0024609
MONDO:0857059 vulvar neoplasm of skin appendage origin NCIT:C40303 MONDO:equivalentTo Vulvar Neoplasm of Skin Appendage Origin A benign or malignant vulvar neoplasm with differentiating characteristics towards sweat or sebaceous glands or hair follicles. Representative examples include trichoepithelioma, syringoma, and eccrine adenocarcinoma. MONDO:0002297
MONDO:0857061 vulvar soft tissue neoplasm NCIT:C40316 MONDO:equivalentTo Vulvar Soft Tissue Neoplasm A benign or malignant mesenchymal neoplasm of the vulva. Representative examples include leiomyoma, cellular angiofibroma, angiomyxoma, leiomyosarcoma, liposarcoma, and childhood botryoid-type embryonal rhabdomyosarcoma. MONDO:0021049
MONDO:0857062 superficial angiomyxoma NCIT:C40323 MONDO:equivalentTo Superficial Angiomyxoma An angiomyxoma arising from the dermis or subcutaneous tissues. It may recur following resection. MONDO:0006086
MONDO:0857067 vulvar melanocytic neoplasm NCIT:C40335 MONDO:equivalentTo Vulvar Melanocytic Neoplasm A neoplasm that originates from melanocytes and arises from the vulva. This category includes congenital and acquired melanocytic nevus, blue nevus, dysplastic melanocytic nevus, atypical melanocytic nevus of genital type, and melanoma. MONDO:0021143
MONDO:0857071 breast carcinoma with osteoclast-like stromal giant cells NCIT:C40349 MONDO:equivalentTo Breast Carcinoma with Osteoclast-Like Stromal Giant Cells An invasive breast adenocarcinoma characterised by the presence of non-neoplastic stromal osteoclastic giant cells. The carcinomatous component is usually an invasive ductal carcinoma, although all other breast adenocarcinoma subtypes have also been described. The prognosis depends on the characteristics of the adenocarcinomatous component, and is not related to the presence of the giant cells. MONDO:0004953
MONDO:0857072 breast carcinoma with choriocarcinomatous features NCIT:C40350 MONDO:equivalentTo Breast Carcinoma with Choriocarcinomatous Features An invasive ductal breast carcinoma, not otherwise specified, characterized by increased levels of human beta-chorionic gonadotropin in the serum. Morphologic evidence of choriocarcinomatous differentiation is rare. MONDO:0004953
MONDO:0857073 breast carcinoma with melanotic features NCIT:C40351 MONDO:equivalentTo Breast Carcinoma with Melanotic Features A very rare primary malignant tumor of the breast, characterized by an invasive breast carcinoma that co-exists with a melanoma component. The vast majority of melanotic tumors that affect the breast are metastatic melanomas that originate in extra-mammary sites. MONDO:0004953
MONDO:0857075 low grade breast adenosquamous carcinoma NCIT:C40362 MONDO:equivalentTo Low Grade Breast Adenosquamous Carcinoma A low grade metaplastic carcinoma of the breast with morphologic features similar to the adenosquamous carcinoma of the skin. In the majority of cases the prognosis is excellent. MONDO:0003548
MONDO:0857076 acute myeloid leukemia arising from previous myelodysplastic syndrome NCIT:C4037 MONDO:equivalentTo Acute Myeloid Leukemia Arising from Previous Myelodysplastic Syndrome An acute myeloid leukemia developing in patients with a prior history of myelodysplastic syndrome. MONDO:0019457
MONDO:0857078 postradiation breast angiosarcoma NCIT:C40378 MONDO:equivalentTo Postradiation Breast Angiosarcoma A malignant vascular neoplasm arising from the skin of the breast secondary to radiation treatment for breast cancer. MONDO:0003024
MONDO:0857080 salivary gland myoepithelial tumor NCIT:C40393 MONDO:equivalentTo Salivary Gland Myoepithelial Tumor A benign or malignant tumor that arises from the salivary glands. It is characterized by the presence of neoplastic cells with myoepithelial differentiation. This category includes benign myoepithelioma and myoepithelial carcinoma. MONDO:0002380
MONDO:0857083 breast soft tissue neoplasm NCIT:C40406 MONDO:equivalentTo Breast Soft Tissue Neoplasm A benign, intermediate, or malignant mesenchymal neoplasm that arises from the breast. MONDO:0006424
MONDO:0857084 breast pleomorphic adenoma NCIT:C40408 MONDO:equivalentTo Breast Pleomorphic Adenoma A rare, benign and well circumscribed neoplasm that arises from the breast. It is characterized by the proliferation of epithelial and myoepithelial cells surrounded by chondroid stroma. MONDO:0008401
MONDO:0857089 ovarian sex cord-stromal tumor associated with peutz-jeghers syndrome NCIT:C40436 MONDO:equivalentTo Ovarian Sex Cord-Stromal Tumor Associated with Peutz-Jeghers Syndrome A sex cord-stromal tumor that arises from the ovary in a patient diagnosed with Peutz-Jeghers syndrome. MONDO:0021657
MONDO:0857091 esophageal polyp NCIT:C4057 MONDO:equivalentTo Esophageal Polyp A benign intraluminal polypoid neoplasm of the esophagus. It includes the squamous papilloma and the giant fibrovascular polyp. MONDO:0021459
MONDO:0857095 polycythemia vera, polycythemic phase NCIT:C41232 MONDO:equivalentTo Polycythemia Vera, Polycythemic Phase Polycythemia vera characterized by the proliferation of the erythroid, granulocytic, and megakaryocytic lineages. The peripheral blood shows excess of red blood cells, neutrophilia, and thrombocytosis. The bone marrow is hypercellular for the patient's age. MONDO:0009891
MONDO:0857096 polycythemia vera, post-polycythemic myelofibrosis phase NCIT:C41233 MONDO:equivalentTo Polycythemia Vera, Post-Polycythemic Myelofibrosis Phase Progression of polycythemia vera characterized by decreased erythropoiesis and granulopoiesis, reticulin and collagen fibrosis of the bone marrow, leucoerythroblastic reaction in the peripheral blood, poikilocytosis, tear-drop shaped red blood cells, and splenomegaly. MONDO:0009891
MONDO:0857097 overt primary myelofibrosis NCIT:C41238 MONDO:equivalentTo Overt Primary Myelofibrosis Primary myelofibrosis characterized by reticulin or collagen fibrosis in the bone marrow. The bone marrow is usually normocellular or hypocellular. Myeloblasts account for less than 10% of the bone marrow cells. Atypical megakaryocytes are present. MONDO:0009692
MONDO:0857098 metastatic adenocarcinoma NCIT:C4124 MONDO:equivalentTo Metastatic Adenocarcinoma An adenocarcinoma that has spread from its original site of growth to another anatomic site. MONDO:0004970
MONDO:0857100 solid carcinoma NCIT:C4137 MONDO:equivalentTo Solid Carcinoma A carcinoma morphologically characterized by the presence of solid sheets of malignant epithelial cells in tissues. MONDO:0004993
MONDO:0857101 basophilic adenocarcinoma NCIT:C4150 MONDO:equivalentTo Basophilic Adenocarcinoma A malignant epithelial neoplasm of the anterior pituitary gland in which the neoplastic cells stain positive with basic dyes. MONDO:0004970
MONDO:0857102 juxtaglomerular cell tumor NCIT:C4162 MONDO:equivalentTo Juxtaglomerular Cell Tumor A benign, well circumscribed neoplasm arising from the cortex of the kidney. It secrets renin and the patients usually present with severe hypertension and marked hypokalemia. Morphologically, it is characterized by the presence of sheets of polygonal or spindle-shaped neoplastic cells forming a hemangiopericytic pattern. MONDO:0002513
MONDO:0857103 adrenal cortical compact cell adenoma NCIT:C4163 MONDO:equivalentTo Adrenal Cortical Compact Cell Adenoma An adenoma of the adrenal cortex composed of neoplastic compact cells with eosinophilic cytoplasm. MONDO:0003924
MONDO:0857104 pigmented adrenal cortical adenoma NCIT:C4164 MONDO:equivalentTo Pigmented Adrenal Cortical Adenoma A usually functioning adenoma of the adrenal cortex. Grossly, it has a dark brown appearance and is characterized by the presence of neoplastic cells containing abundant intracytoplasmic lipofuscin. It may be associated with Cushing syndrome. MONDO:0003924
MONDO:0857105 adrenal cortical clear cell adenoma NCIT:C4165 MONDO:equivalentTo Adrenal Cortical Clear Cell Adenoma An adenoma of the adrenal cortex composed of neoplastic clear cells containing intracytoplasmic lipid droplets. MONDO:0003924
MONDO:0857106 adrenal cortical glomerulosa cell adenoma NCIT:C4166 MONDO:equivalentTo Adrenal Cortical Glomerulosa Cell Adenoma An adenoma of the adrenal cortex composed of neoplastic cells with cytologic features of glomerulosa cells. MONDO:0003924
MONDO:0857107 adrenal cortical mixed cell adenoma NCIT:C4167 MONDO:equivalentTo Adrenal Cortical Mixed Cell Adenoma An adenoma of the adrenal cortex composed of a mixed neoplastic cellular population, including varying numbers of neoplastic clear and compact cells. MONDO:0003421
MONDO:0857109 papillary serous cystadenoma NCIT:C4180 MONDO:equivalentTo Papillary Serous Cystadenoma A serous benign or low malignant potential cystic epithelial neoplasm characterized by the presence of glandular epithelial cells forming papillary structures. MONDO:0005177
MONDO:0857110 serous surface papillary carcinoma NCIT:C4182 MONDO:equivalentTo Serous Surface Papillary Carcinoma An invasive serous adenocarcinoma arising from the ovary and rarely the peritoneum. Morphologically, it may be a well, moderately, or poorly differentiated neoplasm. It is characterized by a papillary growth pattern often associated with the presence of psammoma bodies. MONDO:0005278
MONDO:0857111 papillary mucinous cystadenoma NCIT:C4184 MONDO:equivalentTo Papillary Mucinous Cystadenoma A usually benign and less often low malignant potential cystic epithelial neoplasm composed of cells which contain intracytoplasmic mucin. It is characterized by the presence of papillary structures. MONDO:0021091
MONDO:0857112 gliomatosis cerebri type i NCIT:C41842 MONDO:equivalentTo Gliomatosis Cerebri Type I A classic form of gliomatosis cerebri. It is characterized by diffuse growth of neoplastic glial tissue without any focal mass. MONDO:0016683
MONDO:0857113 gliomatosis cerebri type ii NCIT:C41843 MONDO:equivalentTo Gliomatosis Cerebri Type II A classic form of gliomatosis cerebri. It is characterized by diffuse growth of neoplastic glial tissue without any focal mass. MONDO:0016683
MONDO:0857115 thyroid gland medullary carcinoma with amyloid stroma NCIT:C4193 MONDO:equivalentTo Thyroid Gland Medullary Carcinoma with Amyloid Stroma A medullary thyroid gland carcinoma characterized by the presence of amyloid stroma. The majority of medullary carcinomas of the thyroid gland are associated with amyloid deposits. The latter are highlighted with Congo red staining method. MONDO:0015277
MONDO:0857117 acinar cell neoplasm NCIT:C4197 MONDO:equivalentTo Acinar Cell Neoplasm A benign or malignant glandular epithelial neoplasm consisting of secretory cells forming acinar patterns. It includes the acinar cell adenoma and acinar cell carcinoma. MONDO:0024276
MONDO:0857118 ovarian luteinized thecoma NCIT:C4203 MONDO:equivalentTo Ovarian Luteinized Thecoma A variant of ovarian thecoma characterized by the presence of lutein cells. It is associated with a lower frequency of estrogenic manifestations compared to typical thecomas. In a minority of cases androgenic manifestations are present. MONDO:0037253
MONDO:0857119 undifferentiated neuroblastoma NCIT:C42046 MONDO:equivalentTo Undifferentiated Neuroblastoma A neuroblastoma characterized by the absence of differentiating neuroblasts. MONDO:0005072
MONDO:0857120 poorly differentiated neuroblastoma NCIT:C42047 MONDO:equivalentTo Poorly Differentiated Neuroblastoma A neuroblastoma in which the differentiating neuroblasts constitute less than five-percent of the tumor cells. MONDO:0005072
MONDO:0857121 malignant granulosa cell tumor NCIT:C4205 MONDO:equivalentTo Malignant Granulosa Cell Tumor A granulosa cell tumor which has an aggressive clinical course and metastasizes to other anatomic sites. MONDO:0006036
MONDO:0857122 maturing ganglioneuroma NCIT:C42064 MONDO:equivalentTo Maturing Ganglioneuroma A ganglioneuroma characterized by the presence of differentiating neuroblasts, maturing and mature ganglion cells. MONDO:0005033
MONDO:0857123 mature ganglioneuroma NCIT:C42065 MONDO:equivalentTo Mature Ganglioneuroma A ganglioneuroma characterized by the presence of mature ganglion cells and a mature Schwannian stroma. MONDO:0005033
MONDO:0857125 ovarian sex cord tumor with annular tubules NCIT:C4208 MONDO:equivalentTo Ovarian Sex Cord Tumor with Annular Tubules An ovarian sex cord-stromal tumor characterized by the presence of Sertoli cells forming annular tubules. It may be associated with Peutz-Jeghers syndrome. Cases associated with Peutz-Jeghers syndrome have followed a benign clinical course. Cases which are not associated with Peutz-Jeghers syndrome have been reported having a clinically malignant course. MONDO:0021657
MONDO:0857126 well differentiated ovarian sertoli-leydig cell tumor NCIT:C4209 MONDO:equivalentTo Well Differentiated Ovarian Sertoli-Leydig Cell Tumor A Sertoli-Leydig tumor of the ovary characterized by the presence of Sertoli cells in tubules without evidence of significant nuclear atypia or mitotic activity. Primitive gonadal stromal cells are not present. It usually follows a benign clinical course. MONDO:0036595
MONDO:0857127 poorly differentiated ovarian sertoli-leydig cell tumor NCIT:C4210 MONDO:equivalentTo Poorly Differentiated Ovarian Sertoli-Leydig Cell Tumor A Sertoli-Leydig tumor of the ovary characterized by the presence of a sarcomatoid stroma which contains primitive gonadal stromal cells. It may behave in a malignant fashion and metastasize to other anatomic sites. MONDO:0018172
MONDO:0857128 ovarian steroid cell tumor NCIT:C4215 MONDO:equivalentTo Ovarian Steroid Cell Tumor An ovarian tumor in which the vast majority of the cells (more than 90% of the tumor cells) resemble steroid hormone-secreting cells. It usually presents with androgenic manifestations. Approximately one-third of the cases follow a malignant clinical course. MONDO:0021657
MONDO:0857129 balloon cell nevus NCIT:C4226 MONDO:equivalentTo Balloon Cell Nevus An uncommon variant of melanocytic nevus. It presents as a small pigmented skin lesion. It is characterized by the presence of large melanocytes with clear, foamy or finely vacuolated cytoplasm. It may recur if it is not completely excised. MONDO:0044794
MONDO:0857130 regressing melanoma NCIT:C4228 MONDO:equivalentTo Regressing Melanoma A skin lesion characterized by the disappearance of the melanoma cells from the primary melanoma site. The disappearance of the malignant cells is associated with fibroplasia of the papillary dermis. According to some authors, complete regression of the primary melanoma may occur in 4-8% of patients. MONDO:0005105
MONDO:0857131 neuronevus NCIT:C4229 MONDO:equivalentTo Neuronevus An intradermal nevus characterized by the presence of nests of atrophic nevus cells which are hyalinized and resemble nerve bundles. MONDO:0006813
MONDO:0857132 junctional nevus NCIT:C4231 MONDO:equivalentTo Junctional Nevus A nevus characterized by the presence of an intraepidermal proliferation of nevus cells. The nevus cells form multiple nests in the dermal-epidermal junction. It presents as a small, slightly raised, pigmented skin lesion. MONDO:0005073
MONDO:0857133 melanoma in junctional nevus NCIT:C4232 MONDO:equivalentTo Melanoma in Junctional Nevus A melanoma arising from a melanocytic nevus which involves the dermal-epidermal junction of the skin. MONDO:0005012
MONDO:0857134 type a spindle cell melanoma NCIT:C4238 MONDO:equivalentTo Type A Spindle Cell Melanoma A melanoma characterized by the presence of malignant spindle-shaped melanocytes with slender nuclei and no visible nucleoli. Representative example is the type A spindle cell uveal melanoma. MONDO:0006427
MONDO:0857135 type b spindle cell melanoma NCIT:C4239 MONDO:equivalentTo Type B Spindle Cell Melanoma A melanoma characterized by the presence of malignant spindle-shaped melanocytes with larger nuclei and distinct nucleoli. Representative example is the type B spindle cell uveal melanoma. MONDO:0006427
MONDO:0857136 melanoma arising in blue nevus NCIT:C4240 MONDO:equivalentTo Melanoma Arising in Blue Nevus A rare melanoma which develops in a pre-existing blue nevus. It occurs more frequently on the scalp, face, orbit, back, buttocks, extremities, hands, and feet. MONDO:0005012
MONDO:0857137 cellular blue nevus NCIT:C4241 MONDO:equivalentTo Cellular Blue Nevus A blue nevus characterized by a multinodular cellular infiltrate with a dumb-bell architecture occupying the reticular dermis. The cellular infiltrate often extends into the subcutaneous tissue. The cellular infiltrate is composed of spindle-shaped melanocytes with pale cytoplasm alternating with bundles of pigmented spindle-shaped melanocytes. In occasional cases an increased mitotic activity, focal necrosis, and nuclear pleomorphism may be seen. Such cases with atypical features may have an uncertain malignant potential. MONDO:0006680
MONDO:0857138 fibrolipoma NCIT:C4249 MONDO:equivalentTo Fibrolipoma A benign well-circumscribed tumor composed of mature adipocytes, characterized by areas of abundant fibrous tissue. MONDO:0005106
MONDO:0857139 fibromyxolipoma NCIT:C4251 MONDO:equivalentTo Fibromyxolipoma A benign well-circumscribed tumor composed of mature adipocytes, characterized by areas of abundant fibrous tissue and extensive myxoid change. MONDO:0005106
MONDO:0857140 lipoblastomatosis NCIT:C4255 MONDO:equivalentTo Lipoblastomatosis A neoplastic process characterized by the presence of multiple lipoblastomas. MONDO:0044983
MONDO:0857141 sporadic retinoblastoma NCIT:C42596 MONDO:equivalentTo Sporadic Retinoblastoma A retinoblastoma that occurs in a patient without a family history of the disease. MONDO:0008380
MONDO:0857144 acute myelomonocytic leukemia without abnormal eosinophils NCIT:C42779 MONDO:equivalentTo Acute Myelomonocytic Leukemia without Abnormal Eosinophils Acute myelomonocytic leukemia without an abnormal eosinophilic component in the bone marrow. MONDO:0018871
MONDO:0857145 pericardial solitary fibrous tumor NCIT:C4281 MONDO:equivalentTo Pericardial Solitary Fibrous Tumor A localized neoplasm of probable fibroblastic derivation, that arises from the pericardium. It is characterized by the presence of round to spindle-shaped cells, hylanized stroma formation, thin-walled branching blood vessels, and thin bands of collagen. MONDO:0021381
MONDO:0857146 benign hemangiopericytoma NCIT:C4300 MONDO:equivalentTo Benign Hemangiopericytoma A hemangiopericytoma without malignant morphologic or clinical characteristics. MONDO:0005094
MONDO:0857147 benign odontogenic neoplasm NCIT:C4306 MONDO:equivalentTo Benign Odontogenic Neoplasm A benign, slow growing neoplasm arising from tooth-forming tissues. It occurs in the maxillofacial skeleton or the gingiva. Representative examples include adenomatoid odontogenic tumor, calcifying cystic odontogenic tumor, and squamous odontogenic tumor. MONDO:0021445
MONDO:0857152 pure cutaneous mastocytosis NCIT:C43277 MONDO:equivalentTo Pure Cutaneous Mastocytosis Mastocytosis that manifests with pure cutaneous involvement. MONDO:0019023
MONDO:0857155 germinative follicular epithelium neoplasm NCIT:C43311 MONDO:equivalentTo Germinative Follicular Epithelium Neoplasm A neoplasm involving the germinative follicular epithelium. MONDO:0003413
MONDO:0857156 adamantinoid trichoblastoma NCIT:C43312 MONDO:equivalentTo Adamantinoid Trichoblastoma A trichoblastoma characterized by the presence of neoplastic epithelial cell forming nodules. There are palisaded basaloid cells present at the periphery and pale larger cells with vesicular nuclei, prominent nucleoli, and abundant cytoplasm present at the center of the nodules. The epithelial cells are admixed with numerous small lymphocytes and occasional large multinucleated cells that resemble Reed-Sternberg cells. MONDO:0020593
MONDO:0857160 outer hair sheath and infundibulum neoplasm NCIT:C43324 MONDO:equivalentTo Outer Hair Sheath and Infundibulum Neoplasm A neoplasm involving the outer hair sheath and infundibulum. MONDO:0003413
MONDO:0857163 superficial epithelioma with sebaceous differentiation NCIT:C43334 MONDO:equivalentTo Superficial Epithelioma with Sebaceous Differentiation A benign epithelial neoplasm occurring in the head, neck or back region. It is characterized by proliferation of basaloid cells in the upper dermis with broad attachments to the epidermis. MONDO:0021490
MONDO:0857164 sebaceoma NCIT:C43336 MONDO:equivalentTo Sebaceoma A benign neoplasm characterized by sebaceous cell differentiation. It arises from the dermis and typically affects the face and neck. MONDO:0021490
MONDO:0857165 extraocular cutaneous sebaceous carcinoma NCIT:C43341 MONDO:equivalentTo Extraocular Cutaneous Sebaceous Carcinoma A rare variant of sebaceous carcinoma that does not affect the ocular region. MONDO:0006962
MONDO:0857166 apocrine hidrocystoma NCIT:C43342 MONDO:equivalentTo Apocrine Hidrocystoma A slow-growing, usually solitary, dome-shaped benign sweat gland adenoma, most frequently located on the eyelid. It is characterized by a cystic proliferation of apocrine glands. Surgical excision is curative. MONDO:0002804
MONDO:0857167 cylindrocarcinoma NCIT:C43344 MONDO:equivalentTo Cylindrocarcinoma A carcinoma that arises in a cylindroma. MONDO:0005524
MONDO:0857168 ductal eccrine carcinoma with spindle cell elements NCIT:C43346 MONDO:equivalentTo Ductal Eccrine Carcinoma with Spindle Cell Elements A variant of ductal eccrine carcinoma with spindled cell appearance. MONDO:0024245
MONDO:0857169 squamoid eccrine ductal carcinoma NCIT:C43347 MONDO:equivalentTo Squamoid Eccrine Ductal Carcinoma A variant of ductal eccrine carcinoma with squamoid metaplasia. MONDO:0024245
MONDO:0857170 ductal eccrine carcinoma with abundant fibromyxoid stroma NCIT:C43349 MONDO:equivalentTo Ductal Eccrine Carcinoma with Abundant Fibromyxoid Stroma A variant of ductal eccrine carcinoma with abundant fibromyxoid stroma. MONDO:0024245
MONDO:0857171 sporadic cylindroma NCIT:C43351 MONDO:equivalentTo Sporadic Cylindroma A cylindroma occurring as a solitary sporadic lesion. MONDO:0021812
MONDO:0857172 classic poroma NCIT:C43353 MONDO:equivalentTo Classic Poroma A poroma characterized by the presence of cords and aggregates of neoplastic cells in the superficial dermis in connection with the epidermis. MONDO:0006738
MONDO:0857173 porocarcinoma in situ NCIT:C43354 MONDO:equivalentTo Porocarcinoma In Situ A rare intraepidermal neoplasia that arises from the acrosyringial portion of the eccrine duct. MONDO:0006189
MONDO:0857174 aleukemic lymphoid leukemia NCIT:C4343 MONDO:equivalentTo Aleukemic Lymphoid Leukemia MONDO:0003730
MONDO:0857175 sporadic gastric adenocarcinoma NCIT:C43527 MONDO:equivalentTo Sporadic Gastric Adenocarcinoma A primary adenocarcinoma of the stomach in a patient with no family history of gastric cancer or inherited high risk mutations. MONDO:0005036
MONDO:0857177 small intestinal adenosquamous carcinoma NCIT:C43535 MONDO:equivalentTo Small Intestinal Adenosquamous Carcinoma A carcinoma that arises from the small intestine. It is composed of malignant glandular cells and malignant squamous cells. MONDO:0005522
MONDO:0857178 small intestinal mucinous adenocarcinoma NCIT:C43536 MONDO:equivalentTo Small Intestinal Mucinous Adenocarcinoma An invasive adenocarcinoma that arises from the small intestine. It is composed of malignant glandular cells which contain intracytoplasmic mucin. Often, the infiltrating glandular structures are associated with mucoid stromal formation. MONDO:0003198
MONDO:0857179 small intestinal medullary carcinoma NCIT:C43537 MONDO:equivalentTo Small Intestinal Medullary Carcinoma A carcinoma that arises from the small intestine. It is characterized by the presence of malignant epithelial cells with vesicular nucleus, distinct nucleolus, and abundant pink cytoplasm. MONDO:0005522
MONDO:0857180 small intestinal undifferentiated carcinoma NCIT:C43538 MONDO:equivalentTo Small Intestinal Undifferentiated Carcinoma A carcinoma that arises from the small intestine. It is composed of malignant epithelial cells which do not display evidence of glandular, squamous, or transitional cell differentiation. MONDO:0005522
MONDO:0857181 pituitary neuroendocrine tumor/microadenoma NCIT:C43541 MONDO:equivalentTo Pituitary Neuroendocrine Tumor/Microadenoma A pituitary neuroendocrine tumor with a diameter equal or less than 10 mm. MONDO:0006373
MONDO:0857182 pituitary neuroendocrine tumor/macroadenoma NCIT:C43542 MONDO:equivalentTo Pituitary Neuroendocrine Tumor/Macroadenoma A pituitary neuroendocrine tumor with a diameter greater than 10 mm. Clinical manifestations include headache, visual field disturbances, pituitary insufficiency, and mild hyperprolactinemia. MONDO:0006373
MONDO:0857183 small intestinal signet ring cell carcinoma NCIT:C43543 MONDO:equivalentTo Small Intestinal Signet Ring Cell Carcinoma An invasive adenocarcinoma that arises from the small intestine. It is characterized by the presence of malignant glandular cells in which the nucleus is pressed to one side by the presence of intracytoplasmic mucus. MONDO:0003198
MONDO:0857184 appendix tubular adenoma NCIT:C43546 MONDO:equivalentTo Appendix Tubular Adenoma An adenoma arising from the appendix. It is characterized by the presence of tubular epithelial structures and it is associated with dysplasia. MONDO:0006088
MONDO:0857185 appendix tubulovillous adenoma NCIT:C43547 MONDO:equivalentTo Appendix Tubulovillous Adenoma An adenoma arising from the appendix. It is characterized by the presence of tubular and villous epithelial structures and it is associated with dysplasia. MONDO:0006088
MONDO:0857187 eyelid squamous papilloma NCIT:C4355 MONDO:equivalentTo Eyelid Squamous Papilloma A papilloma that arises from the eyelid. It is composed of squamous cells and is characterized by the presence of an acanthotic epithelium with hyperkeratosis and papillary projections with an inner fibrovascular core. It is the most common benign epithelial tumor of eyelid. It usually affects middle-aged or older adults. MONDO:0001825
MONDO:0857188 small intestinal villous adenoma NCIT:C43551 MONDO:equivalentTo Small Intestinal Villous Adenoma A neoplasm that arises from the glandular epithelium of the small intestine. It is characterized by a villous architectural pattern. The neoplastic glandular cells have dysplastic features. MONDO:0000502
MONDO:0857189 appendix signet ring cell carcinoma NCIT:C43554 MONDO:equivalentTo Appendix Signet Ring Cell Carcinoma An adenocarcinoma arising from the appendix, characterized by the presence of signet-ring, mucin-producing malignant cells. The signet-ring cells constitute more than fifty-percent of the malignant cells. MONDO:0006087
MONDO:0857190 appendix undifferentiated carcinoma NCIT:C43556 MONDO:equivalentTo Appendix Undifferentiated Carcinoma A high grade carcinoma arising from the appendix, characterized by the absence of glandular or squamous differentiation. MONDO:0003196
MONDO:0857191 appendix mixed adenoneuroendocrine carcinoma NCIT:C43564 MONDO:equivalentTo Appendix Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the appendix. It is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0857192 appendix tubular carcinoid NCIT:C43565 MONDO:equivalentTo Appendix Tubular Carcinoid A neuroendocrine tumor that arises from the appendix. It does not show the morphologic characteristics of typical carcinoid tumors (neoplastic cells forming solid nests). In contrast, the tumor cells form small discrete tubules. MONDO:0015066
MONDO:0857194 rectosigmoid adenocarcinoma NCIT:C43584 MONDO:equivalentTo Rectosigmoid Adenocarcinoma An adenocarcinoma arising from the rectosigmoid area. It is more frequently seen in populations with a Western type diet and in patients with a history of chronic inflammatory bowel disease. Signs and symptoms include intestinal bleeding, anemia, and change in bowel habits. According to the degree of cellular differentiation, rectosigmoid adenocarcinomas are divided into well, moderately, and poorly differentiated. Histologic variants include mucinous adenocarcinoma, signet ring cell carcinoma, medullary carcinoma, serrated adenocarcinoma, cribriform comedo-type adenocarcinoma, and micropapillary adenocarcinoma. MONDO:0005008
MONDO:0857195 colorectal mucinous adenocarcinoma NCIT:C43585 MONDO:equivalentTo Colorectal Mucinous Adenocarcinoma An invasive colorectal adenocarcinoma characterized by the presence of extracellular mucin pools that contain malignant glandular epithelial structures. The extracellular mucin pools occupy more than 50% of the malignant lesion. MONDO:0005008
MONDO:0857196 colorectal undifferentiated carcinoma NCIT:C43591 MONDO:equivalentTo Colorectal Undifferentiated Carcinoma An invasive malignant epithelial tumor that arises from the colon or rectum. There is no morphologic, immunophenotypic, or molecular biological evidence of glandular or squamous differentiation. MONDO:0005617
MONDO:0857198 gallbladder adenocarcinoma, intestinal-type NCIT:C43604 MONDO:equivalentTo Gallbladder Adenocarcinoma, Intestinal-Type An adenocarcinoma that arises from the gallbladder. It is characterized by the presence of neoplastic tubular glands lined by columnar cells or neoplastic glands lined by goblet cells. MONDO:0006215
MONDO:0857199 gallbladder clear cell adenocarcinoma NCIT:C43605 MONDO:equivalentTo Gallbladder Clear Cell Adenocarcinoma A rare morphologic variant of gallbladder adenocarcinoma composed of malignant glandular epithelium with a predominance of glycogen rich clear cells. The cells display hyperchromic nuclei and well-defined cytoplasmic borders. MONDO:0006215
MONDO:0857200 gallbladder flat biliary intraepithelial neoplasia NCIT:C43607 MONDO:equivalentTo Gallbladder Flat Biliary Intraepithelial Neoplasia Biliary intraepithelial neoplasia that affects the gallbladder epithelium. It is characterized by the absence of intraluminal micropapillary projections. MONDO:0006218
MONDO:0857201 gallbladder papillary biliary intraepithelial neoplasia NCIT:C43609 MONDO:equivalentTo Gallbladder Papillary Biliary Intraepithelial Neoplasia Biliary intraepithelial neoplasia that affects the gallbladder epithelium. It is characterized by the presence of intraluminal micropapillary projections. MONDO:0006218
MONDO:0857202 pleomorphic hepatocellular carcinoma NCIT:C43625 MONDO:equivalentTo Pleomorphic Hepatocellular Carcinoma A morphologic variant of hepatocellular carcinoma, characterized by the presence of malignant cells which show marked variation in their size and shape. Bizarre mononuclear or multinucleated giant cells are often present. MONDO:0007256
MONDO:0857203 sarcomatoid hepatocellular carcinoma NCIT:C43627 MONDO:equivalentTo Sarcomatoid Hepatocellular Carcinoma A morphologic variant of hepatocellular carcinoma characterized by the presence of malignant spindle cells or atypical giant cells. MONDO:0007256
MONDO:0857206 accessory urethral gland neoplasm NCIT:C4378 MONDO:equivalentTo Accessory Urethral Gland Neoplasm A benign or malignant, primary or metastatic neoplasm affecting the accessory urethral gland. MONDO:0021239
MONDO:0857208 clear cell intrahepatic cholangiocarcinoma NCIT:C43848 MONDO:equivalentTo Clear Cell Intrahepatic Cholangiocarcinoma A morphologic variant of intrahepatic cholangiocarcinoma composed of malignant glandular epithelium, an abundant fibrous stroma, and the presence of clear cells. Clinical symptoms include abdominal pain, weight loss and malaise. MONDO:0005004
MONDO:0857210 anogenital papillomaviral intraepithelial neoplasia NCIT:C4394 MONDO:equivalentTo Anogenital Papillomaviral Intraepithelial Neoplasia MONDO:0024475
MONDO:0857211 posterior tongue neoplasm NCIT:C4400 MONDO:equivalentTo Posterior Tongue Neoplasm A benign or malignant neoplasm that affects the base of the tongue. MONDO:0021240
MONDO:0857212 pyriform fossa neoplasm NCIT:C4424 MONDO:equivalentTo Pyriform Fossa Neoplasm A benign or malignant neoplasm that affects the pyriform sinus. MONDO:0021358
MONDO:0857213 gastric pylorus carcinoma in situ ajcc v6 and v7 NCIT:C4431 MONDO:equivalentTo Gastric Pylorus Carcinoma In Situ AJCC v6 and v7 Stage 0 includes: Tis, N0, M0. Tis: Carcinoma in situ: intraepithelial tumor without invasion of the lamina propria. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0003971
MONDO:0857215 lung epithelioid hemangioendothelioma NCIT:C4453 MONDO:equivalentTo Lung Epithelioid Hemangioendothelioma A low-grade malignant blood vessel neoplasm arising from the lung. It is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma. MONDO:0008903
MONDO:0857216 dermal duct tumor NCIT:C4473 MONDO:equivalentTo Dermal Duct Tumor A poroma characterized by the presence of small nodules of neoplastic cells in the superficial dermis without connection to the epidermis. MONDO:0006738
MONDO:0857217 cutaneous neural neoplasm NCIT:C4479 MONDO:equivalentTo Cutaneous Neural Neoplasm A peripheral nervous system neoplasm that arises from the dermis. MONDO:0001406
MONDO:0857219 malignant skin hemangiopericytoma NCIT:C4493 MONDO:equivalentTo Malignant Skin Hemangiopericytoma A malignant hemangiopericytoma arising in the skin. MONDO:0021424
MONDO:0857220 cockade nevus NCIT:C4495 MONDO:equivalentTo Cockade Nevus A rare speckled nevus with concentric pattern of pigmentation and central papule surrounded by clear zone. MONDO:0044794
MONDO:0857222 common blue nevus NCIT:C4496 MONDO:equivalentTo Common Blue Nevus A blue nevus that is not associated with increased cellularity. MONDO:0006680
MONDO:0857223 nevus spilus NCIT:C4498 MONDO:equivalentTo Nevus Spilus A melanocytic nevus that contains a variable number of darkly pigmented macules and papules. MONDO:0044792
MONDO:0857224 benign ovarian epithelial tumor NCIT:C4510 MONDO:equivalentTo Benign Ovarian Epithelial Tumor A neoplasm that arises from the surface epithelium of the ovary and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. Representative examples include serous cystadenoma, mucinous cystadenoma, clear cell adenofibroma, and benign Brenner tumor. MONDO:0002229
MONDO:0857229 classical low grade fibromyxoid sarcoma NCIT:C45210 MONDO:equivalentTo Classical Low Grade Fibromyxoid Sarcoma A low grade fibromyxoid sarcoma that may have poorly formed collagen rosettes, but lacks prominent, well formed collagen rosettes. MONDO:0006272
MONDO:0857233 cutaneous hematopoietic and lymphoid cell neoplasm NCIT:C45240 MONDO:equivalentTo Cutaneous Hematopoietic and Lymphoid Cell Neoplasm A neoplasm of hematopoietic and lymphoid cell origin that affects the skin. MONDO:0002531
MONDO:0857240 lacrimal gland pleomorphic adenoma NCIT:C4542 MONDO:equivalentTo Lacrimal Gland Pleomorphic Adenoma A benign, usually encapsulated neoplasm of the lacrimal gland composed of epithelial and mesenchymal cells. Pleomorphic adenomas are neoplasms that develop in the salivary glands or heterotopic salivary gland tissues. It has been suggested that myoepithelial cells play a major role in the histogenesis of these tumors. In the lacrimal gland, pleomorphic adenomas presumably develop from metaplastic myoepithelial cells. MONDO:0008401
MONDO:0857244 orbit capillary hemangioma NCIT:C4545 MONDO:equivalentTo Orbit Capillary Hemangioma A capillary hemangioma arising from the orbit. MONDO:0001974
MONDO:0857245 orbit hemangiopericytoma NCIT:C4547 MONDO:equivalentTo Orbit Hemangiopericytoma A benign or malignant hemangiopericytoma arising from the orbit. MONDO:0005094
MONDO:0857247 lymphangioma circumscriptum NCIT:C45485 MONDO:equivalentTo Lymphangioma Circumscriptum A localized lymphangioma characterized by microcystic changes. MONDO:0002013
MONDO:0857248 lung squamous cell carcinoma, papillary variant NCIT:C45502 MONDO:equivalentTo Lung Squamous Cell Carcinoma, Papillary Variant A morphologic variant of squamous cell lung carcinoma characterized by the presence of papillary structures. MONDO:0005056
MONDO:0857249 lung squamous cell carcinoma, clear cell variant NCIT:C45503 MONDO:equivalentTo Lung Squamous Cell Carcinoma, Clear Cell Variant A morphologic variant of squamous cell lung carcinoma characterized by the presence of clear cells. MONDO:0005056
MONDO:0857250 lung squamous cell carcinoma, small cell variant NCIT:C45504 MONDO:equivalentTo Lung Squamous Cell Carcinoma, Small Cell Variant A poorly differentiated morphologic variant of squamous cell lung carcinoma characterized by the presence of small tumor cells with focal squamous differentiation. MONDO:0005056
MONDO:0857251 lung basaloid squamous cell carcinoma NCIT:C45507 MONDO:equivalentTo Lung Basaloid Squamous Cell Carcinoma A morphologic variant of squamous cell lung carcinoma characterized by nuclear palisading. MONDO:0003486
MONDO:0857252 lung spindle cell carcinoma NCIT:C45541 MONDO:equivalentTo Lung Spindle Cell Carcinoma A morphologic variant of sarcomatoid carcinoma characterized by the presence of malignant spindle cells and focal lymphoplasmacytic infiltrates. Adenocarcinoma cells, malignant squamous cells, and giant cells are not present. MONDO:0006279
MONDO:0857253 lung pleomorphic carcinoma NCIT:C45542 MONDO:equivalentTo Lung Pleomorphic Carcinoma A morphologic variant of sarcomatoid carcinoma characterized by the presence of malignant glandular or squamous cells associated with malignant giant and spindle cells. MONDO:0006279
MONDO:0857254 lung carcinosarcoma NCIT:C45543 MONDO:equivalentTo Lung Carcinosarcoma A morphologic variant of lung sarcomatoid carcinoma composed of a mixture of non-small cell lung carcinoma and a sarcomatous component. MONDO:0006279
MONDO:0857256 lung neuroendocrine tumor g2 NCIT:C45551 MONDO:equivalentTo Lung Neuroendocrine Tumor G2 A neuroendocrine tumor of the lung showing focal necrotic changes or a number of mitotic figures between 2 and 10/10 high power fields. MONDO:0006041
MONDO:0857259 ciliary body malignant medulloepithelioma NCIT:C4557 MONDO:equivalentTo Ciliary Body Malignant Medulloepithelioma A rare, unilateral, malignant embryonal neoplasm typically presenting as a ciliary body mass during childhood. It arises from primitive medullary epithelium. MONDO:0002969
MONDO:0857260 lung squamous papilloma NCIT:C45573 MONDO:equivalentTo Lung Squamous Papilloma A papillary neoplasm that arises endobronchially. It is characterized by the presence of a delicate fibrovascular core lined by stratified squamous epithelium. Squamous cell papillomas can be solitary or multiple. Patients usually present with signs and symptoms of bronchial obstruction. Because of the possibility of recurrence and reported cases of squamous cell carcinomas arising at the excision site of squamous cell papillomas, complete excision is indicated. MONDO:0006278
MONDO:0857262 bronchial glandular papilloma NCIT:C45601 MONDO:equivalentTo Bronchial Glandular Papilloma A benign papillary neoplasm that arises endobronchially. It is characterized by the presence of fibrovascular cores lined by columnar, cuboidal, and goblet cells. Patients usually present with signs and symptoms of bronchial obstruction. Complete resection is curative. MONDO:0006278
MONDO:0857263 bronchial mixed squamous cell and glandular papilloma NCIT:C45602 MONDO:equivalentTo Bronchial Mixed Squamous Cell and Glandular Papilloma An exceedingly rare benign endobronchial neoplasm characterized by the presence of fibrovascular cores which are lined by both squamous and glandular epithelium. Patients present with obstructive symptoms. Complete resection is curative. MONDO:0021043
MONDO:0857264 lung pleomorphic adenoma NCIT:C45603 MONDO:equivalentTo Lung Pleomorphic Adenoma A very rare, well circumscribed, benign epithelial neoplasm that arises from the bronchus. It is characterized by the presence of epithelial cells, myoepithelial cells, and fibromyxoid stroma. MONDO:0008401
MONDO:0857265 lung mucinous cystadenoma NCIT:C45604 MONDO:equivalentTo Lung Mucinous Cystadenoma A very rare, well circumscribed, benign cystic neoplasm that arises from the lung. It is characterized by the presence of cysts which are lined by tall mucinous epithelium and filled with mucin. MONDO:0003422
MONDO:0857267 lung soft tissue neoplasm NCIT:C45612 MONDO:equivalentTo Lung Soft Tissue Neoplasm A benign, intermediate, or malignant mesenchymal neoplasm that arises from the lung. MONDO:0006424
MONDO:0857268 malignant lung and pleural neoplasm NCIT:C45625 MONDO:equivalentTo Malignant Lung and Pleural Neoplasm A primary or metastatic malignant neoplasm that affects the lung and pleura. MONDO:0003274
MONDO:0857270 lung synovial sarcoma NCIT:C45631 MONDO:equivalentTo Lung Synovial Sarcoma A synovial sarcoma arising from the lungs. MONDO:0002426
MONDO:0857273 intrapulmonary thymoma NCIT:C45638 MONDO:equivalentTo Intrapulmonary Thymoma An epithelial neoplasm that arises from ectopic thymic tissue in the lung. Histologically it is identical to the thymomas that arise from the mediastinum. Signs and symptoms include cough, dyspnea, fever, and weight loss. Surgical excision is the recommended treatment. MONDO:0006456
MONDO:0857274 mediastinal thymoma NCIT:C45639 MONDO:equivalentTo Mediastinal Thymoma An invasive or non-invasive thymoma that arises from the mediastinum. Thymomas are the most common anterior mediastinal tumors. MONDO:0006456
MONDO:0857275 lung melanoma NCIT:C45652 MONDO:equivalentTo Lung Melanoma A rare malignant neoplasm that derives from melanocytes and arises from the lung in a patient with no history of previous melanoma and no evidence of melanoma in another site at the time of diagnosis. It usually presents as a solitary lesion and the prognosis is poor. MONDO:0006320
MONDO:0857276 pleural well differentiated papillary mesothelial tumor NCIT:C45660 MONDO:equivalentTo Pleural Well Differentiated Papillary Mesothelial Tumor A rare, non-invasive, localized or multifocal mesothelial neoplasm that arises from the pleura. It is characterized by the presence of papillae with myxoid fibrovascular cores, lined by a single layer of mesothelial cells. The clinical course is usually indolent. MONDO:0003308
MONDO:0857278 pleural lymphoma NCIT:C45687 MONDO:equivalentTo Pleural Lymphoma A rare extranodal lymphoma that arises from the pleura with no evidence of involvement of other sites at the time of diagnosis. This category includes primary effusion lymphoma and pyothorax-associated lymphoma. MONDO:0017207
MONDO:0857279 pleural epithelioid hemangioendothelioma NCIT:C45695 MONDO:equivalentTo Pleural Epithelioid Hemangioendothelioma A low-grade malignant blood vessel neoplasm arising from the pleura. It is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma. MONDO:0015523
MONDO:0857280 pleural synovial sarcoma NCIT:C45696 MONDO:equivalentTo Pleural Synovial Sarcoma A synovial sarcoma arising in the pleural cavity. MONDO:0006294
MONDO:0857282 micronodular thymoma with lymphoid stroma NCIT:C45706 MONDO:equivalentTo Micronodular Thymoma with Lymphoid Stroma A rare type of thymoma characterized by the presence of multiple, well formed epithelial nodules separated by a lymphocytic stroma that usually contains germinal centers. Reported cases have not been associated with recurrences or metastases. MONDO:0006456
MONDO:0857283 metaplastic thymoma NCIT:C45707 MONDO:equivalentTo Metaplastic Thymoma A rare type of well circumscribed or encapsulated thymoma with a biphasic architecture, consisting of epithelial cell islands and bundles of spindle cells. The vast majority of reported cases had a benign clinical course. MONDO:0006456
MONDO:0857284 microscopic thymoma NCIT:C45708 MONDO:equivalentTo Microscopic Thymoma A rare type of thymoma, composed of multifocal epithelial proliferations less than 1 mm in diameter. This type of thymoma usually occurs in myasthenia gravis patients without any macroscopic (gross) evidence of tumor. MONDO:0006456
MONDO:0857285 sclerosing thymoma NCIT:C45709 MONDO:equivalentTo Sclerosing Thymoma A rare type of thymoma, characterized by an exuberant amount of collagen-rich stroma. MONDO:0006456
MONDO:0857286 malignant respiratory system neoplasm NCIT:C4571 MONDO:equivalentTo Malignant Respiratory System Neoplasm A primary or metastatic malignant neoplasm that affects the lung parenchyma, bronchial tree, or trachea. Representative examples include lung carcinoma, carcinoid tumor, lung lymphoma, lung sarcoma, and tracheal carcinoma. MONDO:0020641
MONDO:0857287 thymus lipofibroadenoma NCIT:C45710 MONDO:equivalentTo Thymus Lipofibroadenoma A benign thymic tumor morphologically resembling fibroadenoma of the breast. MONDO:0021512
MONDO:0857289 combined thymic epithelial neoplasm NCIT:C45722 MONDO:equivalentTo Combined Thymic Epithelial Neoplasm A primary thymic epithelial neoplasm, characterized by the presence of at least two distinct areas, one representing a thymoma and the other a carcinoma. The most aggressive component usually determines the clinical outcome. MONDO:0018079
MONDO:0857290 malignant skin appendage neoplasm NCIT:C4573 MONDO:equivalentTo Malignant Skin Appendage Neoplasm A malignant neoplasm that arises from the skin appendages. MONDO:0002898
MONDO:0857291 mediastinal germ cell tumor with somatic-type malignancy NCIT:C45732 MONDO:equivalentTo Mediastinal Germ Cell Tumor with Somatic-Type Malignancy A rare extragonadal germ cell tumor that arises from the mediastinum and is associated with the presence of a somatic-type malignant component. The somatic malignancy is usually a sarcoma (e.g., embryonal rhabdomyosarcoma, angiosarcoma, or leiomyosarcoma), adenocarcinoma, squamous cell carcinoma, adenosquamous carcinoma, or primitive neuroectodermal tumor. The prognosis is poor. MONDO:0006298
MONDO:0857292 mediastinal t lymphoblastic leukemia/lymphoma NCIT:C45738 MONDO:equivalentTo Mediastinal T Lymphoblastic Leukemia/Lymphoma A precursor T-cell lymphoid neoplasm composed of small to medium-sized lymphoblasts that affects the mediastinum. MONDO:0003537
MONDO:0857294 mediastinal myeloid sarcoma NCIT:C45741 MONDO:equivalentTo Mediastinal Myeloid Sarcoma A mass-forming malignant neoplasm that arises from the mediastinum and is characterized by the proliferation of myeloblasts or immature myeloid cells. It may present in association with or precede acute myeloid leukemia, or it may be the first manifestation of relapse of acute myeloid leukemia. MONDO:0005843
MONDO:0857295 mediastinal paraganglioma NCIT:C45743 MONDO:equivalentTo Mediastinal Paraganglioma An extra-adrenal parasympathetic paraganglioma that arises from paraganglia in the mediastinum. Clinical signs and symptoms include chest pain, cough, hoarseness, and dysphagia. MONDO:0003098
MONDO:0857296 mediastinal solitary fibrous tumor NCIT:C45744 MONDO:equivalentTo Mediastinal Solitary Fibrous Tumor A localized neoplasm of probable fibroblastic derivation, that arises from the mediastinum. It is characterized by the presence of round to spindle-shaped cells, hylanized stroma formation, thin-walled branching blood vessels, and thin bands of collagen. MONDO:0016238
MONDO:0857297 adult cardiac cellular rhabdomyoma NCIT:C45747 MONDO:equivalentTo Adult Cardiac Cellular Rhabdomyoma A rare cardiac rhabdomyoma occurring in adults. It is characterized by the presence of neoplastic striated muscle cells with eosinophilic granular cytoplasm and increased cellularity. MONDO:0006123
MONDO:0857298 cardiac hemangioma NCIT:C45749 MONDO:equivalentTo Cardiac Hemangioma A hemangioma arising from the heart. MONDO:0021450
MONDO:0857300 cardiac inflammatory myofibroblastic tumor NCIT:C45753 MONDO:equivalentTo Cardiac Inflammatory Myofibroblastic Tumor An intermediate fibroblastic neoplasm arising from the heart. It is characterized by the presence of spindle-shaped fibroblasts and myofibroblasts, and a chronic inflammatory infiltrate composed of eosinophils, lymphocytes, and plasma cells. MONDO:0015798
MONDO:0857301 cystic tumor of the atrioventricular node NCIT:C45754 MONDO:equivalentTo Cystic Tumor of the Atrioventricular Node A multicystic tumor arising in the inferior interatrial septum in the region of the atrioventricular node. The vast majority of patients present with complete heart block and a minority with partial heart block. Sudden death is reported in approximately 10% of the cases. It is a morphologically benign tumor composed of cuboidal, transitional, or squamoid cells. The cells may also show sebaceous differentiation and originate from the endoderm. MONDO:0021450
MONDO:0857302 cardiac undifferentiated pleomorphic sarcoma NCIT:C45755 MONDO:equivalentTo Cardiac Undifferentiated Pleomorphic Sarcoma An undifferentiated pleomorphic sarcoma usually arising from the left atrium of the heart. It is characterized by the presence of fibrohistiocytic cells, giant cells, and spindle cells arrranged iin a storiform pattern. Clinical presentation includes signs and symptoms associated with left atrial hemodynamic changes. MONDO:0003354
MONDO:0857303 cardiac synovial sarcoma NCIT:C45756 MONDO:equivalentTo Cardiac Synovial Sarcoma A synovial sarcoma arising from the heart. MONDO:0003354
MONDO:0857305 cardiac rhabdomyosarcoma NCIT:C45759 MONDO:equivalentTo Cardiac Rhabdomyosarcoma A rare malignant mesenchymal tumor with skeletal muscle differentiation arising within the myocardium. It is characterized by the presence of small round spindle cells. Most cardiac rhabodomyosarcomas are of embryonal type and usually present in children and young adults. MONDO:0003354
MONDO:0857306 pericardial germ cell tumor NCIT:C45761 MONDO:equivalentTo Pericardial Germ Cell Tumor A rare benign or malignant germ cell tumor that arises from the pericardium. The reported cases have been teratomas and yolk sac tumors. MONDO:0021381
MONDO:0857308 corneal kaposi sarcoma NCIT:C4579 MONDO:equivalentTo Corneal Kaposi Sarcoma A Kaposi sarcoma arising from the cornea. MONDO:0005055
MONDO:0857310 metastatic malignant neoplasm in the bone marrow NCIT:C4582 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Bone Marrow The spread of a malignant neoplasm from its original site of growth to the bone marrow. MONDO:0024880
MONDO:0857311 pancreatic neuroendocrine microtumor NCIT:C45834 MONDO:equivalentTo Pancreatic Neuroendocrine Microtumor A non-functioning pancreatic neuroendocrine tumor measuring less than 0.5 cm in diameter. MONDO:0004334
MONDO:0857315 sellar gangliocytoma NCIT:C45917 MONDO:equivalentTo Sellar Gangliocytoma A tumor that arises in the sellar region and is characterized by the presence of mature ganglion cells and neuronal differentiation. It is often associated with the presence of pituitary neuroendocrine tumors/adenomas. MONDO:0016730
MONDO:0857316 hypothalamic gangliocytoma NCIT:C45918 MONDO:equivalentTo Hypothalamic Gangliocytoma A tumor characterized by the presence of mature ganglion cells and neuronal differentiation, arising in the hypothalamus. It is often associated with the presence of pituitary gland adenomas. Symptoms include acromegaly and precocious puberty. MONDO:0016730
MONDO:0857317 anterior pituitary gland neoplasm NCIT:C45921 MONDO:equivalentTo Anterior Pituitary Gland Neoplasm A neoplasm arising from the anterior lobe of the pituitary gland. The vast majority are pituitary neuroendocrine tumors (formerly pituitary adenomas). MONDO:0017611
MONDO:0857319 densely granulated somatotroph pituitary neuroendocrine tumor NCIT:C45925 MONDO:equivalentTo Densely Granulated Somatotroph Pituitary Neuroendocrine Tumor A growth hormone-producing pituitary neuroendocrine tumor composed of medium-sized acidophilic cells with granular cytoplasm and abundant secretory granules. MONDO:0006238
MONDO:0857320 sparsely granulated somatotroph pituitary neuroendocrine tumor NCIT:C45926 MONDO:equivalentTo Sparsely Granulated Somatotroph Pituitary Neuroendocrine Tumor A growth hormone-producing pituitary neuroendocrine tumor composed of small, round cells containing fibrous bodies and scarce, small secretory granules. MONDO:0006238
MONDO:0857321 densely granulated lactotroph pituitary neuroendocrine tumor NCIT:C45931 MONDO:equivalentTo Densely Granulated Lactotroph Pituitary Neuroendocrine Tumor A rare prolactin-producing pituitary neuroendocrine tumor composed of acidophilic cells with many large secretory granules. The endoplasmic reticulum is not as abundant as in the sparsely granulated subtype. MONDO:0010911
MONDO:0857322 sparsely granulated lactotroph pituitary neuroendocrine tumor NCIT:C45932 MONDO:equivalentTo Sparsely Granulated Lactotroph Pituitary Neuroendocrine Tumor A prolactin-producing pituitary neuroendocrine tumor composed of relatively large, chromophobic or slightly acidophilic cells with well developed, abundant endoplasmic reticulum, and many immature secretory granules. Mature secretory granules are sparse. MONDO:0010911
MONDO:0857324 benign palate neoplasm NCIT:C4599 MONDO:equivalentTo Benign Palate Neoplasm A non-metastasizing neoplasm that arises from the hard palate, soft palate, or uvula. MONDO:0005286
MONDO:0857325 thyroid gland oncocytic neoplasm NCIT:C46068 MONDO:equivalentTo Thyroid Gland Oncocytic Neoplasm An adenoma or carcinoma arising from the follicular cells of the thyroid gland. It is composed of large oncocytic cells with abundant granular eosinophilic cytoplasm. MONDO:0015074
MONDO:0857326 unilateral breast carcinoma NCIT:C46073 MONDO:equivalentTo Unilateral Breast Carcinoma Breast carcinoma of one breast, or one side of the breast. MONDO:0004989
MONDO:0857327 nonestrogen-dependent malignant neoplasm NCIT:C46080 MONDO:equivalentTo Nonestrogen-Dependent Malignant Neoplasm Cancer that is not dependent upon the presence of estrogen for metastasis or growth. 2005 MONDO:0004992
MONDO:0857330 macrofollicular variant thyroid gland papillary carcinoma NCIT:C46092 MONDO:equivalentTo Macrofollicular Variant Thyroid Gland Papillary Carcinoma A morphologic variant of papillary carcinoma of the thyroid gland characterized by the predominance or the exclusive presence of macrofollicles. Some of the malignant follicular cells display the nuclear features that characterize the papillary adenocarcinomas of the thyroid gland. MONDO:0005075
MONDO:0857331 clear cell variant thyroid gland papillary carcinoma NCIT:C46094 MONDO:equivalentTo Clear Cell Variant Thyroid Gland Papillary Carcinoma A morphologic variant of papillary carcinoma of the thyroid gland characterized by the predominance of malignant follicular clear cells. These cells have the nuclear features that characterize the papillary carcinomas of the thyroid gland. MONDO:0005075
MONDO:0857333 thyroid gland follicular carcinoma, clear cell variant NCIT:C46096 MONDO:equivalentTo Thyroid Gland Follicular Carcinoma, Clear Cell Variant A morphologic variant of follicular carcinoma of the thyroid gland characterized by the predominance of malignant follicular clear cells. These cells lack the nuclear features that characterize the papillary carcinomas of the thyroid gland. MONDO:0005034
MONDO:0857334 sporadic thyroid gland medullary carcinoma NCIT:C46098 MONDO:equivalentTo Sporadic Thyroid Gland Medullary Carcinoma A non-hereditary medullary carcinoma of the thyroid gland not associated with multiple endocrine neoplasia. The majority of thyroid gland medullary carcinomas are sporadic. MONDO:0015277
MONDO:0857336 thyroid gland mixed medullary and follicular cell-derived carcinoma NCIT:C46104 MONDO:equivalentTo Thyroid Gland Mixed Medullary and Follicular Cell-Derived Carcinoma A primary carcinoma of the thyroid gland containing a medullary carcinoma component that is immunohistochemically positive for calcitonin, and follicular cell-derived carcinoma component that is immunohistochemically positive for thyroglobulin. MONDO:0015075
MONDO:0857337 intrathyroid thymic carcinoma NCIT:C46106 MONDO:equivalentTo Intrathyroid Thymic Carcinoma A rare primary carcinoma of the thyroid gland, composed of groups of carcinoma cells with thymic epithelial differentiation. MONDO:0015075
MONDO:0857338 thyroid gland follicular adenoma with papillary hyperplasia NCIT:C46111 MONDO:equivalentTo Thyroid Gland Follicular Adenoma with Papillary Hyperplasia A thyroid gland adenoma characterized by the presence of papillae lined by cells that range from cuboidal to columnar. The papillae are usually cystic and non-branching. Aggregates of follicles may be found within the papillary structures. MONDO:0002533
MONDO:0857339 thyroid gland signet ring cell follicular adenoma NCIT:C46115 MONDO:equivalentTo Thyroid Gland Signet Ring Cell Follicular Adenoma A thyroid gland adenoma characterized by the presence of signet ring cells that stain positive for thyroglobulin. MONDO:0005032
MONDO:0857340 thyroid gland mucinous follicular adenoma NCIT:C46116 MONDO:equivalentTo Thyroid Gland Mucinous Follicular Adenoma A thyroid gland adenoma composed of follicles and characterized by the presence of abundant extracellular mucin. MONDO:0005032
MONDO:0857341 thyroid gland lipoadenoma NCIT:C46118 MONDO:equivalentTo Thyroid Gland Lipoadenoma A thyroid gland adenoma composed of follicular structures and mature adipocytes. MONDO:0003431
MONDO:0857342 thyroid gland clear cell follicular adenoma NCIT:C46119 MONDO:equivalentTo Thyroid Gland Clear Cell Follicular Adenoma A thyroid gland adenoma composed of follicular cells with cytoplasmic clearing. MONDO:0003426
MONDO:0857343 thyroid gland hyperfunctioning adenoma NCIT:C46122 MONDO:equivalentTo Thyroid Gland Hyperfunctioning Adenoma A thyroid gland adenoma producing thyroxin. It is associated with hyperthyroidism. Radioactive iodine scan reveals a hot nodule. MONDO:0005032
MONDO:0857345 thyroid gland paraganglioma NCIT:C46125 MONDO:equivalentTo Thyroid Gland Paraganglioma A rare, circumscribed or encapsulated neuroendocrine tumor arising from the thyroid gland. Microscopically, it is characterized by the presence of tumor cells arranged in a nesting (Zellballen) growth pattern. The reported cases have followed a benign clinical course. MONDO:0006239
MONDO:0857346 benign skin appendage neoplasm NCIT:C4615 MONDO:equivalentTo Benign Skin Appendage Neoplasm A neoplasm that arises from the hair follicles, sebaceous glands, or sweat glands. It is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. Representative examples include cylindroma, hidrocystoma, hidradenoma, and sebaceoma. MONDO:0021440
MONDO:0857349 pineal region germ cell tumor NCIT:C4659 MONDO:equivalentTo Pineal Region Germ Cell Tumor A germ cell tumor that arises in the pineal region. Representative examples include teratoma, germinoma, and choriocarcinoma. MONDO:0021232
MONDO:0857356 adenocarcinoma with metaplasia NCIT:C4712 MONDO:equivalentTo Adenocarcinoma with Metaplasia An adenocarcinoma characterized by the presence of metaplasia. MONDO:0004970
MONDO:0857357 atypical meningioma NCIT:C4723 MONDO:equivalentTo Atypical Meningioma A WHO grade II meningioma characterized by the presence of brain invasion and an increased mitotic activity, or at least three of the following morphologic features: small cells, high cellularity, prominent nucleoli, lack of architectural pattern, and necrosis. MONDO:0045056
MONDO:0857358 neoplasm by morphology NCIT:C4741 MONDO:equivalentTo Neoplasm by Morphology A classification system grouping neoplasms according to their cellular characteristics. MONDO:0005070
MONDO:0857359 benign squamous cell neoplasm NCIT:C4742 MONDO:equivalentTo Benign Squamous Cell Neoplasm A non-metastasizing neoplasm composed of squamous cells. The neoplastic cells do not display malignant features. MONDO:0036976
MONDO:0857360 skin cavernous hemangioma NCIT:C4750 MONDO:equivalentTo Skin Cavernous Hemangioma A cavernous hemangioma arising from the skin. MONDO:0003110
MONDO:0857361 malignant olfactory nerve neoplasm NCIT:C4768 MONDO:equivalentTo Malignant Olfactory Nerve Neoplasm A primary or metastatic malignant neoplasm affecting the olfactory nerve. MONDO:0002722
MONDO:0857362 benign extrahepatic bile duct neoplasm NCIT:C4776 MONDO:equivalentTo Benign Extrahepatic Bile Duct Neoplasm A neoplasm that arises from the extrahepatic bile ducts and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021385
MONDO:0857363 breast carcinoma with chondroid metaplasia NCIT:C47847 MONDO:equivalentTo Breast Carcinoma with Chondroid Metaplasia An invasive carcinoma of the breast showing differentiation towards cartilaginous structures. MONDO:0004274
MONDO:0857364 breast carcinoma with osseous metaplasia NCIT:C47848 MONDO:equivalentTo Breast Carcinoma with Osseous Metaplasia An invasive breast carcinoma showing differentiation towards bone structures. MONDO:0004274
MONDO:0857365 breast paget disease without invasive carcinoma NCIT:C47858 MONDO:equivalentTo Breast Paget Disease without Invasive Carcinoma Paget disease involving the skin overlying the mammary gland, without accompanying invasive ductal or lobular breast carcinoma. MONDO:0002648
MONDO:0857366 breast hyperplasia NCIT:C4804 MONDO:equivalentTo Breast Hyperplasia A general term that refers to hyperplastic proliferations of the epithelial cells in the breast parenchyma. Examples include atypical ductal hyperplasia, usual ductal hyperplasia, columnar cell hyperplasia, and atypical lobular hyperplasia. MONDO:0005043
MONDO:0857367 malignant odontogenic neoplasm NCIT:C4812 MONDO:equivalentTo Malignant Odontogenic Neoplasm A rare neoplasm arising from tooth-forming tissues. It occurs in the maxillofacial skeleton or the gingiva. Symptoms include swelling, pain, bleeding, mobility of affected teeth, and oral mucosa ulcerations. It may metastasize to lymph nodes and distant anatomic sites early. MONDO:0021192
MONDO:0857369 tongue carcinoma NCIT:C4824 MONDO:equivalentTo Tongue Carcinoma A malignant tumor arising from the epithelium that covers the tongue. The vast majority of tongue carcinomas are moderately or poorly differentiated squamous cell carcinomas. MONDO:0044925
MONDO:0857370 parathyroid gland lipoadenoma NCIT:C48283 MONDO:equivalentTo Parathyroid Gland Lipoadenoma A parathyroid gland adenoma that contains mature adipocytes. MONDO:0003431
MONDO:0857371 atypical parathyroid gland tumor NCIT:C48285 MONDO:equivalentTo Atypical Parathyroid Gland Tumor A parathyroid gland tumor that shares certain morphologic characteristics with parathyroid gland carcinomas (e.g. broad fibrous bands formation with or without hemosiderin deposition, presence of mitotic figures) but lacks unequivocal evidence of capsular or vascular invasion. It is considered a tumor of uncertain malignant potential. (WHO) MONDO:0021360
MONDO:0857375 non-metastatic paraganglioma NCIT:C48314 MONDO:equivalentTo Non-Metastatic Paraganglioma A paraganglioma that is confined to the site of origin. MONDO:0000448
MONDO:0857376 nasopharyngeal paraganglioma NCIT:C48316 MONDO:equivalentTo Nasopharyngeal Paraganglioma An extra-adrenal paraganglioma arising from the nasopharynx and nose. Epistaxis or nasal obstruction are common presenting symptoms. MONDO:0006239
MONDO:0857377 primary bone osteosarcoma NCIT:C4834 MONDO:equivalentTo Primary Bone Osteosarcoma A usually aggressive malignant bone-forming mesenchymal neoplasm arising from the bone. It usually involves the long bones and predominantly affects adolescents and young adults. Pain and a palpable mass are the most frequent clinical sign and symptom. It may spread to other anatomic sites, particularly the lungs. MONDO:0002629
MONDO:0857378 adrenal cortical oncocytic adenoma NCIT:C48447 MONDO:equivalentTo Adrenal Cortical Oncocytic Adenoma A usually non-functioning variant of adrenal cortex adenoma, composed of large cells with abundant granular eosinophilic cytoplasm. MONDO:0003924
MONDO:0857379 androgen-producing adrenal cortical adenoma NCIT:C48454 MONDO:equivalentTo Androgen-Producing Adrenal Cortical Adenoma A rare adenoma of the adrenal cortex that produces androgens. Female patients usually have symptoms related to virilism. MONDO:0006408
MONDO:0857380 estrogen-producing adrenal cortical adenoma NCIT:C48456 MONDO:equivalentTo Estrogen-Producing Adrenal Cortical Adenoma A rare adenoma of the adrenal cortex that produces estrogens. Male patients may develop gynecomastia and impotence. MONDO:0006408
MONDO:0857382 invasive prostate carcinoma NCIT:C48596 MONDO:equivalentTo Invasive Prostate Carcinoma A carcinoma that is not confined to the prostatic epithelium but has spread to the surrounding stroma of the prostate gland. The vast majority of invasive prostate carcinomas are adenocarcinomas. MONDO:0005159
MONDO:0857383 minimal deviation melanoma NCIT:C48612 MONDO:equivalentTo Minimal Deviation Melanoma A melanocytic neoplasm displaying morphologic features that are intermediate between those of benign nevus and melanoma. It is characterized by a nodular architectural growth resembling a melanoma, and a loss of nevus cell maturation. The melanocytic cells forming the nodular growth are uniform, and they may display a high mitotic rate, but they do not show cytologic atypia. MONDO:0005012
MONDO:0857384 melanoma arising in congenital melanocytic nevus NCIT:C48613 MONDO:equivalentTo Melanoma Arising in Congenital Melanocytic Nevus A melanoma of the skin arising in a congenital melanocytic nevus. MONDO:0005012
MONDO:0857385 desmoplastic neurotropic melanoma NCIT:C48614 MONDO:equivalentTo Desmoplastic Neurotropic Melanoma A desmoplastic melanoma characterized by the presence of nerve infiltration by atypical spindled melanocytes. MONDO:0044785
MONDO:0857386 mucosal lentiginous melanoma NCIT:C48622 MONDO:equivalentTo Mucosal Lentiginous Melanoma An acral lentiginous melanoma affecting mucosal surfaces. MONDO:0000544
MONDO:0857388 metastatic malignant neoplasm in the trachea NCIT:C4887 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Trachea A malignant neoplasm that has spread to the trachea from another anatomic site. MONDO:0024880
MONDO:0857389 splenic lymphoma NCIT:C48873 MONDO:equivalentTo Splenic Lymphoma A non-Hodgkin lymphoma or rarely Hodgkin lymphoma that arises from the spleen. MONDO:0017207
MONDO:0857390 dedifferentiated chordoma NCIT:C48876 MONDO:equivalentTo Dedifferentiated Chordoma A high-grade malignant bone tumor arising from the remnants of the notochord. It is characterized by a lobulated growth pattern, myxoid stroma formation, the presence of physaliphorous cells, and a sarcomatous component. MONDO:0008978
MONDO:0857391 benign lung hilum neoplasm NCIT:C4888 MONDO:equivalentTo Benign Lung Hilum Neoplasm A neoplasm that arises from the hilar region of lung and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0003639
MONDO:0857393 hiv lipodystrophy NCIT:C48899 MONDO:equivalentTo HIV Lipodystrophy A neoplastic process characterized by a diffuse poorly circumscribed overgrowth of adipose tissue in the breast and cervical areas, and an accumulation of visceral fat. It is associated with antiretroviral therapy. Clinical presentation includes hyperlipidemia, insulin resistance, and fat atrophy of the face and limbs. MONDO:0006573
MONDO:0857394 gardner fibroma NCIT:C49017 MONDO:equivalentTo Gardner Fibroma An uncommon, poorly circumscribed, benign neoplasm arising in the soft tissues of infants, children and adolescents. It is characterized by the presence of haphazardly arranged spindle-shaped fibroblasts, collagenous stroma formation, and plaque-like growth pattern. There is a strong genetic component associating the neoplasm with Gardners syndrome and deep fibromatosis/desmoid tumor. MONDO:0005167
MONDO:0857397 skin fibrous histiocytoma, fibroblastic variant NCIT:C49076 MONDO:equivalentTo Skin Fibrous Histiocytoma, Fibroblastic Variant A morphologic variant of fibrous histiocytoma of the skin. It is characterized by the presence of spindle-shaped fibrohistiocytic cells and associated acanthosis. MONDO:0006717
MONDO:0857398 skin fibrous histiocytoma, histiocytic variant NCIT:C49077 MONDO:equivalentTo Skin Fibrous Histiocytoma, Histiocytic Variant A morphologic variant of fibrous histiocytoma of the skin. It is characterized by the presence of xanthomatous fibrohistiocytic cells, giant cells, and hemosiderin deposition. MONDO:0006717
MONDO:0857399 skin fibrous histiocytoma, cellular variant NCIT:C49078 MONDO:equivalentTo Skin Fibrous Histiocytoma, Cellular Variant A morphologic variant of fibrous histiocytoma of the skin. It is characterized by the presence of spindle-shaped fibrohistiocytic cells and increased cellularity. MONDO:0006717
MONDO:0857400 skin fibrous histiocytoma, epithelioid variant NCIT:C49079 MONDO:equivalentTo Skin Fibrous Histiocytoma, Epithelioid Variant A morphologic variant of fibrous histiocytoma of the skin. It is characterized by the presence of epithelioid fibrohistiocytic cells. MONDO:0006717
MONDO:0857401 solid angioleiomyoma NCIT:C49110 MONDO:equivalentTo Solid Angioleiomyoma A morphologic variant of angioleiomyoma characterized by the presence of numerous small, slit-like vascular channels. MONDO:0006646
MONDO:0857402 venous angioleiomyoma NCIT:C49111 MONDO:equivalentTo Venous Angioleiomyoma A morphologic variant of angioleiomyoma characterized by the presence of thick-walled veins. MONDO:0006646
MONDO:0857403 cavernous angioleiomyoma NCIT:C49115 MONDO:equivalentTo Cavernous Angioleiomyoma A morphologic variant of angioleiomyoma characterized by the presence of markedly dilated vascular channels. MONDO:0006646
MONDO:0857404 conventional cardiac rhabdomyoma NCIT:C49179 MONDO:equivalentTo Conventional Cardiac Rhabdomyoma A cardiac rhabdomyoma characterized by the presence of neoplastic large striated muscle cells with clear cytoplasm and spider cells. MONDO:0006123
MONDO:0857405 anaplastic embryonal rhabdomyosarcoma NCIT:C49204 MONDO:equivalentTo Anaplastic Embryonal Rhabdomyosarcoma A morphologic variant of embryonal rhabdomyosarcoma. It is characterized by the presence of large hyperchromatic and anaplastic cells. MONDO:0009993
MONDO:0857407 duodenal adenoma NCIT:C4932 MONDO:equivalentTo Duodenal Adenoma A circumscribed neoplasm that arises from the glandular epithelium of the duodenum. Morphologically, it is characterized by a proliferation of neoplastic glandular cells and it is associated with dysplasia. According to the growth pattern, it may be classified as tubular, villous, or tubulovillous. MONDO:0021303
MONDO:0857409 benign lymphoproliferative disorder NCIT:C4939 MONDO:equivalentTo Benign Lymphoproliferative Disorder A proliferation of lymphocytes without atypia seen in infections, hypersensitivity reactions or autoimmune diseases.
MONDO:0857412 intracranial neoplasm NCIT:C4953 MONDO:equivalentTo Intracranial Neoplasm A benign or malignant neoplasm that arises from or metastasizes to structures within the cranium. This includes meningeal and other tumors that occur in the spaces that surround the brain, and neoplasms of the brain. MONDO:0006130
MONDO:0857413 leptomeningeal neoplasm NCIT:C4958 MONDO:equivalentTo Leptomeningeal Neoplasm A malignant neoplasm that has spread from its original site to the two innermost layers of tissue that cover the brain and spinal cord. MONDO:0016743
MONDO:0857415 benign infratentorial neoplasm NCIT:C4965 MONDO:equivalentTo Benign Infratentorial Neoplasm A neoplasm that arises from the infratentorial region and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021451
MONDO:0857417 primary brain stem neoplasm NCIT:C4975 MONDO:equivalentTo Primary Brain Stem Neoplasm A neoplasm that originates from the brain stem. MONDO:0021228
MONDO:0857419 carcinoma unspecified site NCIT:C4979 MONDO:equivalentTo Carcinoma Unspecified Site Carcinoma in which the site of involvement is not specified. MONDO:0004993
MONDO:0857430 verrucous lesion NCIT:C5028 MONDO:equivalentTo Verrucous Lesion A papillomavirus related epithelial overgrowth. It can be located anywhere on the body though when it involves the perineal region it is generally referred to as condyloma acuminatum. MONDO:0002532
MONDO:0857438 primary cerebral diffuse large b-cell lymphoma NCIT:C5054 MONDO:equivalentTo Primary Cerebral Diffuse Large B-Cell Lymphoma A diffuse large B-cell lymphoma that arises in the cerebrum. MONDO:0003655
MONDO:0857466 renomedullary interstitial cell tumor NCIT:C5100 MONDO:equivalentTo Renomedullary Interstitial Cell Tumor A benign, asymptomatic kidney tumor arising from renomedullary interstitial cells. It is often found incidentally at the time of nephrectomy in adults. These tumors are either single or multiple and usually measure 1-10 mm in diameter. Microscopically the tumor cells are small, stellate, or spindled cells, embedded in a faintly basophilic stroma reminiscent of renal medullary stroma. (WHO 2016) MONDO:0002513
MONDO:0857469 solid glomus tumor NCIT:C51133 MONDO:equivalentTo Solid Glomus Tumor The most common morphologic variant of glomus tumor. It is characterized by the presence of a nest of glomus cells surrounding capillary sized vessels. MONDO:0018327
MONDO:0857473 adult central nervous system neoplasm NCIT:C5131 MONDO:equivalentTo Adult Central Nervous System Neoplasm A benign or malignant neoplasm of the brain, spinal cord, or meninges occurring in adults. Representative examples of primary neoplasms include astrocytoma, meningioma, pituitary adenoma, and neurilemoma. Representative examples of tumor metastases from other organs to the central nervous system include lung and breast carcinoma. MONDO:0006130
MONDO:0857476 breast ductal carcinoma in situ, non-comedo type NCIT:C5137 MONDO:equivalentTo Breast Ductal Carcinoma In Situ, Non-Comedo Type Breast ductal carcinoma in situ characterized by the presence of sheets of tumor cells without evidence of central necrosis or cell death. MONDO:0005023
MONDO:0857477 invasive breast cribriform carcinoma NCIT:C5142 MONDO:equivalentTo Invasive Breast Cribriform Carcinoma An invasive adenocarcinoma of the breast with a favorable clinical outcome, characterized by the presence of a sieve-like or cribriform infiltrating pattern. MONDO:0004988
MONDO:0857478 malignant breast adenomyoepithelioma NCIT:C5143 MONDO:equivalentTo Malignant Breast Adenomyoepithelioma An adenomyoepithelioma of the breast in which the epithelial, myoepithelial, or both components have undergone malignant transformation. Such cases may follow an aggressive clinical course, including recurrences and local and distant metastases. MONDO:0002066
MONDO:0857479 infratentorial glioblastoma NCIT:C5148 MONDO:equivalentTo Infratentorial Glioblastoma A glioblastoma that occurs in the infratentorial region. MONDO:0003107
MONDO:0857480 supratentorial glioblastoma NCIT:C5149 MONDO:equivalentTo Supratentorial Glioblastoma A glioblastoma that occurs in the supratentorial region. MONDO:0002071
MONDO:0857482 breast high grade mucoepidermoid carcinoma NCIT:C5167 MONDO:equivalentTo Breast High Grade Mucoepidermoid Carcinoma An aggressive mucoepidermoid carcinoma that arises from the breast. It is characterized by the presence of focal necrosis and high mitotic activity. Lymph node and distant metastases are common. The prognosis is usually poor. MONDO:0003087
MONDO:0857483 breast low grade mucoepidermoid carcinoma NCIT:C5168 MONDO:equivalentTo Breast Low Grade Mucoepidermoid Carcinoma A slow growing mucoepidermoid carcinoma that arises from the breast. It is characterized by the presence of keratinization in the neoplastic squamous cells and lumina formation by glandular neoplastic cells. Complete excision may be curative. MONDO:0003087
MONDO:0857486 breast non-hodgkin lymphoma NCIT:C5181 MONDO:equivalentTo Breast Non-Hodgkin Lymphoma A non-Hodgkin lymphoma that arises from the breast. There is no history of extramammary breast non-Hodgkin lymphoma and ipsilateral axillary lymph node involvement does not exclude the diagnosis of primary breast non-Hodgkin lymphoma. Most patients present with a painless breast lump. The vast majority of cases are B-cell non-Hodgkin lymphomas. Diffuse large B-cell lymphoma, follicular lymphoma, and extranodal marginal zone B-cell lymphoma of mucosa associated lymphoid tissue are the most common types of primary non-Hodgkin lymphoma of the breast. MONDO:0018908
MONDO:0857487 breast complex fibroadenoma NCIT:C5194 MONDO:equivalentTo Breast Complex Fibroadenoma A breast fibroadenoma that displays fibrocystic changes including apocrine metaplasia, sclerosing adenosis, and cyst formation. MONDO:0002056
MONDO:0857488 benign nipple neoplasm NCIT:C5197 MONDO:equivalentTo Benign Nipple Neoplasm A neoplasm that arises from the nipple and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0000620
MONDO:0857490 breast papillary neoplasm NCIT:C5206 MONDO:equivalentTo Breast Papillary Neoplasm A benign or malignant papillary neoplasm that arises from the breast. It is characterized by the presence of epithelial proliferations that are supported by fibrovascular cores. Representative examples are intraductal papilloma and papillary carcinoma. MONDO:0021100
MONDO:0857492 malignant nipple neoplasm NCIT:C5213 MONDO:equivalentTo Malignant Nipple Neoplasm A malignant neoplasm that affects the area of the nipple. MONDO:0007254
MONDO:0857493 benign ovarian thecoma NCIT:C5219 MONDO:equivalentTo Benign Ovarian Thecoma A thecoma of the ovary that does not metastasize to other anatomic sites. MONDO:0024387
MONDO:0857496 ovarian soft tissue neoplasm NCIT:C5244 MONDO:equivalentTo Ovarian Soft Tissue Neoplasm A benign, intermediate, or malignant mesenchymal neoplasm of the ovary. Representative examples include leiomyoma, myxoma, and sarcoma. MONDO:0006424
MONDO:0857498 gastric burkitt lymphoma NCIT:C5251 MONDO:equivalentTo Gastric Burkitt Lymphoma An extranodal Burkitt lymphoma that arises from the stomach with the bulk of the mass located in the stomach. MONDO:0042493
MONDO:0857499 gastric t-cell non-hodgkin lymphoma NCIT:C5254 MONDO:equivalentTo Gastric T-Cell Non-Hodgkin Lymphoma A rare, extranodal T-cell non-Hodgkin lymphoma that arises from the stomach with the bulk of the mass located in the stomach. MONDO:0042493
MONDO:0857502 deletion of the short arm of chromosome 1 (1p) associated meningioma NCIT:C5294 MONDO:equivalentTo Deletion of the Short Arm of Chromosome 1 (1p) Associated Meningioma A meningioma that is associated with deletion of chromosomal arm 1p. MONDO:0016642
MONDO:0857503 deletion of chromosome 22 associated meningioma NCIT:C5305 MONDO:equivalentTo Deletion of Chromosome 22 Associated Meningioma A meningioma that is associated with deletion of chromosome 22. This abnormality is the most consistent cytogenetic finding that is detected in meningiomas. MONDO:0016642
MONDO:0857504 deletion of chromosome 3p associated meningioma NCIT:C5306 MONDO:equivalentTo Deletion of Chromosome 3p Associated Meningioma A meningioma that is associated with deletion of chromosomal arm 3p. MONDO:0016642
MONDO:0857507 extra-adrenal retroperitoneal paraganglioma NCIT:C5328 MONDO:equivalentTo Extra-Adrenal Retroperitoneal Paraganglioma A sympathetic paraganglioma arising from the retroperitoneum, outside the adrenal gland. MONDO:0024645
MONDO:0857508 hereditary paraganglioma NCIT:C5329 MONDO:equivalentTo Hereditary Paraganglioma A hereditary neoplasm arising from paraganglia. The majority of cases (up to 80%) are multifocal. It is caused by mutations in SDHA, SDHB, SDHC, SDHD, and SDHAF2 genes. MONDO:0000448
MONDO:0857513 great vessel neoplasm NCIT:C5348 MONDO:equivalentTo Great Vessel Neoplasm A neoplasm involving a great vessel. MONDO:0024757
MONDO:0857514 mesenchymal chondrosarcoma of bone NCIT:C53493 MONDO:equivalentTo Mesenchymal Chondrosarcoma of Bone A morphologic variant of chondrosarcoma arising from the bone. It is characterized by the presence of malignant small round cells, biphasic growth pattern, and well differentiated hyaline cartilage. Clinical presentation includes pain and swelling. The clinical course is aggressive, with local recurrences and distant metastases. MONDO:0021054
MONDO:0857518 cardiac schwannoma NCIT:C5358 MONDO:equivalentTo Cardiac Schwannoma A benign peripheral nervous system neoplasm that is composed of well-differentiated Schwann cells and affects the heart. MONDO:0021450
MONDO:0857519 cardiac epithelioid hemangioendothelioma NCIT:C5362 MONDO:equivalentTo Cardiac Epithelioid Hemangioendothelioma A low-grade malignant blood vessel neoplasm, arising from the heart. IIt is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma. MONDO:0015523
MONDO:0857520 cardiac kaposi sarcoma NCIT:C5363 MONDO:equivalentTo Cardiac Kaposi Sarcoma A Kaposi sarcoma arising from the heart. MONDO:0005055
MONDO:0857524 cardiac myeloid sarcoma NCIT:C5370 MONDO:equivalentTo Cardiac Myeloid Sarcoma A rare extramedullary myeloid tumor that arises from the heart. It may present in association with or as a site of relapse of acute myeloid leukemia. Rare cases of myeloid sarcoma of the heart preceding acute myeloid leukemia have also been reported. MONDO:0001340
MONDO:0857525 secondary osteosarcoma NCIT:C53704 MONDO:equivalentTo Secondary Osteosarcoma An osteosarcoma arising from a pre-existing lesion of the bone, usually Paget disease, or due to radiation therapy. MONDO:0002629
MONDO:0857526 malignant inferior vena cava neoplasm NCIT:C5377 MONDO:equivalentTo Malignant Inferior Vena Cava Neoplasm A malignant neoplasm involving the inferior vena cava. MONDO:0040676
MONDO:0857527 malignant superior vena cava neoplasm NCIT:C5379 MONDO:equivalentTo Malignant Superior Vena Cava Neoplasm A malignant neoplasm involving the superior vena cava. MONDO:0040676
MONDO:0857528 malignant pulmonary artery neoplasm NCIT:C5380 MONDO:equivalentTo Malignant Pulmonary Artery Neoplasm A malignant neoplasm involving the pulmonary artery. MONDO:0040676
MONDO:0857529 malignant pulmonary vein neoplasm NCIT:C5383 MONDO:equivalentTo Malignant Pulmonary Vein Neoplasm A malignant neoplasm involving the pulmonary vein. MONDO:0040676
MONDO:0857532 leiomyosarcoma of vessels NCIT:C5387 MONDO:equivalentTo Leiomyosarcoma of Vessels An aggressive malignant smooth muscle neoplasm, arising from the walls of the vascular system. It is characterized by a proliferation of neoplastic spindle cells. MONDO:0005058
MONDO:0857533 benign atrial neoplasm NCIT:C5389 MONDO:equivalentTo Benign Atrial Neoplasm A neoplasm that arises from the right or left atrium and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021450
MONDO:0857535 solitary adult fibroma NCIT:C5394 MONDO:equivalentTo Solitary Adult Fibroma A solitary benign neoplasm arising from the fibrous soft tissues. The tumor is characterized by the presence of spindle-shaped fibroblasts. MONDO:0005167
MONDO:0857536 fibrous histiocytoma of bone NCIT:C53963 MONDO:equivalentTo Fibrous Histiocytoma of Bone A rare, benign neoplasm usually arising from the non-metaphyseal regions of long bones or pelvis. It is characterized by the presence of fibroblastic spindle cells arranged in a whorled storiform pattern, osteoclast-like giant cells, foam cells, inflammatory cells, hemosiderin deposition and stromal hemorrhage. MONDO:0000631
MONDO:0857537 bone leiomyoma NCIT:C53964 MONDO:equivalentTo Bone Leiomyoma A rare leiomyoma affecting the bone. MONDO:0001572
MONDO:0857542 benign gastrointestinal stromal tumor NCIT:C53998 MONDO:equivalentTo Benign Gastrointestinal Stromal Tumor A gastrointestinal stromal tumor that is characterized by a maximum diameter equal or less than 5 cm (gastric localization), or equal or less than 2 cm (intestinal localization) and no more than 5 mitotic figures per 50 high power fields. MONDO:0044335
MONDO:0857543 malignant gastrointestinal stromal tumor NCIT:C53999 MONDO:equivalentTo Malignant Gastrointestinal Stromal Tumor A gastrointestinal stromal tumor that is characterized by large size (diameter greater than 10 cm for gastric localization and greater than 5 cm for intestinal localization) or more than 5 mitotic figures per 50 high power fields. MONDO:0011719
MONDO:0857546 region 17p13 allelic loss associated medulloblastoma NCIT:C5402 MONDO:equivalentTo Region 17p13 Allelic Loss Associated Medulloblastoma A medulloblastoma characterized by the loss of one of the p13 regions of chromosome 17. Loss of genetic material of chromosome arm 17p is the most common molecular genetic abnormality found in medulloblastomas. MONDO:0007959
MONDO:0857547 nevoid basal cell carcinoma syndrome associated medulloblastoma NCIT:C5405 MONDO:equivalentTo Nevoid Basal Cell Carcinoma Syndrome Associated Medulloblastoma A medulloblastoma developing in patients with multiple basal cell carcinomas. It is observed in patients with nevoid basal cell carcinoma syndrome and it is associated with PTCH gene inactivation. MONDO:0007959
MONDO:0857548 central nervous system t-cell non-hodgkin lymphoma NCIT:C5409 MONDO:equivalentTo Central Nervous System T-Cell Non-Hodgkin Lymphoma A T-cell lymphoblastic lymphoma or a mature T-cell and NK-cell neoplasm that affects the brain, meninges, or spinal cord. MONDO:0015760
MONDO:0857549 gastric granular cell tumor NCIT:C54094 MONDO:equivalentTo Gastric Granular Cell Tumor A benign or malignant granular cell tumor that arises from the stomach. MONDO:0006235
MONDO:0857550 malignant central nervous system germ cell tumor NCIT:C54099 MONDO:equivalentTo Malignant Central Nervous System Germ Cell Tumor A germ cell tumor that affects the central nervous system, characterized by the presence of malignant morphologic characteristics. Representative examples include choriocarcinoma, embryonal carcinoma, and germinoma. MONDO:0003000
MONDO:0857552 breast columnar cell lesion NCIT:C54180 MONDO:equivalentTo Breast Columnar Cell Lesion A morphologic spectrum of lesions that arise in the terminal ductal lobular units of the breast parenchyma. These lesions are characterized by the presence of columnar epithelial cells that line dilated terminal ductal lobular units. Cytological and architectural atypia may be absent or minimal, or significant enough to raise the possibility of atypical ductal hyperplasia or ductal carcinoma in situ. Columnar cell lesions are frequently found in breast biopsies but their biologic significance is not known. MONDO:0021100
MONDO:0857556 head and neck keratinizing squamous cell carcinoma NCIT:C54283 MONDO:equivalentTo Head and Neck Keratinizing Squamous Cell Carcinoma A squamous cell carcinoma that arises from the head and neck region and is characterized by prominent production of keratin. MONDO:0005056
MONDO:0857559 metastasizing ameloblastoma NCIT:C54297 MONDO:equivalentTo Metastasizing Ameloblastoma A rare, well differentiated, cytologically benign ameloblastoma which paradoxically metastasizes. MONDO:0024883
MONDO:0857562 lipomatosis of nerve NCIT:C5431 MONDO:equivalentTo Lipomatosis of Nerve A tumor composed of mature adipocytes and fibrous tissue infiltrating the epineurium and peripheral nerves. It is often seen at birth or during childhood and may be associated with macrodactyly. MONDO:0000648
MONDO:0857564 laryngeal papillary squamous cell carcinoma NCIT:C54335 MONDO:equivalentTo Laryngeal Papillary Squamous Cell Carcinoma A variant of squamous cell carcinoma that arises from the larynx. It is characterized by exophytic and papillary growth usually in the supraglottic area. The papillae are covered by a malignant stratified squamous epithelium. MONDO:0002979
MONDO:0857565 laryngeal spindle cell squamous carcinoma NCIT:C54336 MONDO:equivalentTo Laryngeal Spindle Cell Squamous Carcinoma A squamous cell carcinoma that arises from the larynx. It is characterized by the presence of a malignant spindle cell cellular component. In some cases, there is a biphasic morphology due to the presence of a well-differentiated squamous cell carcinoma component. The latter is either in situ or invasive squamous cell carcinoma. MONDO:0005595
MONDO:0857566 laryngeal acantholytic squamous cell carcinoma NCIT:C54337 MONDO:equivalentTo Laryngeal Acantholytic Squamous Cell Carcinoma A rare variant of squamous cell carcinoma that arises from the larynx. It is characterized by acantholysis of the tumor cells that results in the formation of pseudolumina that resemble glandular structures. MONDO:0003487
MONDO:0857567 laryngeal adenosquamous carcinoma NCIT:C54338 MONDO:equivalentTo Laryngeal Adenosquamous Carcinoma A rare, aggressive carcinoma that arises from the larynx. It is characterized by the presence of squamous cell carcinoma and adenocarcinoma components. Hoarseness, sore throat, and dysphagia are the presenting symptoms. MONDO:0002358
MONDO:0857568 laryngeal undifferentiated carcinoma NCIT:C54339 MONDO:equivalentTo Laryngeal Undifferentiated Carcinoma An undifferentiated carcinoma that arises from the larynx. This category includes lymphoepithelial carcinoma and giant cell carcinoma. MONDO:0005617
MONDO:0857570 kadish stage c olfactory neuroblastoma NCIT:C5435 MONDO:equivalentTo Kadish Stage C Olfactory Neuroblastoma An olfactory neuroblastoma that extends beyond the nasal cavity and paranasal sinuses. MONDO:0006329
MONDO:0857571 drop metastasis in the spinal cord NCIT:C5439 MONDO:equivalentTo Drop Metastasis in the Spinal Cord An intradural extramedullary spinal metastasis from an intracranial tumor through the cerebrospinal fluid. MONDO:0044912
MONDO:0857572 nasopharyngeal low grade papillary adenocarcinoma NCIT:C54400 MONDO:equivalentTo Nasopharyngeal Low Grade Papillary Adenocarcinoma A low-grade exophytic adenocarcinoma with papillary growth that arises from the epithelium of the nasopharynx. If it is completely removed, the prognosis is excellent. MONDO:0002512
MONDO:0857574 meningeal gliomatosis NCIT:C5446 MONDO:equivalentTo Meningeal Gliomatosis Diffuse or multifocal infiltration of the meninges by malignant glioma. MONDO:0100342
MONDO:0857575 invasive breast apocrine carcinoma NCIT:C5457 MONDO:equivalentTo Invasive Breast Apocrine Carcinoma An invasive breast adenocarcinoma with cytological and immunophenotypic characteristics of apocrine differentiation in more than 90 percent of the malignant cells. MONDO:0006256
MONDO:0857576 breast nevus NCIT:C54658 MONDO:equivalentTo Breast Nevus A benign melanocytic nevus that arises from the breast skin. MONDO:0044794
MONDO:0857577 acral nevus NCIT:C54659 MONDO:equivalentTo Acral Nevus A melanocytic nevus that arises from the palms, soles, and nails. MONDO:0044794
MONDO:0857578 flexural skin nevus NCIT:C54660 MONDO:equivalentTo Flexural Skin Nevus A benign nevus occurring in the flexural skin. MONDO:0044794
MONDO:0857580 nevoid melanoma NCIT:C54662 MONDO:equivalentTo Nevoid Melanoma A rare variant of cutaneous melanoma occurring mostly in adults in their fifth decade. Morphologically it resembles an ordinary compound or dermal nevus. MONDO:0005012
MONDO:0857581 signet ring melanoma NCIT:C54663 MONDO:equivalentTo Signet Ring Melanoma A rare variant of cutaneous melanoma, characterized by the presence of malignant cells with signet-ring morphology. MONDO:0005012
MONDO:0857583 invasive breast lobular carcinoma, signet ring variant NCIT:C54691 MONDO:equivalentTo Invasive Breast Lobular Carcinoma, Signet Ring Variant An invasive lobular carcinoma characterized by the presence of malignant epithelial cells with large intracytoplasmic lumina that cause displacement of the nuclei towards one pole of the cells. MONDO:0002671
MONDO:0857587 central nervous system dermoid cyst NCIT:C5508 MONDO:equivalentTo Central Nervous System Dermoid Cyst A dermoid cyst arising in the central nervous system. MONDO:0003733
MONDO:0857589 appendix mucinous cystadenoma NCIT:C5510 MONDO:equivalentTo Appendix Mucinous Cystadenoma A cystically dilated epithelial neoplasm arising from the appendix. It is characterized by the presence of a cystic structure that is filled with mucus. MONDO:0006859
MONDO:0857592 prostate kaposi sarcoma NCIT:C5523 MONDO:equivalentTo Prostate Kaposi Sarcoma A Kaposi sarcoma arising from the prostate. MONDO:0002854
MONDO:0857593 prostate myeloid sarcoma NCIT:C5527 MONDO:equivalentTo Prostate Myeloid Sarcoma Myeloid sarcoma that affects the prostate gland. It may present in association with or as a site of relapse of acute myeloid leukemia. Cases of myeloid sarcoma of the prostate gland preceding acute myeloid leukemia have also been reported. MONDO:0008315
MONDO:0857595 prostate non-hodgkin lymphoma NCIT:C5534 MONDO:equivalentTo Prostate Non-Hodgkin Lymphoma A rare non-Hodgkin lymphoma that arises from the prostate gland. MONDO:0018908
MONDO:0857596 ceruminous neoplasm NCIT:C5558 MONDO:equivalentTo Ceruminous Neoplasm An adenoma or carcinoma that arises from the ceruminous glands in the external auditory canal. MONDO:0003686
MONDO:0857599 stage i skin cancer NCIT:C5581 MONDO:equivalentTo Stage I Skin Cancer Stage I includes: T1, N0, M0. T1: Tumor 2 cm or less in greatest dimension with less than two high-risk features. High-risk features for the primary tumor staging are defined as follows: depth/invasion of more than 2 mm thickness, Clark level equal or greater than IV, and perineural invasion. Anatomic location: primary site ear and primary site non-hair-bearing lip. Differentiation: poorly differentiated or undifferentiated. N0: No regional lymph node metastasis. M0: No clinical or radiographic evidence of distant metastasis. (AJCC 7th ed.) MONDO:0002656
MONDO:0857600 stage ii skin cancer NCIT:C5582 MONDO:equivalentTo Stage II Skin Cancer Stage II includes: T2, N0, M0. T2: Tumor size greater than 2 cm in greatest dimension or tumor of any size with two or more high-risk features. High-risk features for the primary tumor staging are defined as follows: depth/invasion of more than 2 mm thickness; Clark level equal or greater than IV; and perineural invasion. Anatomic location: primary site ear and primary site non-hair-bearing lip. Differentiation: poorly differentiated or undifferentiated. N0: No regional lymph node metastasis. M0: No clinical or radiographic evidence of distant metastasis. (AJCC 7th ed.) MONDO:0002656
MONDO:0857601 stage iii skin cancer NCIT:C5583 MONDO:equivalentTo Stage III Skin Cancer Stage III includes: (T3, N0, M0); (T1, N1, M0); (T2, N1, M0); (T3, N1, M0). T3: Tumor with invasion of maxilla, mandible, orbit, or temporal bone. T1: Tumor 2 cm or less in greatest dimension with less than two high-risk features. T2: Tumor size greater than 2 cm in greatest dimension or tumor of any size with two or more high-risk features. N0: No regional lymph node metastasis. N1: Metastasis in a single ipsilateral lymph node, 3 cm or less in greatest dimension. M0: No clinical or radiographic evidence of distant metastasis. (AJCC 7th Ed.) MONDO:0002656
MONDO:0857602 stage iv skin cancer NCIT:C5584 MONDO:equivalentTo Stage IV Skin Cancer Stage IV includes: (T1, N2, M0); (T2, N2, M0); (T3, N2, M0); (T Any, N3, M0); (T4, N Any, M0); (T Any, N Any, M1). T1: Tumor 2 cm or less in greatest dimension with less than two high-risk features. T2: Tumor size greater than 2 cm in greatest dimension or tumor of any size with two or more high-risk features. T3: Tumor with invasion of maxilla, mandible, orbit, or temporal bone. T4: Tumor with invasion of skeleton or perineural invasion of skull base. N0: No regional lymph node metastasis. N2: Metastasis in a single ipsilateral lymph node, more than 3 cm but not more than 6 cm in greatest dimension; or in multiple ipsilateral lymph nodes, none more than 6 cm in greatest dimension; or in bilateral or contralateral lymph nodes, none more than 6 cm in greatest dimension. N3: Metastasis in a lymph node, more than 6 cm in greatest dimension. M1: Distant metastases. (AJCC 7th Ed.) MONDO:0002656
MONDO:0857604 jugular foramen neoplasm NCIT:C5589 MONDO:equivalentTo Jugular Foramen Neoplasm A neoplasm that affects the jugular foramen. Representative examples include paraganglioma, schwannoma, and meningioma. MONDO:0021351
MONDO:0857607 benign anal granular cell tumor NCIT:C5607 MONDO:equivalentTo Benign Anal Granular Cell Tumor A granular cell tumor that arises from the anus and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021469
MONDO:0857611 metastatic malignant neoplasm in the skin NCIT:C5629 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Skin The spread of a malignant neoplasm to the skin. This may be from a primary skin malignant neoplasm, or from a malignant neoplasm at a distant site. MONDO:0002898
MONDO:0857613 occult lung carcinoma NCIT:C5641 MONDO:equivalentTo Occult Lung Carcinoma A lung carcinoma detectable by sputum cytology or bronchial washings only. The primary tumor is undetectable radiographically or during bronchoscopy; therefore, it can not be assessed. MONDO:0005138
MONDO:0857614 endobronchial hamartoma NCIT:C5662 MONDO:equivalentTo Endobronchial Hamartoma A benign neoplasm that arises endobronchially. It is characterized by the presence of mesenchymal tissues admixed with entrapped respiratory epithelium. It presents with signs and symptoms of bronchial obstruction. Bronchoplastic resection is usually curative. Recurrence is very rare. MONDO:0021540
MONDO:0857615 multiple pulmonary hamartomas NCIT:C5663 MONDO:equivalentTo Multiple Pulmonary Hamartomas The presence of multiple hamartomas in the lungs. Hamartomas are usually solitary lesions on chest-x-rays. Multiple lung hamartomas are rare. MONDO:0021540
MONDO:0857619 colorectal adenoma with severe dysplasia NCIT:C5685 MONDO:equivalentTo Colorectal Adenoma with Severe Dysplasia An adenoma that arises from the colon or rectum. It is characterized by the presence of severe epithelial dysplasia. MONDO:0005484
MONDO:0857623 esophageal schwannoma NCIT:C5703 MONDO:equivalentTo Esophageal Schwannoma A slowly growing, benign, usually encapsulated neoplasm arising from the esophagus. Morphologically, it is composed of neoplastic differentiated Schwann cells. MONDO:0021459
MONDO:0857629 extrahepatic bile duct undifferentiated carcinoma NCIT:C5780 MONDO:equivalentTo Extrahepatic Bile Duct Undifferentiated Carcinoma A carcinoma without evidence of differentiation arising from the extrahepatic bile ducts. MONDO:0005617
MONDO:0857635 esophageal neuroendocrine neoplasm NCIT:C5821 MONDO:equivalentTo Esophageal Neuroendocrine Neoplasm A neoplasm with neuroendocrine differentiation that arises from the esophagus. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). MONDO:0021355
MONDO:0857638 extrahepatic bile duct tubular adenoma NCIT:C5850 MONDO:equivalentTo Extrahepatic Bile Duct Tubular Adenoma An adenoma that arises from the extrahepatic bile ducts. It is characterized by the presence of a tubular pattern. MONDO:0003445
MONDO:0857646 oral cavity granular cell tumor NCIT:C5912 MONDO:equivalentTo Oral Cavity Granular Cell Tumor A rare neoplasm that arises from the oral cavity, usually the tongue. It is characterized by the presence of plump eosinophilic cells with abundant granular cytoplasm. The neoplastic cells extend into the surrounding tissues, usually skeletal muscle. The vast majority of cases follow a benign clinical course. Recurrences are rare after removal of the tumor. MONDO:0006235
MONDO:0857647 oral cavity adenoma NCIT:C5913 MONDO:equivalentTo Oral Cavity Adenoma A monomorphic or pleomorphic adenoma that arises from the salivary glands in the oral cavity. MONDO:0004972
MONDO:0857648 oral cavity adenocarcinoma NCIT:C5914 MONDO:equivalentTo Oral Cavity Adenocarcinoma An adenocarcinoma that arises from the oral cavity. MONDO:0044925
MONDO:0857660 minor salivary gland mucoepidermoid carcinoma NCIT:C5953 MONDO:equivalentTo Minor Salivary Gland Mucoepidermoid Carcinoma A carcinoma that arises from the minor salivary glands. It usually presents as a firm and painless mass. It is characterized by the presence of epidermoid cells, mucus producing cells, and cells of intermediate type. The majority of cases have a favorable outcome. MONDO:0021009
MONDO:0857661 minor salivary gland small cell neuroendocrine carcinoma NCIT:C5956 MONDO:equivalentTo Minor Salivary Gland Small Cell Neuroendocrine Carcinoma An infrequent small cell carcinoma that arises from a minor salivary gland. It is characterized by the presence of neuroendocrine differentiation and a high number of mitotic figures. MONDO:0006405
MONDO:0857663 minor salivary gland squamous cell carcinoma NCIT:C5959 MONDO:equivalentTo Minor Salivary Gland Squamous Cell Carcinoma A squamous cell carcinoma that affects the minor salivary glands. MONDO:0045069
MONDO:0857671 oropharyngeal polyp NCIT:C5988 MONDO:equivalentTo Oropharyngeal Polyp A benign exophytic growth that arises from the oropharynx. MONDO:0005079
MONDO:0857679 lung mature b-cell neoplasm NCIT:C60310 MONDO:equivalentTo Lung Mature B-Cell Neoplasm A neoplasm that arises from mature B-lymphocytes or plasma cells in the lung. Representative examples include mucosa-associated lymphoid tissue lymphoma, diffuse large B-cell lymphoma, lymphomatoid granulomatosis, and primary pulmonary plasmacytoma. MONDO:0021117
MONDO:0857682 nasopharyngeal polyp NCIT:C6034 MONDO:equivalentTo Nasopharyngeal Polyp A benign exophytic growth that arises from the nasopharynx. MONDO:0005079
MONDO:0857683 stage 0 nasopharyngeal undifferentiated carcinoma ajcc v6, v7, and v8 NCIT:C6035 MONDO:equivalentTo Stage 0 Nasopharyngeal Undifferentiated Carcinoma AJCC v6, v7, and v8 Stage 0 includes: Tis, N0, M0. Tis: Carcinoma in situ. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th, 7th, and 8th eds.) MONDO:0021297
MONDO:0857685 nasopharyngeal squamous papilloma NCIT:C6037 MONDO:equivalentTo Nasopharyngeal Squamous Papilloma A benign exophytic neoplasm that arises from the nasopharynx. It is characterized by the presence of a connective tissue core covered by stratified squamous epithelium. MONDO:0021478
MONDO:0857686 oropharyngeal squamous papilloma NCIT:C6038 MONDO:equivalentTo Oropharyngeal Squamous Papilloma A benign exophytic neoplasm that arises from the oropharynx. It is characterized by the presence of a connective tissue core covered by stratified squamous epithelium. MONDO:0001825
MONDO:0857687 stage 0 oropharyngeal squamous cell carcinoma ajcc v6 and v7 NCIT:C6039 MONDO:equivalentTo Stage 0 Oropharyngeal Squamous Cell Carcinoma AJCC v6 and v7 Stage 0 includes: Tis, N0, M0. Tis: Carcinoma in situ. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0044704
MONDO:0857689 stage 0 hypopharyngeal squamous cell carcinoma ajcc v6, v7, and v8 NCIT:C6048 MONDO:equivalentTo Stage 0 Hypopharyngeal Squamous Cell Carcinoma AJCC v6, v7, and v8 Stage 0 includes: Tis, N0, M0. Tis: Carcinoma in situ. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th, 7th, and 8th eds.) MONDO:0021288
MONDO:0857690 stage 0 oral cavity squamous cell carcinoma ajcc v6 and v7 NCIT:C6052 MONDO:equivalentTo Stage 0 Oral Cavity Squamous Cell Carcinoma AJCC v6 and v7 Stage 0 includes: Tis, N0, M0. Tis: Carcinoma in situ. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0004958
MONDO:0857692 anterior tongue neoplasm NCIT:C6062 MONDO:equivalentTo Anterior Tongue Neoplasm A benign or malignant neoplasm that affects the anterior portion of the tongue. MONDO:0021240
MONDO:0857697 neck carcinoma NCIT:C6077 MONDO:equivalentTo Neck Carcinoma A carcinoma that arises from the anatomic structures of the neck region. MONDO:0021310
MONDO:0857698 external ear actinic keratosis NCIT:C6080 MONDO:equivalentTo External Ear Actinic Keratosis Actinic keratosis that develops in the skin of the external ear. MONDO:0021235
MONDO:0857700 middle ear paraganglioma NCIT:C6085 MONDO:equivalentTo Middle Ear Paraganglioma A jugulotympanic paraganglioma arising from paraganglia in the middle ear. MONDO:0021366
MONDO:0857702 benign uveal neoplasm NCIT:C6104 MONDO:equivalentTo Benign Uveal Neoplasm A neoplasm that arises from the uvea and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential.. MONDO:0021225
MONDO:0857703 stage 0 laryngeal squamous cell carcinoma ajcc v6, v7, and v8 NCIT:C6121 MONDO:equivalentTo Stage 0 Laryngeal Squamous Cell Carcinoma AJCC v6, v7, and v8 Stage 0 includes: Tis, N0, M0. Tis: Carcinoma in situ. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th, 7th, and 8th eds.) MONDO:0004693
MONDO:0857715 testicular typical seminoma NCIT:C61383 MONDO:equivalentTo Testicular Typical Seminoma A testicular seminoma characterized by the presence of uniform round germ cells with glycogen-rich cytoplasm and large nuclei, and a lymphocytic infiltrate. MONDO:0003669
MONDO:0857719 ureter undifferentiated carcinoma NCIT:C6159 MONDO:equivalentTo Ureter Undifferentiated Carcinoma Undifferentiated carcinoma that affects the ureter. MONDO:0006481
MONDO:0857720 urethral undifferentiated carcinoma NCIT:C6168 MONDO:equivalentTo Urethral Undifferentiated Carcinoma An undifferentiated carcinoma arising from the urethra. MONDO:0021327
MONDO:0857725 hard palate mucoepidermoid carcinoma NCIT:C6214 MONDO:equivalentTo Hard Palate Mucoepidermoid Carcinoma A mucoepidermoid carcinoma arising from the minor salivary glands in the hard palate. MONDO:0044964
MONDO:0857728 salivary gland clear cell carcinoma NCIT:C62191 MONDO:equivalentTo Salivary Gland Clear Cell Carcinoma A carcinoma that arises from the salivary glands, most often the minor salivary glands. It is characterized by the presence of a monomorphic population of malignant epithelial cells with clear cytoplasm and the absence of morphologic features that define other primary neoplasms of the salivary glands. MONDO:0000521
MONDO:0857729 breast tubular adenoma NCIT:C62210 MONDO:equivalentTo Breast Tubular Adenoma A benign, well circumscribed neoplasm that arises from the breast. It is composed entirely of tubular structures that contain epithelial and myoepithelial cells. MONDO:0002058
MONDO:0857730 conjunctival squamous papilloma NCIT:C6224 MONDO:equivalentTo Conjunctival Squamous Papilloma A papilloma that arises from the conjunctival squamous epithelium. It is associated with human papillomavirus infection. MONDO:0001825
MONDO:0857731 skin nodular basal cell carcinoma NCIT:C62282 MONDO:equivalentTo Skin Nodular Basal Cell Carcinoma A basal cell carcinoma of the skin that often appears as elevated nodules which may become ulcerated. MONDO:0005341
MONDO:0857732 superficial basal cell carcinoma NCIT:C62284 MONDO:equivalentTo Superficial Basal Cell Carcinoma A variant of basal cell carcinoma of the skin presenting as erythematous, often multiple patches. Morphologically, it is characterized by the presence of superficial lobules of basaloid cells projecting into the dermis. The basaloid cell lobules are surrounded by myxoid stroma and are usually confined to the papillary dermis. MONDO:0005341
MONDO:0857734 minor salivary gland acinic cell carcinoma NCIT:C6243 MONDO:equivalentTo Minor Salivary Gland Acinic Cell Carcinoma An adenocarcinoma with serous acinar cell differentiation that arises from the minor salivary glands. MONDO:0006304
MONDO:0857736 ovarian endometrioid tumor NCIT:C6257 MONDO:equivalentTo Ovarian Endometrioid Tumor A benign, borderline, or malignant epithelial tumor of the ovary characterized by the presence of glands and/or cysts lined by neoplastic cells that resemble endometrial cells. MONDO:0002480
MONDO:0857738 childhood cerebral ependymoma, not otherwise specified NCIT:C6268 MONDO:equivalentTo Childhood Cerebral Ependymoma, Not Otherwise Specified An ependymoma, not otherwise specified that arises from the cerebral hemispheres and occurs during childhood. MONDO:0004249
MONDO:0857739 fallopian tube undifferentiated carcinoma NCIT:C6281 MONDO:equivalentTo Fallopian Tube Undifferentiated Carcinoma An invasive carcinoma arising from the fallopian tube. It is characterized by the presence of a diffuse malignant infiltrate that is composed of epithelial cells without evidence of glandular or squamous differentiation. MONDO:0005617
MONDO:0857740 vaginal verrucous carcinoma NCIT:C6325 MONDO:equivalentTo Vaginal Verrucous Carcinoma A squamous cell carcinoma that arises from the vagina and is characterized by a papillary growth pattern, acanthotic epithelium with minimal or absent atypia, and pushing borders. MONDO:0006490
MONDO:0857743 benign uterine corpus mixed epithelial and mesenchymal neoplasm NCIT:C6335 MONDO:equivalentTo Benign Uterine Corpus Mixed Epithelial and Mesenchymal Neoplasm A non-metastasizing neoplasm that arises from the uterine corpus and is composed of epithelial and mesenchymal elements. Representative examples include adenomyoma and adenofibroma. MONDO:0021525
MONDO:0857744 cervical undifferentiated carcinoma NCIT:C6345 MONDO:equivalentTo Cervical Undifferentiated Carcinoma A rare carcinoma that arises from the cervix and is characterized by the lack of specific cellular differentiation. MONDO:0005617
MONDO:0857745 testicular mixed embryonal carcinoma and seminoma NCIT:C6350 MONDO:equivalentTo Testicular Mixed Embryonal Carcinoma and Seminoma A malignant mixed germ cell tumor arising from the testis. It is characterized by the presence of a mixture of embryonal carcinoma and a seminomatous component. MONDO:0003120
MONDO:0857746 testicular mixed embryonal carcinoma and teratoma NCIT:C6351 MONDO:equivalentTo Testicular Mixed Embryonal Carcinoma and Teratoma A malignant mixed germ cell tumor arising from the testis, characterized by the presence of an embryonal carcinomatous component and a teratomatous component. MONDO:0003403
MONDO:0857747 testicular mixed embryonal carcinoma and teratoma with seminoma NCIT:C6352 MONDO:equivalentTo Testicular Mixed Embryonal Carcinoma and Teratoma with Seminoma A malignant mixed germ cell tumor arising from the testis. It is characterized by the presence of a mixture of embryonal carcinoma, a teratomatous component, and a seminomatous component. MONDO:0003120
MONDO:0857748 kidney lymphoma NCIT:C63532 MONDO:equivalentTo Kidney Lymphoma A lymphoma that arises from the kidney. There is no evidence of a systemic lymphoproliferative disorder. MONDO:0002367
MONDO:0857750 testicular mature teratoma NCIT:C6355 MONDO:equivalentTo Testicular Mature Teratoma A teratoma that arises from the testis and is composed of well differentiated, adult-type tissues. MONDO:0018193
MONDO:0857752 undifferentiated carcinoma with osteoclast-like giant cells NCIT:C63622 MONDO:equivalentTo Undifferentiated Carcinoma with Osteoclast-Like Giant Cells A usually aggressive malignant epithelial neoplasm composed of atypical cells which do not display evidence of glandular or squamous differentiation and giant cells resembling osteoclasts. MONDO:0005617
MONDO:0857753 penile kaposi sarcoma NCIT:C6377 MONDO:equivalentTo Penile Kaposi Sarcoma A Kaposi sarcoma arising from the penis. MONDO:0022293
MONDO:0857758 orbit paraganglioma NCIT:C6408 MONDO:equivalentTo Orbit Paraganglioma An extra-adrenal paraganglioma arising from the orbit. Patients may present with visual disturbances or proptosis. MONDO:0006239
MONDO:0857759 laryngeal paraganglioma NCIT:C6409 MONDO:equivalentTo Laryngeal Paraganglioma An extra-adrenal parasympathetic paraganglioma arising from paraganglia adjacent to the larynx. Patients may present with hoarseness and dysphagia. MONDO:0006239
MONDO:0857760 intrathoracic paravertebral paraganglioma NCIT:C6411 MONDO:equivalentTo Intrathoracic Paravertebral Paraganglioma An intrathoracic sympathetic paraganglioma arising from paravertebral paraganglia. In functional tumors, the hypersecretion of catecholamines results in hypertension. MONDO:0000550
MONDO:0857763 foregut neuroendocrine tumor NCIT:C6421 MONDO:equivalentTo Foregut Neuroendocrine Tumor A neuroendocrine tumor that arises from the esophagus, stomach, or duodenum. MONDO:0000386
MONDO:0857765 hindgut neuroendocrine tumor NCIT:C6423 MONDO:equivalentTo Hindgut Neuroendocrine Tumor A neuroendocrine tumor that arises from the sigmoid colon, descending colon, or rectum. MONDO:0000386
MONDO:0857767 malignant mediastinal nongerminomatous germ cell tumor NCIT:C6439 MONDO:equivalentTo Malignant Mediastinal Nongerminomatous Germ Cell Tumor An extragonadal nongerminomatous malignant germ cell tumor that arises from the mediastinum. This category includes embryonal carcinoma, yolk sac tumor, choriocarcinoma, and mixed germ cell tumors. MONDO:0003578
MONDO:0857768 gastric germ cell tumor NCIT:C6448 MONDO:equivalentTo Gastric Germ Cell Tumor A benign or malignant germ cell tumor that arises from the stomach. Representative examples include teratoma and choriocarcinoma. MONDO:0018201
MONDO:0857769 benign germ cell tumor NCIT:C6449 MONDO:equivalentTo Benign Germ Cell Tumor A germ cell tumor without evidence of atypia and metastatic potential. MONDO:0005165
MONDO:0857770 invasive thymoma NCIT:C6453 MONDO:equivalentTo Invasive Thymoma A thymoma of any morphologic type that extends beyond the capsule and infiltrates the surrounding tissues. MONDO:0006456
MONDO:0857771 bone hemangioma NCIT:C6477 MONDO:equivalentTo Bone Hemangioma A hemangioma arising in the bone. MONDO:0000631
MONDO:0857772 bone glomus tumor NCIT:C6480 MONDO:equivalentTo Bone Glomus Tumor A benign or malignant glomus tumor arising from the bone. MONDO:0019060
MONDO:0857773 extraabdominal fibromatosis NCIT:C6489 MONDO:equivalentTo Extraabdominal Fibromatosis An insidious poorly circumscribed neoplasm arising from the soft tissues outside the abdomen. It is characterized by the presence of elongated spindle-shaped fibroblasts, vascular collagenous stroma formation, and an infiltrative growth pattern. MONDO:0007608
MONDO:0857774 deep lipoma NCIT:C6498 MONDO:equivalentTo Deep Lipoma A benign well-circumscribed tumor, composed of mature adipocytes, that arises within deep soft tissues. MONDO:0005106
MONDO:0857775 benign skeletal muscle neoplasm NCIT:C6515 MONDO:equivalentTo Benign Skeletal Muscle Neoplasm A benign mesenchymal neoplasm arising from skeletal muscle tissue. MONDO:0002848
MONDO:0857776 non-small cell carcinoma NCIT:C65151 MONDO:equivalentTo Non-Small Cell Carcinoma A malignant epithelial neoplasm characterized by the absence of neoplastic small epithelial cells. A representative example is the lung non-small cell carcinoma. MONDO:0004993
MONDO:0857777 malignant neoplasm, uncertain whether primary or metastatic NCIT:C65153 MONDO:equivalentTo Malignant Neoplasm, Uncertain Whether Primary or Metastatic A malignant neoplasm in which the examined tissue can not be determined with certainty if it represents the primary site of tumor growth or tumor spread from another anatomic site. MONDO:0004992
MONDO:0857778 papillary carcinoma in situ NCIT:C65163 MONDO:equivalentTo Papillary Carcinoma In Situ An epithelial neoplasm with a papillary growth pattern in which the malignant cells are confined to the epithelium, without evidence of invasion. MONDO:0004647
MONDO:0857779 non-invasive papillary squamous cell carcinoma NCIT:C65164 MONDO:equivalentTo Non-Invasive Papillary Squamous Cell Carcinoma A well differentiated squamous cell carcinoma characterized by a papillary, exophytic growth pattern, hyperkeratosis, and absence of invasion of adjacent tissues. MONDO:0002979
MONDO:0857780 inverted squamous papilloma NCIT:C65165 MONDO:equivalentTo Inverted Squamous Papilloma A benign epithelial neoplasm characterized by an endophytic growth, papillary pattern, and proliferation of neoplastic squamous cells without morphologic evidence of malignancy. MONDO:0002537
MONDO:0857781 non-keratinizing large cell squamous cell carcinoma NCIT:C65173 MONDO:equivalentTo Non-Keratinizing Large Cell Squamous Cell Carcinoma A squamous cell carcinoma composed of large atypical cells, without morphologic evidence of keratin production. MONDO:0005096
MONDO:0857782 non-keratinizing small cell squamous cell carcinoma NCIT:C65175 MONDO:equivalentTo Non-Keratinizing Small Cell Squamous Cell Carcinoma A squamous cell carcinoma composed of small atypical cells, without morphologic evidence of keratin production. MONDO:0005096
MONDO:0857783 squamous cell carcinoma in situ with questionable stromal invasion NCIT:C65176 MONDO:equivalentTo Squamous Cell Carcinoma In Situ with Questionable Stromal Invasion A malignant epithelial neoplasm involving all the layers of the squamous epithelium, but it is not certain if it is confined to the squamous epithelium or it has invaded the basement membrane and the underlying stroma. MONDO:0005096
MONDO:0857785 squamous cell carcinoma with horn formation NCIT:C65179 MONDO:equivalentTo Squamous Cell Carcinoma with Horn Formation A keratinizing squamous cell carcinoma characterized by the presence of horn pearls. Representative examples include squamous cell carcinomas of the face presenting as a cutaneous horn. MONDO:0005056
MONDO:0857786 squamous cell carcinoma, clear cell type NCIT:C65180 MONDO:equivalentTo Squamous Cell Carcinoma, Clear Cell Type A squamous cell carcinoma characterized by the presence of malignant cells with clear cytoplasm. MONDO:0005096
MONDO:0857787 non-invasive papillary transitional cell carcinoma NCIT:C65181 MONDO:equivalentTo Non-Invasive Papillary Transitional Cell Carcinoma A transitional cell carcinoma characterized by a papillary growth pattern and lack of stromal invasion. MONDO:0006350
MONDO:0857789 malignant pancreatic insulinoma NCIT:C65186 MONDO:equivalentTo Malignant Pancreatic Insulinoma An insulin-producing neuroendocrine tumor arising from the beta cells of the pancreas. Patients exhibit symptoms related to hypoglycemia due to inappropriate secretion of insulin. It displays vascular invasion and metastasizes to other anatomic sites. MONDO:0024677
MONDO:0857790 malignant pancreatic glucagonoma NCIT:C65187 MONDO:equivalentTo Malignant Pancreatic Glucagonoma A glucagon-producing neuroendocrine tumor arising from the alpha cells of the pancreas. It may be associated with necrolytic erythema migrans, diarrhea, diabetes, glossitis, weight loss, malabsorption, and anemia. It displays vascular invasion and metastasizes to other anatomic sites. MONDO:0019959
MONDO:0857791 malignant gastrinoma NCIT:C65188 MONDO:equivalentTo Malignant Gastrinoma A gastrin-producing neuroendocrine tumor. It is characterized by inappropriate secretion of gastrin and associated with Zollinger Ellison syndrome. It displays vascular invasion and metastasizes to other anatomic sites. MONDO:0003523
MONDO:0857792 malignant vipoma NCIT:C65189 MONDO:equivalentTo Malignant Vipoma An aggressive neuroendocrine tumor located in the pancreas or small intestine. It is composed of cells containing vasoactive intestinal peptide. It is associated with watery diarrhea, hypokalemia, and hypochlorhydria or achlorhydria. It displays vascular invasion and metastasizes to other anatomic sites. MONDO:0019960
MONDO:0857793 malignant somatostatinoma NCIT:C65190 MONDO:equivalentTo Malignant Somatostatinoma A neuroendocrine tumor arising from delta cells which produce somatostatin. It displays vascular invasion and metastasizes to other anatomic sites. MONDO:0006976
MONDO:0857794 flat adenoma NCIT:C65193 MONDO:equivalentTo Flat Adenoma An adenoma of the gastrointestinal tract mucosa which grossly and morphologically does not appear as an elevated or polypoid lesion. MONDO:0006180
MONDO:0857795 glandular papillomatosis NCIT:C65198 MONDO:equivalentTo Glandular Papillomatosis Multifocal neoplastic proliferations of the glandular epithelium displaying a papillary pattern. MONDO:0021098
MONDO:0857796 thyroid gland follicular carcinoma, minimally invasive NCIT:C65200 MONDO:equivalentTo Thyroid Gland Follicular Carcinoma, Minimally Invasive A follicular carcinoma of the thyroid gland showing capsular invasion only. MONDO:0040677
MONDO:0857797 papillary mucinous cystadenocarcinoma NCIT:C65204 MONDO:equivalentTo Papillary Mucinous Cystadenocarcinoma An invasive adenocarcinoma characterized by cystic changes, papillary growth pattern, and the presence of malignant glandular cells which contain intracytoplasmic mucin. MONDO:0005074
MONDO:0857798 malignant testicular sertoli cell tumor NCIT:C6523 MONDO:equivalentTo Malignant Testicular Sertoli Cell Tumor A Sertoli cell tumor that arises from the testis and is characterized by nuclear pleomorphism, increased mitotic activity and necrotic changes. Metastases may be present at diagnosis. MONDO:0020808
MONDO:0857799 malignant pericytic neoplasm NCIT:C6530 MONDO:equivalentTo Malignant Pericytic Neoplasm A malignant mesenchymal neoplasm arising from the perivascular cells of the connective and soft tissues. It is characterized by the presence of pericytes that grow in a circumferential pattern around vessels, and cytologic atypia. MONDO:0002604
MONDO:0857802 ancient schwannoma NCIT:C6556 MONDO:equivalentTo Ancient Schwannoma A schwannoma that is characterized by degenerative changes such as hyalinization, hemorrhage, calcification and cystic change. MONDO:0002546
MONDO:0857803 extraskeletal cartilaginous and osseous neoplasm NCIT:C6570 MONDO:equivalentTo Extraskeletal Cartilaginous and Osseous Neoplasm A benign or malignant mesenchymal neoplasm with cartilaginous or osseous differentiation arising from the soft tissues exclusively. Representative examples include chondroma, osteoma, and osteosarcoma. MONDO:0006424
MONDO:0857804 intramuscular myxoma NCIT:C6579 MONDO:equivalentTo Intramuscular Myxoma A benign, painless soft tissue tumor that arises in a muscle, usually in a large muscle of the thigh, buttocks, shoulder, or upper arm. It is associated with point mutations of the GNAS gene. Grossly it is characterized by a gelatinous and lobulated cut surface. Morphologically it is composed of uniform spindled and stellate-shaped cells without atypia. The cells are separated by myxoid stroma. No recurrences have been reported. MONDO:0044784
MONDO:0857805 juxta-articular myxoma NCIT:C6580 MONDO:equivalentTo Juxta-Articular Myxoma A rare myxoma that usually arises in an area close to a large joint. Morphologically it resembles a cellular myxoma. In contrast to an intramuscular myxoma, it is not associated with mutations of the GNAS gene. MONDO:0044784
MONDO:0857806 peripheral neuroblastoma NCIT:C6591 MONDO:equivalentTo Peripheral Neuroblastoma A neuroblastoma arising from the peripheral nervous system. MONDO:0002749
MONDO:0857807 benign mediastinal soft tissue neoplasm NCIT:C6593 MONDO:equivalentTo Benign Mediastinal Soft Tissue Neoplasm A mesenchymal neoplasm that arises from the mediastinum and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. Representative examples include lipoma, leiomyoma, and rhabdomyoma. MONDO:0021521
MONDO:0857810 soft tissue fibrosarcoma NCIT:C6605 MONDO:equivalentTo Soft Tissue Fibrosarcoma A usually aggressive malignant neoplasm arising from the soft tissue. It is characterized by the presence of spindle-shaped fibroblasts and collagenous stroma formation in a herringbone growth pattern. MONDO:0018078
MONDO:0857811 mediastinal malignant peripheral nerve sheath tumor NCIT:C6626 MONDO:equivalentTo Mediastinal Malignant Peripheral Nerve Sheath Tumor A malignant peripheral nerve sheath tumor that arises from the mediastinum. It may be associated with neurofibromatosis. It often spreads to the lungs or pleura. MONDO:0003098
MONDO:0857812 mediastinal ganglioneuroma NCIT:C6632 MONDO:equivalentTo Mediastinal Ganglioneuroma A ganglioneuroma arising from the mediastinum. MONDO:0021521
MONDO:0857813 mediastinal hodgkin lymphoma NCIT:C6634 MONDO:equivalentTo Mediastinal Hodgkin Lymphoma A Hodgkin lymphoma that arises from the mediastinum. It usually involves mediastinal lymph nodes and/or the thymus. Signs and symptoms include fever, weight loss, fatigue, and night sweats. MONDO:0004021
MONDO:0857814 stage 1 neuroblastoma NCIT:C6638 MONDO:equivalentTo Stage 1 Neuroblastoma Localized tumor with complete gross excision, with or without microscopic residual disease; representative ipsilateral lymph nodes negative for tumor microscopically. (cancer.gov) MONDO:0005072
MONDO:0857815 stage 2 neuroblastoma NCIT:C6639 MONDO:equivalentTo Stage 2 Neuroblastoma Stage 2 includes stage 2A and stage 2B. Stage 2A: Localized tumor with incomplete gross excision; representative ipsilateral nonadherent lymph nodes negative for tumor microscopically. Stage 2B: Localized tumor with or without complete gross excision, with ipsilateral nonadherent lymph nodes positive for tumor. Enlarged contralateral lymph nodes must be negative microscopically. (cancer.gov) MONDO:0005072
MONDO:0857816 stage 3 neuroblastoma NCIT:C6640 MONDO:equivalentTo Stage 3 Neuroblastoma Unresectable unilateral tumor infiltrating across the midline, with or without regional lymph node involvement; or localized unilateral tumor with contralateral regional lymph node involvement; or midline tumor with bilateral extension by infiltration (unresectable) or by lymph node involvement. The midline is defined as the vertebral column. Tumors originating on one side and crossing the midline must infiltrate to or beyond the opposite side of the vertebral column. (cancer.gov) MONDO:0005072
MONDO:0857817 stage 4 neuroblastoma NCIT:C6641 MONDO:equivalentTo Stage 4 Neuroblastoma Any primary tumor with dissemination to distant lymph nodes, bone, bone marrow, liver, skin, and/or other organs, except as defined for stage 4S. (cancer.gov) MONDO:0005072
MONDO:0857821 breast atypical medullary carcinoma NCIT:C66719 MONDO:equivalentTo Breast Atypical Medullary Carcinoma An invasive ductal breast carcinoma characterized by the presence of a predominantly syncytial architectural pattern. It may have some, but not all the strictly defined additional morphologic criteria which are necessary for the diagnosis of medullary breast carcinoma (presence of a diffuse lymphoplasmacytic infiltrate, neoplastic round cells with abundant cytoplasm and vesicular nuclei, complete histological circumscription, and absence of glandular or tubular structures). It does not have the relatively favorable outcome that characterizes medullary breast carcinoma. MONDO:0004953
MONDO:0857822 adenocarcinoma with neuroendocrine differentiation NCIT:C66745 MONDO:equivalentTo Adenocarcinoma with Neuroendocrine Differentiation An invasive adenocarcinoma characterized by the presence of focal or extensive neuroendocrine differentiation. MONDO:0004970
MONDO:0857823 testicular sex cord-stromal tumor, not otherwise specified NCIT:C66748 MONDO:equivalentTo Testicular Sex Cord-Stromal Tumor, Not Otherwise Specified A sex cord-stromal tumor of the testis in which the neoplastic cells do not show specific differentiation. MONDO:0003125
MONDO:0857824 ovarian stromal tumor with minor sex cord elements NCIT:C66749 MONDO:equivalentTo Ovarian Stromal Tumor with Minor Sex Cord Elements A rare, benign sex cord-stromal tumor of the ovary characterized by the presence of a fibrothecomatous stroma and scattered sex cord elements. Although it is usually hormonally inactive, cases associated with endometrial hyperplasia or adenocarcinoma have been reported. MONDO:0021657
MONDO:0857825 adult granulosa cell tumor NCIT:C66750 MONDO:equivalentTo Adult Granulosa Cell Tumor A low-grade malignant sex cord-stromal tumor occurring in the ovary and rarely in the testis. It is composed of granulosa cells in an often fibrothecomatous stroma. The neoplastic cells may form various patterns including the microfollicular, which is characterized by the presence of Call-Exner bodies, macrofollicular, insular, trabecular, and diffuse pattern. In females, it affects middle aged to post-menopausal women. Signs and symptoms include abdominal mass, hemoperitoneum, and ascites. Estrogenic and rarely androgenic manifestations may be present. The vast majority of cases present as stage I tumors; however, all tumors have a potential for aggressive clinical course. In males, it is reported in the age range of 16-76 years and the average age at presentation is 44 years. A minority of patients have gynecomastia. Metastases have been reported in a minority of patients. MONDO:0006036
MONDO:0857826 melanoma in precancerous melanosis NCIT:C66753 MONDO:equivalentTo Melanoma in Precancerous Melanosis A melanoma arising from an atypical intraepithelial melanocytic hyperplasia. MONDO:0005012
MONDO:0857827 small congenital melanocytic nevus NCIT:C66754 MONDO:equivalentTo Small Congenital Melanocytic Nevus A congenital melanocytic nevus of small size, with a diameter smaller than 15 mm. It presents as a macular, papular or plaque-like lesion. MONDO:0044792
MONDO:0857828 proliferative nodules in congenital melanocytic nevus NCIT:C66755 MONDO:equivalentTo Proliferative Nodules in Congenital Melanocytic Nevus A benign proliferation of epithelioid or spindled melanocytes usually in the upper or mid dermis in a background of congenital melanocytic nevus. The congenital melanocytic nevus is usually of the deep type, involving the dermis and extending into the subcutaneous tissue. It presents as a dark plaque or nodule above a giant congenital melanocytic nevus. MONDO:0044792
MONDO:0857829 periosteal fibroma NCIT:C66761 MONDO:equivalentTo Periosteal Fibroma A benign fibrous neoplasm arising from the periosteal connective tissue that surrounds a bone. MONDO:0000631
MONDO:0857830 fascial fibroma NCIT:C66764 MONDO:equivalentTo Fascial Fibroma A benign fibrous tumor arising from the fascial connective tissue. MONDO:0005167
MONDO:0857831 fascial fibrosarcoma NCIT:C66765 MONDO:equivalentTo Fascial Fibrosarcoma A malignant fibroblastic neoplasm arising from the fascial connective tissue. MONDO:0005164
MONDO:0857834 choriocarcinoma combined with other germ cell elements NCIT:C66777 MONDO:equivalentTo Choriocarcinoma Combined with Other Germ Cell Elements A malignant mixed germ cell tumor characterized by the presence of a choriocarcinomatous component admixed with another germ cell component (e.g. embryonal carcinoma, teratoma, or seminoma). MONDO:0015864
MONDO:0857835 hemolymphangioma NCIT:C66792 MONDO:equivalentTo Hemolymphangioma A hemorrhagic lymphatic lesion characterized by the presence of dilated lymphatic spaces, extravasation of red blood cells, hemosiderin deposition, and fibrosis. MONDO:0002013
MONDO:0857836 ganglioneuromatosis NCIT:C66804 MONDO:equivalentTo Ganglioneuromatosis Extensive and diffuse infiltration of tissues by ganglioneuroma. MONDO:0005033
MONDO:0857837 ciliary body benign medulloepithelioma NCIT:C66807 MONDO:equivalentTo Ciliary Body Benign Medulloepithelioma A rare, unilateral, benign embryonal neoplasm typically presenting as a ciliary body mass during childhood. It arises from primitive medullary epithelium. MONDO:0021486
MONDO:0857838 ciliary body teratoid medulloepithelioma NCIT:C66810 MONDO:equivalentTo Ciliary Body Teratoid Medulloepithelioma A rare, unilateral, benign or malignant embryonal neoplasm typically presenting as a ciliary body mass during childhood. It arises from primitive medullary epithelium and contains heterologous elements, particularly cartilage, skeletal muscle, and brain tissue. MONDO:0017050
MONDO:0857839 retinocytoma NCIT:C66812 MONDO:equivalentTo Retinocytoma A rare, unilateral or bilateral benign neoplasm that arises from the retina. There is an increased risk of malignant transformation to retinoblastoma; therefore, patients with a diagnosis of retinocytoma should be closely observed. MONDO:0021453
MONDO:0857840 differentiated retinoblastoma NCIT:C66813 MONDO:equivalentTo Differentiated Retinoblastoma A retinoblastoma with well differentiated features. It often produces Flexner-Wintersteiner rosettes or Homer-Wright rosettes. In some cases the tumor cells form fleurettes. MONDO:0008380
MONDO:0857841 undifferentiated retinoblastoma NCIT:C66814 MONDO:equivalentTo Undifferentiated Retinoblastoma A retinoblastoma composed of small, undifferentiated cells. It is often associated with necrotic changes. MONDO:0008380
MONDO:0857842 diffuse retinoblastoma NCIT:C66815 MONDO:equivalentTo Diffuse Retinoblastoma A retinoblastoma characterized by the absence of a distinct retinal mass and the presence of malignant cells diffusely infiltrating the retina. It is often confused with uveitis and endophthalmitis, resulting in delayed diagnosis of the malignancy. MONDO:0008380
MONDO:0857844 melanotic neurofibroma NCIT:C66841 MONDO:equivalentTo Melanotic Neurofibroma A rare neurofibroma characterized by the presence of melanin-laden cells and the absence of atypia. MONDO:0016755
MONDO:0857846 testicular mixed sex cord-stromal tumor NCIT:C66991 MONDO:equivalentTo Testicular Mixed Sex Cord-Stromal Tumor A sex cord-stromal tumor of the testis which may contain any combination of cell types, for example Sertoli cells, Leydig cells, and granulosa cells. Symptoms include testicular swelling and gynecomastia. MONDO:0003125
MONDO:0857847 pyriform fossa carcinoma NCIT:C6700 MONDO:equivalentTo Pyriform Fossa Carcinoma A carcinoma that arises from the pyriform sinus. Patients usually present with advanced stage disease and the prognosis is poor. MONDO:0005216
MONDO:0857848 ovarian serous adenocarcinofibroma NCIT:C67092 MONDO:equivalentTo Ovarian Serous Adenocarcinofibroma A malignant neoplasm of the ovary with an invasive epithelial component and a fibrotic stroma. The epithelial component is characterized by the presence of malignant epithelial cells of serous type, forming glandular, papillary, and solid patterns. MONDO:0024885
MONDO:0857849 sternal chondromyxoid fibroma NCIT:C6714 MONDO:equivalentTo Sternal Chondromyxoid Fibroma An uncommon benign cartilaginous neoplasm arising from the sternum. It is characterized by the presence of spindle-shaped or stellate chondrocytes, a lobulated growth pattern, myxoid stroma formation, and sometimes multinucleated giant cells. MONDO:0021456
MONDO:0857850 olfactory neurogenic tumor NCIT:C67155 MONDO:equivalentTo Olfactory Neurogenic Tumor A rare, benign (olfactory neurocytoma) or malignant (olfactory neuroblastoma) neuroectodermal tumor originating from olfactory receptor cells in the nasal cavity. MONDO:0002722
MONDO:0857852 nodular sclerosis classic hodgkin lymphoma, cellular phase NCIT:C67171 MONDO:equivalentTo Nodular Sclerosis Classic Hodgkin Lymphoma, Cellular Phase A nodular sclerosis Hodgkin lymphoma characterized by the presence of lacunar cells, nodular growth, and the absence of fibrosis. MONDO:0004665
MONDO:0857853 sternal intraosseous schwannoma NCIT:C6718 MONDO:equivalentTo Sternal Intraosseous Schwannoma A rare schwannoma that arises from the sternum. MONDO:0021456
MONDO:0857854 peripheral primitive neuroectodermal tumor of the kidney NCIT:C67214 MONDO:equivalentTo Peripheral Primitive Neuroectodermal Tumor of the Kidney A small round cell tumor with neural differentiation arising from the kidney. MONDO:0018271
MONDO:0857855 chest wall hodgkin lymphoma NCIT:C6723 MONDO:equivalentTo Chest Wall Hodgkin Lymphoma A Hodgkin lymphoma that affects the structures of the chest wall. MONDO:0003985
MONDO:0857858 benign glomus tumor NCIT:C6748 MONDO:equivalentTo Benign Glomus Tumor A glomus tumor of small size characterized by the absence of nuclear atypia and mitotic activity. MONDO:0003342
MONDO:0857859 malignant sex cord-stromal tumor NCIT:C67561 MONDO:equivalentTo Malignant Sex Cord-Stromal Tumor A gonadal sex cord-stromal tumor with malignant characteristics. It includes the poorly differentiated ovarian Sertoli-Leydig cell tumor, malignant ovarian granulosa cell tumor, malignant ovarian steroid cell tumor, and malignant ovarian thecoma. MONDO:0002149
MONDO:0857860 myxoid leiomyoma NCIT:C67563 MONDO:equivalentTo Myxoid Leiomyoma A leiomyoma characterized by the presence of abundant myxoid matrix. MONDO:0001572
MONDO:0857862 stromal neoplasm NCIT:C6781 MONDO:equivalentTo Stromal Neoplasm A benign or malignant mesenchymal neoplasm composed of stromal cells. Representative examples include gastrointestinal stromal tumor, endometrial stromal sarcoma, and prostate stromal sarcoma. MONDO:0002616
MONDO:0857864 benign apocrine neoplasm NCIT:C6799 MONDO:equivalentTo Benign Apocrine Neoplasm An epithelial neoplasm that arises from the apocrine glands and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021489
MONDO:0857866 benign external ear neoplasm NCIT:C6807 MONDO:equivalentTo Benign External Ear Neoplasm A neoplasm that arises from the external ear and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. Representative examples include ceruminous adenoma, polyp, and lipoma. MONDO:0021235
MONDO:0857867 prostate ductal adenocarcinoma NCIT:C6813 MONDO:equivalentTo Prostate Ductal Adenocarcinoma A usually aggressive invasive adenocarcinoma of the prostate gland composed of large glands containing tall columnar cells. The columnar cells have abundant cytoplasm and are reminiscent of endometrial carcinoma. This type of adenocarcinoma has a tendency to metastasize to the lung and penis. MONDO:0005082
MONDO:0857872 kadish stage a olfactory neuroblastoma NCIT:C6853 MONDO:equivalentTo Kadish Stage A Olfactory Neuroblastoma An olfactory neuroblastoma that is confined to the nasal cavity MONDO:0006329
MONDO:0857873 kadish stage b olfactory neuroblastoma NCIT:C6854 MONDO:equivalentTo Kadish Stage B Olfactory Neuroblastoma An olfactory neuroblastoma that involves the nasal cavity and paranasal sinuses. MONDO:0006329
MONDO:0857874 oropharyngeal undifferentiated carcinoma NCIT:C68610 MONDO:equivalentTo Oropharyngeal Undifferentiated Carcinoma A non-keratinizing carcinoma arising from the oropharynx. It is characterized by the presence of large malignant cells with vesicular nuclei, prominent nucleoli, syncytial growth pattern, and a lymphoplasmacytic infiltrate. MONDO:0003572
MONDO:0857876 childhood extracranial germ cell tumor NCIT:C68627 MONDO:equivalentTo Childhood Extracranial Germ Cell Tumor A childhood benign or malignant germ cell tumor arising from an anatomic site other than the brain. MONDO:0003751
MONDO:0857879 childhood extragonadal malignant germ cell tumor NCIT:C68632 MONDO:equivalentTo Childhood Extragonadal Malignant Germ Cell Tumor A malignant germ cell tumor in children arising from an anatomic site other than the testis or ovary. MONDO:0003113
MONDO:0857881 adrenal cortical low grade carcinoma NCIT:C68635 MONDO:equivalentTo Adrenal Cortical Low Grade Carcinoma A carcinoma that arises from the adrenal cortex and is characterized by the presence of twenty or less mitoses per ten square millimeters. MONDO:0006639
MONDO:0857882 adrenal cortical sarcomatoid carcinoma NCIT:C68644 MONDO:equivalentTo Adrenal Cortical Sarcomatoid Carcinoma A carcinoma that arises from the adrenal cortex and is characterized by the partial or complete loss of adrenal cortical differentiation. MONDO:0006406
MONDO:0857884 hodgkin lymphoma by clinical course NCIT:C68666 MONDO:equivalentTo Hodgkin Lymphoma by Clinical Course MONDO:0004952
MONDO:0857892 adult gliosarcoma NCIT:C68701 MONDO:equivalentTo Adult Gliosarcoma A gliosarcoma occurring in adults. MONDO:0020690
MONDO:0857893 adult giant cell glioblastoma NCIT:C68702 MONDO:equivalentTo Adult Giant Cell Glioblastoma A giant cell glioblastoma occurring in adults. MONDO:0016682
MONDO:0857895 pancreatic mixed acinar carcinoma-neuroendocrine carcinoma NCIT:C6878 MONDO:equivalentTo Pancreatic Mixed Acinar Carcinoma-Neuroendocrine Carcinoma A carcinoma that arises from the pancreas and is composed of acinar carcinoma and neuroendocrine carcinoma components in both the primary tumor and the metastatic sites. MONDO:0044727
MONDO:0857896 cellular fibroma NCIT:C6892 MONDO:equivalentTo Cellular Fibroma A morphologic variant of fibroma characterized by increased cellularity. MONDO:0005167
MONDO:0857897 malignant solitary fibrous tumor NCIT:C6894 MONDO:equivalentTo Malignant Solitary Fibrous Tumor A malignant neoplasm of probable fibroblastic derivation. It is characterized by the presence of atypical round to spindle-shaped cells, increased cellularity, necrotic change and high mitotic activity. MONDO:0016238
MONDO:0857899 atypical burkitt/burkitt-like lymphoma NCIT:C6917 MONDO:equivalentTo Atypical Burkitt/Burkitt-Like Lymphoma A morphologic variant of Burkitt lymphoma characterized by marked nuclear pleomorphism, abundant apoptotic debris, and the presence of tangible body macrophages. MONDO:0007243
MONDO:0857900 acute myeloid leukemia with a variant kmt2a rearrangement NCIT:C6924 MONDO:equivalentTo Acute Myeloid Leukemia with a Variant KMT2A Rearrangement A term referring to acute myeloid leukemias with rearrangement of the KMT2A gene that results in translocations with various genes other than the MLLT3 (AF9) gene. MONDO:0100404
MONDO:0857901 malignant ovarian thecoma NCIT:C6929 MONDO:equivalentTo Malignant Ovarian Thecoma A thecoma of the ovary which may metastasize to another anatomic site. It is usually characterized by nuclear atypia and mitotic activity. Malignant thecomas are rare. MONDO:0018172
MONDO:0857902 solitary plasmacytoma NCIT:C6932 MONDO:equivalentTo Solitary Plasmacytoma A localized malignant neoplasm that arises in the bony skeleton or soft tissue. It is composed of clonal (malignant) plasma cells forming a tumor mass. MONDO:0005615
MONDO:0857903 deep (aggressive) angiomyxoma NCIT:C6936 MONDO:equivalentTo Deep (Aggressive) Angiomyxoma A locally infiltrating, non-metastasizing angiomyxoma arising from the pelviperineal region. It may recur following resection MONDO:0006086
MONDO:0857904 cardiac fibroma NCIT:C6947 MONDO:equivalentTo Cardiac Fibroma A rare benign heart neoplasm usually occurring in young children. It is characterized by the presence of bland spindle cells and collagenous stroma formation. Clinical presentation may include cardiac arrhythmia, cyanosis, heart failure or sudden death. MONDO:0005167
MONDO:0857906 anaplastic kidney wilms tumor NCIT:C6952 MONDO:equivalentTo Anaplastic Kidney Wilms Tumor Wilms tumor of the kidney characterized by the presence of nuclear anaplasia. Anaplasia is defined by the presence of all of the following: multipolar polyploid mitotic figures, marked nuclear enlargement, and hyperchromasia. When anaplasia is diffuse, it is associated with an unfavorable clinical outcome. MONDO:0020633
MONDO:0857907 simple endometrial hyperplasia with atypia NCIT:C6991 MONDO:equivalentTo Simple Endometrial Hyperplasia with Atypia A proliferation of endometrial cells resulting in glandular enlargement and budding without changes in the basic structure of the endometrium. Epithelial atypia is present. MONDO:0006410
MONDO:0857910 central nervous system kaposi sarcoma NCIT:C7006 MONDO:equivalentTo Central Nervous System Kaposi Sarcoma A Kaposi sarcoma arising from the brain, spinal cord, or meninges. MONDO:0002217
MONDO:0857913 central nervous system inflammatory myofibroblastic tumor NCIT:C7020 MONDO:equivalentTo Central Nervous System Inflammatory Myofibroblastic Tumor A multinodular intermediate fibroblastic neoplasm affecting the central nervous system. It is characterized by the presence of spindle-shaped fibroblasts and myofibroblasts, and a chronic inflammatory infiltrate composed of eosinophils, lymphocytes and plasma cells. MONDO:0015798
MONDO:0857918 meningioma by site NCIT:C7051 MONDO:equivalentTo Meningioma by Site MONDO:0016642
MONDO:0857919 mature b-cell non-hodgkin lymphoma NCIT:C7056 MONDO:equivalentTo Mature B-Cell Non-Hodgkin Lymphoma A non-Hodgkin lymphoma that originates from mature B lymphocytes. Representative examples include diffuse large B-cell lymphoma, follicular lymphoma, marginal zone lymphoma, mantle cell lymphoma, and small lymphocytic lymphoma. MONDO:0004949
MONDO:0857921 neoplasm by special category NCIT:C7062 MONDO:equivalentTo Neoplasm by Special Category A neoplasm defined by its unique characteristic as they apply to clinical presentation and course, morphologic patterns, frequency, and/or age distribution. MONDO:0005070
MONDO:0857925 megakaryocytic neoplasm NCIT:C7066 MONDO:equivalentTo Megakaryocytic Neoplasm A neoplasm affecting cells of the megakaryocytic lineage. MONDO:0005170
MONDO:0857926 prostate cancer by whitmore-jewett stage NCIT:C7079 MONDO:equivalentTo Prostate Cancer by Whitmore-Jewett Stage A term that refers to the staging of prostate carcinoma according to the Whitmore-Jewett staging system. MONDO:0005159
MONDO:0857931 metastatic non-cutaneous melanoma NCIT:C7092 MONDO:equivalentTo Metastatic Non-Cutaneous Melanoma A non-cutaneous melanoma that has spread from its original site of growth to another anatomic site. MONDO:0005191
MONDO:0857935 teratoid hepatoblastoma NCIT:C7098 MONDO:equivalentTo Teratoid Hepatoblastoma A mixed epithelial and mesenchymal hepatoblastoma characterized by the presence of heterologous elements. The latter include neuroectoderm, endoderm, or melanin-holding cells. Muscle, cartilage and osteoid may or may not be present. MONDO:0003650
MONDO:0857937 adult pilocytic astrocytoma NCIT:C71016 MONDO:equivalentTo Adult Pilocytic Astrocytoma A pilocytic astrocytoma occurring in adults. MONDO:0002503
MONDO:0857940 liver non-epithelial neoplasm NCIT:C7107 MONDO:equivalentTo Liver Non-Epithelial Neoplasm A benign or malignant non-epithelial neoplasm that affects the liver. MONDO:0024477
MONDO:0857943 stage i liver cancer NCIT:C7116 MONDO:equivalentTo Stage I Liver Cancer Stage I carcinoma of the liver according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0018531
MONDO:0857944 stage ii liver cancer NCIT:C7117 MONDO:equivalentTo Stage II Liver Cancer Stage II carcinoma of the liver according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0018531
MONDO:0857945 stage iii liver cancer NCIT:C7118 MONDO:equivalentTo Stage III Liver Cancer Stage III carcinoma of the liver according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0018531
MONDO:0857946 stage iv liver cancer NCIT:C7121 MONDO:equivalentTo Stage IV Liver Cancer Stage IV carcinoma of the liver according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0018531
MONDO:0857947 intrahepatic bile duct microcystic adenoma NCIT:C7127 MONDO:equivalentTo Intrahepatic Bile Duct Microcystic Adenoma An adenoma that arises from the intrahepatic bile ducts and it is characterized by the presence of microcystic changes. MONDO:0003444
MONDO:0857948 gallbladder benign non-epithelial neoplasm NCIT:C7129 MONDO:equivalentTo Gallbladder Benign Non-Epithelial Neoplasm A non-epithelial neoplasm that arises from the gallbladder and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. Representative examples include leiomyoma, lipoma, and neurofibroma. MONDO:0021503
MONDO:0857950 childhood grade 2 meningioma NCIT:C71301 MONDO:equivalentTo Childhood Grade 2 Meningioma A grade II meningioma that occurs during childhood. MONDO:0045056
MONDO:0857952 ovarian sertoli cell tumor NCIT:C7133 MONDO:equivalentTo Ovarian Sertoli Cell Tumor A rare, typically benign ovarian neoplasm composed of Sertoli cells. Patients may present with pseudoprecocity, menometrorrhagia, amenorrhea, hirsutism, and hoarseness. Rarely it may invade the ovarian stroma and extend beyond the ovary. MONDO:0002696
MONDO:0857961 benign fibroblastic neoplasm NCIT:C7147 MONDO:equivalentTo Benign Fibroblastic Neoplasm A benign mesenchymal neoplasm characterized by the presence of neoplastic fibroblasts without malignant characteristics. MONDO:0044335
MONDO:0857962 soft tissue tumor of uncertain differentiation NCIT:C7148 MONDO:equivalentTo Soft Tissue Tumor of Uncertain Differentiation A benign,intermediate, or malignant soft tissue neoplasm in which the line of differentiation is uncertain. Representative examples include neoplasm with perivascular epithelioid cell differentiation, alveolar soft part sarcoma, desmoplastic small round cell tumor, epithelioid sarcoma, extraskeletal myxoid chondrosarcoma, and synovial sarcoma. MONDO:0006424
MONDO:0857963 monoclonal immunoglobulin deposition disease NCIT:C7151 MONDO:equivalentTo Monoclonal Immunoglobulin Deposition Disease A mature B-cell neoplasm characterized by the deposition of immunoglobulin in tissues, resulting in impaired organ function. It includes the following entities: primary amyloidosis, heavy chain deposition disease, and light chain deposition disease. MONDO:0004949
MONDO:0857964 erythroleukemia NCIT:C7152 MONDO:equivalentTo Erythroleukemia Acute erythroid leukemia characterised by the presence of at least 50% erythroid precursors and at least 20% myeloblasts in the bone marrow. MONDO:0017858
MONDO:0857965 primary central chondrosarcoma NCIT:C7155 MONDO:equivalentTo Primary Central Chondrosarcoma A chondrosarcoma arising from the central portion of bone without a benign precursor. MONDO:0008977
MONDO:0857966 benign dermal neoplasm NCIT:C7158 MONDO:equivalentTo Benign Dermal Neoplasm A neoplasm that arises from the dermis and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0002300
MONDO:0857967 grade 1 nodular sclerosis classic hodgkin lymphoma NCIT:C7165 MONDO:equivalentTo Grade 1 Nodular Sclerosis Classic Hodgkin Lymphoma Nodular sclerosis Hodgkin lymphoma in which at least 75% of the tumor nodules contain scattered Reed-Sternberg cells. The background cellular infiltrate is lymphocytic, mixed, or fibrohistiocytic. MONDO:0004665
MONDO:0857968 grade 2 nodular sclerosis classic hodgkin lymphoma NCIT:C7166 MONDO:equivalentTo Grade 2 Nodular Sclerosis Classic Hodgkin Lymphoma Nodular sclerosis Hodgkin lymphoma in which at least 25% of the tumor nodules contain increased numbers of Reed-Sternberg cells. MONDO:0004665
MONDO:0857971 adult diffuse astrocytoma NCIT:C7174 MONDO:equivalentTo Adult Diffuse Astrocytoma A low grade (WHO grade II) astrocytoma occurring during adulthood. It is characterized by a high degree of cellular differentiation, slow growth, and diffuse infiltration of neighboring brain structures. MONDO:0016686
MONDO:0857972 spindle cell/pleomorphic lipoma NCIT:C7180 MONDO:equivalentTo Spindle Cell/Pleomorphic Lipoma A benign lipomatous neoplasm characterized by the presence of an admixture of mature adipose tissue and bland spindle cells. The pleomorphic variant contains in addition multinucleated giant cells. It usually arises in the neck and upper trunk in older males. MONDO:0005106
MONDO:0857973 classical burkitt lymphoma NCIT:C7188 MONDO:equivalentTo Classical Burkitt Lymphoma A Burkitt lymphoma characterized by the presence of a uniform malignant lymphocytic infiltrate that is composed of medium-sized cells with round nuclei and multiple basophilic nucleoli, abundant mitotic figures, and a starry-sky pattern due to the presence of multiple tangible body macrophages. MONDO:0007243
MONDO:0857974 burkitt lymphoma with plasmacytoid differentiation NCIT:C7189 MONDO:equivalentTo Burkitt Lymphoma with Plasmacytoid Differentiation Burkitt lymphoma characterized by the presence of malignant cells with eccentric basophilic cytoplasm. The nucleoli of these cells are often single and central. This morphologic variant of Burkitt lymphoma is more often seen in patients with immunodeficiency. MONDO:0007243
MONDO:0857975 type b lymphomatoid papulosis NCIT:C7198 MONDO:equivalentTo Type B Lymphomatoid Papulosis A variant of lymphomatoid papulosis characterized by an epidermotropic infiltrate composed of small atypical cerebriform-like lymphocytes. MONDO:0020326
MONDO:0857976 lymphoepithelioid variant peripheral t-cell lymphoma, not otherwise specified NCIT:C7205 MONDO:equivalentTo Lymphoepithelioid Variant Peripheral T-Cell Lymphoma, Not Otherwise Specified A variant of peripheral T-cell lymphoma, not otherwise specified. It is characterized by the presence of neoplastic small lymphocytes infiltrating the lymph nodes in a diffuse and less frequently interfollicular pattern. There is an associated proliferation of epithelioid histiocytes forming confluent clusters. MONDO:0004964
MONDO:0857977 common variant anaplastic large cell lymphoma NCIT:C7206 MONDO:equivalentTo Common Variant Anaplastic Large Cell Lymphoma An anaplastic large cell lymphoma, characterized by CD30 positive lymphoid cells. MONDO:0020325
MONDO:0857978 lymphohistiocytic variant anaplastic large cell lymphoma NCIT:C7207 MONDO:equivalentTo Lymphohistiocytic Variant Anaplastic Large Cell Lymphoma A histologic variant of anaplastic large cell lymphoma characterized by the presence of a large number of histiocytes admixed with the anaplastic lymphoma cells. MONDO:0020325
MONDO:0857981 non-hodgkin lymphoma by clinical course NCIT:C7215 MONDO:equivalentTo Non-Hodgkin Lymphoma by Clinical Course MONDO:0018908
MONDO:0857982 primary cutaneous hodgkin lymphoma NCIT:C7221 MONDO:equivalentTo Primary Cutaneous Hodgkin Lymphoma Hodgkin lymphoma primarily involving the skin. This diagnosis can only be made when there is no evidence of Hodgkin lymphoma in the lymph nodes or other anatomic sites. Patients usually present with papules or nodular lesions. Morphologically, primary cutaneous Hodgkin lymphoma may resemble lymphomatoid papulosis or anaplastic large cell lymphoma. Immunohistochemical tissue evaluation is essential in establishing the diagnosis. MONDO:0018898
MONDO:0857984 blastoid variant mantle cell lymphoma NCIT:C7229 MONDO:equivalentTo Blastoid Variant Mantle Cell Lymphoma An aggressive mantle cell lymphoma characterized by the presence of neoplastic B-lymphocytes resembling lymphoblasts. MONDO:0018876
MONDO:0857995 follicular lymphoma with predominantly diffuse growth pattern NCIT:C7264 MONDO:equivalentTo Follicular Lymphoma with Predominantly Diffuse Growth Pattern A lymphoma with the morphologic and immunophenotypic features of a follicular lymphoma characterized by the presence of a diffuse growth pattern with only focal and usually small micronodular foci. MONDO:0018906
MONDO:0857996 minimally invasive lung mucinous adenocarcinoma NCIT:C7268 MONDO:equivalentTo Minimally Invasive Lung Mucinous Adenocarcinoma A morphologic variant of minimally invasive lung adenocarcinoma characterized by tall columnar cells and mucin production. MONDO:0004991
MONDO:0857997 minimally invasive lung non-mucinous adenocarcinoma NCIT:C7269 MONDO:equivalentTo Minimally Invasive Lung Non-Mucinous Adenocarcinoma A morphologic variant of minimally invasive lung adenocarcinoma characterized by the presence of Clara cells and/or type II cells. MONDO:0004991
MONDO:0857998 ovarian dermoid cyst with secondary tumor NCIT:C7284 MONDO:equivalentTo Ovarian Dermoid Cyst with Secondary Tumor An adult-type tumor that has derived from an ovarian dermoid cyst. Representative examples include dermoid cyst with secondary carcinoma, dermoid cyst with secondary sarcoma, and dermoid cyst with pituitary-type tumor. MONDO:0003331
MONDO:0857999 ovarian granulosa-stromal cell tumor NCIT:C7287 MONDO:equivalentTo Ovarian Granulosa-Stromal Cell Tumor A group of sex cord-stromal tumors that arise from the ovary. These tumors are characterized by the presence of granulosa cells, stromal cells, and/or theca cells. This group includes granulosa cell tumor and tumors of the thecoma/fibroma group. MONDO:0021657
MONDO:0858001 malignant splenic soft tissue neoplasm NCIT:C7292 MONDO:equivalentTo Malignant Splenic Soft Tissue Neoplasm A malignant mesenchymal neoplasm that arises from the spleen. MONDO:0005966
MONDO:0858002 splenic manifestation of t-cell prolymphocytic leukemia NCIT:C7298 MONDO:equivalentTo Splenic Manifestation of T-Cell Prolymphocytic Leukemia Infiltration and expansion of the white and red pulp of the spleen by T-cell prolymphocytic leukemia. MONDO:0002966
MONDO:0858003 splenic manifestation of b-cell prolymphocytic leukemia NCIT:C7299 MONDO:equivalentTo Splenic Manifestation of B-Cell Prolymphocytic Leukemia Infiltration and expansion of the white and red pulp of the spleen by B-cell prolymphocytic leukemia. MONDO:0002966
MONDO:0858004 splenic manifestation of chronic lymphocytic leukemia NCIT:C7300 MONDO:equivalentTo Splenic Manifestation of Chronic Lymphocytic Leukemia Infiltration of the spleen by chronic lymphocytic leukemia. It primarily involves the white pulp. MONDO:0004107
MONDO:0858005 splenic manifestation of t-cell large granular lymphocyte leukemia NCIT:C7302 MONDO:equivalentTo Splenic Manifestation of T-Cell Large Granular Lymphocyte Leukemia Infiltration and expansion of the red pulp cords and sinusoids of the spleen by T-cell large granular lymphocyte leukemia. The white pulp of the spleen is not involved and is often hyperplastic. MONDO:0004107
MONDO:0858006 splenic manifestation of chronic myeloid leukemia, bcr-abl1 positive NCIT:C7303 MONDO:equivalentTo Splenic Manifestation of Chronic Myeloid Leukemia, BCR-ABL1 Positive Infiltration and expansion of the red pulp and sinusoids of the spleen by chronic myeloid leukemia, BCR-ABL1 positive. MONDO:0011996
MONDO:0858007 splenic lymphoplasmacytic lymphoma NCIT:C7305 MONDO:equivalentTo Splenic Lymphoplasmacytic Lymphoma A lymphoplasmacytic lymphoma occurring in the spleen. MONDO:0000432
MONDO:0858008 splenic lymphoblastic lymphoma NCIT:C7312 MONDO:equivalentTo Splenic Lymphoblastic Lymphoma Lymphoblastic lymphoma that affects the spleen. MONDO:0000873
MONDO:0858010 acute monoblastic and monocytic leukemia NCIT:C7318 MONDO:equivalentTo Acute Monoblastic and Monocytic Leukemia Acute myeloid leukemia in which 80% or more of the leukemic cells are of monocytic lineage, including monoblasts, promonocytes, and monocytes. Bleeding disorders are common presenting features. MONDO:0015667
MONDO:0858011 childhood chronic myeloid leukemia, bcr-abl1 positive NCIT:C7320 MONDO:equivalentTo Childhood Chronic Myeloid Leukemia, BCR-ABL1 Positive A chronic myeloid leukemia, BCR-ABL1 positive occurring during childhood. MONDO:0011996
MONDO:0858012 ovarian mixed germ cell-sex cord-stromal tumor NCIT:C7321 MONDO:equivalentTo Ovarian Mixed Germ Cell-Sex Cord-Stromal Tumor A neoplasm that arises from the ovary and is characterized by the presence of germ cell and sex cord-stromal tissues that are intimately admixed. If there is no malignant germ cell component present, the clinical course is benign. MONDO:0021068
MONDO:0858013 testicular mixed germ cell-sex cord-stromal tumor NCIT:C7322 MONDO:equivalentTo Testicular Mixed Germ Cell-Sex Cord-Stromal Tumor A tumor that arises from the testis and is characterized by the presence of a neoplastic germ cell component and a neoplastic sex cord-stromal component. MONDO:0021348
MONDO:0858016 reproductive endocrine neoplasm NCIT:C7335 MONDO:equivalentTo Reproductive Endocrine Neoplasm A benign or malignant endocrine neoplasm that arises from the testis or the ovary. MONDO:0006054
MONDO:0858017 high grade intraepithelial neoplasia NCIT:C7348 MONDO:equivalentTo High Grade Intraepithelial Neoplasia A precancerous neoplastic process that affects the squamous, glandular, or transitional cell epithelium without evidence of invasion. According to the degree of nuclear atypia, number of mitotic figures, and presence of architectural distortion, it is classified as grade II (moderate dysplasia) or grade III (severe dysplasia). MONDO:0024474
MONDO:0858019 cerebellar glioneuronal and neuronal tumors NCIT:C7372 MONDO:equivalentTo Cerebellar Glioneuronal and Neuronal Tumors Glioneuronal and neuronal tumors occurring in the cerebellum. MONDO:0016729
MONDO:0858020 benign vascular neoplasm NCIT:C7389 MONDO:equivalentTo Benign Vascular Neoplasm A mesenchymal neoplasm that arises from vascular tissue usually of the skin. It is characterized by the presence of vascular channel formation and endothelial cells. There is no evidence of atypical or malignant cytological and architectural features, invasive features, or metastases. MONDO:0024296
MONDO:0858021 malignant vascular neoplasm NCIT:C7390 MONDO:equivalentTo Malignant Vascular Neoplasm A malignant neoplasm arising from the vascular tissue. It is characterized by vascular channel formation and malignant endothelial cells. MONDO:0024296
MONDO:0858024 precancerous condition by site NCIT:C7422 MONDO:equivalentTo Precancerous Condition by Site
MONDO:0858025 oral cavity and lip precancerous condition NCIT:C7425 MONDO:equivalentTo Oral Cavity and Lip Precancerous Condition A premalignant pathologic process that affects the mucosa surface of the oral cavity or lip. It includes leukoplakia, erythroplakia, and smoker's keratosis.
MONDO:0858029 invasive papillary adenocarcinoma NCIT:C7438 MONDO:equivalentTo Invasive Papillary Adenocarcinoma A carcinoma that has papillary growth and invades the wall and/or the surrounding tissues of the organ it originates from. MONDO:0040677
MONDO:0858030 benign myoepithelioma NCIT:C7442 MONDO:equivalentTo Benign Myoepithelioma A tumor with myoepithelial differentiation that lacks an infiltrative growth pattern and does not metastasize. MONDO:0002380
MONDO:0858036 pure erythroid leukemia NCIT:C7467 MONDO:equivalentTo Pure Erythroid Leukemia Acute erythroid leukemia characterized by the presence of immature erythroid cells in the bone marrow (at least 80% of the cellular component), without evidence of a significant myeloblastic cell population present. MONDO:0017858
MONDO:0858037 anal extramucosal (perianal) adenocarcinoma NCIT:C7474 MONDO:equivalentTo Anal Extramucosal (Perianal) Adenocarcinoma An anal adenocarcinoma arising from the lining of an anorectal fistulous tract or the anal glands. The overlying anal mucosa does not show evidence of neoplastic changes. It usually presents as a submucosal tumor. MONDO:0002652
MONDO:0858042 ameloblastic carcinoma-primary type NCIT:C7493 MONDO:equivalentTo Ameloblastic Carcinoma-Primary Type A rare, aggressive odontogenic malignant tumor that arises usually from the mandible and less frequently from the maxilla. It combines the histologic features of an ameloblastoma and carcinoma. MONDO:0006079
MONDO:0858043 ameloblastic carcinoma-secondary type (dedifferentiated) NCIT:C7496 MONDO:equivalentTo Ameloblastic Carcinoma-Secondary Type (Dedifferentiated) A very rare ameloblastic carcinoma that originates from a pre-existing benign ameloblastoma. MONDO:0006079
MONDO:0858044 ameloblastic carcinoma derived from odontogenic cyst NCIT:C7497 MONDO:equivalentTo Ameloblastic Carcinoma Derived From Odontogenic Cyst A rare, aggressive malignant tumor that originates from an odontogenic cyst in the maxillomandibular region. It combines the histologic features of an ameloblastoma and carcinoma. MONDO:0006079
MONDO:0858045 primary intraosseous carcinoma, not otherwise specified, derived from odontogenic cyst NCIT:C7500 MONDO:equivalentTo Primary Intraosseous Carcinoma, Not Otherwise Specified, Derived from Odontogenic Cyst A rare primary intraosseous carcinoma, not otherwise specified, that arises from the lining of an odontogenic cyst. MONDO:0006385
MONDO:0858049 metastatic malignant neoplasm in the breast NCIT:C7511 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Breast The spread of a malignant neoplasm to the breast. This may be from a primary breast malignant neoplasm on the opposite side, or from a malignant neoplasm at a distant site. MONDO:0007254
MONDO:0858050 malignant esophageal neoplasm by anatomic region NCIT:C7512 MONDO:equivalentTo Malignant Esophageal Neoplasm by Anatomic Region MONDO:0007576
MONDO:0858051 malignant esophageal neoplasm by topographic region NCIT:C7513 MONDO:equivalentTo Malignant Esophageal Neoplasm by Topographic Region Esophageal segments used primarily in pathology, and distinct from the anatomic segments used for clinical purposes. MONDO:0007576
MONDO:0858052 kidney and ureter neoplasm NCIT:C7514 MONDO:equivalentTo Kidney and Ureter Neoplasm A benign or malignant, primary or metastatic neoplasm affecting the kidney and ureter. MONDO:0021066
MONDO:0858059 atypical adenoma NCIT:C7559 MONDO:equivalentTo Atypical Adenoma An adenoma characterized by increased cellularity and nuclear atypia without evidence of vascular or capsular invasion. A representative example is thyroid gland atypical follicular adenoma. MONDO:0004972
MONDO:0858060 eccrine hidrocystoma NCIT:C7565 MONDO:equivalentTo Eccrine Hidrocystoma A benign sweat gland cystic lesion that arises from the dermis. It is lined by a thin epithelial layer of cells with a slightly eosinophilic cytoplasm. MONDO:0006787
MONDO:0858066 regressing nevus NCIT:C7603 MONDO:equivalentTo Regressing Nevus A nevus associated with focal regression-like changes. MONDO:0044794
MONDO:0858068 cerebral non-hodgkin lymphoma NCIT:C7609 MONDO:equivalentTo Cerebral Non-Hodgkin Lymphoma A non-Hodgkin lymphoma that arises in the cerebral hemispheres as a primary lesion. MONDO:0003655
MONDO:0858069 malignant thymoma NCIT:C7612 MONDO:equivalentTo Malignant Thymoma A thymoma that has an aggressive clinical course (capsular invasion, infiltration of the surrounding tissues) and can metastasize. Although any morphologic subtype of thymoma may eventually have a malignant clinical course, this term is most often associated with thymoma types B3 and C. MONDO:0002586
MONDO:0858070 cutaneous lymphoproliferative disorder NCIT:C7614 MONDO:equivalentTo Cutaneous Lymphoproliferative Disorder A lymphoproliferative disorder that affects the skin.
MONDO:0858074 bilateral malignant neoplasm NCIT:C7627 MONDO:equivalentTo Bilateral Malignant Neoplasm A malignant neoplasm that affects both sides of an organ in a simultaneous or non-simultaneous manner. MONDO:0004992
MONDO:0858080 intermediate soft tissue neoplasm NCIT:C7653 MONDO:equivalentTo Intermediate Soft Tissue Neoplasm A soft tissue neoplasm characterized by an increased risk of local recurrence and/or a low risk of metastasis. MONDO:0006424
MONDO:0858081 carcinoma in a polyp NCIT:C7682 MONDO:equivalentTo Carcinoma in a Polyp Carcinoma arising in a polyp. MONDO:0004993
MONDO:0858082 invasive breast ductal carcinoma and lobular carcinoma in situ NCIT:C7689 MONDO:equivalentTo Invasive Breast Ductal Carcinoma and Lobular Carcinoma In Situ An invasive ductal breast carcinoma associated with an in situ lobular carcinomatous component. MONDO:0005050
MONDO:0858083 breast ductal carcinoma in situ and lobular carcinoma NCIT:C7690 MONDO:equivalentTo Breast Ductal Carcinoma In Situ and Lobular Carcinoma A breast carcinoma characterized by the presence of a ductal carcinoma in situ component and an in situ or invasive lobular carcinomatous component. MONDO:0006306
MONDO:0858086 adult hodgkin lymphoma NCIT:C7702 MONDO:equivalentTo Adult Hodgkin Lymphoma Hodgkin lymphoma occurring in adults. MONDO:0004952
MONDO:0858087 adult non-hodgkin lymphoma NCIT:C7704 MONDO:equivalentTo Adult Non-Hodgkin Lymphoma Non-Hodgkin lymphoma occurring in adults. MONDO:0018908
MONDO:0858088 childhood non-hodgkin lymphoma NCIT:C7706 MONDO:equivalentTo Childhood Non-Hodgkin Lymphoma Non-Hodgkin lymphoma occurring in childhood. MONDO:0003659
MONDO:0858089 adult soft tissue sarcoma NCIT:C7707 MONDO:equivalentTo Adult Soft Tissue Sarcoma Soft tissue sarcoma occurring in adults. MONDO:0018078
MONDO:0858091 adult liver carcinoma NCIT:C7711 MONDO:equivalentTo Adult Liver Carcinoma A hepatocellular carcinoma or intrahepatic cholangiocarcinoma that occurs during adulthood. MONDO:0018531
MONDO:0858092 childhood hodgkin lymphoma NCIT:C7714 MONDO:equivalentTo Childhood Hodgkin Lymphoma Hodgkin lymphoma occurring in childhood. MONDO:0004952
MONDO:0858094 gingival carcinoma NCIT:C7721 MONDO:equivalentTo Gingival Carcinoma A carcinoma of the oral cavity that arises from the upper or lower gingiva. MONDO:0044925
MONDO:0858095 vaginal clear cell adenocarcinoma NCIT:C7735 MONDO:equivalentTo Vaginal Clear Cell Adenocarcinoma A morphologic variant of adenocarcinoma that arises from the vagina. It is characterized by the presence of malignant glandular epithelium and clear cells containing glycogen. MONDO:0020653
MONDO:0858096 digestive system hemangioma NCIT:C7741 MONDO:equivalentTo Digestive System Hemangioma A hemangioma arising from any part of the digestive system. MONDO:0000385
MONDO:0858097 mucous membrane hemangioma NCIT:C7744 MONDO:equivalentTo Mucous Membrane Hemangioma A hemangioma arising from the mucous membranes. MONDO:0006500
MONDO:0858099 cardiac myxoma NCIT:C7748 MONDO:equivalentTo Cardiac Myxoma A myxoma arising from the endocardium. MONDO:0044784
MONDO:0858100 malignant pericarditis NCIT:C7753 MONDO:equivalentTo Malignant Pericarditis Pericarditis caused by the infiltration of the pericardium by a malignant neoplasm. The diagnosis is based on the cytological examination of pericardial fluid or the histologic examination of pericardial tissue. MONDO:0001322
MONDO:0858108 adult leiomyosarcoma NCIT:C7810 MONDO:equivalentTo Adult Leiomyosarcoma An aggressive malignant smooth muscle neoplasm, occurring in adults. It is characterized by a proliferation of neoplastic spindle cells. MONDO:0005058
MONDO:0858116 regional neuroblastoma NCIT:C7836 MONDO:equivalentTo Regional Neuroblastoma A neuroblastoma confined to a specific anatomic region without evidence of dissemination. MONDO:0005072
MONDO:0858119 stage i kidney wilms tumor NCIT:C7840 MONDO:equivalentTo Stage I Kidney Wilms Tumor Wilms tumor that is found in one kidney and can be completely removed with surgery. (National Wilms Tumor Study Group Staging System) MONDO:0019004
MONDO:0858120 stage ii kidney wilms tumor NCIT:C7841 MONDO:equivalentTo Stage II Kidney Wilms Tumor Wilms tumor that is found in the kidney and in the fat, soft tissue, or blood vessels near the kidney. It may have spread to the renal sinus. The renal sinus is the part of the kidney where blood and fluid enter and exit the organ. The tumor can be completely removed with surgery. (National Wilms Tumor Study Group Staging System) MONDO:0019004
MONDO:0858121 stage iii kidney wilms tumor NCIT:C7842 MONDO:equivalentTo Stage III Kidney Wilms Tumor Wilms tumor that is found in areas near the kidney and cannot be completely removed with surgery. The tumor may have spread to nearby organs and blood vessels or throughout the abdomen and to nearby lymph nodes. Lymph nodes are tiny, bean-shaped organs that help fight infection. Stage III cancer has not spread outside the abdomen. (National Wilms Tumor Study Group Staging System) MONDO:0019004
MONDO:0858122 stage iv kidney wilms tumor NCIT:C7843 MONDO:equivalentTo Stage IV Kidney Wilms Tumor Wilms tumor that has spread to other more distant organs, such as the lungs, liver, bones, and brain, or to lymph nodes outside the abdomen (National Wilms Tumor Study Group Staging System) MONDO:0019004
MONDO:0858123 stage v kidney wilms tumor NCIT:C7844 MONDO:equivalentTo Stage V Kidney Wilms Tumor Wilms tumor that affects both kidneys at the same time. The tumor in each kidney is staged separately (National Wilms Tumor Study Group Staging System) MONDO:0019004
MONDO:0858126 limited stage lung small cell carcinoma NCIT:C7853 MONDO:equivalentTo Limited Stage Lung Small Cell Carcinoma Small cell lung carcinoma which is confined to one hemi-thorax and the regional lymph nodes. MONDO:0008433
MONDO:0858151 grade i lymphomatoid granulomatosis NCIT:C7931 MONDO:equivalentTo Grade I Lymphomatoid Granulomatosis Lymphomatoid granulomatosis characterized by the presence of a polymorphous lymphoid infiltrate without cytologic atypia. Large lymphocytes are absent or rare. By in situ hybridization, EBV-positive cells are infrequently seen. MONDO:0019466
MONDO:0858152 grade ii lymphomatoid granulomatosis NCIT:C7932 MONDO:equivalentTo Grade II Lymphomatoid Granulomatosis Lymphomatoid granulomatosis characterized by the presence of occasional large lymphoid cells or immunoblasts in a polymorphous background. Necrosis is more commonly seen as compared to grade I lymphomatoid granulomatosis. By in situ hybridization, EBV-positive cells are readily seen. MONDO:0019466
MONDO:0858155 breast ductal carcinoma in situ, high grade NCIT:C7949 MONDO:equivalentTo Breast Ductal Carcinoma In Situ, High Grade Breast ductal carcinoma in situ characterized by the presence of neoplastic cells with severe dysplasia and the formation of micropapillary, cribriform, or solid patterns. The nuclei show marked pleomorphism and have prominent nucleoli. Mitotic activity is usually present. There is comedo-type of necrosis present in the ducts. The necrotic debris is surrounded by pleomorphic malignant cells. MONDO:0005023
MONDO:0858156 breast paget disease with invasive ductal carcinoma NCIT:C7951 MONDO:equivalentTo Breast Paget Disease with Invasive Ductal Carcinoma Paget disease involving the skin overlying the mammary gland, accompanied by invasive ductal breast carcinoma. MONDO:0006256
MONDO:0858161 childhood acute promyelocytic leukemia with t(15;17)(q24.1;q21.2); pml-rara NCIT:C7968 MONDO:equivalentTo Childhood Acute Promyelocytic Leukemia with t(15;17)(q24.1;q21.2); PML-RARA An acute promyelocytic leukemia with PML-RARA fusion occurring in children. MONDO:0012883
MONDO:0858166 distal bile duct adenocarcinoma NCIT:C7976 MONDO:equivalentTo Distal Bile Duct Adenocarcinoma An adenocarcinoma that arises from the common bile duct distal to the insertion of the cystic duct. MONDO:0002665
MONDO:0858169 carcinoma arising from craniopharyngioma NCIT:C79949 MONDO:equivalentTo Carcinoma Arising from Craniopharyngioma A rare condition characterized by the development of a carcinoma in a pre-existing craniopharyngioma. MONDO:0024878
MONDO:0858170 testicular mixed embryonal carcinoma and yolk sac tumor NCIT:C8001 MONDO:equivalentTo Testicular Mixed Embryonal Carcinoma and Yolk Sac Tumor A malignant non-seminomatous germ cell tumor arising from the testis. It is characterized by a mixture of embryonal carcinoma and yolk sac morphologic elements. Patients may present with painless or painful testicular swelling. MONDO:0003403
MONDO:0858171 testicular mixed yolk sac tumor and teratoma NCIT:C8002 MONDO:equivalentTo Testicular Mixed Yolk Sac Tumor and Teratoma A malignant non-seminomatous germ cell tumor arising from the testis. It is characterized by a mixture of yolk sac and teratomatous morphologic elements. Patients may present with painless or painful testicular swelling. MONDO:0003403
MONDO:0858172 testicular mixed yolk sac tumor and teratoma with seminoma NCIT:C8003 MONDO:equivalentTo Testicular Mixed Yolk Sac Tumor and Teratoma with Seminoma A malignant germ cell tumor arising from the testis. It is characterized by a mixture of yolk sac, teratomatous, and seminomatous morphologic elements. Patients may present with painless or painful testicular swelling. MONDO:0003120
MONDO:0858173 pancreatic somatostatin-producing neuroendocrine tumor NCIT:C8006 MONDO:equivalentTo Pancreatic Somatostatin-Producing Neuroendocrine Tumor A usually malignant, somatostatin producing neuroendocrine tumor, arising from the delta cells of the pancreas. It may or may not be associated with inappropriate secretion of somatostatin and an associated clinical syndrome. MONDO:0006976
MONDO:0858174 salivary gland low grade carcinoma NCIT:C8012 MONDO:equivalentTo Salivary Gland Low Grade Carcinoma A salivary gland carcinoma with low-grade histopathologic features. It includes the salivary gland polymorphous low grade adenocarcinoma, salivary gland low grade cribriform cystadenocarcinoma, and low grade salivary gland mucoepidermoid carcinoma. It usually follows a non-aggressive clinical course. MONDO:0000521
MONDO:0858175 lip basal cell carcinoma NCIT:C8014 MONDO:equivalentTo Lip Basal Cell Carcinoma A basal cell carcinoma arising from the lip. MONDO:0005341
MONDO:0858176 salivary gland intermediate grade mucoepidermoid carcinoma NCIT:C8017 MONDO:equivalentTo Salivary Gland Intermediate Grade Mucoepidermoid Carcinoma A salivary gland mucoepidermoid carcinoma with intermediate-grade histopathologic features. MONDO:0021009
MONDO:0858177 salivary gland high grade carcinoma NCIT:C8018 MONDO:equivalentTo Salivary Gland High Grade Carcinoma A usually aggressive salivary gland carcinoma with high-grade histopathologic features. It includes the salivary duct carcinoma, salivary gland oncocytic carcinoma, and high grade salivary gland mucoepidermoid carcinoma. MONDO:0000521
MONDO:0858178 salivary gland adenocarcinoma NCIT:C8021 MONDO:equivalentTo Salivary Gland Adenocarcinoma An adenocarcinoma arising from the salivary gland. It includes the salivary gland polymorphous low grade adenocarcinoma, salivary gland oncocytic carcinoma, salivary gland mucinous adenocarcinoma, salivary gland low grade cribriform cystadenocarcinoma, salivary gland cystadenocarcinoma, salivary gland basal cell adenocarcinoma, salivary gland acinic cell carcinoma, salivary duct carcinoma, and salivary gland adenocarcinoma not otherwise specified. MONDO:0000521
MONDO:0858179 salivary gland poorly differentiated squamous cell carcinoma NCIT:C8022 MONDO:equivalentTo Salivary Gland Poorly Differentiated Squamous Cell Carcinoma A poorly differentiated squamous cell carcinoma arising from the salivary gland. MONDO:0044740
MONDO:0858180 salivary gland undifferentiated carcinoma NCIT:C8024 MONDO:equivalentTo Salivary Gland Undifferentiated Carcinoma A salivary gland carcinoma characterized by the presence of undifferentiated, anaplastic malignant epithelial cells. MONDO:0005617
MONDO:0858182 diffuse large b-cell lymphoma, not otherwise specified NCIT:C80280 MONDO:equivalentTo Diffuse Large B-Cell Lymphoma, Not Otherwise Specified A term referring to a group of diffuse large B-cell lymphomas which are biologically heterogeneous. These lymphomas have a centroblastic, immunoblastic, or anaplastic morphology. MONDO:0018905
MONDO:0858183 diffuse large b-cell lymphoma associated with chronic inflammation NCIT:C80289 MONDO:equivalentTo Diffuse Large B-Cell Lymphoma Associated with Chronic Inflammation A diffuse large B-cell lymphoma arising in body cavities or narrow spaces of long standing chronic inflammation. The classic example is the pyothorax-associated lymphoma that arises in the pleural cavity of patients with a history of long standing pyothorax. MONDO:0018905
MONDO:0858184 progressive hairy cell leukemia initial treatment NCIT:C8029 MONDO:equivalentTo Progressive Hairy Cell Leukemia Initial Treatment A hairy cell leukemia requiring initial treatment because of the presence of signs of progression. Signs of progression include cytopenia (especially if symptomatic), increasing splenomegaly, and infectious complications. Therapy is not necessary if the patients are asymptomatic and the blood counts are maintained in an acceptable range. MONDO:0018935
MONDO:0858185 high grade b-cell lymphoma, not otherwise specified NCIT:C80291 MONDO:equivalentTo High Grade B-Cell Lymphoma, Not Otherwise Specified High-grade B-cell lymphoma with blastoid features or features between diffuse large B-cell lymphoma and Burkitt lymphoma that lacks MYC, BCL2, and BCL6 gene rearrangements. MONDO:0044889
MONDO:0858186 pediatric-type follicular lymphoma NCIT:C80297 MONDO:equivalentTo Pediatric-Type Follicular Lymphoma A nodal follicular lymphoma with favorable prognosis. It lacks BCL-2 rearrangement and 14;18 translocation. Nearly all cases are localized. It is usually seen in the pediatric population but similar lymphomas may occur in adults. MONDO:0018906
MONDO:0858189 monoclonal b-cell lymphocytosis NCIT:C80310 MONDO:equivalentTo Monoclonal B-Cell Lymphocytosis A monoclonal expansion of B-lymphocytes with or without the characteristic immunophenotype of chronic lymphocytic leukemia. It precedes virtually all cases of chronic lymphocytic leukemia/small lymphocytic lymphoma. MONDO:0004949
MONDO:0858190 b lymphoblastic leukemia/lymphoma, not otherwise specified NCIT:C80326 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma, Not Otherwise Specified B-lymphoblastic leukemias/lymphomas characterized by the absence of recurrent genetic abnormalities. MONDO:0004947
MONDO:0858191 b lymphoblastic leukemia/lymphoma with t(1;19)(q23;p13.3); tcf3-pbx1 NCIT:C80341 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma with t(1;19)(q23;p13.3); TCF3-PBX1 A precursor lymphoid neoplasm which is composed of B-lymphoblasts and carries a translocation between the E2A gene on chromosome 19 and the PBX1 gene on chromosome 1. MONDO:0035605
MONDO:0858205 regional adrenal gland pheochromocytoma NCIT:C8045 MONDO:equivalentTo Regional Adrenal Gland Pheochromocytoma A pheochromocytoma that has not spread to other regions. MONDO:0004974
MONDO:0858211 stage i ovarian germ cell tumor ajcc v6 and v7 NCIT:C8083 MONDO:equivalentTo Stage I Ovarian Germ Cell Tumor AJCC v6 and v7 Stage I includes: (T1, N0, M0). T1: Tumor limited to ovaries (one or both). N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th Eds.) MONDO:0018171
MONDO:0858212 stage ii ovarian germ cell tumor ajcc v6 and v7 NCIT:C8084 MONDO:equivalentTo Stage II Ovarian Germ Cell Tumor AJCC v6 and v7 Stage II includes: T2, N0, M0. T2: Tumor involves one or both ovaries with pelvic extension and/or implants. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0018171
MONDO:0858213 stage iii ovarian germ cell tumor ajcc v6 and v7 NCIT:C8085 MONDO:equivalentTo Stage III Ovarian Germ Cell Tumor AJCC v6 and v7 Stage III includes: T3, N0, M0. T3: Tumor involves one or both both ovaries with microscopically confirmed peritoneal metastasis outside pelvis. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0018171
MONDO:0858214 stage iv ovarian germ cell tumor ajcc v6 and v7 NCIT:C8086 MONDO:equivalentTo Stage IV Ovarian Germ Cell Tumor AJCC v6 and v7 Stage IV includes: Any T, Any N, M1. M1: Distant metastasis (excludes peritoneal metastasis). (AJCC 6th and 7th eds.) MONDO:0018171
MONDO:0858219 regional renal pelvis and ureter urothelial carcinoma NCIT:C8168 MONDO:equivalentTo Regional Renal Pelvis and Ureter Urothelial Carcinoma Urothelial carcinoma of the renal pelvis or ureter that has spread to adjacent tissues and/or regional lymph nodes but not to distant anatomic sites. MONDO:0020654
MONDO:0858221 buccal mucosa verrucous carcinoma NCIT:C8175 MONDO:equivalentTo Buccal Mucosa Verrucous Carcinoma A verrucous carcinoma of the oral cavity that arises from the buccal mucosa. MONDO:0021538
MONDO:0858222 fibroblastic reticular cell sarcoma NCIT:C81758 MONDO:equivalentTo Fibroblastic Reticular Cell Sarcoma A very rare dendritic cell sarcoma affecting the lymph nodes, spleen, and soft tissues. Morphologically it is similar to the interdigitating dendritic cell sarcoma or follicular dendritic cell sarcoma. The tumor cells are positive for cytokeratin and CD68. MONDO:0006247
MONDO:0858224 disseminated juvenile xanthogranuloma NCIT:C81772 MONDO:equivalentTo Disseminated Juvenile Xanthogranuloma Juvenile xanthogranuloma disseminated to extracutaneous sites including mucosal surfaces, lung, central nervous system, pituitary, lymph nodes, eye, liver, and bone marrow. It is characterized by the presence of lipid-laden, foamy histiocytes and Touton-type giant cells forming nodules in the affected anatomic sites. MONDO:0006247
MONDO:0858225 oral cavity adenoid cystic carcinoma NCIT:C8179 MONDO:equivalentTo Oral Cavity Adenoid Cystic Carcinoma An adenoid cystic carcinoma arising from the minor salivary glands in the oral cavity. MONDO:0004971
MONDO:0858240 mixed phenotype acute leukemia, b/myeloid NCIT:C82212 MONDO:equivalentTo Mixed Phenotype Acute Leukemia, B/Myeloid A rare mixed phenotype acute leukemia in which the blasts express B-lymphoid and myeloid lineage markers but are negative for KMT2A rearrangement and t(9;22)(q34;q11.2) translocation. The prognosis is usually unfavorable. MONDO:0020743
MONDO:0858241 mixed phenotype acute leukemia, t/myeloid NCIT:C82213 MONDO:equivalentTo Mixed Phenotype Acute Leukemia, T/Myeloid A rare mixed phenotype acute leukemia in which the blasts express T-lymphoid and myeloid lineage markers but are negative for KMT2A rearrangement and t(9;22)(q34;q11.2) translocation. The prognosis is usually unfavorable. MONDO:0020743
MONDO:0858242 natural killer cell lymphoblastic leukemia/lymphoma NCIT:C82217 MONDO:equivalentTo Natural Killer Cell Lymphoblastic Leukemia/Lymphoma A precursor lymphoid neoplasm that expresses CD56 and immature T-cell markers, lacks B-lymphoid and myeloid markers, and has immunoglobulin and T-cell receptor genes in the germline configuration. MONDO:0003538
MONDO:0858245 myelodysplastic/myeloproliferative neoplasm post cytotoxic therapy NCIT:C82397 MONDO:equivalentTo Myelodysplastic/Myeloproliferative Neoplasm Post Cytotoxic Therapy A myelodysplastic/myeloproliferative neoplasm arising as a result of the mutagenic effect of chemotherapy agents and/or radiation that are used for the treatment of neoplastic or non-neoplastic disorders. MONDO:0006311
MONDO:0858246 acute myeloid leukemia with myelodysplasia-related gene mutations NCIT:C82430 MONDO:equivalentTo Acute Myeloid Leukemia with Myelodysplasia-Related Gene Mutations A group of acute myeloid leukemias characterized by the presence of gene mutations that are associated with myelodysplasia. MONDO:0100409
MONDO:0858249 de novo myelodysplastic syndrome NCIT:C8253 MONDO:equivalentTo de novo Myelodysplastic Syndrome A primary myelodysplastic syndrome not associated with prior radiation or chemotherapy treatment. MONDO:0018881
MONDO:0858251 adult anaplastic astrocytoma NCIT:C8257 MONDO:equivalentTo Adult Anaplastic Astrocytoma An astrocytoma occurring in adults that is characterized by the presence of high mitotic activity, cytologic atypia, and architectural distortion. MONDO:0004320
MONDO:0858252 refractory neutropenia NCIT:C82593 MONDO:equivalentTo Refractory Neutropenia A myelodysplastic syndrome characterized by the presence of at least 10% dysplastic neutrophils in the bone marrow or the peripheral blood. MONDO:0005272
MONDO:0858253 refractory thrombocytopenia NCIT:C82594 MONDO:equivalentTo Refractory Thrombocytopenia A myelodysplastic syndrome characterized by the presence of at least 10% dysplastic megakaryocytes, found within at least 30 megakaryocytes examined in the bone marrow. MONDO:0005272
MONDO:0858254 myelodysplastic syndrome with excess blasts and fibrosis NCIT:C82595 MONDO:equivalentTo Myelodysplastic Syndrome with Excess Blasts and Fibrosis Myelodysplastic syndrome with excess blasts associated with significant reticulin fibrosis of the bone marrow. MONDO:0019454
MONDO:0858256 myelodysplastic/myeloproliferative neoplasm with ring sideroblasts and thrombocytosis, not otherwise specified NCIT:C82616 MONDO:equivalentTo Myelodysplastic/Myeloproliferative Neoplasm with Ring Sideroblasts and Thrombocytosis, Not Otherwise Specified A myelodysplastic/myeloproliferative neoplasm characterized by marked thrombocytosis, anemia, erythroid lineage dysplasia, presence or absence of multilineage dysplasia, 15% or more ring sideroblasts, blasts less than 5% in bone marrow and less than 1% in peripheral blood, absence of BCR/ABL fusion, absence of SF3B1 mutation, absence of genetic abnormalities associated with myeloid/lymphoid neoplasms with eosinophilia and tyrosine kinase gene fusions, and no history of other myelodysplastic/myeloproliferative neoplasms or myeloproliferative neoplasms and myelodysplastic syndromes. MONDO:0006311
MONDO:0858257 adult cholangiocarcinoma NCIT:C8265 MONDO:equivalentTo Adult Cholangiocarcinoma A cholangiocarcinoma occurring in adults. MONDO:0019087
MONDO:0858258 meyerson nevus NCIT:C82862 MONDO:equivalentTo Meyerson Nevus A benign melanocytic nevus surrounded by eczematous changes. MONDO:0044794
MONDO:0858259 cystic oncocytic neoplasm NCIT:C82890 MONDO:equivalentTo Cystic Oncocytic Neoplasm An oncocytoma with cystic degenerative changes. MONDO:0010795
MONDO:0858265 duodenal extraskeletal osteosarcoma NCIT:C82972 MONDO:equivalentTo Duodenal Extraskeletal Osteosarcoma An extraskeletal osteosarcoma affecting the duodenum. MONDO:0000920
MONDO:0858272 cellular pleomorphic adenoma NCIT:C83174 MONDO:equivalentTo Cellular Pleomorphic Adenoma A pleomorphic adenoma with increased cellularity. MONDO:0008401
MONDO:0858275 atypical hyperplasia NCIT:C8355 MONDO:equivalentTo Atypical Hyperplasia
MONDO:0858277 low grade intraepithelial neoplasia NCIT:C8367 MONDO:equivalentTo Low Grade Intraepithelial Neoplasia A precancerous neoplastic process that affects the squamous, glandular, or transitional cell epithelium without evidence of invasion. It is characterized by the presence of mild epithelial dysplasia. MONDO:0024474
MONDO:0858280 lymphangiomatosis NCIT:C8373 MONDO:equivalentTo Lymphangiomatosis A lymphangioma affecting several anatomic sites. MONDO:0036870
MONDO:0858283 fibrohistiocytic neoplasm NCIT:C8402 MONDO:equivalentTo Fibrohistiocytic Neoplasm A benign, intermediate, or malignant mesenchymal neoplasm composed of fibrohistiocytic cells, spindle fibroblastic cells, and histiocytes, in a storiform pattern. MONDO:0002616
MONDO:0858284 benign supraglottis neoplasm NCIT:C8414 MONDO:equivalentTo Benign Supraglottis Neoplasm A neoplasm that arises from the supraglottis and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0004427
MONDO:0858285 benign bartholin gland neoplasm NCIT:C8418 MONDO:equivalentTo Benign Bartholin Gland Neoplasm A non-metastasizing neoplasm that arises from the Bartholin gland. Representative examples include adenoma and adenomyoma. MONDO:0000643
MONDO:0858286 diffuse malignant mesothelioma NCIT:C8420 MONDO:equivalentTo Diffuse Malignant Mesothelioma A diffuse malignant neoplasm that arises from mesothelial cells, usually in the pleura or peritoneum. Histologic variants include biphasic, epithelioid, sarcomatoid, and desmoplastic mesothelioma. MONDO:0006292
MONDO:0858287 renal benign mesenchymoma NCIT:C84256 MONDO:equivalentTo Renal Benign Mesenchymoma A benign mesenchymoma arising from the kidney. MONDO:0002382
MONDO:0858288 diffuse neurofibroma NCIT:C8426 MONDO:equivalentTo Diffuse Neurofibroma A rare neurofibroma with an infiltrative growth pattern. It involves the skin and subcutaneous tissue and grows in a plaque-like fashion. Malignant transformation is rare. MONDO:0016755
MONDO:0858289 anaplastic astroblastoma, mn1-altered NCIT:C84347 MONDO:equivalentTo Anaplastic Astroblastoma, MN1-Altered An astroblastoma, MN1-altered, characterized by the presence of high mitotic activity, cytologic atypia, and architectural distortion. MONDO:0016707
MONDO:0858299 asbestos-related lung disorder NCIT:C84472 MONDO:equivalentTo Asbestos-Related Lung Disorder A disorder affecting the lungs due to asbestos exposure. Examples include asbestosis and lung carcinoma.
MONDO:0858304 central nervous system cavernous hemangioma NCIT:C84621 MONDO:equivalentTo Central Nervous System Cavernous Hemangioma A cavernous hemangioma arising from the central nervous system. MONDO:0003241
MONDO:0858314 invasive malignant neoplasm NCIT:C8505 MONDO:equivalentTo Invasive Malignant Neoplasm Cancer that has spread beyond the layer of tissue in which it developed and is growing into surrounding, healthy tissues. MONDO:0004992
MONDO:0858316 refractory carcinoma NCIT:C8511 MONDO:equivalentTo Refractory Carcinoma A carcinoma that does not respond to treatment. MONDO:0036501
MONDO:0858321 locally advanced malignant neoplasm NCIT:C8524 MONDO:equivalentTo Locally Advanced Malignant Neoplasm A malignant neoplasm that has spread from its original site of growth to nearby tissues or lymph nodes. MONDO:0024880
MONDO:0858324 benign respiratory system neoplasm NCIT:C8531 MONDO:equivalentTo Benign Respiratory System Neoplasm A neoplasm that arises from the respiratory system and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0005165
MONDO:0858330 metastatic malignant neoplasm in the nervous system NCIT:C8547 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Nervous System The spread of a malignant neoplasm to the nervous system. This may be from a primary nervous system malignant neoplasm, or from a malignant neoplasm at a distant site. MONDO:0005872
MONDO:0858334 metastatic malignant neoplasm in the retina NCIT:C8555 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Retina A malignant neoplasm that has spread to the retina from another anatomic site. MONDO:0003072
MONDO:0858337 metastatic malignant neoplasm of unknown primary NCIT:C8566 MONDO:equivalentTo Metastatic Malignant Neoplasm of Unknown Primary The spread of a malignant neoplasm from an unknown primary to another region remote from the primary site. MONDO:0024880
MONDO:0858339 invasive cervical carcinoma NCIT:C8577 MONDO:equivalentTo Invasive Cervical Carcinoma A carcinoma that arises from the cervix and invades into the stromal tissue. MONDO:0040677
MONDO:0858341 precancerous polyp NCIT:C8587 MONDO:equivalentTo Precancerous Polyp A polyp with severe dysplastic features. MONDO:0021075
MONDO:0858342 leukemic phase of lymphoma NCIT:C8594 MONDO:equivalentTo Leukemic Phase of Lymphoma A usually terminal event in the clinical course of lymphomas. The term indicates the presence of atypical, clonal (malignant) lymphocytes (lymphoma cells) in the peripheral blood. MONDO:0005402
MONDO:0858343 postcricoid carcinoma NCIT:C8595 MONDO:equivalentTo Postcricoid Carcinoma A carcinoma of the hypopharynx that arises from the postcricoid region. MONDO:0005216
MONDO:0858346 anaplastic (malignant) intraspinal meningioma NCIT:C8605 MONDO:equivalentTo Anaplastic (Malignant) Intraspinal Meningioma An anaplastic (malignant) meningioma involving the spinal meninges. MONDO:0020635
MONDO:0858350 malignant hepatobiliary neoplasm NCIT:C8609 MONDO:equivalentTo Malignant Hepatobiliary Neoplasm A malignant neoplasm that affects the liver parenchyma, bile ducts, and gallbladder. Representative examples include hepatocellular carcinoma, intrahepatic and extrahepatic cholangiocarcinoma, and gallbladder carcinoma. MONDO:0002514
MONDO:0858351 metastatic malignant neoplasm in the adrenal gland NCIT:C8610 MONDO:equivalentTo Metastatic Malignant Neoplasm in the Adrenal Gland A malignant tumor that has spread to the adrenal gland from an adjacent or distant anatomic site. The majority of cases are metastatic carcinomas, and less frequently lymphomas. MONDO:0002817
MONDO:0858363 stage i t lymphoblastic leukemia/lymphoma NCIT:C8697 MONDO:equivalentTo Stage I T Lymphoblastic Leukemia/Lymphoma Ann Arbor Classification: Stage I: Involvement of a single lymph node region (I); or localized involvement of a single extralymphatic organ or site in the absence of any lymph node involvement (IE) (Rare in Hodgkin lymphoma). MONDO:0003537
MONDO:0858364 stage ii t lymphoblastic leukemia/lymphoma NCIT:C8698 MONDO:equivalentTo Stage II T Lymphoblastic Leukemia/Lymphoma Ann Arbor Classification: Stage II: Involvement of two or more lymph node regions on the same side of the diaphragm (II); or localized involvement of a single extralymphatic organ or site in a with regional lymph node involvement with or without involvement of other lymph node regions on the same side of the diaphragm (IIE). MONDO:0003537
MONDO:0858365 stage iii t lymphoblastic leukemia/lymphoma NCIT:C8699 MONDO:equivalentTo Stage III T Lymphoblastic Leukemia/Lymphoma Ann Arbor Classification: Stage III: Involvement of lymph node regions on both sides of the diaphragm (III), which also may be accompanied by extralymphatic extension in association with adjacent lymph node involvement (IIIE) or by involvement of the spleen (IIIS) or both (IIIE,S). MONDO:0003537
MONDO:0858366 stage iv t lymphoblastic leukemia/lymphoma NCIT:C8700 MONDO:equivalentTo Stage IV T Lymphoblastic Leukemia/Lymphoma Ann Arbor Classification: Stage IV: Diffuse or disseminated involvement of one or more extralymphatic organs, with or without associated lymph node involvement; or isolated extralymphatic organ involvement in the absence of adjacent regional lymph node involvement, but in conjunction with disease in distant site(s); or any involvement of the liver or bone marrow, or nodular involvement of the lungs(s). MONDO:0003537
MONDO:0858370 metastatic malignant hemangiopericytoma NCIT:C8709 MONDO:equivalentTo Metastatic Malignant Hemangiopericytoma A malignant hemangiopericytoma which has spread to another anatomical site. MONDO:0009330
MONDO:0858371 primary malignant hemangiopericytoma NCIT:C8710 MONDO:equivalentTo Primary Malignant Hemangiopericytoma A rare malignant mesenchymal neoplasm that is believed to have its origin in smooth muscle derived pericytes without evidence of metastases. MONDO:0009330
MONDO:0858381 stage i ovarian choriocarcinoma NCIT:C8730 MONDO:equivalentTo Stage I Ovarian Choriocarcinoma Stage I includes: T1, N0, M0. T1: Tumor limited to ovaries (one or both). N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0003507
MONDO:0858382 stage ii ovarian choriocarcinoma NCIT:C8731 MONDO:equivalentTo Stage II Ovarian Choriocarcinoma Stage II includes: T2, N0, M0. T2: Tumor involves one or both ovaries with pelvic extension and/or implants. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0003507
MONDO:0858383 stage iii ovarian choriocarcinoma NCIT:C8732 MONDO:equivalentTo Stage III Ovarian Choriocarcinoma Stage III includes: T3, N0, M0. T3: Tumor involves one or both both ovaries with microscopically confirmed peritoneal metastasis outside pelvis. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0003507
MONDO:0858384 stage iv ovarian choriocarcinoma NCIT:C8733 MONDO:equivalentTo Stage IV Ovarian Choriocarcinoma Stage IV includes: Any T, Any N, M1. M1: Distant metastasis (excludes peritoneal metastasis). (AJCC 6th and 7th eds.) MONDO:0003507
MONDO:0858395 stage i pharyngeal cancer NCIT:C8768 MONDO:equivalentTo Stage I Pharyngeal Cancer Stage I carcinoma of the pharynx according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0021345
MONDO:0858396 stage ii pharyngeal cancer NCIT:C8769 MONDO:equivalentTo Stage II Pharyngeal Cancer Stage II carcinoma of the pharynx according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0021345
MONDO:0858397 stage iii pharyngeal cancer NCIT:C8770 MONDO:equivalentTo Stage III Pharyngeal Cancer Stage III carcinoma of the pharynx according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0021345
MONDO:0858398 stage iv pharyngeal cancer NCIT:C8771 MONDO:equivalentTo Stage IV Pharyngeal Cancer Stage IV carcinoma of the pharynx according to the American Joint Committee on Cancer, 6th, 7th, and 8th editions. MONDO:0021345
MONDO:0858443 b lymphoblastic lymphoma NCIT:C8868 MONDO:equivalentTo B Lymphoblastic Lymphoma An uncommon type of lymphoma. It constitutes approximately 10% of cases of lymphoblastic lymphoma. Approximately 75% of cases reported in a literature review involved patients who were less than 18 years of age. The most commonly affected sites are the skin, bone, soft tissue, and lymph nodes. It has a high remission rate with a median survival of approximately 60 months. (WHO, 2001) MONDO:0000873
MONDO:0858446 extragonadal embryonal carcinoma NCIT:C8880 MONDO:equivalentTo Extragonadal Embryonal Carcinoma An embryonal carcinoma that develops as a primary tumor in an anatomic site other than the testis or ovary. MONDO:0003578
MONDO:0858459 pediatric disorder NCIT:C89328 MONDO:equivalentTo Pediatric Disorder A non-neoplastic or neoplastic disorder which occurs during infancy, childhood, or adolescence.
MONDO:0858464 fundic gland polyp NCIT:C8961 MONDO:equivalentTo Fundic Gland Polyp The most common gastric polyp in the Western hemisphere. The lesion consists of a localized hyperplasia of the deep epithelial compartment of the oxyntic mucosa, with variable degrees of cystic dilatation. Malignant transformation is the exception. (WHO, 2000) MONDO:0006221
MONDO:0858471 oral neoplasm NCIT:C8989 MONDO:equivalentTo Oral Neoplasm A benign or malignant neoplasm involving the oral cavity and/or the lips. MONDO:0005586
MONDO:0858472 malignant mastocytosis NCIT:C8991 MONDO:equivalentTo Malignant Mastocytosis A group of malignant mast cell disorders including aggressive systemic mastocytosis, mast cell leukemia, mast cell sarcoma, and systemic mastocytosis with an associated myeloid neoplasm. Individuals with advanced systemic mastocytosis have a reduced life expectancy, with median survival measured in months to years. MONDO:0004992
MONDO:0858473 benign adrenal cortical neoplasm NCIT:C9004 MONDO:equivalentTo Benign Adrenal Cortical Neoplasm A neoplasm that arises from the adrenal cortex and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021511
MONDO:0858474 acute myelomonocytic leukemia with abnormal eosinophils NCIT:C9020 MONDO:equivalentTo Acute Myelomonocytic Leukemia with Abnormal Eosinophils Acute myelomonocytic leukemia characterized by the presence of abnormal bone marrow eosinophils. It is associated with inv(16)(p13.1;q22) or t(16;16)(p13.1;q22). It has a favorable prognosis. MONDO:0018871
MONDO:0858475 sarcoma by fnclcc grade NCIT:C9023 MONDO:equivalentTo Sarcoma by FNCLCC Grade Grading of sarcomas according to the French Federation of Cancer Centers Sarcoma Group (FNCLCC). This sarcoma grading system is based on three factors: differentiation, mitotic count, and tumor necrosis. The scores for each factor are added to determine the grade (1 to 3) for the sarcoma. MONDO:0005089
MONDO:0858477 atypical cartilaginous tumor/chondrosarcoma, grade 1 NCIT:C9027 MONDO:equivalentTo Atypical Cartilaginous Tumor/Chondrosarcoma, Grade 1 A low-grade chondrosarcoma characterized by the presence of moderate cellularity, hyperchromatic and plump nuclei of uniform size, and occasional binucleated cells. Mitotic figures are absent. MONDO:0008977
MONDO:0858479 renal cell cancer by ajcc v6 stage NCIT:C90343 MONDO:equivalentTo Renal Cell Cancer by AJCC v6 Stage A term that refers to the staging of renal cell cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0005549
MONDO:0858480 bladder cancer by ajcc v6 stage NCIT:C90344 MONDO:equivalentTo Bladder Cancer by AJCC v6 Stage A term that refers to the staging of bladder cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0004986
MONDO:0858481 vulvar cancer by ajcc v6 stage NCIT:C90345 MONDO:equivalentTo Vulvar Cancer by AJCC v6 Stage A term that refers to the staging of vulvar carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0005215
MONDO:0858482 vaginal cancer by ajcc v6 stage NCIT:C90347 MONDO:equivalentTo Vaginal Cancer by AJCC v6 Stage A term that refers to the staging of vaginal cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0015867
MONDO:0858483 adult angiosarcoma NCIT:C9040 MONDO:equivalentTo Adult Angiosarcoma An angiosarcoma occurring in the adult population. MONDO:0016982
MONDO:0858485 extensive stage lung small cell carcinoma NCIT:C9049 MONDO:equivalentTo Extensive Stage Lung Small Cell Carcinoma Small cell lung carcinoma which has spread beyond one hemi-thorax and the regional lymph nodes. MONDO:0008433
MONDO:0858486 cervical cancer by ajcc v6 stage NCIT:C90493 MONDO:equivalentTo Cervical Cancer by AJCC v6 Stage A term that refers to the staging of cervical cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0005131
MONDO:0858487 uterine corpus cancer by ajcc v6 stage NCIT:C90494 MONDO:equivalentTo Uterine Corpus Cancer by AJCC v6 Stage A term that refers to the staging of uterine corpus cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0006003
MONDO:0858488 fallopian tube cancer by ajcc v6 stage NCIT:C90499 MONDO:equivalentTo Fallopian Tube Cancer by AJCC v6 Stage A term that refers to the staging of fallopian tube carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0006206
MONDO:0858489 esophageal cancer by ajcc v6 stage NCIT:C90500 MONDO:equivalentTo Esophageal Cancer by AJCC v6 Stage A term that refers to the staging of esophageal carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0019086
MONDO:0858490 gastric cancer by ajcc v6 stage NCIT:C90503 MONDO:equivalentTo Gastric Cancer by AJCC v6 Stage MONDO:0004950
MONDO:0858491 colorectal cancer by ajcc v6 stage NCIT:C90506 MONDO:equivalentTo Colorectal Cancer by AJCC v6 Stage A term that refers to the staging of colorectal carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0024331
MONDO:0858493 hepatocellular carcinoma by ajcc v6 stage NCIT:C90510 MONDO:equivalentTo Hepatocellular Carcinoma by AJCC v6 Stage A term that refers to the staging of hepatocellular carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0007256
MONDO:0858494 gallbladder cancer by ajcc v6 stage NCIT:C90512 MONDO:equivalentTo Gallbladder Cancer by AJCC v6 Stage A term that refers to the staging of gallbladder cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0003220
MONDO:0858495 breast cancer by ajcc v6 stage NCIT:C90513 MONDO:equivalentTo Breast Cancer by AJCC v6 Stage A term that refers to the staging of breast cancer according to the American Joint Committee on Cancer, 6th edition. MONDO:0004989
MONDO:0858496 cutaneous melanoma by ajcc v6 stage NCIT:C90514 MONDO:equivalentTo Cutaneous Melanoma by AJCC v6 Stage A term that refers to the staging of cutaneous melanoma, following the rules of the TNM AJCC v6 classification system. MONDO:0005012
MONDO:0858497 lung cancer by ajcc v6 stage NCIT:C90519 MONDO:equivalentTo Lung Cancer by AJCC v6 Stage A term that refers to the staging of lung carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0005138
MONDO:0858498 penile cancer by ajcc v6 stage NCIT:C90520 MONDO:equivalentTo Penile Cancer by AJCC v6 Stage A term that refers to the staging of penile carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0006360
MONDO:0858499 prostate cancer by ajcc v6 stage NCIT:C90521 MONDO:equivalentTo Prostate Cancer by AJCC v6 Stage A term that refers to the staging of prostate carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0005159
MONDO:0858502 pharyngeal carcinoma by ajcc v6 stage NCIT:C90525 MONDO:equivalentTo Pharyngeal Carcinoma by AJCC v6 Stage A term that refers to the staging of pharyngeal carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0021345
MONDO:0858503 laryngeal cancer by ajcc v6 stage NCIT:C90527 MONDO:equivalentTo Laryngeal Cancer by AJCC v6 Stage A term that refers to the staging of laryngeal carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0002358
MONDO:0858504 sinonasal cancer by ajcc v6 stage NCIT:C90528 MONDO:equivalentTo Sinonasal Cancer by AJCC v6 Stage A term that refers to the staging of nasal cavity and paranasal sinus carcinoma according to the American Joint Committee on Cancer, 6th edition. MONDO:0056819
MONDO:0858510 kaposi sarcoma related to immunosuppressive treatment NCIT:C9113 MONDO:equivalentTo Kaposi Sarcoma Related to Immunosuppressive Treatment A Kaposi sarcoma that develops after immunosuppressive treatment. MONDO:0005188
MONDO:0858511 renal cell cancer by ajcc v7 stage NCIT:C91201 MONDO:equivalentTo Renal Cell Cancer by AJCC v7 Stage A term that refers to the staging of renal cell cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0005549
MONDO:0858512 bladder cancer by ajcc v7 stage NCIT:C91202 MONDO:equivalentTo Bladder Cancer by AJCC v7 Stage A term that refers to the staging of bladder cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0004986
MONDO:0858513 vulvar cancer by ajcc v7 stage NCIT:C91203 MONDO:equivalentTo Vulvar Cancer by AJCC v7 Stage A term that refers to the staging of vulvar carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0005215
MONDO:0858514 vaginal cancer by ajcc v7 stage NCIT:C91204 MONDO:equivalentTo Vaginal Cancer by AJCC v7 Stage A term that refers to the staging of vaginal cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0015867
MONDO:0858515 cervical cancer by ajcc v7 stage NCIT:C91208 MONDO:equivalentTo Cervical Cancer by AJCC v7 Stage A term that refers to the staging of cervical cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0005131
MONDO:0858516 uterine corpus cancer by ajcc v7 stage NCIT:C91218 MONDO:equivalentTo Uterine Corpus Cancer by AJCC v7 Stage A term that refers to the staging of uterine corpus cancer (carcinoma or carcinosarcoma) according to the American Joint Committee on Cancer, 7th edition. MONDO:0006003
MONDO:0858517 fallopian tube cancer by ajcc v7 stage NCIT:C91219 MONDO:equivalentTo Fallopian Tube Cancer by AJCC v7 Stage A term that refers to the staging of fallopian tube carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0006206
MONDO:0858518 esophageal cancer by ajcc v7 stage NCIT:C91221 MONDO:equivalentTo Esophageal Cancer by AJCC v7 Stage A term that refers to the staging of esophageal carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0019086
MONDO:0858519 gastric cancer by ajcc v7 stage NCIT:C91222 MONDO:equivalentTo Gastric Cancer by AJCC v7 Stage A term that refers to the staging of gastric carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0004950
MONDO:0858520 colorectal cancer by ajcc v7 stage NCIT:C91223 MONDO:equivalentTo Colorectal Cancer by AJCC v7 Stage A term that refers to the staging of colorectal carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0024331
MONDO:0858522 hepatocellular carcinoma by ajcc v7 stage NCIT:C91228 MONDO:equivalentTo Hepatocellular Carcinoma by AJCC v7 Stage A term that refers to the staging of hepatocellular carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0007256
MONDO:0858523 gallbladder cancer by ajcc v7 stage NCIT:C91229 MONDO:equivalentTo Gallbladder Cancer by AJCC v7 Stage A term that refers to the staging of gallbladder cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0003220
MONDO:0858524 breast cancer by ajcc v7 stage NCIT:C91230 MONDO:equivalentTo Breast Cancer by AJCC v7 Stage A term that refers to the staging of breast cancer according to the American Joint Committee on Cancer, 7th edition. MONDO:0004989
MONDO:0858525 cutaneous melanoma by ajcc v7 stage NCIT:C91231 MONDO:equivalentTo Cutaneous Melanoma by AJCC v7 Stage A term that refers to the staging of cutaneous melanoma, following the rules of the TNM AJCC v7 classification system. MONDO:0005012
MONDO:0858526 lung cancer by ajcc v7 stage NCIT:C91232 MONDO:equivalentTo Lung Cancer by AJCC v7 Stage A term that refers to the staging of lung carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0005138
MONDO:0858527 prostate cancer by ajcc v7 stage NCIT:C91233 MONDO:equivalentTo Prostate Cancer by AJCC v7 Stage A term that refers to the staging of prostate carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0005159
MONDO:0858528 penile cancer by ajcc v7 stage NCIT:C91234 MONDO:equivalentTo Penile Cancer by AJCC v7 Stage A term that refers to the staging of penile carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0006360
MONDO:0858531 pharyngeal carcinoma by ajcc v7 stage NCIT:C91252 MONDO:equivalentTo Pharyngeal Carcinoma by AJCC v7 Stage A term that refers to the staging of pharyngeal carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0021345
MONDO:0858532 sinonasal cancer by ajcc v7 stage NCIT:C91255 MONDO:equivalentTo Sinonasal Cancer by AJCC v7 Stage A term that refers to the staging of nasal cavity and paranasal sinus carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0056819
MONDO:0858533 laryngeal cancer by ajcc v7 stage NCIT:C91256 MONDO:equivalentTo Laryngeal Cancer by AJCC v7 Stage A term that refers to the staging of laryngeal carcinoma according to the American Joint Committee on Cancer, 7th edition. MONDO:0002358
MONDO:0858534 chronic myeloid leukemia, philadelphia chromosome positive, bcr-abl1 positive NCIT:C9128 MONDO:equivalentTo Chronic Myeloid Leukemia, Philadelphia Chromosome Positive, BCR-ABL1 Positive A chronic myeloid leukemia characterized by the t(9;22)(q34;q11) chromosomal translocation, resulting in the presence of the Philadelphia chromosome and the BCR-ABL1 fusion gene. MONDO:0024685
MONDO:0858535 adult rhabdomyosarcoma NCIT:C9130 MONDO:equivalentTo Adult Rhabdomyosarcoma An aggressive malignant mesenchymal neoplasm arising from skeletal muscle in adults. MONDO:0005212
MONDO:0858536 invasive breast carcinoma of no special type with predominant intraductal component NCIT:C9132 MONDO:equivalentTo Invasive Breast Carcinoma of No Special Type with Predominant Intraductal Component An invasive breast carcinoma of no special type characterized by the presence of a predominant ductal carcinoma in situ component and a minor component of invasive carcinoma. MONDO:0004953
MONDO:0858537 invasive breast lobular carcinoma with predominant in situ component NCIT:C9136 MONDO:equivalentTo Invasive Breast Lobular Carcinoma with Predominant In Situ Component A breast carcinoma characterized by the presence of a predominant lobular carcinoma in situ component and a minor component of invasive carcinoma. MONDO:0005051
MONDO:0858538 adult acute myeloid leukemia NCIT:C9154 MONDO:equivalentTo Adult Acute Myeloid Leukemia An acute myeloid leukemia occurring in adults. MONDO:0018874
MONDO:0858543 testicular mixed embryonal carcinoma and yolk sac tumor with seminoma NCIT:C9172 MONDO:equivalentTo Testicular Mixed Embryonal Carcinoma and Yolk Sac Tumor with Seminoma A malignant germ cell tumor arising from the testis. It is characterized by a mixture of embryonal carcinoma, yolk sac, and seminomatous morphologic elements. Patients may present with painless or painful testicular swelling. MONDO:0003120
MONDO:0858546 good prognosis metastatic gestational trophoblastic tumor NCIT:C9177 MONDO:equivalentTo Good Prognosis Metastatic Gestational Trophoblastic Tumor Metastatic gestational trophoblastic tumor in which risk factors are absent. MONDO:0018944
MONDO:0858547 poor prognosis metastatic gestational trophoblastic tumor NCIT:C9178 MONDO:equivalentTo Poor Prognosis Metastatic Gestational Trophoblastic Tumor Metastatic gestational trophoblastic tumor in which risk factors are present. MONDO:0018944
MONDO:0858549 intraocular schwannoma NCIT:C92182 MONDO:equivalentTo Intraocular Schwannoma A benign schwannoma occurring in the eye. MONDO:0021454
MONDO:0858550 esophageal malignant peripheral nerve sheath tumor NCIT:C92185 MONDO:equivalentTo Esophageal Malignant Peripheral Nerve Sheath Tumor A malignant peripheral nerve sheath tumor that affects the esophageal wall. MONDO:0001204
MONDO:0858551 intraocular malignant peripheral nerve sheath tumor NCIT:C92186 MONDO:equivalentTo Intraocular Malignant Peripheral Nerve Sheath Tumor A malignant peripheral nerve sheath tumor that occurs in the intraocular area. MONDO:0002236
MONDO:0858558 non-hematologic malignancy NCIT:C9226 MONDO:equivalentTo Non-Hematologic Malignancy A malignant neoplasm that arises from a site other than the bone marrow and lymphoid tissue. MONDO:0004992
MONDO:0858562 recurrent malignant hemangiopericytoma NCIT:C9254 MONDO:equivalentTo Recurrent Malignant Hemangiopericytoma A rare malignant mesenchymal neoplasm, believed to have its origin in smooth muscle derived pericytes, which has recurred after treatment. MONDO:0009330
MONDO:0858563 multifocal glioblastomas NCIT:C92549 MONDO:equivalentTo Multifocal Glioblastomas The occurrence of multiple and independent glioblastomas that are unrelated to inherited neoplastic syndromes. MONDO:0018177
MONDO:0858565 glioneuronal tumor with neuropil-like islands NCIT:C92550 MONDO:equivalentTo Glioneuronal Tumor with Neuropil-Like Islands A rare, WHO grade II or III infiltrating astrocytoma characterized by the presence of sharply demarcated foci, composed of a neuropil-like matrix. MONDO:0019781
MONDO:0858569 anaplastic medulloblastoma NCIT:C92625 MONDO:equivalentTo Anaplastic Medulloblastoma A medulloblastoma characterized by marked nuclear pleomorphism, and high mitotic activity. MONDO:0007959
MONDO:0858573 malignant peripheral nerve sheath tumor with mesenchymal differentiation NCIT:C92647 MONDO:equivalentTo Malignant Peripheral Nerve Sheath Tumor with Mesenchymal Differentiation A malignant peripheral nerve sheath tumor characterized by the presence of mesenchymal differentiation. Representative example is the malignant Triton tumor which contains a rhabdomyosarcomatous component. MONDO:0017827
MONDO:0858574 mycosis fungoides and sezary syndrome NCIT:C9265 MONDO:equivalentTo Mycosis Fungoides and Sezary Syndrome Mature T and NK neoplasms predominantly affecting the skin and the peripheral blood. Peripheral blood involvement by abnormal T-cells (cerebriform cells) is a late manifestation of mycosis fungoides, whereas it is the presenting finding in Sezary syndrome. MONDO:0000430
MONDO:0858580 advanced malignant neoplasm NCIT:C9270 MONDO:equivalentTo Advanced Malignant Neoplasm A malignant neoplasm that has spread extensively to other anatomic sites or is no longer responding to treatment. MONDO:0024880
MONDO:0858584 lymphocyte-depleted classic hodgkin lymphoma NCIT:C9283 MONDO:equivalentTo Lymphocyte-Depleted Classic Hodgkin Lymphoma A diffuse subtype of classic Hodgkin lymphoma which is rich in Hodgkin and Reed-Sternberg cells and/or depleted in non-neoplastic lymphocytes. (WHO, 2008) MONDO:0009348
MONDO:0858585 central nervous system histiocytic and dendritic cell neoplasm NCIT:C92944 MONDO:equivalentTo Central Nervous System Histiocytic and Dendritic Cell Neoplasm A neoplasm that originates from histiocytes and accessory cells and affects the central nervous system. It is usually associated with the presence of identical tumors outside the central nervous system. Representative examples include Langerhans cell histiocytosis, histiocytic sarcoma, and follicular dendritic cell sarcoma. MONDO:0006247
MONDO:0858588 peritoneal malignant mesothelioma NCIT:C9350 MONDO:equivalentTo Peritoneal Malignant Mesothelioma An aggressive malignant mesothelioma that arises from the peritoneum. Patients usually present with abdominal pain and ascites. MONDO:0006292
MONDO:0858595 combined lung small cell carcinoma and lung adenocarcinoma NCIT:C9379 MONDO:equivalentTo Combined Lung Small Cell Carcinoma and Lung Adenocarcinoma A lung carcinoma characterized by a combination of small cell carcinoma and adenocarcinoma. MONDO:0003438
MONDO:0858597 well differentiated malignant hemangiopericytoma NCIT:C9392 MONDO:equivalentTo Well Differentiated Malignant Hemangiopericytoma A malignant hemangiopericytoma with well-differentiated morphological features. MONDO:0009330
MONDO:0858598 malignant hemangiopericytoma nci grade 2 NCIT:C9393 MONDO:equivalentTo Malignant Hemangiopericytoma NCI Grade 2 MONDO:0002789
MONDO:0858599 malignant hemangiopericytoma nci grade 3 NCIT:C9394 MONDO:equivalentTo Malignant Hemangiopericytoma NCI Grade 3 MONDO:0002789
MONDO:0858600 round cell liposarcoma nci grade 2 NCIT:C9401 MONDO:equivalentTo Round Cell Liposarcoma NCI Grade 2 MONDO:0005238
MONDO:0858601 round cell liposarcoma nci grade 3 NCIT:C9402 MONDO:equivalentTo Round Cell Liposarcoma NCI Grade 3 MONDO:0005238
MONDO:0858603 childhood hematopoietic and lymphoid cell neoplasm NCIT:C9431 MONDO:equivalentTo Childhood Hematopoietic and Lymphoid Cell Neoplasm A neoplasm of hematopoietic and lymphoid cell origin that occurs during childhood. Representative examples include acute leukemias and lymphomas. MONDO:0021079
MONDO:0858619 grade 1 colorectal adenocarcinoma NCIT:C9446 MONDO:equivalentTo Grade 1 Colorectal Adenocarcinoma A colorectal adenocarcinoma characterized by the presence of a malignant cellular infiltrate with more than 95% glandular formation. MONDO:0005008
MONDO:0858620 grade 2 colorectal adenocarcinoma NCIT:C9447 MONDO:equivalentTo Grade 2 Colorectal Adenocarcinoma A colorectal adenocarcinoma characterized by the presence of a malignant cellular infiltrate with 50-95% glandular formation. MONDO:0005008
MONDO:0858621 grade 3 colorectal adenocarcinoma NCIT:C9448 MONDO:equivalentTo Grade 3 Colorectal Adenocarcinoma A colorectal adenocarcinoma characterized by the presence of a malignant cellular infiltrate with less than 50% glandular formation. MONDO:0005008
MONDO:0858623 spindle cell oncocytoma NCIT:C94537 MONDO:equivalentTo Spindle Cell Oncocytoma A very rare, WHO grade 1 neoplasm of the posterior pituitary. It is characterized by the presence of spindle cells with eosinophilic, granular cytoplasm forming fascicles. Electron microscopic studies demonstrate the accumulation of intracytoplasmic mitochondria and lack of secretory granules. Immunohistochemical studies are negative for pituitary hormones. Patients may present with pituitary hypofunction, visual disturbances, headache, nausea and vomiting. The clinical course is usually benign. MONDO:0010795
MONDO:0858625 breast ductal carcinoma in situ, intermediate grade NCIT:C9456 MONDO:equivalentTo Breast Ductal Carcinoma In Situ, Intermediate Grade Breast ductal carcinoma in situ characterized by the presence of monomorphic neoplastic cells that form cribriform, micropapillary, or solid patterns. Intraluminal necrosis is present in some ducts. Ducts that contain neoplastic cells with occasional nucleoli and coarse chromatin may also be present. MONDO:0005023
MONDO:0858626 breast ductal carcinoma in situ, low grade NCIT:C9457 MONDO:equivalentTo Breast Ductal Carcinoma In Situ, Low Grade Breast ductal carcinoma in situ characterized by the presence of small, monomorphic neoplastic cells that form cribriform, micropapillary, or solid patterns. The nuclei are uniform and mitotic figures are rare. MONDO:0005023
MONDO:0858627 borderline ovarian brenner tumor NCIT:C9459 MONDO:equivalentTo Borderline Ovarian Brenner Tumor A neoplasm of low malignant potential arising from the ovary. It is characterized by the presence of neoplastic atypical urothelial-type cells in a fibrotic stroma without evidence of invasion. MONDO:0016093
MONDO:0858628 systemic anaplastic large cell lymphoma NCIT:C9470 MONDO:equivalentTo Systemic Anaplastic Large Cell Lymphoma An anaplastic large cell lymphoma that is not confined to a single anatomic site and involves multiple nodal and/or extranodal sites. MONDO:0020325
MONDO:0858630 meningeal leukemia NCIT:C94754 MONDO:equivalentTo Meningeal Leukemia Infiltration of the meninges by an acute or chronic leukemia. MONDO:0700219
MONDO:0858631 meningeal lymphoma NCIT:C94756 MONDO:equivalentTo Meningeal Lymphoma Involvement of the meninges by Hodgkin or non-Hodgkin lymphoma. MONDO:0002571
MONDO:0858632 multifocal breast carcinoma NCIT:C94770 MONDO:equivalentTo Multifocal Breast Carcinoma A breast carcinoma characterized by the presence of multiple cancerous tumors that originate from the same clone and are usually located in the same quadrant of the breast. MONDO:0004989
MONDO:0858633 multicentric breast carcinoma NCIT:C94772 MONDO:equivalentTo Multicentric Breast Carcinoma A breast carcinoma characterized by the presence of multiple cancerous tumors that originate from different clones and are usually located in different quadrants of the breast. MONDO:0004989
MONDO:0858634 early stage breast carcinoma NCIT:C94774 MONDO:equivalentTo Early Stage Breast Carcinoma Breast carcinoma that has not spread beyond the breast and the axillary lymph nodes. MONDO:0004989
MONDO:0858635 hereditary malignant neoplasm NCIT:C9479 MONDO:equivalentTo Hereditary Malignant Neoplasm Malignant neoplasms occurring in families at a rate greater than that expected by chance and caused by germline mutations in a specific gene. MONDO:0004992
MONDO:0858637 stage i borderline ovarian surface epithelial-stromal tumor NCIT:C94821 MONDO:equivalentTo Stage I Borderline Ovarian Surface Epithelial-Stromal Tumor Stage I includes: T1, N0, M0. T1: Tumor limited to ovaries (one or both). N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0016093
MONDO:0858638 stage ii borderline ovarian surface epithelial-stromal tumor NCIT:C94822 MONDO:equivalentTo Stage II Borderline Ovarian Surface Epithelial-Stromal Tumor Stage II includes: T2, N0, M0. T2: Tumor involves one or both ovaries with pelvic extension and/or implants. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0016093
MONDO:0858639 stage iii borderline ovarian surface epithelial-stromal tumor NCIT:C94824 MONDO:equivalentTo Stage III Borderline Ovarian Surface Epithelial-Stromal Tumor Stage III includes: T3, N0, M0. T3: Tumor involves one or both ovaries with microscopically confirmed peritoneal metastasis outside pelvis. N0: No regional lymph node metastasis. M0: No distant metastasis. (AJCC 6th and 7th eds.) MONDO:0016093
MONDO:0858640 stage iv borderline ovarian surface epithelial-stromal tumor NCIT:C94825 MONDO:equivalentTo Stage IV Borderline Ovarian Surface Epithelial-Stromal Tumor Stage IV includes: Any T, Any N, M1. M1: Distant metastasis (excludes peritoneal metastasis). (AJCC 6th and 7th eds.) MONDO:0016093
MONDO:0858648 melanocytoma NCIT:C9498 MONDO:equivalentTo Melanocytoma A usually benign neoplasm that arises from the sun-exposed skin, eye, and meninges. It is composed of spindle and/or epithelioid melanocytes and melanophages. It rarely progresses to melanoma. MONDO:0021143
MONDO:0858649 myolipoma NCIT:C9502 MONDO:equivalentTo Myolipoma A benign extrauterine tumor composed of mature adipocytes and smooth muscle cells. MONDO:0005106
MONDO:0858650 thymoliposarcoma NCIT:C95038 MONDO:equivalentTo Thymoliposarcoma A liposarcoma that arises from the thymus gland. It is characterized by the presence of a liposarcomatous malignant infiltrate that entraps lobules of thymic tissue. MONDO:0003601
MONDO:0858651 ectopic cervical thymoma NCIT:C95048 MONDO:equivalentTo Ectopic Cervical Thymoma A thymoma that arises in the cervical region and is not connected with the thymus gland. MONDO:0006456
MONDO:0858656 intramucosal adenocarcinoma NCIT:C95397 MONDO:equivalentTo Intramucosal Adenocarcinoma A neoplastic lesion that shows morphologic evidence of invasion into the lamina propria or muscularis mucosa. There is no evidence of invasion into the submucosa. Evidence of invasion may refer to stromal invasion by single cells or clusters of cells, presence of atypical and complex glandular architectural patterns beyond those that are present in normal mucosa, desmoplasia, and/or vascular invasion. MONDO:0004970
MONDO:0858658 pancreatic well differentiated ductal adenocarcinoma NCIT:C95426 MONDO:equivalentTo Pancreatic Well Differentiated Ductal Adenocarcinoma A pancreatic ductal adenocarcinoma characterized by the presence of duct-like structures and medium-sized malignant glandular structures. MONDO:0005184
MONDO:0858659 pancreatic moderately differentiated ductal adenocarcinoma NCIT:C95427 MONDO:equivalentTo Pancreatic Moderately Differentiated Ductal Adenocarcinoma A pancreatic ductal adenocarcinoma characterized by the presence of medium-sized duct-like structures and small malignant tubular glandular structures. MONDO:0005184
MONDO:0858660 pancreatic poorly differentiated ductal adenocarcinoma NCIT:C95428 MONDO:equivalentTo Pancreatic Poorly Differentiated Ductal Adenocarcinoma A pancreatic ductal adenocarcinoma characterized by the presence of small and irregular malignant glandular structures, solid sheets of malignant cells, and single malignant cells. MONDO:0005184
MONDO:0858661 pancreatic mixed acinar-ductal carcinoma NCIT:C95458 MONDO:equivalentTo Pancreatic Mixed Acinar-Ductal Carcinoma A carcinoma that arises from the pancreas showing either extensive mucin accumulation and acinar neoplastic cells or a mixture of columnar or signet-ring cells and acinar neoplastic cells. MONDO:0006047
MONDO:0858662 pancreatic mixed ductal adenocarcinoma-acinar carcinoma-neuroendocrine carcinoma NCIT:C95460 MONDO:equivalentTo Pancreatic Mixed Ductal Adenocarcinoma-Acinar Carcinoma-Neuroendocrine Carcinoma A very rare carcinoma that arises from the pancreas and is composed of ductal adenocarcinoma, acinar carcinoma, and neuroendocrine carcinoma components. MONDO:0044727
MONDO:0858663 pancreatic hepatoid adenocarcinoma NCIT:C95465 MONDO:equivalentTo Pancreatic Hepatoid Adenocarcinoma A rare adenocarcinoma that arises from the pancreas. It is characterized by marked hepatocellular differentiation. MONDO:0006243
MONDO:0858664 pancreatic medullary carcinoma NCIT:C95466 MONDO:equivalentTo Pancreatic Medullary Carcinoma A pancreatic ductal adenocarcinoma characterized by poor differentiation and a prominent syncytial growth pattern. The prognosis is more favorable compared to conventional pancreatic ductal adenocarcinoma. MONDO:0005184
MONDO:0858665 pancreatic serous adenoma NCIT:C95470 MONDO:equivalentTo Pancreatic Serous Adenoma A benign, non-metastasizing, usually cystic epithelial neoplasm arising from the exocrine pancreas. It is composed of glycogen-rich epithelial cells which produce a watery fluid. Signs and symptoms include abdominal mass, abdominal pain, nausea, vomiting, and weight loss. MONDO:0021441
MONDO:0858666 pancreatic intraductal neoplasm NCIT:C95505 MONDO:equivalentTo Pancreatic Intraductal Neoplasm A group of cystic or mass-forming epithelial neoplasms that arise from the exocrine pancreas, exhibit ductal differentiation, and grow mostly within the pancreatic ducts. This group includes the pancreatic intraductal papillary mucinous neoplasms and the pancreatic intraductal tubulopapillary neoplasms. MONDO:0024276
MONDO:0858667 pancreatic intraductal papillary mucinous neoplasm, gastric-type NCIT:C95508 MONDO:equivalentTo Pancreatic Intraductal Papillary Mucinous Neoplasm, Gastric-Type A pancreatic intraductal papillary mucinous neoplasm characterized by the presence of neoplastic epithelial cells that are similar to gastric foveolar epithelial cells. MONDO:0004286
MONDO:0858668 pancreatic intraductal papillary mucinous neoplasm, intestinal-type NCIT:C95510 MONDO:equivalentTo Pancreatic Intraductal Papillary Mucinous Neoplasm, Intestinal-Type A pancreatic intraductal papillary mucinous neoplasm characterized by the presence of neoplastic epithelial cells that form tall papillae, similar to those that are present in colonic villous adenomas. MONDO:0004286
MONDO:0858669 pancreatic intraductal papillary mucinous neoplasm, pancreatobiliary-type NCIT:C95512 MONDO:equivalentTo Pancreatic Intraductal Papillary Mucinous Neoplasm, Pancreatobiliary-Type A pancreatic intraductal papillary mucinous neoplasm characterized by the presence of neoplastic epithelial cells that form thin-branching papillae and exhibit high grade dysplasia. MONDO:0004286
MONDO:0858675 non-functioning pancreatic neuroendocrine tumor g1 NCIT:C95585 MONDO:equivalentTo Non-Functioning Pancreatic Neuroendocrine Tumor G1 A low grade well differentiated neoplasm with neuroendocrine differentiation that arises from the pancreas. It is characterized by the absence of a hormone-related clinical syndrome. MONDO:0004334
MONDO:0858676 pancreatic vipoma NCIT:C95599 MONDO:equivalentTo Pancreatic Vipoma A usually malignant pancreatic neuroendocrine tumor producing vasoactive intestinal peptide (VIP). It is associated with watery diarrhea, hypokalemia, and hypochlorhydria or achlorhydria. One third of cases are metastatic at the time of diagnosis. MONDO:0023206
MONDO:0858677 esophageal spindle cell carcinoma NCIT:C95608 MONDO:equivalentTo Esophageal Spindle Cell Carcinoma An esophageal squamous cell carcinoma characterized by the presence of a spindle-cell carcinomatous component. Crossly it has a polypoid appearance and usually arises from the middle or lower third of the esophagus. MONDO:0005580
MONDO:0858678 esophageal well differentiated squamous cell carcinoma NCIT:C95610 MONDO:equivalentTo Esophageal Well Differentiated Squamous Cell Carcinoma An esophageal squamous cell carcinoma characterized by the presence of prominent keratinization and low mitotic activity. MONDO:0005580
MONDO:0858679 esophageal moderately differentiated squamous cell carcinoma NCIT:C95611 MONDO:equivalentTo Esophageal Moderately Differentiated Squamous Cell Carcinoma An esophageal squamous cell carcinoma characterized by the presence of variable morphologic characteristics that include areas of prominent and poor keratinization. MONDO:0005580
MONDO:0858680 esophageal poorly differentiated squamous cell carcinoma NCIT:C95612 MONDO:equivalentTo Esophageal Poorly Differentiated Squamous Cell Carcinoma An esophageal squamous cell carcinoma characterized by the presence of basal-like malignant squamous cells that form nests, often associated with central necrosis. MONDO:0005580
MONDO:0858681 esophageal mixed adenoneuroendocrine carcinoma NCIT:C95621 MONDO:equivalentTo Esophageal Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the esophagus and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0019086
MONDO:0858683 esophageal synovial sarcoma NCIT:C95624 MONDO:equivalentTo Esophageal Synovial Sarcoma A synovial sarcoma that affects the esophageal wall. MONDO:0001204
MONDO:0858686 gastric adenoma, gastric-type NCIT:C95775 MONDO:equivalentTo Gastric Adenoma, Gastric-Type A neoplastic polyp that arises from the stomach. It is characterized by the presence of gastric epithelial differentiation. It includes pyloric gland adenomas and foveolar-type adenomas. MONDO:0006221
MONDO:0858689 gastric mixed adenoneuroendocrine carcinoma NCIT:C95886 MONDO:equivalentTo Gastric Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the stomach and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0858691 gastric schwannoma NCIT:C95901 MONDO:equivalentTo Gastric Schwannoma A rare schwannoma that arises from the stomach. It follows a benign clinical course. MONDO:0004820
MONDO:0858693 ampulla of vater pancreatobiliary type adenocarcinoma NCIT:C95963 MONDO:equivalentTo Ampulla of Vater Pancreatobiliary Type Adenocarcinoma An invasive adenocarcinoma that arises from the ampulla of Vater. It is characterized by the presence of malignant cells that resemble the malignant cells of the pancreatic ductal or extrahepatic bile duct carcinomas. MONDO:0002670
MONDO:0858694 ampulla of vater hepatoid adenocarcinoma NCIT:C95966 MONDO:equivalentTo Ampulla of Vater Hepatoid Adenocarcinoma A very rare adenocarcinoma that arises from the ampulla of Vater. It is usually of the intestinal type and is characterized by the presence of malignant polygonal cells with abundant eosinophilic cytoplasm resembling hepatocytes. MONDO:0006243
MONDO:0858695 ampulla of vater neuroendocrine neoplasm NCIT:C95980 MONDO:equivalentTo Ampulla of Vater Neuroendocrine Neoplasm A neoplasm with neuroendocrine differentiation that arises from the ampulla of Vater and periampullary region. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). MONDO:0000921
MONDO:0858696 ampulla of vater mixed adenoneuroendocrine carcinoma NCIT:C95986 MONDO:equivalentTo Ampulla of Vater Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the ampulla of Vater and the periampullary region. It is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0858702 intestinal neuroendocrine tumor NCIT:C96062 MONDO:equivalentTo Intestinal Neuroendocrine Tumor A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the small or large intestine. MONDO:0000386
MONDO:0858703 small intestinal mixed adenoneuroendocrine carcinoma NCIT:C96066 MONDO:equivalentTo Small Intestinal Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the small intestine and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0005522
MONDO:0858705 colorectal neuroendocrine neoplasm NCIT:C96152 MONDO:equivalentTo Colorectal Neuroendocrine Neoplasm A neoplasm with neuroendocrine differentiation that arises from the colon or rectum. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). MONDO:0002883
MONDO:0858706 colorectal mixed adenoneuroendocrine carcinoma NCIT:C96158 MONDO:equivalentTo Colorectal Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the colon or rectum and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0858707 digestive system neuroendocrine tumor g2 NCIT:C96166 MONDO:equivalentTo Digestive System Neuroendocrine Tumor G2 A well differentiated, intermediate grade neoplasm with neuroendocrine differentiation that arises from the digestive system. The mitotic count is 2-20 per 10 HPF and/or the Ki67 index is 3 to 20 percent. MONDO:0000386
MONDO:0858715 serrated lesions and polyps NCIT:C96414 MONDO:equivalentTo Serrated Lesions and Polyps Polyps that arises from the large intestine and the appendix. They are characterized by the presence of serrated glands and the absence of generalized dysplasia. MONDO:0006180
MONDO:0858717 appendix enterochromaffin cell serotonin-producing neuroendocrine tumor NCIT:C96424 MONDO:equivalentTo Appendix Enterochromaffin Cell Serotonin-Producing Neuroendocrine Tumor A well differentiated neuroendocrine tumor arising from the wall of the appendix. It is characterized by the presence of neoplastic cells forming round solid nests and occasionally glandular structures. The majority of the cases are asymptomatic, and they are found incidentally in appendectomy specimens. The majority of the tumors are located in the distal end of the appendix and they are enterochromaffin-cell carcinoid tumors producing serotonin. Most cases show morphologic evidence of appendiceal wall and lymphatic vessel invasion by tumor cells. Despite the morphologic evidence of invasion, appendiceal carcinoid tumors only infrequently produce lymph node or distant metastases. MONDO:0015066
MONDO:0858721 rectal serrated lesions and polyps NCIT:C96465 MONDO:equivalentTo Rectal Serrated Lesions and Polyps Polyps that arises from the rectum. They are characterized by the presence of serrated glands and the absence of generalized dysplasia. MONDO:0000530
MONDO:0858725 colon serrated adenocarcinoma NCIT:C96486 MONDO:equivalentTo Colon Serrated Adenocarcinoma A rare, invasive colon adenocarcinoma characterized by the presence of a malignant infiltrate with serrated glandular architecture. MONDO:0006163
MONDO:0858726 rectal serrated adenocarcinoma NCIT:C96487 MONDO:equivalentTo Rectal Serrated Adenocarcinoma A rare, invasive rectal adenocarcinoma characterized by the presence of a malignant infiltrate with serrated glandular architecture. MONDO:0006163
MONDO:0858729 colorectal sarcomatoid carcinoma NCIT:C96494 MONDO:equivalentTo Colorectal Sarcomatoid Carcinoma A biphasic colorectal carcinoma with a spindle cell, sarcomatoid component. MONDO:0024331
MONDO:0858735 colorectal schwannoma NCIT:C96512 MONDO:equivalentTo Colorectal Schwannoma A schwannoma that arises from the colon or rectum. It may cause gastrointestinal bleeding and luminal obstruction. MONDO:0021444
MONDO:0858736 colorectal ganglioneuroma NCIT:C96514 MONDO:equivalentTo Colorectal Ganglioneuroma A ganglioneuroma that arises from the colon or rectum. It usually presents as a small mucosal polyp. MONDO:0021444
MONDO:0858737 colorectal benign granular cell tumor NCIT:C96516 MONDO:equivalentTo Colorectal Benign Granular Cell Tumor A granular cell tumor that arises from the colon or rectum and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021444
MONDO:0858738 anal canal undifferentiated carcinoma NCIT:C96529 MONDO:equivalentTo Anal Canal Undifferentiated Carcinoma A usually aggressive malignant epithelial neoplasm that arises from the anal canal. It is composed of malignant cells which do not display evidence of glandular or squamous differentiation. MONDO:0007108
MONDO:0858741 anal canal mixed adenoneuroendocrine carcinoma NCIT:C96553 MONDO:equivalentTo Anal Canal Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the anal canal. It is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0858742 anal canal squamous papilloma NCIT:C96554 MONDO:equivalentTo Anal Canal Squamous Papilloma A benign epithelial neoplasm that arises from the anal canal. It is characterized by a papillary growth pattern and a proliferation of neoplastic squamous cells without morphologic evidence of malignancy. MONDO:0021469
MONDO:0858743 anal hidradenoma papilliferum NCIT:C96699 MONDO:equivalentTo Anal Hidradenoma Papilliferum A benign neoplasm arising from the perianal sweat glands. It presents as a cystic nodular lesion and is characterized by the presence of cystic and papillary structures. The papillary structures contain connective tissue and are covered by two layers of epithelium. MONDO:0021469
MONDO:0858745 hnf1alpha-inactivated hepatocellular adenoma NCIT:C96758 MONDO:equivalentTo HNF1alpha-Inactivated Hepatocellular Adenoma A hepatocellular adenoma caused by inactivating mutations of the HNF1A gene. It is characterized by the presence of lobulated contours, steatosis, and absence of inflammation or nuclear atypia. MONDO:0018902
MONDO:0858746 beta-catenin-activated hepatocellular adenoma NCIT:C96759 MONDO:equivalentTo Beta-Catenin-Activated Hepatocellular Adenoma A hepatocellular adenoma caused by activating mutations of beta-catenin. It is characterized by the presence of nuclear atypia and absence of inflammation or steatosis. There is an increased risk of malignant transformation. MONDO:0018902
MONDO:0858747 inflammatory hepatocellular adenoma NCIT:C96760 MONDO:equivalentTo Inflammatory Hepatocellular Adenoma A hepatocellular adenoma that occurs more often in women. It is characterized by increased levels of inflammation-associated proteins. It is usually associated with steatosis and obesity. MONDO:0018902
MONDO:0858748 unclassified hepatocellular adenoma NCIT:C96761 MONDO:equivalentTo Unclassified Hepatocellular Adenoma A hepatocellular adenoma without distinguished morphologic characteristics or known molecular abnormalities. MONDO:0018902
MONDO:0858750 liver neuroendocrine neoplasm NCIT:C96786 MONDO:equivalentTo Liver Neuroendocrine Neoplasm An extremely rare neoplasm with neuroendocrine differentiation that arises from the liver. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). MONDO:0024477
MONDO:0858751 lymphocyte-rich hepatocellular carcinoma NCIT:C96788 MONDO:equivalentTo Lymphocyte-Rich Hepatocellular Carcinoma A rare type of hepatocellular carcinoma characterized by the presence of pleomorphic malignant cells that are intermixed with lymphocytes. MONDO:0007256
MONDO:0858752 well differentiated hepatocellular carcinoma NCIT:C96789 MONDO:equivalentTo Well Differentiated Hepatocellular Carcinoma A hepatocellular carcinoma characterized by the presence of malignant cells with mild atypia and an increased nuclear/cytoplasmic ratio forming thin trabecular patterns. It is usually associated with small tumors and an early stage. MONDO:0007256
MONDO:0858753 moderately differentiated hepatocellular carcinoma NCIT:C96790 MONDO:equivalentTo Moderately Differentiated Hepatocellular Carcinoma A hepatocellular carcinoma characterized by the presence of malignant cells with abundant eosinophilic cytoplasm forming trabecular and pseudoglandular patterns. It is usually associated with tumors that are larger than 3 cm in diameter. MONDO:0007256
MONDO:0858754 poorly differentiated hepatocellular carcinoma NCIT:C96791 MONDO:equivalentTo Poorly Differentiated Hepatocellular Carcinoma A hepatocellular carcinoma characterized by the presence of malignant pleomorphic cells forming solid patterns. MONDO:0007256
MONDO:0858755 liver undifferentiated carcinoma NCIT:C96792 MONDO:equivalentTo Liver Undifferentiated Carcinoma A rare carcinoma that arises from the liver. The diagnosis is made by immunohistochemical studies. Morphologic studies alone cannot establish the diagnosis of carcinoma or further subclassify the malignant tumor. MONDO:0018531
MONDO:0858756 small duct intrahepatic cholangiocarcinoma NCIT:C96805 MONDO:equivalentTo Small Duct Intrahepatic Cholangiocarcinoma An intrahepatic cholangiocarcinoma that arises from the small interlobular bile ducts. MONDO:0003210
MONDO:0858757 bile duct intraductal papillary neoplasm with an associated invasive carcinoma NCIT:C96810 MONDO:equivalentTo Bile Duct Intraductal Papillary Neoplasm with an Associated Invasive Carcinoma An intraductal papillary neoplasm that arises from the epithelium of the intrahepatic or extrahepatic bile ducts and it is associated with an invasive carcinomatous component. MONDO:0003455
MONDO:0858758 extrahepatic bile duct tubulopapillary adenoma NCIT:C96811 MONDO:equivalentTo Extrahepatic Bile Duct Tubulopapillary Adenoma An adenoma that arises from the extrahepatic bile ducts. It is characterized by the presence of tubular and papillary growth patterns. MONDO:0003445
MONDO:0858760 liver synovial sarcoma NCIT:C96845 MONDO:equivalentTo Liver Synovial Sarcoma A synovial sarcoma that affects the liver. MONDO:0002397
MONDO:0858761 liver carcinosarcoma NCIT:C96848 MONDO:equivalentTo Liver Carcinosarcoma An aggressive carcinoma with a sarcomatous component that arises from the liver. The sarcomatous component is clonally related to the more differentiated, carcinomatous component. The prognosis is usually poor. MONDO:0002928
MONDO:0858765 gallbladder mucinous cystic neoplasm NCIT:C96881 MONDO:equivalentTo Gallbladder Mucinous Cystic Neoplasm An epithelial, usually multiloculated neoplasm arising from the gallbladder. It occurs predominantly in females. Signs and symptoms include abdominal mass, abdominal pain, and jaundice. Morphologically, the cystic spaces are lined by columnar epithelium and contain mucinous or serous fluid. MONDO:0021253
MONDO:0858766 gallbladder carcinosarcoma NCIT:C96888 MONDO:equivalentTo Gallbladder Carcinosarcoma A carcinoma that arises from the gallbladder and it is characterized by the presence of a sarcomatous component. The sarcomatous component may contain osteosarcoma, chondrosarcoma, or rhabdomyosarcoma elements. MONDO:0003220
MONDO:0858767 gallbladder hepatoid adenocarcinoma NCIT:C96890 MONDO:equivalentTo Gallbladder Hepatoid Adenocarcinoma A rare variant of gallbladder adenocarcinoma. It is characterized by the presence of a malignant glandular epithelial infiltrate that resembles hepatocellular carcinoma. MONDO:0006215
MONDO:0858768 gallbladder cribriform carcinoma NCIT:C96891 MONDO:equivalentTo Gallbladder Cribriform Carcinoma A rare variant of gallbladder adenocarcinoma. It is characterized by the presence of a malignant glandular epithelial infiltrate with a cribriform growth pattern. MONDO:0006215
MONDO:0858769 gallbladder adenocarcinoma, biliary type NCIT:C96915 MONDO:equivalentTo Gallbladder Adenocarcinoma, Biliary Type A well or moderately differentiated adenocarcinoma that arises from the gallbladder. It is the most common type of gallbladder carcinoma and is characterized by the presence of malignant tubular glands. Intestinal differentiation may be present. MONDO:0006215
MONDO:0858770 gallbladder adenocarcinoma, gastric foveolar type NCIT:C96916 MONDO:equivalentTo Gallbladder Adenocarcinoma, Gastric Foveolar Type An unusual, well differentiated adenocarcinoma that arises from the gallbladder. It is characterized by the presence of tall malignant columnar cells with mucin-containing cytoplasm and basally located nuclei. MONDO:0006215
MONDO:0858774 gallbladder mixed adenoneuroendocrine carcinoma NCIT:C96927 MONDO:equivalentTo Gallbladder Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the gallbladder and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0003220
MONDO:0858775 gallbladder tubular carcinoid NCIT:C96930 MONDO:equivalentTo Gallbladder Tubular Carcinoid A neuroendocrine tumor that arises from the gallbladder. It does not show the morphologic characteristics of typical carcinoid tumors (neoplastic cells forming solid nests). In contrast, the tumor cells form small discrete tubules. MONDO:0015073
MONDO:0858776 extrahepatic bile duct adenocarcinoma, biliary type NCIT:C96936 MONDO:equivalentTo Extrahepatic Bile Duct Adenocarcinoma, Biliary Type A well or moderately differentiated adenocarcinoma that arises from the extrahepatic bile ducts. It is characterized by the presence of malignant tubular glands. MONDO:0002665
MONDO:0858777 extrahepatic bile duct adenocarcinoma, gastric foveolar type NCIT:C96937 MONDO:equivalentTo Extrahepatic Bile Duct Adenocarcinoma, Gastric Foveolar Type An unusual, well differentiated adenocarcinoma that arises from the extrahepatic bile ducts. It is characterized by the presence of tall malignant columnar cells with mucin-containing cytoplasm and basally located nuclei. MONDO:0002665
MONDO:0858778 extrahepatic bile duct adenocarcinoma, intestinal type NCIT:C96938 MONDO:equivalentTo Extrahepatic Bile Duct Adenocarcinoma, Intestinal Type An adenocarcinoma that arises from the extrahepatic bile ducts. It is characterized by the presence of neoplastic tubular glands lined by columnar cells or neoplastic glands lined by goblet cells. MONDO:0002665
MONDO:0858779 extrahepatic bile duct carcinosarcoma NCIT:C96939 MONDO:equivalentTo Extrahepatic Bile Duct Carcinosarcoma A carcinoma that arises from the extrahepatic bile ducts and it is characterized by the presence of a sarcomatous component. MONDO:0003090
MONDO:0858780 extrahepatic bile duct mucinous cystic neoplasm with an associated invasive carcinoma NCIT:C96946 MONDO:equivalentTo Extrahepatic Bile Duct Mucinous Cystic Neoplasm with an Associated Invasive Carcinoma A mucinous cystic neoplasm that arises from the extrahepatic bile ducts and it is associated with an invasive carcinomatous component. MONDO:0002665
MONDO:0858781 intrahepatic bile duct mucinous cystic neoplasm with an associated invasive carcinoma NCIT:C96947 MONDO:equivalentTo Intrahepatic Bile Duct Mucinous Cystic Neoplasm with an Associated Invasive Carcinoma A mucinous cystic neoplasm that arises from the intrahepatic bile ducts and it is associated with an invasive carcinomatous component. MONDO:0002868
MONDO:0858783 extrahepatic bile duct lymphoma NCIT:C96952 MONDO:equivalentTo Extrahepatic Bile Duct Lymphoma A lymphoma that arises from the extrahepatic bile ducts, with the bulk of the disease located at this site. MONDO:0021321
MONDO:0858785 extrahepatic bile duct neuroendocrine neoplasm NCIT:C96954 MONDO:equivalentTo Extrahepatic Bile Duct Neuroendocrine Neoplasm A neoplasm with neuroendocrine differentiation that arises from the extrahepatic bile ducts. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). MONDO:0021385
MONDO:0858786 extrahepatic bile duct mixed adenoneuroendocrine carcinoma NCIT:C96959 MONDO:equivalentTo Extrahepatic Bile Duct Mixed Adenoneuroendocrine Carcinoma A carcinoma that arises from the extrahepatic bile ducts and is characterized by the presence of a malignant glandular epithelial component and a malignant neuroendocrine component. At least 30 percent of either component should be present for the diagnosis to be made. MONDO:0006182
MONDO:0858788 invasive breast lobular carcinoma, alveolar variant NCIT:C97049 MONDO:equivalentTo Invasive Breast Lobular Carcinoma, Alveolar Variant A grade I invasive lobular carcinoma of the breast, characterized by the presence of round groups of neoplastic cells. MONDO:0005051
MONDO:0858789 invasive breast lobular carcinoma, pleomorphic variant NCIT:C97051 MONDO:equivalentTo Invasive Breast Lobular Carcinoma, Pleomorphic Variant A grade II invasive lobular carcinoma of the breast, characterized by the presence of neoplastic cells with large and atypical nuclei. MONDO:0005051
MONDO:0858790 invasive breast lobular carcinoma, solid variant NCIT:C97052 MONDO:equivalentTo Invasive Breast Lobular Carcinoma, Solid Variant A grade I invasive lobular carcinoma of the breast, characterized by the presence of neoplastic cells that form trabeculae and groups infiltrating collagen bundles. MONDO:0005051
MONDO:0858791 invasive breast lobular carcinoma, tubulolobular variant NCIT:C97053 MONDO:equivalentTo Invasive Breast Lobular Carcinoma, Tubulolobular Variant An invasive lobular carcinoma of the breast, characterized by the presence of neoplastic cells forming small tubular structures. MONDO:0005051
MONDO:0858792 mixed congenital mesoblastic nephroma NCIT:C97058 MONDO:equivalentTo Mixed Congenital Mesoblastic Nephroma A congenital mesoblastic nephroma characterized by the presence of classic and cellular areas. MONDO:0017043
MONDO:0858851 contralateral breast carcinoma NCIT:C99390 MONDO:equivalentTo Contralateral Breast Carcinoma Breast carcinoma that develops in the opposite breast of a patient with an already diagnosed primary breast carcinoma. MONDO:0003982
MONDO:0859471 neoplastic medium-sized lymphocyte NCIT:C37004 MONDO:equivalentTo Neoplastic Medium-Sized Lymphocyte
MONDO:0859472 neoplastic b-lymphocyte NCIT:C38640 MONDO:equivalentTo Neoplastic B-Lymphocyte
MONDO:0859554 medaka melanoma NCIT:C134572 MONDO:equivalentTo Medaka Melanoma Melanoma that occurs in Oryzias latipes. MONDO:0700196
MONDO:0859555 xiphophorus melanoma NCIT:C134575 MONDO:equivalentTo Xiphophorus Melanoma Melanoma that occurs in Xiphophorus. MONDO:0700196
MONDO:0859556 non-human or experimental organism neoplasm NCIT:C134576 MONDO:equivalentTo Non-Human or Experimental Organism Neoplasm A neoplastic condition occurring in a non-human organism; this includes neoplasms occurring in organisms used in research settings.
MONDO:0859560 tubulostromal adenoma NCIT:C79953 MONDO:equivalentTo Tubulostromal Adenoma A benign ovarian epithelial tumor. It has been described in mice and rats and is rare in other animal species. Morphologically it is characterized by the presence of tubular structures and interstitial stroma.
MONDO:0859561 tubulostromal adenocarcinoma NCIT:C80356 MONDO:equivalentTo Tubulostromal Adenocarcinoma A malignant ovarian epithelial tumor. It has been described in mice and rats and is characterized by marked pleomorphism, atypia, and an infiltrative growth pattern.
MONDO:0859730 vaginal non-keratinizing squamous cell carcinoma NCIT:C40244 MONDO:equivalentTo Vaginal Non-Keratinizing Squamous Cell Carcinoma A squamous cell carcinoma that arises from the vagina and is characterized by the presence of polygonal squamous cells. Intercellular bridges and cytoplasmic keratinization may be present, but keratin pearls are absent. MONDO:0006490
MONDO:0860042 lymphoproliferative disease associated with primary immune disorder NCIT:C150673 MONDO:equivalentTo Lymphoproliferative Disease Associated with Primary Immune Disorder A lymphoid proliferation that arises in the setting of immune deficiency due to a primary immunodeficiency or immunoregulatory disorder. The primary immune disorders most frequently associated with lymphoproliferative disorders are ataxia-telangiectasia, Wiskott-Aldrich syndrome, common variable immunodeficiency, severe combined immunodeficiency, X-linked lymphoproliferative disease, Nijmegen breakage syndrome, hyper-IgM syndrome, and autoimmune lymphoproliferative syndrome. (WHO 2017)
MONDO:0860043 genitourinary system disorder NCIT:C156660 MONDO:equivalentTo Genitourinary System Disorder A non-neoplastic or neoplastic disorder that affects the genitourinary system.
MONDO:0860044 recurrent hiv-related lymphoproliferative disorder NCIT:C157685 MONDO:equivalentTo Recurrent HIV-Related Lymphoproliferative Disorder The reemergence of HIV-associated lymphoproliferative disorder after a period of remission.
MONDO:0860045 refractory hiv-related lymphoproliferative disorder NCIT:C157687 MONDO:equivalentTo Refractory HIV-Related Lymphoproliferative Disorder HIV-associated lymphoproliferative disorder that is resistant to treatment.
MONDO:0860046 hiv-related lymphoproliferative disorder NCIT:C157709 MONDO:equivalentTo HIV-Related Lymphoproliferative Disorder A lymphoproliferative disorder that develops in an individual with HIV infection.
MONDO:0860047 ebv-related lymphoproliferative disease with primary immunodeficiency NCIT:C160150 MONDO:equivalentTo EBV-Related Lymphoproliferative Disease with Primary Immunodeficiency An EBV-related lymphoid proliferation that arises in the setting of immune deficiency due to a primary immunodeficiency or immunoregulatory disorder.
MONDO:0860048 recurrent ebv-related lymphoproliferative disease with primary immunodeficiency NCIT:C160151 MONDO:equivalentTo Recurrent EBV-Related Lymphoproliferative Disease with Primary Immunodeficiency The reemergence of EBV-associated lymphoproliferative disease with primary immunodeficiency after a period of remission.
MONDO:0860049 refractory ebv-related lymphoproliferative disease with primary immunodeficiency NCIT:C160152 MONDO:equivalentTo Refractory EBV-Related Lymphoproliferative Disease with Primary Immunodeficiency EBV-associated lymphoproliferative disease with primary immunodeficiency that is resistant to treatment.
MONDO:0860050 tonsillar disorder NCIT:C173797 MONDO:equivalentTo Tonsillar Disorder A non-neoplastic or neoplastic disorder that affects the tonsils.
MONDO:0860051 soft tissue disorder NCIT:C27042 MONDO:equivalentTo Soft Tissue Disorder A non-neoplastic or neoplastic disorder that affects the soft tissue.
MONDO:0860052 connective and soft tissue disorder NCIT:C27574 MONDO:equivalentTo Connective and Soft Tissue Disorder A non-neoplastic or neoplastic disorder that affects the connective and soft tissue.
MONDO:0860053 neck disorder NCIT:C27648 MONDO:equivalentTo Neck Disorder A non-neoplastic or neoplastic disorder that affects the anatomic structures of the neck region. This category includes disorders of the pharynx, larynx, thyroid gland, and parathyroid gland.
MONDO:0860054 peritoneal and retroperitoneal disorder NCIT:C27664 MONDO:equivalentTo Peritoneal and Retroperitoneal Disorder A non-neoplastic or neoplastic disorder that affects the peritoneum and/or retroperitoneum.
MONDO:0860055 female reproductive system precancerous condition NCIT:C27788 MONDO:equivalentTo Female Reproductive System Precancerous Condition A precancerous lesion that arises from the female reproductive system. Representative examples include atypical endometrial hyperplasia, endometrial intraepithelial neoplasia, and cervical intraepithelial neoplasia.
MONDO:0860056 tobacco use disorder NCIT:C35074 MONDO:equivalentTo Tobacco Use Disorder Any disease or disorder that is caused by the use of tobacco.
MONDO:0860057 sternal disorder NCIT:C35744 MONDO:equivalentTo Sternal Disorder A non-neoplastic or neoplastic disorder that affects the sternum.
MONDO:0860058 chest wall disorder NCIT:C35745 MONDO:equivalentTo Chest Wall Disorder A non-neoplastic or neoplastic disorder that affects the structures of the chest wall. Representative examples include infection, chest wall lipoma, and chest wall lymphoma.
MONDO:0860059 axillary disorder NCIT:C35746 MONDO:equivalentTo Axillary Disorder A non-neoplastic or neoplastic disorder that affects the structures of the axilla. Representative examples include axillary lymphadenitis, axillary lipoma, and metastatic carcinoma to the axillary lymph nodes.
MONDO:0860060 hematopoietic and lymphatic system disorder NCIT:C35814 MONDO:equivalentTo Hematopoietic and Lymphatic System Disorder A non-neoplastic or neoplastic disorder that affects the hematopoietic and lymphatic system.
MONDO:0860062 anal precancerous condition NCIT:C7407 MONDO:equivalentTo Anal Precancerous Condition
MONDO:0860063 esophageal precancerous condition NCIT:C7423 MONDO:equivalentTo Esophageal Precancerous Condition
MONDO:0860064 gastric precancerous condition NCIT:C7424 MONDO:equivalentTo Gastric Precancerous Condition
MONDO:0860065 pulmonary precancerous condition NCIT:C7435 MONDO:equivalentTo Pulmonary Precancerous Condition A premalignant pathologic process that affects the lungs. This category includes bronchial intraepithelial neoplasia and atypical adenomatous hyperplasia.
MONDO:0860066 hepatobiliary precancerous condition NCIT:C7655 MONDO:equivalentTo Hepatobiliary Precancerous Condition
MONDO:0860067 intestinal precancerous condition NCIT:C7657 MONDO:equivalentTo Intestinal Precancerous Condition
MONDO:0860068 digestive system precancerous condition NCIT:C7659 MONDO:equivalentTo Digestive System Precancerous Condition
MONDO:0860069 cutaneous precancerous condition NCIT:C8957 MONDO:equivalentTo Cutaneous Precancerous Condition
MONDO:0860070 neonatal disorder NCIT:C98996 MONDO:equivalentTo Neonatal Disorder A non-neoplastic or neoplastic disorder which occurs during the neonatal period.
MONDO:0950158 core binding factor acute myeloid leukemia NCIT:C122688 MONDO:equivalentTo Core Binding Factor Acute Myeloid Leukemia Acute myeloid leukemia characterized by the presence of t(8;21)(q22;q22) or inv(16)(p13q22)/t(16;16)(p13;q22). These cytogenetic abnormalities result in disruption of the transcription factor CBF, which is a regulator of normal hematopoiesis. MONDO:0020078
MONDO:0955884 adult acute eosinophilic leukemia NCIT:C7963 MONDO:equivalentTo Adult Acute Eosinophilic Leukemia An acute eosinophilic leukemia occurring in adults. MONDO:0043881
MONDO:0956044 acute myeloid leukemia (megakaryoblastic) with t(1;22)(p13.3;q13.1); rbm15-mkl1 NCIT:C82427 MONDO:equivalentTo Acute Myeloid Leukemia (Megakaryoblastic) with t(1;22)(p13.3;q13.1); RBM15-MKL1 An acute myeloid leukemia associated with t(1;22)(p13.3;q13.1) resulting in the expression of RBM15-MKL1 fusion protein. It affects infants and children and usually shows megakaryocytic maturation. MONDO:0020078
MONDO:0956704 childhood acute eosinophilic leukemia NCIT:C9165 MONDO:equivalentTo Childhood Acute Eosinophilic Leukemia An acute eosinophilic leukemia occurring in children. MONDO:0043881
MONDO:0956756 acute myeloid leukemia with inv(16)(p13.1q22) or t(16;16)(p13.1;q22); cbfb-myh11 NCIT:C9287 MONDO:equivalentTo Acute Myeloid Leukemia with inv(16)(p13.1q22) or t(16;16)(p13.1;q22); CBFB-MYH11 An acute myeloid leukemia with monocytic and granulocytic differentiation and the presence of a characteristically abnormal eosinophil component in the bone marrow. This type of acute myeloid leukemia has a favorable prognosis. (WHO, 2001) MONDO:0020078
MONDO:0956757 acute myeloid leukemia with t(8;21)(q22; q22.1); runx1-runx1t1 NCIT:C9288 MONDO:equivalentTo Acute Myeloid Leukemia with t(8;21)(q22; q22.1); RUNX1-RUNX1T1 An acute myeloid leukemia with t(8;21)(q22; q22.1) giving rise to RUNX1/RUNX1T1 fusion transcript and showing maturation in the neutrophil lineage. The bone marrow and the peripheral blood show large myeloblasts with abundant basophilic cytoplasm, often containing azurophilic granules. This type of AML is associated with good response to chemotherapy and high complete remission rate. MONDO:0020078
MONDO:0957380 cic-rearranged sarcoma NCIT:C120224 MONDO:equivalentTo CIC-Rearranged Sarcoma An undifferentiated, high grade small round cell sarcoma affecting predominantly young adults. It is characterized by a recurrent translocation involving the CIC gene on chromosome 19 and either DUX4 gene on chromosome 4 or DUX4L gene on chromosome 10. The translocation results in either CIC-DUX4, t(4;19)(q35;q13) or CIC-DUX4L, t(10;19)(q26;q13) fusions. MONDO:0858921
MONDO:0957623 smoldering systemic mastocytosis NCIT:C115460 MONDO:equivalentTo Smoldering Systemic Mastocytosis Slowly progressive systemic mastocytosis with uncertain prognosis. It is characterized by organomegaly and absence of aggressive disease. MONDO:0016586
MONDO:0957624 indolent clonal t-cell lymphoproliferative disorder of the gastrointestinal tract NCIT:C139021 MONDO:equivalentTo Indolent Clonal T-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract A clonal T-cell lymphoproliferative disorder that can involve the mucosa in all sites of the gastrointestinal tract, but is most common in the small intestine and colon. The lymphoid cells infiltrate the lamina propria but usually do not show invasion of the epithelium. The clinical course is indolent, but most patients do not respond to conventional chemotherapy. A subset of cases progress to a higher-grade T-cell lymphoma with spread beyond the gastrointestinal tract. (WHO 2017) MONDO:0005169
MONDO:0957625 penile adenosquamous carcinoma NCIT:C159248 MONDO:equivalentTo Penile Adenosquamous Carcinoma An extremely rare carcinoma that arises from the penis and is characterized by the presence of glandular and squamous components. MONDO:0006360
MONDO:0957626 seminal vesicle soft tissue neoplasm NCIT:C161637 MONDO:equivalentTo Seminal Vesicle Soft Tissue Neoplasm A mesenchymal neoplasm that arises from the seminal vesicle. MONDO:0002790
MONDO:0957627 hepatocellular malignant neoplasm, not otherwise specified NCIT:C161838 MONDO:equivalentTo Hepatocellular Malignant Neoplasm, Not Otherwise Specified A rare childhood malignant liver neoplasm with overlapping features of hepatoblastoma and hepatocellular carcinoma. MONDO:0018666
MONDO:0957628 epididymal melanotic neuroectodermal tumor NCIT:C162488 MONDO:equivalentTo Epididymal Melanotic Neuroectodermal Tumor A rare neoplasm that arises from the epididymis and is characterized by the presence of a mixture of melanin-containing epithelial cells and smaller neuroblast-like cells. It usually occurs in infants and has a benign clinical course. MONDO:0002072
MONDO:0957629 systemic mastocytosis with an associated germ cell tumor NCIT:C186735 MONDO:equivalentTo Systemic Mastocytosis with an Associated Germ Cell Tumor A disorder characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells and the presence of a co-occurring germ cell tumor. MONDO:0016586
MONDO:0957630 estrogen receptor-positive breast carcinoma NCIT:C188366 MONDO:equivalentTo Estrogen Receptor-Positive Breast Carcinoma Breast adenocarcinoma that is positive for estrogen receptors.
MONDO:0957631 childhood myelodysplastic syndrome with excess blasts NCIT:C188449 MONDO:equivalentTo Childhood Myelodysplastic Syndrome with Excess Blasts Myelodysplastic syndrome with excess blasts that occurs during childhood. MONDO:0044873
MONDO:0957632 childhood acute myeloid leukemia with t(9;11)(p21.3;q23.3); mllt3-kmt2a NCIT:C188451 MONDO:equivalentTo Childhood Acute Myeloid Leukemia with t(9;11)(p21.3;q23.3); MLLT3-KMT2A An acute myeloid leukemia with t(9;11)(p21.3;q23.3); MLLT3-KMT2A occurring in children. MONDO:0004996
MONDO:0957633 lung small cell carcinoma neuroendocrine subtype NCIT:C188753 MONDO:equivalentTo Lung Small Cell Carcinoma Neuroendocrine Subtype A header term that refers to the classification of lung small cell carcinoma based on the expression pattern of different neuroendocrine markers such as chromogranin A, synaptophysin, neural cell adhesion molecule 1, and gastrin-releasing peptide. MONDO:0008433
MONDO:0957634 lung small cell carcinoma molecular subtypes NCIT:C188756 MONDO:equivalentTo Lung Small Cell Carcinoma Molecular Subtypes A header term that refers to the molecular classification of lung small cell carcinoma according to the relative expression of four transcription factors: achaete-scute homolog 1 (ASCL1), neurogenic differentiation factor 1 (NEUROD1), yes-associated protein 1 (YAP1), and POU class 2 homeobox 3 (POU2F3). MONDO:0008433
MONDO:0957635 adult ganglioneuroma NCIT:C188947 MONDO:equivalentTo Adult Ganglioneuroma A ganglioneuroma that occurs in adults. MONDO:0005033
MONDO:0957636 childhood nervous system neoplasm NCIT:C188950 MONDO:equivalentTo Childhood Nervous System Neoplasm A neoplasm that affects the nervous system during childhood. MONDO:0021079
MONDO:0957637 choroidal ganglioneuroma NCIT:C188956 MONDO:equivalentTo Choroidal Ganglioneuroma A rare ganglioneuroma that arises from the choroid. MONDO:0021487
MONDO:0957638 childhood connective and soft tissue neoplasm NCIT:C188963 MONDO:equivalentTo Childhood Connective and Soft Tissue Neoplasm A soft tissue or bone neoplasm that occurs during childhood. MONDO:0021079
MONDO:0957639 childhood low grade fibromyxoid sarcoma NCIT:C188970 MONDO:equivalentTo Childhood Low Grade Fibromyxoid Sarcoma A low-grade fibromyxoid sarcoma that occurs during childhood. MONDO:0006272
MONDO:0957640 extragonadal teratoma NCIT:C189045 MONDO:equivalentTo Extragonadal Teratoma A teratoma that develops as a primary tumor in an anatomic site other than the testis or ovary. MONDO:0018201
MONDO:0957641 testicular teratoma, postpubertal-type NCIT:C189057 MONDO:equivalentTo Testicular Teratoma, Postpubertal-Type A testicular teratoma associated with germ cell neoplasia in situ and chromosome 12p amplification. MONDO:0018193
MONDO:0957642 kidney carcinoma molecular subtypes NCIT:C189241 MONDO:equivalentTo Kidney Carcinoma Molecular Subtypes A term that refers to the classification of kidney carcinomas according to their molecular characteristics. MONDO:0005206
MONDO:0957644 ovarian sertoli-leydig cell tumor molecular subtypes NCIT:C189319 MONDO:equivalentTo Ovarian Sertoli-Leydig Cell Tumor Molecular Subtypes A term that refers to the classification of ovarian Sertoli-Leydig cell tumors according to their molecular characteristics. MONDO:0036595
MONDO:0957645 mullerian papilloma NCIT:C189336 MONDO:equivalentTo Mullerian Papilloma A benign papillary neoplasm that arises from the cervix or vagina. It mostly occurs in prepubertal girls and rarely in adolescents or young adults. It is characterized by the presence of a fibrovascular core covered by cuboidal or columnar epithelial cells. Squamous metaplasia may be present. Cytologic atypia is absent. MONDO:0021078
MONDO:0957646 childhood breast neoplasm NCIT:C189338 MONDO:equivalentTo Childhood Breast Neoplasm A neoplasm that affects the breast and occurs during childhood. MONDO:0021079
MONDO:0957647 childhood digestive system neoplasm NCIT:C189869 MONDO:equivalentTo Childhood Digestive System Neoplasm A neoplasm that affects any part of the digestive system and occurs during childhood. MONDO:0021079
MONDO:0957648 epithelial hepatoblastoma NCIT:C189923 MONDO:equivalentTo Epithelial Hepatoblastoma A subtype of hepatoblastoma characterized by the presence of an epithelial component and absence of mesenchymal elements. It includes hepatoblastoma with pure fetal epithelial differentiation, hepatoblastoma with combined fetal and embryonal epithelial differentiation, macrotrabecular hepatoblastoma, and small cell undifferentiated hepatoblastoma (small cell undifferentiated hepatoblastoma with loss of INI1 nuclear staining should be classified as rhabdoid tumor). MONDO:0018666
MONDO:0957649 non-teratoid hepatoblastoma NCIT:C189926 MONDO:equivalentTo Non-Teratoid Hepatoblastoma A mixed epithelial and mesenchymal hepatoblastoma characterized by the absence of heterologous elements, muscle, cartilage or osteoid. MONDO:0003650
MONDO:0957650 hepatoblastoma by pretext stage NCIT:C189927 MONDO:equivalentTo Hepatoblastoma by PRETEXT Stage A term that refers to the staging of hepatoblastoma, following the rules of the PRETEXT (pre-treatment extent of tumor) system. MONDO:0018666
MONDO:0957651 hepatoblastoma by postsurgical stage NCIT:C189929 MONDO:equivalentTo Hepatoblastoma by Postsurgical Stage A term that refers to the staging of hepatoblastoma according to post-operative findings. MONDO:0018666
MONDO:0957652 childhood fibrolamellar carcinoma NCIT:C189932 MONDO:equivalentTo Childhood Fibrolamellar Carcinoma A fibrolamellar variant of hepatocellular carcinoma that occurs during childhood. MONDO:0018055
MONDO:0957653 childhood endocrine neoplasm NCIT:C190056 MONDO:equivalentTo Childhood Endocrine Neoplasm A benign or malignant neoplasm arising from the epithelial cells of an endocrine organ during childhood. MONDO:0021079
MONDO:0957654 childhood thoracic neoplasm NCIT:C190090 MONDO:equivalentTo Childhood Thoracic Neoplasm A benign or malignant neoplasm that involves the tissues of the thorax during childhood. MONDO:0021079
MONDO:0957655 childhood head and neck neoplasm NCIT:C190119 MONDO:equivalentTo Childhood Head and Neck Neoplasm A benign or malignant neoplasm that affects the anatomic structures of the head and neck region and occurs during childhood. MONDO:0005586
MONDO:0957656 childhood skin neoplasm NCIT:C190123 MONDO:equivalentTo Childhood Skin Neoplasm A benign, intermediate, or malignant neoplasm that affects the skin and occurs during childhood. MONDO:0002531
MONDO:0957657 childhood carcinoma NCIT:C190275 MONDO:equivalentTo Childhood Carcinoma A rare carcinoma that occurs during childhood. MONDO:0004993
MONDO:0957658 refractory t/nk-cell lymphoproliferative disorder NCIT:C190397 MONDO:equivalentTo Refractory T/NK-Cell Lymphoproliferative Disorder T/NK-cell lymphoproliferative disorder that is resistant to treatment.
MONDO:0957659 recurrent t/nk-cell lymphoproliferative disorder NCIT:C190398 MONDO:equivalentTo Recurrent T/NK-Cell Lymphoproliferative Disorder The reemergence of T/NK-cell lymphoproliferative disorder after a period of remission.
MONDO:0957660 ebv-related t/nk-cell lymphoproliferative disorder NCIT:C190402 MONDO:equivalentTo EBV-Related T/NK-Cell Lymphoproliferative Disorder T/NK-cell lymphoproliferative disorder that is associated with Epstein-Barr virus.
MONDO:0957661 childhood benign neoplasm NCIT:C190573 MONDO:equivalentTo Childhood Benign Neoplasm A neoplasm that occurs during childhood and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0021079
MONDO:0957662 benign liver neoplasm NCIT:C190592 MONDO:equivalentTo Benign Liver Neoplasm A neoplasm that arises from the liver and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0024477
MONDO:0957663 high grade endometrial carcinoma NCIT:C190680 MONDO:equivalentTo High Grade Endometrial Carcinoma A group of aggressive endometrial carcinomas with high-grade histological features. It includes high grade endometrial endometrioid adenocarcinoma, endometrial clear cell adenocarcinoma, endometrial serous adenocarcinoma, and endometrial undifferentiated carcinoma. MONDO:0002447
MONDO:0957664 iridociliary melanoma NCIT:C190746 MONDO:equivalentTo Iridociliary Melanoma Melanoma that affects both the iris and ciliary body. MONDO:0006486
MONDO:0957665 b acute lymphoblastic leukemia associated with down syndrome NCIT:C190847 MONDO:equivalentTo B Acute Lymphoblastic Leukemia Associated with Down Syndrome A B-acute lymphoblastic leukemia that occurs in patients with Down syndrome. It usually affects young children, but it can occur in adults as well. It has an unfavorable clinical outcome. Cases of T-acute lymphoblastic leukemia in patients with Down syndrome have not been reported. MONDO:0020511
MONDO:0957666 androgen receptor-positive breast carcinoma NCIT:C190851 MONDO:equivalentTo Androgen Receptor-Positive Breast Carcinoma Breast carcinoma that is positive for androgen receptors.
MONDO:0957667 b lymphoblastic leukemia/lymphoma with etv6-runx1-like features NCIT:C190956 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma with ETV6-RUNX1-Like Features B lymphoblastic leukemia/lymphoma characterized by a gene-expression profile similar to that of ETV6-RUNX1-positive B lymphoblastic leukemia/lymphoma, absence of the pathognomonic ETV6-RUNX1 rearrangement, and rearrangements or deletions of ETV6 and IKZF1 genes. MONDO:0035605
MONDO:0957668 renal cell carcinoma, not otherwise specified NCIT:C191370 MONDO:equivalentTo Renal Cell Carcinoma, Not Otherwise Specified A renal cell carcinoma that cannot be classified into one of the established subtypes of renal cell carcinoma. MONDO:0005549
MONDO:0957669 kidney classic angiomyolipoma NCIT:C191391 MONDO:equivalentTo Kidney Classic Angiomyolipoma A benign mesenchymal tumor that arises from the kidney and is composed of mature adipose tissue, thick-walled blood vessels, and epithelioid and spindle smooth muscle cells. MONDO:0002513
MONDO:0957670 secondary plasma cell leukemia NCIT:C191432 MONDO:equivalentTo Secondary Plasma Cell Leukemia Transformation of plasma cell myeloma to plasma cell leukemia. MONDO:0018689
MONDO:0957671 papillary urothelial neoplasm of low malignant potential NCIT:C191672 MONDO:equivalentTo Papillary Urothelial Neoplasm of Low Malignant Potential A papillary neoplasm of the urothelium. The papillary structures exhibit minimal architectural distortion and minimal atypia. Mitoses are infrequent. It usually occurs in the urinary bladder, but it can arise from other sites in the urinary tract. Patients are at an increased risk of developing new papillary lesions. Occasionally, the new lesions are urothelial carcinomas. MONDO:0003755
MONDO:0957672 invasive lymphoepithelioma-like urothelial carcinoma NCIT:C191678 MONDO:equivalentTo Invasive Lymphoepithelioma-Like Urothelial Carcinoma Invasive urothelial carcinoma with lymphoepithelioma-like features. MONDO:0003572
MONDO:0957673 invasive giant cell urothelial carcinoma NCIT:C191679 MONDO:equivalentTo Invasive Giant Cell Urothelial Carcinoma An invasive urothelial carcinoma characterized by the presence of giant cells. MONDO:0040678
MONDO:0957674 invasive urothelial carcinoma with glandular differentiation NCIT:C191680 MONDO:equivalentTo Invasive Urothelial Carcinoma with Glandular Differentiation An invasive urothelial carcinoma that exhibits glandular differentiation. MONDO:0040678
MONDO:0957675 invasive urothelial carcinoma with squamous differentiation NCIT:C191681 MONDO:equivalentTo Invasive Urothelial Carcinoma with Squamous Differentiation An invasive urothelial carcinoma that exhibits squamous differentiation. MONDO:0040678
MONDO:0957676 invasive urothelial carcinoma with trophoblastic differentiation NCIT:C191682 MONDO:equivalentTo Invasive Urothelial Carcinoma with Trophoblastic Differentiation An invasive urothelial carcinoma characterized by the presence of trophoblastic differentiation. MONDO:0040678
MONDO:0957677 invasive clear cell (glycogen-rich) urothelial carcinoma NCIT:C191683 MONDO:equivalentTo Invasive Clear Cell (Glycogen-Rich) Urothelial Carcinoma An invasive urothelial carcinoma characterized by the presence of clear (glycogen-rich) cells. MONDO:0040678
MONDO:0957678 invasive lipid-rich urothelial carcinoma NCIT:C191684 MONDO:equivalentTo Invasive Lipid-Rich Urothelial Carcinoma Invasive urothelial carcinoma characterized by the presence of lipid laden tumor cells. MONDO:0040678
MONDO:0957679 invasive microcystic urothelial carcinoma NCIT:C191685 MONDO:equivalentTo Invasive Microcystic Urothelial Carcinoma Invasive urothelial carcinoma characterized by microcysts formation. MONDO:0040678
MONDO:0957680 invasive nested urothelial carcinoma NCIT:C191687 MONDO:equivalentTo Invasive Nested Urothelial Carcinoma Invasive urothelial carcinoma characterized by a nested growth pattern. MONDO:0040678
MONDO:0957681 invasive plasmacytoid urothelial carcinoma NCIT:C191688 MONDO:equivalentTo Invasive Plasmacytoid Urothelial Carcinoma Invasive urothelial carcinoma characterized by the presence of malignant cells with plasmacytoid features. MONDO:0040678
MONDO:0957682 invasive large nested urothelial carcinoma NCIT:C191725 MONDO:equivalentTo Invasive Large Nested Urothelial Carcinoma A rare invasive urothelial carcinoma characterized by the presence of medium to large nests of malignant cells. MONDO:0040678
MONDO:0957683 invasive tubular urothelial carcinoma NCIT:C191728 MONDO:equivalentTo Invasive Tubular Urothelial Carcinoma Invasive urothelial carcinoma characterized by the presence of a tubular growth pattern. MONDO:0040678
MONDO:0957684 invasive poorly differentiated urothelial carcinoma NCIT:C191730 MONDO:equivalentTo Invasive Poorly Differentiated Urothelial Carcinoma Invasive urothelial carcinoma that lacks the morphological features indicating urothelial origin. Immunohistochemical studies are required to demonstrate the urothelial lineage in these tumors. MONDO:0040678
MONDO:0957685 invasive conventional urothelial carcinoma NCIT:C191734 MONDO:equivalentTo Invasive Conventional Urothelial Carcinoma Invasive urothelial carcinoma characterized by the presence of malignant cells forming trabeculae, cords, sheets, and nests. Individual malignant cells are also present. MONDO:0040678
MONDO:0957686 prostatic intraepithelial neoplasia-like adenocarcinoma NCIT:C191961 MONDO:equivalentTo Prostatic Intraepithelial Neoplasia-Like Adenocarcinoma A rare subtype of prostate acinar adenocarcinoma that morphologically resembles high-grade prostatic intraepithelial neoplasia. It is characterized by the presence of large malignant glands lined with pseudostratified epithelium. It is graded as Gleason score 3+3=6. MONDO:0002493
MONDO:0957687 extrapulmonary neuroendocrine carcinoma NCIT:C191977 MONDO:equivalentTo Extrapulmonary Neuroendocrine Carcinoma A small or large cell neuroendocrine carcinoma that arises from an anatomic site other than the lung. MONDO:0002120
MONDO:0957688 intratubular embryonal carcinoma NCIT:C192096 MONDO:equivalentTo Intratubular Embryonal Carcinoma Intratubular germ cell neoplasia characterized by the filling of the seminiferous tubules by embryonal carcinoma cells. Central necrosis and calcifications are often present. MONDO:0006446
MONDO:0957689 testicular yolk sac tumor, postpubertal-type NCIT:C192099 MONDO:equivalentTo Testicular Yolk Sac Tumor, Postpubertal-Type Testicular yolk sac tumor that is associated with germ cell neoplasia in situ and usually occurs as a component of mixed germ cell tumor. Pure postpubertal-type testicular yolk sac tumor is exceedingly rare. MONDO:0003402
MONDO:0957690 cystic trophoblastic tumor NCIT:C192105 MONDO:equivalentTo Cystic Trophoblastic Tumor A rare trophoblastic neoplasm that arises in metastatic sites of testicular mixed germ cell tumors following chemotherapy, or is part of treated or untreated testicular mixed germ cell tumors, or is secondary to either chemotherapy-induced or spontaneous regression of testicular choriocarcinoma. It has also been described in central nervous system post-chemotherapy primary germ cell tumors. It is characterized by the presence of cysts lined by squamoid trophoblastic cells. The cysts are often compressed surrounded by other germ cell components. MONDO:0021077
MONDO:0957691 testicular teratoma, prepubertal-type NCIT:C192107 MONDO:equivalentTo Testicular Teratoma, Prepubertal-Type A testicular teratoma that is not associated with germ cell neoplasia in situ or chromosome 12p amplification. MONDO:0018193
MONDO:0957692 gonadal myoid stromal tumor NCIT:C192116 MONDO:equivalentTo Gonadal Myoid Stromal Tumor A rare, benign, well-circumscribed tumor that arises from the testis. It is characterized by the presence of fascicles of spindle cells showing muscle cell differentiation. It lacks sex cord differentiation. MONDO:0021447
MONDO:0957693 penile squamous cell carcinoma, not otherwise specified NCIT:C192222 MONDO:equivalentTo Penile Squamous Cell Carcinoma, Not Otherwise Specified A penile squamous cell carcinoma characterized by the absence of special morphologic features and lack of information on p16 immunohistochemistry and human papilloma virus testing status. MONDO:0018352
MONDO:0957694 penile mucoepidermoid carcinoma NCIT:C192223 MONDO:equivalentTo Penile Mucoepidermoid Carcinoma An extremely rare carcinoma that arises from the penis and is characterized by the presence of mucinous and squamous components. MONDO:0006360
MONDO:0957695 urinary tract neoplasm NCIT:C192666 MONDO:equivalentTo Urinary Tract Neoplasm A benign or malignant, primary or metastatic neoplasm involving the urinary tract (renal pelvis, ureter, bladder, and urethra). MONDO:0021066
MONDO:0957696 benign cranial nerve neoplasm NCIT:C193416 MONDO:equivalentTo Benign Cranial Nerve Neoplasm A neoplasm that arises from a cranial nerve and is characterized by the absence of atypical or malignant cytological and architectural features, and absence of invasive features or metastatic potential. MONDO:0002633
MONDO:0957697 benign spinal meningioma NCIT:C193417 MONDO:equivalentTo Benign Spinal Meningioma A grade I, slowly growing meningioma that arises from the spinal meninges. MONDO:0003054
MONDO:0957698 rectal gastrointestinal stromal tumor NCIT:C193420 MONDO:equivalentTo Rectal Gastrointestinal Stromal Tumor Gastrointestinal stromal tumor that arises from the rectum. MONDO:0002165
MONDO:0957699 malignant ileal neoplasm NCIT:C193425 MONDO:equivalentTo Malignant Ileal Neoplasm A primary or metastatic malignant neoplasm involving the ileum. MONDO:0006801
MONDO:0957700 refractory malignant phyllodes tumor NCIT:C193453 MONDO:equivalentTo Refractory Malignant Phyllodes Tumor Malignant phyllodes tumor that is resistant to treatment. MONDO:0037003
MONDO:0957701 childhood cancer stage by toronto guidelines v2 NCIT:C198027 MONDO:equivalentTo Childhood Cancer Stage by Toronto Guidelines v2 A term that refers to the staging of childhood cancers following the rules of the Toronto guidelines v2, 2019. The guidelines were developed to address the lack of consistent information on childhood cancer staging in population registries and are not intended to replace staging systems in clinical use. They include a two-tiered approach that provides less detailed criteria for registries with limited resources and/or limited data access (Tier 1) and more detailed criteria for better-resourced registries (Tier 2). They apply to acute lymphoblastic leukemia, Hodgkin lymphoma, non-Hodgkin lymphoma, neuroblastoma, renal malignant tumors except renal cell carcinoma, rhabdomyosarcoma, non-rhabdomyosarcoma soft tissue sarcoma, malignant bone tumors, retinoblastoma, hepatoblastoma, testicular germ cell tumors, ovarian germ cell tumors, astrocytoma, medulloblastoma and ependymoma. The following changes were noted to the original classification (v1, 2014): a staging system was no longer considered appropriate for acute myeloid leukemia; all renal tumors, with the exception of renal cell carcinomas, should use the endorsed staging systems for Wilms tumor; staging systems for osteosarcoma and Ewing sarcoma were combined into a single recommendation for all malignant bone tumors; a staging system was endorsed for astrocytomas; the S category (serum tumor markers) was confirmed as an integral part of TNM staging for testicular cancer in Tier 2 recommendations; and PRETEXT number was added to Tier 2 recommendations for hepatoblastoma. (adapted from Childhood cancer staging for population registries according to the Toronto Childhood Cancer Stage Guidelines - Version 2. Cancer Council Queensland and Cancer Australia: Brisbane, Australia; 2021.) MONDO:0006517
MONDO:0957702 myeloproliferative neoplasm, bcr-abl1 negative NCIT:C198555 MONDO:equivalentTo Myeloproliferative Neoplasm, BCR-ABL1 Negative A myeloproliferative neoplasm characterized by the absence of Philadelphia chromosome and BCR-ABL1 fusion gene expression. This group includes polycythemia vera, essential thrombocythemia, and primary myelofibrosis. MONDO:0020076
MONDO:0957703 myeloid/lymphoid neoplasms with flt3 rearrangement NCIT:C198559 MONDO:equivalentTo Myeloid/Lymphoid Neoplasms with FLT3 Rearrangement Hematologic neoplasms characterized by the rearrangement of the FLT3 gene, most often resulting in the formation of t(12;13)(p13.2;q12.2)/ETV6-FLT3 fusion transcripts. Patients usually present with T-ALL or myeloid sarcoma. MONDO:0015688
MONDO:0957704 myeloid/lymphoid neoplasms with etv6-abl1 NCIT:C198565 MONDO:equivalentTo Myeloid/Lymphoid Neoplasms with ETV6-ABL1 Hematologic neoplasms characterized by t(9;12)(q34.1;p13.2) that results in ETV6-ABL1 gene fusion. They have clinicopathological features of chronic myeloid leukemia with frequent eosinophilia. MONDO:0015688
MONDO:0957705 bone marrow mastocytosis NCIT:C198573 MONDO:equivalentTo Bone Marrow Mastocytosis A variant of indolent systemic mastocytosis that affects predominantly older males. It is characterized by a limited degree of bone marrow infiltration by clonal mast cells and an absence of skin involvement. The serum tryptase levels are normal or slightly elevated. MONDO:0020331
MONDO:0957706 clonal monocytosis of undetermined significance NCIT:C198580 MONDO:equivalentTo Clonal Monocytosis of Undetermined Significance A myelodysplastic/myeloproliferative neoplasm characterized by the presence of persistent monocytosis, presence of at least one myeloid neoplasm-associated mutation, absence of significant dysplasia or increased blasts in the bone marrow, absence of morphologic findings suggestive of chronic myelomonocytic leukemia in the bone marrow, and absence of history of a reactive condition that would explain the persistent monocytosis. MONDO:0006311
MONDO:0957707 myelodysplastic/myeloproliferative neoplasm with sf3b1 mutation and thrombocytosis NCIT:C198581 MONDO:equivalentTo Myelodysplastic/Myeloproliferative Neoplasm with SF3B1 Mutation and Thrombocytosis A myelodysplastic/myeloproliferative neoplasm characterized by thrombocytosis, anemia, blasts less than 5% in bone marrow and less than 1% in peripheral blood, presence of SF3B1 gene mutation, absence of BCR/ABL fusion, absence of genetic abnormalities associated with myeloid/lymphoid neoplasms with eosinophilia and tyrosine kinase gene fusions, and no history of other myelodysplastic/myeloproliferative neoplasms or myeloproliferative neoplasms and myelodysplastic syndromes. MONDO:0006311
MONDO:0957708 clonal cytopenia with monocytosis of undetermined significance NCIT:C198582 MONDO:equivalentTo Clonal Cytopenia with Monocytosis of Undetermined Significance A myelodysplastic/myeloproliferative neoplasm that fulfills the diagnostic criteria of clonal monocytosis of undetermined significance and is associated with cytopenia. MONDO:0006311
MONDO:0957709 myeloid neoplasm with mutated tp53 NCIT:C198593 MONDO:equivalentTo Myeloid Neoplasm with Mutated TP53 Myeloid neoplasm characterized by the presence of TP53 gene mutations. This category includes myelodysplastic syndrome, myelodysplastic syndrome/acute myeloid leukemia, and acute myeloid leukemia with mutated TP53. MONDO:0005170
MONDO:0957710 myelodysplastic syndrome/acute myeloid leukemia, not otherwise specified NCIT:C198597 MONDO:equivalentTo Myelodysplastic Syndrome/Acute Myeloid Leukemia, Not Otherwise Specified Myelodysplastic syndrome/acute myeloid leukemia in which there is no information on myelodysplasia-related gene mutations and cytogenetic abnormalities. MONDO:0015041
MONDO:0957711 pediatric and/or germline mutation-associated myeloid disorders NCIT:C198663 MONDO:equivalentTo Pediatric and/or Germline Mutation-Associated Myeloid Disorders A group of myeloid disorders that occur in childhood and/or are associated with germline gene mutations. It includes juvenile myelomonocytic leukemia, juvenile myelomonocytic leukemia-like neoplasm, refractory cytopenia of childhood, Noonan syndrome-associated myeloproliferative disorder, and myeloid neoplasm with germline predisposition. MONDO:0005170
MONDO:0957712 b acute lymphoblastic leukemia with germline predisposition NCIT:C198683 MONDO:equivalentTo B Acute Lymphoblastic Leukemia with Germline Predisposition B-acute lymphoblastic leukemia that results from germline gene mutations. This category includes B-acute lymphoblastic leukemia with germline PAX5 mutation and B-acute lymphoblastic leukemia with germline IKZF1 mutation. MONDO:0020511
MONDO:0957713 acute myeloid leukemia with stat3-rara NCIT:C198827 MONDO:equivalentTo Acute Myeloid Leukemia with STAT3-RARA Acute myeloid leukemia with variant RARA rearrangement and expression of STAT3-RARA fusion protein. MONDO:0100375
MONDO:0957714 acute myeloid leukemia with t(1;17)(q42.3;q21.2); irf2bp2-rara NCIT:C198831 MONDO:equivalentTo Acute Myeloid Leukemia with t(1;17)(q42.3;q21.2); IRF2BP2-RARA Acute myeloid leukemia with variant RARA rearrangement associated with t(1;17)(q42.3;q21.2) resulting in IRF2BP2-RARA fusion protein expression. MONDO:0100375
MONDO:0957715 acute myeloid leukemia with tbl1xr1-rara NCIT:C198834 MONDO:equivalentTo Acute Myeloid Leukemia with TBL1XR1-RARA Acute myeloid leukemia with variant RARA rearrangement and expression of TBL1XR1-RARA fusion protein. MONDO:0100375
MONDO:0957716 acute myeloid leukemia with fip1l1-rara NCIT:C198839 MONDO:equivalentTo Acute Myeloid Leukemia with FIP1L1-RARA Acute myeloid leukemia with variant RARA rearrangement and expression of FIP1L1-RARA fusion protein. MONDO:0100375
MONDO:0957717 acute myeloid leukemia with bcor-rara NCIT:C198841 MONDO:equivalentTo Acute Myeloid Leukemia with BCOR-RARA Acute myeloid leukemia with variant RARA rearrangement and expression of BCOR-RARA fusion protein. MONDO:0100375
MONDO:0957718 acute myeloid leukemia with in-frame bzip cebpa mutation NCIT:C198891 MONDO:equivalentTo Acute Myeloid Leukemia with In-Frame bZIP CEBPA Mutation An acute myeloid leukemia characterized by the presence of CEBPA bZIP domain mutation. It is associated with a favorable clinical outcome. MONDO:0017894
MONDO:0957719 acute myeloid leukemia with myelodysplasia-related cytogenetic abnormalities NCIT:C198957 MONDO:equivalentTo Acute Myeloid Leukemia with Myelodysplasia-Related Cytogenetic Abnormalities A group of acute myeloid leukemias classified based on specific karyotype findings. MONDO:0100409
MONDO:0957720 low grade endometrioid adenocarcinoma NCIT:C199146 MONDO:equivalentTo Low Grade Endometrioid Adenocarcinoma Endometrioid adenocarcinoma exhibiting 50% or less solid non-glandular, non-squamous growth. MONDO:0005026
MONDO:0957721 high grade endometrioid adenocarcinoma NCIT:C199149 MONDO:equivalentTo High Grade Endometrioid Adenocarcinoma Endometrioid adenocarcinoma exhibiting more than 50% solid non-glandular, non-squamous growth. MONDO:0005026
MONDO:0957722 early t precursor lymphoblastic leukemia/lymphoma NCIT:C199170 MONDO:equivalentTo Early T Precursor Lymphoblastic Leukemia/Lymphoma T lymphoblastic leukemia/lymphoma in which the blasts have unique immunophenotypic and genetic characteristics suggesting only limited early T-cell differentiation. MONDO:0003537
MONDO:0957724 early t precursor acute lymphoblastic leukemia, not otherwise specified NCIT:C199172 MONDO:equivalentTo Early T Precursor Acute Lymphoblastic Leukemia, Not Otherwise Specified Early T precursor acute lymphoblastic leukemia in which further genetic/molecular characterization is not available. MONDO:0100291
MONDO:0957725 t lymphoblastic leukemia/lymphoma, not otherwise specified NCIT:C199173 MONDO:equivalentTo T Lymphoblastic Leukemia/Lymphoma, Not Otherwise Specified T-lymphoblastic leukemia/lymphoma in which further genetic/molecular characterization is not available. MONDO:0003537
MONDO:0957726 b acute lymphoblastic leukemia with recurrent genetic abnormalities NCIT:C199202 MONDO:equivalentTo B Acute Lymphoblastic Leukemia with Recurrent Genetic Abnormalities B-acute lymphoblastic leukemias characterized by the presence of recurring cytogenetic and/or molecular abnormalities. MONDO:0020511
MONDO:0957727 b lymphoblastic leukemia/lymphoma with myc rearrangement NCIT:C199231 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma with MYC Rearrangement B-lymphoblastic leukemia/lymphoma associated with MYC gene rearrangement. The prognosis is poor. MONDO:0035605
MONDO:0957728 primary cold agglutinin disease NCIT:C199387 MONDO:equivalentTo Primary Cold Agglutinin Disease A clonal B-cell lymphoproliferative disease of the bone marrow that results in autoimmune hemolytic anemia. It is distinct from lymphoplasmacytic lymphoma and IgM monoclonal gammopathy of undetermined significance. It lacks MYD88 gene mutation and is associated with trisomies of chromosomes 3, 12, and 18, and mutations in KMT2D and CARD11 genes. MONDO:0004949
MONDO:0957729 multiple myeloma with recurrent genetic abnormalities NCIT:C199392 MONDO:equivalentTo Multiple Myeloma with Recurrent Genetic Abnormalities Multiple myelomas characterized by the presence of recurring cytogenetic abnormalities. MONDO:0009693
MONDO:0957730 multiple myeloma, not otherwise specified NCIT:C199418 MONDO:equivalentTo Multiple Myeloma, Not Otherwise Specified Multiple myelomas characterized by the absence of recurrent genetic abnormalities. MONDO:0009693
MONDO:0957731 heavy chain class-switched primary cutaneous marginal zone lymphoproliferative disorder NCIT:C199457 MONDO:equivalentTo Heavy Chain Class-Switched Primary Cutaneous Marginal Zone Lymphoproliferative Disorder A primary cutaneous marginal zone lymphoproliferative disorder characterized by class-switched immunoglobulin heavy chain expression. The majority of cases are IgG-positive. MONDO:0015813
MONDO:0957732 igm-positive primary cutaneous marginal zone lymphoproliferative disorder NCIT:C199460 MONDO:equivalentTo IgM-Positive Primary Cutaneous Marginal Zone Lymphoproliferative Disorder A primary cutaneous marginal zone lymphoproliferative disorder characterized by expression of IgM and absence of class-switched immunoglobulin heavy chain expression. MONDO:0015813
MONDO:0957733 bcl2-r-negative, cd23-positive follicle center lymphoma NCIT:C199467 MONDO:equivalentTo BCL2-R-Negative, CD23-Positive Follicle Center Lymphoma Follicular lymphoma characterized by the absence of BCL2 rearrangement and the presence of CD23-positive neoplastic cells. It is associated with STAT6 mutations. It presents with low-stage disease, typically in the inguinal region, and often has a predominant diffuse growth pattern. MONDO:0018906
MONDO:0957734 cyclin d1-positive mantle cell lymphoma NCIT:C199481 MONDO:equivalentTo Cyclin D1-Positive Mantle Cell Lymphoma A molecular subtype of mantle cell lymphoma characterized by the presence of cyclin D1 expression and/or CCND1 rearrangement.. MONDO:0018876
MONDO:0957735 hhv-8 and ebv-negative primary effusion-based lymphoma NCIT:C199576 MONDO:equivalentTo HHV-8 and EBV-Negative Primary Effusion-Based Lymphoma An HHV-8 and EBV-negative primary effusion-based lymphoma that affects elderly, HIV-negative patients with history of medical conditions that result in fluid overload. The majority of cases have been reported in Japan. Most tumors exhibit centroblastic or immunoblastic morphology. The prognosis is good. MONDO:0018905
MONDO:0957736 classic hydroa vacciniforme lymphoproliferative disorder NCIT:C199676 MONDO:equivalentTo Classic Hydroa Vacciniforme Lymphoproliferative Disorder Hydroa vacciniforme lymphoproliferative disorder characterized by the presence of self-limited papulovesicular skin lesions in sun-exposed areas. There is no involvement of internal organs. It has an indolent course and usually affects White individuals. MONDO:0018224
MONDO:0957737 systemic hydroa vacciniforme lymphoproliferative disorder NCIT:C199677 MONDO:equivalentTo Systemic Hydroa Vacciniforme Lymphoproliferative Disorder Hydroa vacciniforme lymphoproliferative disorder characterized by severe clinical course and associated with fever, lymph node involvement, and involvement of internal organs by EBV-positive T-cells and NK-cells. It usually affects Asian and Latin American individuals. MONDO:0018224
MONDO:0957738 indolent nk-cell lymphoproliferative disorder of the gastrointestinal tract NCIT:C200037 MONDO:equivalentTo Indolent NK-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract An indolent lymphoproliferative disorder that affects the gastrointestinal tract. The neoplastic lymphocytes have the typical phenotype of NK-cells, are of medium to large size, show mild pleomorphism, and are EBV infection negative. Features that characterize extranodal NK/T-cell lymphomas (e.g., angioinvasion and angiodestruction) are not present. MONDO:0005169
MONDO:0957739 peripheral t-cell lymphoma-gata3 NCIT:C200073 MONDO:equivalentTo Peripheral T-Cell Lymphoma-GATA3 A molecular subtype of peripheral T-cell lymphoma, not otherwise specified, characterized by high expression of GATA3. It is composed of a monomorphic lymphocytic infiltrate with minimal inflammation and is associated with a poor prognosis. MONDO:0004964
MONDO:0957740 peripheral t-cell lymphoma-tbx21 NCIT:C200074 MONDO:equivalentTo Peripheral T-Cell Lymphoma-TBX21 A molecular subtype of peripheral T-cell lymphoma, not otherwise specified, characterized by high expression of T-box 21 (TBX21). It is composed of a polymorphic lymphocytic infiltrate admixed with abundant inflammatory cells and is associated with a better prognosis compared to peripheral T-cell lymphoma-GATA3. MONDO:0004964
MONDO:0957741 alk-positive histiocytosis NCIT:C200105 MONDO:equivalentTo ALK-Positive Histiocytosis A rare histiocytic neoplasm associated with ALK gene rearrangement leading to activation of signaling pathways. The neoplastic cells have a mature histiocytic phenotype, and usually have a foamy cytoplasm. It is characterized by frequent neurologic involvement and responds to ALK inhibition treatments. MONDO:0006247
MONDO:0957742 vulvar tubulovillous adenoma NCIT:C200207 MONDO:equivalentTo Vulvar Tubulovillous Adenoma An intestinal-type adenoma that arises from the vulva. It is characterized by the presence of a tubulovillous architectural pattern. MONDO:0002198
MONDO:0957743 pancreatic cystic neoplasm NCIT:C200227 MONDO:equivalentTo Pancreatic Cystic Neoplasm A benign, borderline, or malignant cystic neoplasm that arises from the exocrine pancreas. This category includes pancreatic mucinous-cystic neoplasms, pancreatic cystadenomas, and pancreatic cystadenocarcinomas. MONDO:0021077
MONDO:0957744 myelodysplastic syndrome with low blasts NCIT:C200389 MONDO:equivalentTo Myelodysplastic Syndrome with Low Blasts Myelodysplastic syndrome characterized by the presence of less than 5% blasts in bone marrow and less than 2% blasts in peripheral blood. MONDO:0018881
MONDO:0957745 myelodysplastic syndrome with genetic abnormalities NCIT:C200390 MONDO:equivalentTo Myelodysplastic Syndrome with Genetic Abnormalities Myelodysplastic syndrome characterized by the presence of defining genetic abnormalities. MONDO:0018881
MONDO:0957746 myelodysplastic syndrome/acute myeloid leukemia with myelodysplasia-related gene mutations NCIT:C200400 MONDO:equivalentTo Myelodysplastic Syndrome/Acute Myeloid Leukemia with Myelodysplasia-Related Gene Mutations Myelodysplastic syndromes/acute myeloid leukemias characterized by the presence of gene mutations that are associated with myelodysplasia. MONDO:0015041
MONDO:0957747 myelodysplastic syndrome/acute myeloid leukemia with myelodysplasia-related cytogenetic abnormalities NCIT:C200402 MONDO:equivalentTo Myelodysplastic Syndrome/Acute Myeloid Leukemia with Myelodysplasia-Related Cytogenetic Abnormalities Myelodysplastic syndromes/acute myeloid leukemias classified based on specific karyotype findings. MONDO:0015041
MONDO:0957748 acute myeloid leukemia with mecom rearrangement NCIT:C200407 MONDO:equivalentTo Acute Myeloid Leukemia with MECOM Rearrangement Acute myeloid leukemia characterized by rearrangement of the MECOM gene with various genes. MONDO:0020078
MONDO:0957749 acute myeloid leukemia with nup98 rearrangement NCIT:C200411 MONDO:equivalentTo Acute Myeloid Leukemia with NUP98 Rearrangement Acute myeloid leukemia characterized by rearrangement of the NUP98 gene with various genes. MONDO:0020078
MONDO:0957750 acute myeloid leukemia with fus-erg NCIT:C200419 MONDO:equivalentTo Acute Myeloid Leukemia with FUS-ERG Acute myeloid leukemia associated with FUS-ERG gene fusion. The prognosis is poor. MONDO:0020078
MONDO:0957751 acute myeloid leukemia with npm1-mlf1 NCIT:C200420 MONDO:equivalentTo Acute Myeloid Leukemia with NPM1-MLF1 Acute myeloid leukemia associated with NPM1-MLF1 gene fusion. MONDO:0020078
MONDO:0957752 acute myeloid leukemia with kat6a-crebbp NCIT:C200421 MONDO:equivalentTo Acute Myeloid Leukemia with KAT6A-CREBBP Acute myeloid leukemia associated with KAT6A-CREBBP gene fusion. MONDO:0020078
MONDO:0957753 acute leukemia of ambiguous lineage with defining genetic abnormalities NCIT:C200494 MONDO:equivalentTo Acute Leukemia of Ambiguous Lineage with Defining Genetic Abnormalities Acute leukemia of ambiguous lineage characterized by the presence of defined genetic alterations. MONDO:0019460
MONDO:0957754 mature plasmacytoid dendritic cell proliferation associated with myeloid neoplasm NCIT:C200513 MONDO:equivalentTo Mature Plasmacytoid Dendritic Cell Proliferation Associated with Myeloid Neoplasm A clonal proliferation of plasmacytoid dendritic cells in patients with defined myeloid neoplasms. It is characterized by neoplastic proliferations of mature cells with plasmacytoid morphology in the skin, bone marrow, and very rarely, lymph nodes. Patients are predominantly older males. MONDO:0006247
MONDO:0957755 b lymphoblastic leukemia/lymphoma with tcf3-hlf rearrangement NCIT:C200587 MONDO:equivalentTo B Lymphoblastic Leukemia/Lymphoma with TCF3-HLF Rearrangement An exceptionally rare childhood B-lymphoblastic leukemia/lymphoma associated with TCF3-HLF gene rearrangement resulting in the formation of TCF3-HLF chimeric transcription factor. The prognosis is poor. MONDO:0035605
MONDO:0957756 atypical teratoid/rhabdoid tumor molecular subtypes NCIT:C200597 MONDO:equivalentTo Atypical Teratoid/Rhabdoid Tumor Molecular Subtypes A term that refers to the classification of atypical teratoid/rhabdoid tumors according to their molecular characteristics. MONDO:0020560
MONDO:0957757 classic follicular lymphoma NCIT:C200669 MONDO:equivalentTo Classic Follicular Lymphoma A term that refers to follicular lymphoma grade 1, 2, and 3A. MONDO:0018906
MONDO:0957758 follicular lymphoma with unusual cytological features NCIT:C200684 MONDO:equivalentTo Follicular Lymphoma with Unusual Cytological Features An uncommon morphologic variant of follicular lymphoma characterized by the presence of predominantly medium-sized neoplastic lymphocytes with blastoid features or large neoplastic lymphocytes with cleaved nuclei. MONDO:0018906
MONDO:0957759 cyclin d1-negative mantle cell lymphoma NCIT:C200685 MONDO:equivalentTo Cyclin D1-Negative Mantle Cell Lymphoma A molecular subtype of mantle cell lymphoma characterized by the absence of cyclin D1 expression and CCND1 rearrangement. MONDO:0018876
MONDO:0957760 primary large b-cell lymphoma of immune-privileged site NCIT:C200687 MONDO:equivalentTo Primary Large B-Cell Lymphoma of Immune-Privileged Site A term that refers to diffuse large B-cell lymphomas that arise as primary tumors in the central nervous system, vitreoretina, and testis in immunocompetent patients. MONDO:0018905
MONDO:0957761 ebv-negative burkitt lymphoma NCIT:C200688 MONDO:equivalentTo EBV-Negative Burkitt Lymphoma Burkitt lymphoma that is not associated with Epstein-Barr virus infection. MONDO:0007243
MONDO:0957762 plasma cell neoplasm with associated paraneoplastic syndrome NCIT:C200738 MONDO:equivalentTo Plasma Cell Neoplasm with Associated Paraneoplastic Syndrome A term that refers to rare paraneoplastic syndromes associated with plasma cell neoplasms. This category includes the following: POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes); TEMPI syndrome (telangiectasia, elevated erythropoietin and erythrocytosis, monoclonal gammopathy, perinephric fluid collection, and intrapulmonary shunting); and AESOP syndrome (adenopathy and extensive skin patch overlying a plasmacytoma). MONDO:0004959
MONDO:0957763 who grade 4 glioma NCIT:C200758 MONDO:equivalentTo WHO Grade 4 Glioma A group of malignant gliomas that includes the following: glioblastoma; diffuse midline glioma; diffuse hemispheric glioma, H3 G34-mutant; astrocytoma, IDH-mutant, grade 4; and diffuse pediatric-type high grade glioma, H3-wildtype and IDH-wildtype. MONDO:0100342
MONDO:0957764 primary cutaneous peripheral t-cell lymphoma, not otherwise specified NCIT:C201080 MONDO:equivalentTo Primary Cutaneous Peripheral T-Cell Lymphoma, Not Otherwise Specified An exceedingly rare peripheral T-cell lymphoma that arises from the skin and does not meet the criteria that define the other well characterized primary cutaneous peripheral T-cell lymphomas, i.e., it is a diagnosis of exclusion. MONDO:0000607
MONDO:0957765 cribriform comedo-type adenocarcinoma NCIT:C201124 MONDO:equivalentTo Cribriform Comedo-Type Adenocarcinoma An adenocarcinoma characterized by the presence of malignant cribriform glands with central necrotic changes. MONDO:0003575
MONDO:0957766 aleukemic myeloid leukemia NCIT:C201127 MONDO:equivalentTo Aleukemic Myeloid leukemia Myeloid leukemia presenting with leukemic infiltration of tissues and normal or decreased leukocyte count in the peripheral blood. MONDO:0003730
MONDO:0957767 solid pseudopapillary neoplasm NCIT:C201136 MONDO:equivalentTo Solid Pseudopapillary Neoplasm A low-grade malignant neoplasm that arises from the exocrine pancreas. Rare cases arising from ectopic pancreatic tissue in the ovary have also been described. It is characterized by the presence of uniform cells that form solid and pseudopapillary patterns, cystic changes, and hemorrhage. It usually presents as an encapsulated, solitary, and lobulated mass. It occurs predominantly in young women. Complete removal of the tumor is curative in the majority of cases. MONDO:0004992
MONDO:0957768 endemic burkitt lymphoma NCIT:C27122 MONDO:equivalentTo Endemic Burkitt Lymphoma A clinical variant of Burkitt lymphoma that occurs in equatorial Africa. The Epstein-Barr virus has been detected in all patients. It is the most common malignancy of childhood in this area. MONDO:0007243
MONDO:0957769 multicystic mesothelioma NCIT:C3765 MONDO:equivalentTo Multicystic Mesothelioma A mesothelial neoplasm that arises from the peritoneum and rarely the pleura. It is characterized by the presence of multiple cysts lined by flattened or cuboidal mesothelial cells. There is no evidence of significant cytologic atypia or increased mitotic activity. It may reoccur. Rare cases of transformation to malignant mesothelioma have been reported. MONDO:0006856
MONDO:0957770 low grade myofibroblastic sarcoma NCIT:C49024 MONDO:equivalentTo Low Grade Myofibroblastic Sarcoma A low-grade malignant neoplasm arising from the soft tissue and rarely bone. It is characterized by the presence of spindle-shaped myofibroblasts and collagenous stroma formation in a storiform growth pattern. Metastasis is very rare. MONDO:0005164
MONDO:0957771 sclerosing epithelioid fibrosarcoma NCIT:C49027 MONDO:equivalentTo Sclerosing Epithelioid Fibrosarcoma A well-circumscribed malignant fibroblastic neoplasm that usually arises from the soft tissue. It is characterized by the presence of nests of malignant epithelioid fibroblasts and sclerotic collagen stroma formation. MONDO:0005164
MONDO:0957772 meningothelial cell neoplasm NCIT:C6971 MONDO:equivalentTo Meningothelial Cell Neoplasm A neoplasm that arises from meningothelial cells. This category refers to meningiomas. MONDO:0002616
MONDO:0957773 type a lymphomatoid papulosis NCIT:C7197 MONDO:equivalentTo Type A Lymphomatoid Papulosis A variant of lymphomatoid papulosis characterized by the presence of scattered anaplastic large lymphocytes, often resembling Reed-Sternberg cells, admixed with acute and chronic inflammatory cells. MONDO:0020326
MONDO:0957774 type c lymphomatoid papulosis NCIT:C7199 MONDO:equivalentTo Type C Lymphomatoid Papulosis A variant of lymphomatoid papulosis characterized clinically by regressing skin papules, and morphologically by features resembling anaplastic large cell lymphoma. MONDO:0020326
MONDO:0957775 pancreatic intraductal papillary mucinous neoplasm, oncocytic-type NCIT:C95514 MONDO:equivalentTo Pancreatic Intraductal Papillary Mucinous Neoplasm, Oncocytic-Type A pancreatic intraductal papillary mucinous neoplasm characterized by the presence of neoplastic epithelial cells with abundant eosinophilic granular cytoplasm. MONDO:0004286
MONDO:0957850 post-essential thrombocythemia myelofibrosis NCIT:C126806 MONDO:equivalentTo Post-Essential Thrombocythemia Myelofibrosis Myelofibrosis that develops in a patient with history of essential thrombocythemia. MONDO:0005029
MONDO:0957851 recurrent myelofibrosis NCIT:C162424 MONDO:equivalentTo Recurrent Myelofibrosis The reemergence of myelofibrosis after a period of remission.
MONDO:0957852 refractory myelofibrosis NCIT:C162425 MONDO:equivalentTo Refractory Myelofibrosis Myelofibrosis that is resistant to treatment.
MONDO:0957853 bone rosai-dorfman-destombes disease NCIT:C178613 MONDO:equivalentTo Bone Rosai-Dorfman-Destombes Disease Rosai-Dorfman-Destombes disease affecting the bone. MONDO:0019060
MONDO:0957854 stage m0 medulloblastoma NCIT:C186521 MONDO:equivalentTo Stage M0 Medulloblastoma No evidence of subarachnoid or hematogenous metastasis. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0007959
MONDO:0957855 stage m1 medulloblastoma NCIT:C186522 MONDO:equivalentTo Stage M1 Medulloblastoma Microscopic tumor cells are detected in the cerebrospinal fluid. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0007959
MONDO:0957856 stage m2 medulloblastoma NCIT:C186523 MONDO:equivalentTo Stage M2 Medulloblastoma Gross nodular seeding is detected in the cerebellar/cerebral subarachnoid space or in the third or lateral ventricles. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0007959
MONDO:0957857 stage m3 medulloblastoma NCIT:C186524 MONDO:equivalentTo Stage M3 Medulloblastoma Gross nodular seeding is detected in the spinal subarachnoid space. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0007959
MONDO:0957858 stage m4 medulloblastoma NCIT:C186525 MONDO:equivalentTo Stage M4 Medulloblastoma Metastasis outside the cerebrospinal axis. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0007959
MONDO:0957859 stage m0 atypical teratoid/rhabdoid tumor NCIT:C186528 MONDO:equivalentTo Stage M0 Atypical Teratoid/Rhabdoid Tumor No evidence of subarachnoid or hematogenous metastasis. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0020560
MONDO:0957860 stage m1 atypical teratoid/rhabdoid tumor NCIT:C186529 MONDO:equivalentTo Stage M1 Atypical Teratoid/Rhabdoid Tumor Microscopic tumor cells are detected in the cerebrospinal fluid. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0020560
MONDO:0957861 stage m2 atypical teratoid/rhabdoid tumor NCIT:C186530 MONDO:equivalentTo Stage M2 Atypical Teratoid/Rhabdoid Tumor Gross nodular seeding is detected in the cerebellar/cerebral subarachnoid space or in the third or lateral ventricles. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0020560
MONDO:0957862 stage m3 atypical teratoid/rhabdoid tumor NCIT:C186531 MONDO:equivalentTo Stage M3 Atypical Teratoid/Rhabdoid Tumor Gross nodular seeding is detected in the spinal subarachnoid space. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0020560
MONDO:0957863 stage m4 atypical teratoid/rhabdoid tumor NCIT:C186532 MONDO:equivalentTo Stage M4 Atypical Teratoid/Rhabdoid Tumor Metastasis outside the cerebrospinal axis. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0020560
MONDO:0957864 stage m0 pineoblastoma NCIT:C186568 MONDO:equivalentTo Stage M0 Pineoblastoma No evidence of subarachnoid or hematogenous metastasis. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0016722
MONDO:0957865 stage m1 pineoblastoma NCIT:C186569 MONDO:equivalentTo Stage M1 Pineoblastoma Microscopic tumor cells are detected in the cerebrospinal fluid. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0016722
MONDO:0957866 stage m2 pineoblastoma NCIT:C186570 MONDO:equivalentTo Stage M2 Pineoblastoma Gross nodular seeding is detected in the cerebellar/cerebral subarachnoid space or in the third or lateral ventricles. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0016722
MONDO:0957867 stage m3 pineoblastoma NCIT:C186571 MONDO:equivalentTo Stage M3 Pineoblastoma Gross nodular seeding is detected in the spinal subarachnoid space. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0016722
MONDO:0957868 stage m4 pineoblastoma NCIT:C186572 MONDO:equivalentTo Stage M4 Pineoblastoma Metastasis outside the cerebrospinal axis. (Chang CH, Housepian EM, Herbert C. Radiology, 1969; 93(6):1351-9.) MONDO:0016722
MONDO:0958220 colorectal perineurioma NCIT:C96513 MONDO:equivalentTo Colorectal Perineurioma A perineurioma that arises from the colon or rectum. It usually presents as a small sessile polyp. MONDO:0015031
MONDO:0970840 platinum-resistant primary peritoneal carcinoma NCIT:C157622 MONDO:equivalentTo Platinum-Resistant Primary Peritoneal Carcinoma Primary peritoneal carcinoma that progresses between one and six months of completing platinum therapy. MONDO:0015686
MONDO:0970841 platinum-resistant malignant female reproductive system neoplasm NCIT:C169021 MONDO:equivalentTo Platinum-Resistant Malignant Female Reproductive System Neoplasm A malignant female reproductive system neoplasm that progresses between one and six months of completing platinum therapy. MONDO:0001416
MONDO:0970842 extracutaneous merkel cell carcinoma NCIT:C173586 MONDO:equivalentTo Extracutaneous Merkel Cell Carcinoma A rare Merkel cell carcinoma that arises from extracutaneous sites, including the oral cavity, salivary glands, breast, vulva, and vaginal wall. MONDO:0019210
MONDO:0970843 non-neoplastic tonsillar disorder NCIT:C173798 MONDO:equivalentTo Non-Neoplastic Tonsillar Disorder A non-neoplastic disorder that affects the tonsils.
MONDO:0970844 swi/snf complex-deficient sinonasal carcinoma NCIT:C201634 MONDO:equivalentTo SWI/SNF Complex-Deficient Sinonasal Carcinoma A highly aggressive, poorly to undifferentiated carcinoma that arises from the sinonasal tract. It is characterized by loss of one SWI/SNF complex subunit (either SMARCB1 or SMARCA4) and lacks histological features to allow classification into another specific entity. Most patients present with locally advanced disease. MONDO:0056819
MONDO:0970845 tracheal verrucous carcinoma NCIT:C201742 MONDO:equivalentTo Tracheal Verrucous Carcinoma An exophytic, warty, well differentiated, slow growing and non-metastasizing squamous cell carcinoma arising from the trachea. MONDO:0001419
MONDO:0970846 hypopharyngeal verrucous carcinoma NCIT:C201743 MONDO:equivalentTo Hypopharyngeal Verrucous Carcinoma An exophytic, warty, well differentiated, slow growing and non-metastasizing squamous cell carcinoma arising from the hypopharynx. MONDO:0044638
MONDO:0970847 hypopharyngeal papillary squamous cell carcinoma NCIT:C201748 MONDO:equivalentTo Hypopharyngeal Papillary Squamous Cell Carcinoma A variant of squamous cell carcinoma that arises from the hypopharynx. It is characterized by exophytic and papillary growth. The papillae are covered by a malignant stratified squamous epithelium. MONDO:0002979
MONDO:0970848 hypopharyngeal spindle cell squamous carcinoma NCIT:C201749 MONDO:equivalentTo Hypopharyngeal Spindle Cell Squamous Carcinoma A squamous cell carcinoma that arises from the hypopharynx. It is characterized by the presence of a malignant spindle cell cellular component. In some cases, there is a biphasic morphology due to the presence of a well-differentiated squamous cell carcinoma component. The latter is either in situ or invasive squamous cell carcinoma. MONDO:0044638
MONDO:0970849 parotid gland keratocystoma NCIT:C201770 MONDO:equivalentTo Parotid Gland Keratocystoma A benign neoplasm that arises from the parotid gland. It is characterized by the presence of multicystic formations, lined by neoplastic stratified squamous epithelium and containing keratotic lamellae. The neoplastic squamous epithelial cells have bland nuclei and abundant eosinophilic cytoplasm. Focally, solid islands of squamous cells surrounded by collagenous stroma are present. MONDO:0021460
MONDO:0970850 hyalinizing clear cell carcinoma NCIT:C201821 MONDO:equivalentTo Hyalinizing Clear Cell Carcinoma A rare, slow-growing carcinoma characterized by the presence of malignant clear and eosinophilic cells in a hyalinized stroma. It has been described in the salivary glands and lung. Most cases are associated with translocation of EWSR1 and ATF1, resulting in the formation of EWSR1-ATF1 fusion gene. The prognosis is good. MONDO:0004993
MONDO:0970851 tongue verrucous carcinoma NCIT:C201878 MONDO:equivalentTo Tongue Verrucous Carcinoma A well differentiated squamous cell carcinoma arising from the tongue. It is an exophytic, warty, slow growing tumor, usually affecting older males. It is associated with the chronic use of smokeless tobacco. MONDO:0021538
MONDO:0970852 palatine tonsil hamartomatous polyp NCIT:C201900 MONDO:equivalentTo Palatine Tonsil Hamartomatous Polyp A rare hamartomatous polyp that arises from the palatine tonsil.
MONDO:0970853 transformed chronic lymphocytic leukemia to hodgkin lymphoma NCIT:C201960 MONDO:equivalentTo Transformed Chronic Lymphocytic Leukemia to Hodgkin Lymphoma Histologic transformation of chronic lymphocytic leukemia to Hodgkin lymphoma. MONDO:0004948
MONDO:0970854 pineoblastoma molecular subtypes NCIT:C201966 MONDO:equivalentTo Pineoblastoma Molecular Subtypes A term that refers to the classification of pineoblastomas according to their molecular characteristics. MONDO:0016722
MONDO:0970855 spinal cord pilocytic astrocytoma NCIT:C201976 MONDO:equivalentTo Spinal Cord Pilocytic Astrocytoma Pilocytic astrocytoma that arises from the spinal cord. MONDO:0003174
MONDO:0970856 brain low grade glioma NCIT:C201977 MONDO:equivalentTo Brain Low Grade Glioma A low-grade glioma that arises from the brain. MONDO:0021632
MONDO:0970857 clear cell calcifying epithelial odontogenic tumor NCIT:C202057 MONDO:equivalentTo Clear Cell Calcifying Epithelial Odontogenic Tumor A calcifying epithelial odontogenic tumor that contains a variable proportion of clear cells containing diastase-labile PAS-positive material that is consistent with glycogen. MONDO:0022057
MONDO:0970858 cystic/microcystic calcifying epithelial odontogenic tumor NCIT:C202058 MONDO:equivalentTo Cystic/Microcystic Calcifying Epithelial Odontogenic Tumor A calcifying epithelial odontogenic tumor characterized by cystic/microcystic changes. MONDO:0022057
MONDO:0970859 non-calcifying/langerhans cell-rich calcifying epithelial odontogenic tumor NCIT:C202059 MONDO:equivalentTo Non-Calcifying/Langerhans Cell-Rich Calcifying Epithelial Odontogenic Tumor A calcifying epithelial odontogenic tumor that contains significant numbers of Langerhans cells. MONDO:0022057
MONDO:0970860 adenoid ameloblastoma NCIT:C202061 MONDO:equivalentTo Adenoid Ameloblastoma A rare ameloblastoma characterized by the presence of cribriform architecture and the formation of duct-like structures. Dentinoid is usually present. MONDO:0017795
MONDO:0970861 egfr-positive lung non-small cell carcinoma NCIT:C202131 MONDO:equivalentTo EGFR-Positive Lung Non-Small Cell Carcinoma Lung non-small cell carcinoma that is associated with EGFR gene mutation. MONDO:0005233
MONDO:0970862 juvenile trabecular ossifying fibroma NCIT:C202205 MONDO:equivalentTo Juvenile Trabecular Ossifying Fibroma A rare, benign fibro-osseous neoplasm that usually affects the jaws and predominantly arises in children and adolescents. It is characterized by prominent osteoid formation rimmed by osteoblasts in a fibrotic stroma. Patients usually present with painless jaw expansion that is associated with rapid growth and tooth displacement. Amplifications of MDM2 and RASAL1 genes have been detected in some cases. Recurrences have been reported in a minority of cases. MONDO:0002119
MONDO:0970863 psammomatoid ossifying fibroma NCIT:C202209 MONDO:equivalentTo Psammomatoid Ossifying Fibroma A rare, benign fibro-osseous neoplasm that arises from the craniofacial skeleton. It is characterized by the presence of multiple ossicles resembling psammoma bodies in a hypercellular stroma. It usually affects individuals in their second to fourth decades. Recurrences following surgical excision have been reported in a minority of cases. MONDO:0002119
MONDO:0970864 surface osteoma NCIT:C202252 MONDO:equivalentTo Surface Osteoma An osteoma that arises from the surface of the bone. MONDO:0005166
MONDO:0970865 central osteoma NCIT:C202253 MONDO:equivalentTo Central Osteoma An osteoma that arises from the endosteum. MONDO:0005166
MONDO:0970866 rhabdomyosarcoma with tfcp2 rearrangement NCIT:C202263 MONDO:equivalentTo Rhabdomyosarcoma with TFCP2 Rearrangement An aggressive, high-grade rhabdomyosarcoma characterized by TFCP2 rearrangement that results either in TFCP2-FUS or TFCP2-EWSR1 fusion gene formation. It affects young adults and arises from bone and less frequently soft tissue. It predominantly affects the craniofacial bones. Histologically, it usually shows a biphasic pattern with spindle and epithelioid cell areas. It is associated with poor prognosis. MONDO:0005212
MONDO:0970867 non-clear cell renal cell carcinoma NCIT:C202497 MONDO:equivalentTo Non-Clear Cell Renal Cell Carcinoma A group of renal cell carcinomas characterized by the absence of lipid-containing clear adenocarcinoma cells. This category includes the following morphological subtypes: papillary renal cell carcinoma; sarcomatoid renal cell carcinoma; chromophobe renal cell carcinoma; tubulocystic renal cell carcinoma; and eosinophilic solid and cystic renal cell carcinoma. MONDO:0005549
MONDO:0970868 middle ear papilloma NCIT:C202582 MONDO:equivalentTo Middle Ear Papilloma A rare papilloma that arises from the middle ear and resembles a sinonasal papilloma. Approximately half of the patients have concurrent sinonasal or nasopharyngeal papillomas. MONDO:0021078
MONDO:0970869 external auditory canal squamous cell carcinoma NCIT:C202594 MONDO:equivalentTo External Auditory Canal Squamous Cell Carcinoma A squamous cell carcinoma that arises from the keratinizing squamous epithelium that lines the external auditory canal. MONDO:0003501
MONDO:0970870 orbit solitary fibrous tumor NCIT:C202620 MONDO:equivalentTo Orbit Solitary Fibrous Tumor A solitary fibrous tumor that arises from the orbit. Most of these tumors are benign. MONDO:0016238
MONDO:0970871 head and neck soft tissue neoplasm NCIT:C202623 MONDO:equivalentTo Head and Neck Soft Tissue Neoplasm A mesenchymal neoplasm that arises from the soft tissue of the head and neck. MONDO:0006424
MONDO:0970872 proximal colon carcinoma NCIT:C202633 MONDO:equivalentTo Proximal Colon Carcinoma A colon carcinoma that arises from cecum, ascending colon, or hepatic flexure. MONDO:0002032
MONDO:0970873 distal colon carcinoma NCIT:C202634 MONDO:equivalentTo Distal Colon Carcinoma A colon carcinoma that arises from the splenic flexure, descending colon, or sigmoid colon. MONDO:0002032
MONDO:0970874 oral cavity neurofibroma NCIT:C202860 MONDO:equivalentTo Oral Cavity Neurofibroma A neurofibroma that arises from the oral cavity. The tongue is the most frequently affected site. MONDO:0021445
MONDO:0970875 oral cavity schwannoma NCIT:C202876 MONDO:equivalentTo Oral Cavity Schwannoma A schwannoma that arises from the oral cavity. MONDO:0021445
MONDO:0970876 head and neck phosphaturic mesenchymal tumor NCIT:C202879 MONDO:equivalentTo Head and Neck Phosphaturic Mesenchymal Tumor A phosphaturic mesenchymal tumor that arises from the head and neck. It usually affects the paranasal sinuses. The head and neck region is the most frequently involved site for phosphaturic mesenchymal tumors, following the appendicular skeleton. MONDO:0006368
MONDO:0970877 appendicular skeleton phosphaturic mesenchymal tumor NCIT:C202880 MONDO:equivalentTo Appendicular Skeleton Phosphaturic Mesenchymal Tumor A phosphaturic mesenchymal tumor that arises from the appendicular skeleton. The appendicular skeleton is the most frequently involved site for phosphaturic mesenchymal tumors. MONDO:0019060
MONDO:0970878 poorly differentiated synovial sarcoma NCIT:C202883 MONDO:equivalentTo Poorly Differentiated Synovial Sarcoma A synovial sarcoma characterized by the presence of poorly differentiated morphological features and absence of spindle cells. MONDO:0010434
MONDO:0970879 primary cd30-positive t-cell lymphoproliferative disorder NCIT:C202952 MONDO:equivalentTo Primary CD30-Positive T-Cell Lymphoproliferative Disorder A spectrum of T-cell lymphoproliferative disorders that arise from skin, subcutaneous tissue, and head and neck mucosal sites. They are characterized by the presence of CD30-positive neoplastic lymphocytes. Cells that resemble the hallmark cells of anaplastic large cell lymphoma are often seen. MONDO:0005169
MONDO:0970880 head and neck hematopoietic and lymphoid cell neoplasm NCIT:C202954 MONDO:equivalentTo Head and Neck Hematopoietic and Lymphoid Cell Neoplasm A neoplasm of hematopoietic and lymphoid cell origin that affects the head and neck region. MONDO:0005586
MONDO:0970881 head and neck germ cell tumor NCIT:C202977 MONDO:equivalentTo Head and Neck Germ Cell Tumor An exceptionally rare benign or malignant germ cell tumor that arises from the head and neck region. It usually affects the sinonasal tract and nasopharynx. MONDO:0018201
MONDO:0970882 cecum neuroendocrine tumor NCIT:C203386 MONDO:equivalentTo Cecum Neuroendocrine Tumor A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the cecum. MONDO:0005694
MONDO:0970883 ascending colon neuroendocrine tumor NCIT:C203387 MONDO:equivalentTo Ascending Colon Neuroendocrine Tumor A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the ascending colon. MONDO:0015067
MONDO:0970884 descending colon neuroendocrine tumor NCIT:C203388 MONDO:equivalentTo Descending Colon Neuroendocrine Tumor A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the descending colon. MONDO:0015067
MONDO:0970885 sigmoid colon neuroendocrine tumor NCIT:C203389 MONDO:equivalentTo Sigmoid Colon Neuroendocrine Tumor A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the sigmoid colon. MONDO:0015067
MONDO:0970886 transverse colon neuroendocrine tumor NCIT:C203390 MONDO:equivalentTo Transverse Colon Neuroendocrine Tumor A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the transverse colon. MONDO:0015067
MONDO:0970887 histiocytic disorder NCIT:C203422 MONDO:equivalentTo Histiocytic Disorder A group of non-neoplastic and neoplastic disorders characterized by the proliferation of histiocytes. This category includes hemophagocytic lymphohistiocytosis and histiocytic and dendritic cell neoplasms.
MONDO:0970888 myelodysplastic chronic myelomonocytic leukemia NCIT:C203443 MONDO:equivalentTo Myelodysplastic Chronic Myelomonocytic Leukemia Chronic myelomonocytic leukemia characterized by the absence of a markedly elevated white blood cell count in the peripheral blood. MONDO:0020311
MONDO:0970889 myeloproliferative chronic myelomonocytic leukemia NCIT:C203444 MONDO:equivalentTo Myeloproliferative Chronic Myelomonocytic Leukemia Chronic myelomonocytic leukemia characterized by the presence of a markedly elevated white blood cell count in the peripheral blood. MONDO:0020311
MONDO:0970890 t acute lymphoblastic leukemia with recurrent genetic abnormalities NCIT:C203469 MONDO:equivalentTo T Acute Lymphoblastic Leukemia with Recurrent Genetic Abnormalities T-acute lymphoblastic leukemias characterized by the presence of recurring cytogenetic and/or molecular abnormalities. MONDO:0004963
MONDO:0970891 esophageal and gastroesophageal junction carcinoma NCIT:C203673 MONDO:equivalentTo Esophageal and Gastroesophageal Junction Carcinoma A carcinoma that arises from the esophagus or gastroesophageal junction. MONDO:0006181
MONDO:0970892 low grade mucinous carcinoma peritonei NCIT:C203946 MONDO:equivalentTo Low Grade Mucinous Carcinoma Peritonei A low-grade mucinous adenocarcinoma that has spread to the peritoneum. MONDO:0017048
MONDO:0970893 high grade mucinous carcinoma peritonei NCIT:C203948 MONDO:equivalentTo High Grade Mucinous Carcinoma Peritonei A high-grade mucinous adenocarcinoma that has spread to the peritoneum. MONDO:0017048
MONDO:0970894 merkel cell polyoma virus-positive merkel cell carcinoma NCIT:C204383 MONDO:equivalentTo Merkel Cell Polyoma Virus-Positive Merkel Cell Carcinoma A Merkel cell carcinoma that is associated with Merkel cell polyoma virus infection. MONDO:0019210
MONDO:0970895 merkel cell polyoma virus-negative merkel cell carcinoma NCIT:C204385 MONDO:equivalentTo Merkel Cell Polyoma Virus-Negative Merkel Cell Carcinoma A Merkel cell carcinoma that is not associated with Merkel cell polyoma virus infection. MONDO:0019210
MONDO:0970896 lentiginous melanocytic nevus NCIT:C204482 MONDO:equivalentTo Lentiginous Melanocytic Nevus A nevus characterized by an intraepidermal proliferation of nested melanocytes along the basal epidermis. MONDO:0044794
MONDO:0970897 mitf pathway-activated melanocytic tumor NCIT:C204739 MONDO:equivalentTo MITF Pathway-Activated Melanocytic Tumor A cutaneous neoplasm associated with MITF gene rearrangement and either ACTIN-MITF translocation or MITF-CREM translocation. It is composed of large cells with clear cytoplasm that exhibit melanocytic differentiation and proliferate in the dermis. It presents as a single non-pigmented cutaneous nodule. MONDO:0021583
MONDO:0970898 dermal spitz nevus NCIT:C204789 MONDO:equivalentTo Dermal Spitz Nevus A Spitz nevus characterized by the presence of an intradermal melanocytic component without junctional melanocytic activity. MONDO:0006813
MONDO:0970899 spitz tumor NCIT:C204790 MONDO:equivalentTo Spitz Tumor A term that refers to a group of melanocytic neoplasms that are composed of epithelioid and/or spindle cells and extend from the epidermis into the reticular dermis, often in a wedge-shaped configuration. They are usually associated with oncogenic mutations that activate the MAP-kinase pathway. This category includes Spitz nevus, Spitz melanocytoma, and Spitz melanoma. MONDO:0021583
MONDO:0970900 melanoma in intermittently sun-exposed skin NCIT:C204840 MONDO:equivalentTo Melanoma in Intermittently Sun-Exposed Skin A melanoma that arises from the skin in the absence of severe actinic keratosis. It can arise from a pre-existing nevus or de novo. MONDO:0005012
MONDO:0970901 low-csd melanoma, superficial spreading melanoma subtype NCIT:C204843 MONDO:equivalentTo Low-CSD Melanoma, Superficial Spreading Melanoma Subtype A cutaneous melanoma that develops on sun exposed sites with low cumulative sun damage (CSD). It is characterized by a prominent junctional and intraepidermal component with intraepidermal proliferation of individual atypical melanocytes and formation of nests of atypical melanocytes along the dermal-epidermal junction. The dermal component is composed of atypical melanocytes that fail to mature. The atypical melanocytes have large nuclei, prominent nucleoli, and eosinophilic or lightly pigmented cytoplasm. It is the most common melanoma subtype in the Western world. MONDO:0020638
MONDO:0970902 melanoma in chronically sun-exposed skin NCIT:C204864 MONDO:equivalentTo Melanoma in Chronically Sun-Exposed Skin A melanoma that arises from a chronically sun-exposed skin area. It is associated with severe actinic keratosis. MONDO:0005012
MONDO:0970903 mucosal nevus NCIT:C204907 MONDO:equivalentTo Mucosal Nevus A nevus that arises from a mucosal site. MONDO:0005073
MONDO:0970904 dendritic blue nevus NCIT:C204910 MONDO:equivalentTo Dendritic Blue Nevus A blue nevus characterized by the proliferation of dendritic melanocytes in sclerotic stromal collagen. MONDO:0006680
MONDO:0970905 intermediate congenital melanocytic nevus NCIT:C204976 MONDO:equivalentTo Intermediate Congenital Melanocytic Nevus A congenital melanocytic nevus measuring 15-200 mm. It is typically amenable to surgical resection. MONDO:0044792
MONDO:0970906 conjunctival melanocytic neoplasm NCIT:C204977 MONDO:equivalentTo Conjunctival Melanocytic Neoplasm A melanocytic neoplasm that arises from the conjunctiva. This category includes conjunctival nevus, conjunctival melanocytic intraepithelial lesions, and conjunctival melanoma. MONDO:0021143
MONDO:0970907 uveal melanocytic neoplasm NCIT:C205057 MONDO:equivalentTo Uveal Melanocytic Neoplasm A melanocytic neoplasm that arises from the iris, ciliary body, and choroid. This category includes nevus and its subtype melanocytoma, and melanoma. MONDO:0021143
MONDO:0970908 nodular melanoma NCIT:C205125 MONDO:equivalentTo Nodular Melanoma A melanoma that arises from the skin and mucosal sites. It is characterized by a vertical growth phase and lacks a significant radial growth phase. It may or may not arise from a pre-existing nevus. Morphologically, it is characterized by the presence of cohesive aggregates of neoplastic melanocytes in the dermis that often exhibit an epithelioid appearance. The overlying epidermis is often involved. MONDO:0005105
MONDO:0970909 dermal melanoma NCIT:C205129 MONDO:equivalentTo Dermal Melanoma A melanoma that is confined to the dermis and subcutaneous tissue without involvement of the epidermis. MONDO:0005012
MONDO:0970910 metastatic melanoma in the lymph nodes NCIT:C205131 MONDO:equivalentTo Metastatic Melanoma in the Lymph Nodes A melanoma that has spread to the lymph nodes from a cutaneous or extracutaneous primary site. MONDO:0005191
MONDO:0970911 platinum-sensitive endometrial carcinoma NCIT:C205187 MONDO:equivalentTo Platinum-Sensitive Endometrial Carcinoma An endometrial carcinoma that has a documented response to platinum-based chemotherapy. MONDO:0002447
MONDO:0970912 early stage cervical carcinoma NCIT:C205287 MONDO:equivalentTo Early Stage Cervical Carcinoma A stage term that refers to cervical carcinoma stages IA, IB, and IIA. MONDO:0005131
MONDO:0970913 early stage clear cell renal cell carcinoma NCIT:C205289 MONDO:equivalentTo Early Stage Clear Cell Renal Cell Carcinoma A stage term referring to clear cell renal cell carcinoma that presents as a small tumor and is confined to the kidney. MONDO:0005005
MONDO:0970914 early stage colorectal carcinoma NCIT:C205290 MONDO:equivalentTo Early Stage Colorectal Carcinoma A stage term referring to colorectal carcinoma that is limited to the colon/rectum or local lymph nodes, without metastasis to distant anatomic sites. MONDO:0024331
MONDO:0970915 early stage endometrial carcinoma NCIT:C205295 MONDO:equivalentTo Early Stage Endometrial Carcinoma A stage term referring to endometrial carcinoma that is confined to the uterus. MONDO:0002447
MONDO:0970916 early stage esophageal carcinoma NCIT:C205298 MONDO:equivalentTo Early Stage Esophageal Carcinoma A stage term referring to esophageal carcinoma that is confined to the esophageal mucosa or submucosa. MONDO:0019086
MONDO:0970917 early stage hepatocellular carcinoma NCIT:C205301 MONDO:equivalentTo Early Stage Hepatocellular Carcinoma A stage term referring to hepatocellular carcinoma that presents as a single tumor with the largest diameter measuring 2 cm or less. The liver function is well-preserved and there is no vascular invasion or metastasis. (Barcelona Liver Cancer Classification). MONDO:0007256
MONDO:0970918 early stage lung non-small cell carcinoma NCIT:C205303 MONDO:equivalentTo Early Stage Lung Non-Small Cell Carcinoma A stage term that refers to lung non-small cell carcinoma stages I, II, and IIIA. MONDO:0005233
MONDO:0970919 early stage malignant skin neoplasm NCIT:C205307 MONDO:equivalentTo Early Stage Malignant Skin Neoplasm A stage term that refers to a malignant tumor confined to a limited area of the skin without lymph node or distant metastases. MONDO:0002898
MONDO:0970920 primary cutaneous nut adnexal carcinoma NCIT:C205357 MONDO:equivalentTo Primary Cutaneous NUT Adnexal Carcinoma A very rare carcinoma that arises from adnexal structures in the skin. It is characterized by mutations and rearrangement of the NUT gene. It presents as a papular or nodular lesion and has been described in the hand, shoulder, trunk, and lower limb. Histologically, there is a proliferation of malignant epithelial cells in the dermis and/or subcutaneous tissue. The tumor cells display round nuclei with prominent single nucleoli. Features include the presence of small round ducts and foci of abrupt keratinization. MONDO:0005563
MONDO:0970921 trichogerminoma NCIT:C205371 MONDO:equivalentTo Trichogerminoma A rare subtype of trichoblastoma characterized by the presence of lobules of basaloid cells. The lobules are separated by fibrous stroma. It is associated with the expression of recurrent FOXK1/GRHL and GPS2/GRHL gene fusions. MONDO:0020593
MONDO:0970922 apocrine cystadenoma NCIT:C205459 MONDO:equivalentTo Apocrine Cystadenoma A rare, benign cystic neoplasm that arises from the apocrine gland. It is characterized by the presence of papillary-like epithelial projections and more complex architectural patterns compared to apocrine hidrocystoma. MONDO:0002804
MONDO:0970923 eccrine poroma NCIT:C205462 MONDO:equivalentTo Eccrine Poroma A poroma with eccrine differentiation. MONDO:0006738
MONDO:0970924 hidroacanthoma simplex NCIT:C205475 MONDO:equivalentTo Hidroacanthoma Simplex A poroma characterized by the presence of aggregates of basaloid cells confined to the epidermis. MONDO:0006738
MONDO:0970925 solid cystic hidradenoma NCIT:C205539 MONDO:equivalentTo Solid Cystic Hidradenoma A hidradenoma characterized by the presence of solid lobular neoplastic cell proliferations and cystic spaces filled with homogeneous eosinophilic material. MONDO:0002805
MONDO:0970926 sialoblastoma NCIT:C35837 MONDO:equivalentTo Sialoblastoma A rare, malignant primitive neoplasm that occurs in the salivary glands. Most tumors arise from the parotid gland, followed by the submandibular gland, and rarely the minor salivary glands. It is usually diagnosed during the neonatal period and presents with painless face swelling. MONDO:0004669
MONDO:0970927 cribriform trichoblastoma NCIT:C43322 MONDO:equivalentTo Cribriform Trichoblastoma A trichoblastoma characterized by the presence of neoplastic epithelial cells forming cribriform patterns. MONDO:0020593
MONDO:0970928 lung neuroendocrine carcinoma NCIT:C45569 MONDO:equivalentTo Lung Neuroendocrine Carcinoma A high grade malignant neoplasm that arises from the lung and is characterized by the presence of malignant neuroendocrine cells. This category includes small cell lung carcinoma, large cell lung neuroendocrine carcinoma, and combined lung carcinoma. MONDO:0005454
MONDO:0970929 branchioma NCIT:C53595 MONDO:equivalentTo Branchioma A rare, benign, well-circumscribed or encapsulated tumor that arises from the neck and occurs in adults. It is characterized by the presence of spindle cells, epithelial islands, and adipose tissue. MONDO:0021455
MONDO:0970930 ear carcinoma NCIT:C54262 MONDO:equivalentTo Ear Carcinoma A carcinoma that arises from the ear. Representative examples include ceruminous adenocarcinoma and squamous cell carcinoma of the external ear and adenocarcinoma of the middle ear. MONDO:0003277
MONDO:0970931 intracranial melanoma NCIT:C5442 MONDO:equivalentTo Intracranial Melanoma A melanoma that arises from the leptomeninges within the cranium. MONDO:0021632
MONDO:0970932 meckel diverticulum neuroendocrine tumor g1 NCIT:C6424 MONDO:equivalentTo Meckel Diverticulum Neuroendocrine Tumor G1 A well differentiated, low grade neuroendocrine neoplasm that arises in a Meckel diverticulum. MONDO:0021533
MONDO:0970933 duodenal neuroendocrine tumor g1 NCIT:C6425 MONDO:equivalentTo Duodenal Neuroendocrine Tumor G1 A well differentiated, low grade neuroendocrine neoplasm that arises from the duodenum. The mitotic count is less than 2 per 10 HPF and/or the Ki67 index is equal to or less than 2 percent. MONDO:0015063
MONDO:0970934 intracranial myeloid sarcoma NCIT:C7008 MONDO:equivalentTo Intracranial Myeloid Sarcoma A myeloid sarcoma that affects the meninges or the cerebral hemispheres. MONDO:0001657
MONDO:0970935 hamartomatous polyp NCIT:C8372 MONDO:equivalentTo Hamartomatous Polyp A polyp characterized by an overgrowth of mature cells and tissues that normally occur in the affected area.
MONDO:0970936 well differentiated fibrosarcoma NCIT:C9025 MONDO:equivalentTo Well Differentiated Fibrosarcoma A well-differentiated malignant neoplasm arising from the deep soft tissues. It is characterized by the presence of spindle-shaped fibroblasts and collagenous stroma formation in a herringbone growth pattern. MONDO:0005164
MONDO:0970937 poorly differentiated angiosarcoma NCIT:C9031 MONDO:equivalentTo Poorly Differentiated Angiosarcoma An angiosarcoma characterized by the presence of significant cytologic atypia, necrosis and high mitotic activity. MONDO:0016982
MONDO:0970938 well differentiated leiomyosarcoma NCIT:C9389 MONDO:equivalentTo Well Differentiated Leiomyosarcoma Grade I malignant smooth muscle neoplasm. It is characterized by a proliferation of neoplastic spindle cells. MONDO:0005058
MONDO:0970939 poorly differentiated fibrosarcoma NCIT:C9404 MONDO:equivalentTo Poorly Differentiated Fibrosarcoma A usually aggressive malignant neoplasm arising from the deep soft tissue. It is characterized by the presence of poorly-differentiated spindle-shaped fibroblasts, collagenous stroma formation and increased mitotic activity. MONDO:0005164
MONDO:0970940 low grade sarcoma NCIT:C9417 MONDO:equivalentTo Low Grade Sarcoma A sarcoma with the morphologic features of a low-grade tumor and presence of cellular differentiation. MONDO:0005089
MONDO:0970941 high grade sarcoma NCIT:C9418 MONDO:equivalentTo High Grade Sarcoma A sarcoma with the morphologic features of a high-grade tumor and lack of cellular differentiation. MONDO:0005089
MONDO:0975792 childhood glioblastoma NCIT:C5136 MONDO:equivalentTo Childhood Glioblastoma A glioblastoma that occurs during childhood. MONDO:0002505
MONDO:0975793 childhood anaplastic oligodendroglioma NCIT:C5447 MONDO:equivalentTo Childhood Anaplastic Oligodendroglioma An anaplastic oligodendroglioma that arises from the central nervous system and occurs during childhood. MONDO:1010030